Page last updated: 2024-08-23

bezafibrate and Akinetic-Rigid Variant of Huntington Disease

bezafibrate has been researched along with Akinetic-Rigid Variant of Huntington Disease in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's2 (66.67)24.3611
2020's1 (33.33)2.80

Authors

AuthorsStudies
Brondani, M; de Medeiros, MP; Hoffmann, CIH; Leipnitz, G; Ribeiro, RT; Roginski, AC; Seminotti, B; Wajner, M1
Beal, MF; Calingasan, NY; Chandra, A; Johri, A; Sharma, A; Shurubor, Y; White, JM; Yang, XW1
Beal, MF; Calingasan, NY; Chandra, A; Hennessey, TM; Johri, A; Sharma, A; Wille, E; Yang, L1

Other Studies

3 other study(ies) available for bezafibrate and Akinetic-Rigid Variant of Huntington Disease

ArticleYear
Mitochondrial dysfunction, oxidative stress, ER stress and mitochondria-ER crosstalk alterations in a chemical rat model of Huntington's disease: Potential benefits of bezafibrate.
    Toxicology letters, 2023, May-15, Volume: 381

    Topics: Animals; Bezafibrate; Glutathione; Huntington Disease; Mitochondria; Models, Chemical; Nitro Compounds; Oxidative Stress; Propionates; Rats; Rats, Wistar; Superoxide Dismutase; Synaptophysin

2023
Enhanced mitochondrial biogenesis ameliorates disease phenotype in a full-length mouse model of Huntington's disease.
    Human molecular genetics, 2016, 06-01, Volume: 25, Issue:11

    Topics: Animals; Bezafibrate; Corpus Striatum; Disease Models, Animal; Humans; Huntingtin Protein; Huntington Disease; Mice; Mice, Transgenic; Mitochondria; Organelle Biogenesis; Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha; PPAR delta; PPAR gamma; Signal Transduction

2016
Pharmacologic activation of mitochondrial biogenesis exerts widespread beneficial effects in a transgenic mouse model of Huntington's disease.
    Human molecular genetics, 2012, Mar-01, Volume: 21, Issue:5

    Topics: Adipose Tissue, Brown; Animals; Bezafibrate; Corpus Striatum; Diet; Disease Models, Animal; Gliosis; Huntington Disease; Mice; Mice, Transgenic; Mitochondria; Mitochondria, Muscle; Muscle Fibers, Skeletal; Neurons; Neuroprotective Agents; Oxidative Stress; Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha; Phenotype; PPAR gamma; Signal Transduction; Survival Rate; Trans-Activators; Transcription Factors; Transcriptional Activation; Vacuoles

2012