Page last updated: 2024-08-23

bezafibrate and Barth Syndrome

bezafibrate has been researched along with Barth Syndrome in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (50.00)24.3611
2020's1 (50.00)2.80

Authors

AuthorsStudies
Chin, MT; Heyman, A; Hornby, B; Jefferies, J; Pu, WT; Takemoto, C; Thompson, R; Vernon, HJ; Wang, S1
Glukhov, AV; Huang, Y; James, JF; Javadov, S; Jefferies, JL; Khuchua, Z; Moore, V; Phoon, CK; Powers, C; Ren, M; Schafer, C; Strauss, AW; Vaz, FM1

Reviews

1 review(s) available for bezafibrate and Barth Syndrome

ArticleYear
Current and future treatment approaches for Barth syndrome.
    Journal of inherited metabolic disease, 2022, Volume: 45, Issue:1

    Topics: Acyltransferases; Animals; Barth Syndrome; Bezafibrate; Cardiolipins; Cardiomyopathies; Clinical Trials as Topic; Enzyme Therapy; Genetic Therapy; Humans; Mice; Muscular Diseases; Neutropenia; Oligopeptides; Peroxisome Proliferator-Activated Receptors

2022

Other Studies

1 other study(ies) available for bezafibrate and Barth Syndrome

ArticleYear
The PPAR pan-agonist bezafibrate ameliorates cardiomyopathy in a mouse model of Barth syndrome.
    Orphanet journal of rare diseases, 2017, 03-09, Volume: 12, Issue:1

    Topics: Animals; Barth Syndrome; Bezafibrate; Blotting, Western; Cardiolipins; Cardiomyopathies; Disease Models, Animal; Echocardiography; Female; Male; Mice; Peroxisome Proliferator-Activated Receptors; Polymerase Chain Reaction

2017