Page last updated: 2024-10-23

baclofen and Congenital Stiff-Man Syndrome

baclofen has been researched along with Congenital Stiff-Man Syndrome in 28 studies

Research Excerpts

ExcerptRelevanceReference
"Intrathecal baclofen (ITB) is used for unresponsiveness to other treatment for patients with stiff-person syndrome (SPS)."7.72Intrathecal baclofen for stiff-person syndrome: life-threatening intermittent catheter leakage. ( Bardutzky, J; Meinck, HM; Schwab, S; Tronnier, V, 2003)
"Intrathecal baclofen (ITB) is used for unresponsiveness to other treatment for patients with stiff-person syndrome (SPS)."3.72Intrathecal baclofen for stiff-person syndrome: life-threatening intermittent catheter leakage. ( Bardutzky, J; Meinck, HM; Schwab, S; Tronnier, V, 2003)
" They also required higher doses and more rapid dosage increases."2.68Intrathecal baclofen therapy for stiff-man syndrome and progressive encephalomyelopathy with rigidity and myoclonus. ( Dressnandt, J; Marquardt, G; Mauch, E; Meinck, HM; Müller-Schwefe, G; Rieke, K; Schumm, F; Stayer, C; Tronnier, V, 1997)
"A 49-year-old male with type 1 diabetes presented with a 6-month history of muscle rigidity and spasms of his upper and lower extremities."2.46Stiff-person syndrome: a case report and review of the literature. ( Chedebeau, F; Egwuonwu, S, 2010)
"This is the youngest case of sporadic Stiffman syndrome reported in literature."2.40Sporadic Stiffman syndrome in a young girl. ( Dharnidharka, VR; Gajendragadkar, AR; Udani, SV; Udani, VP, 1997)
"However, unusual symptoms such as myoclonus can occur in few cases and together with the rarity of the condition, the prevalence of misdiagnosis is high."1.51Stiff limb syndrome with lower limb myoclonus: A case report. ( Chen, J; Feng, YY; Li, LL; Zhang, CG, 2019)
"It is characterized by muscle spasms triggered by startle, voluntary movement, or tactile or emotional stimuli, occurring predominantly in the axial musculature."1.37Stiff person syndrome and pregnancy. ( Blaskiewicz, R; Goldkamp, J; Myles, T, 2011)

Research

Studies (28)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's10 (35.71)18.2507
2000's8 (28.57)29.6817
2010's7 (25.00)24.3611
2020's3 (10.71)2.80

Authors

AuthorsStudies
Dalakas, MC1
Zhang, CG1
Li, LL1
Feng, YY1
Chen, J1
Oh, DC1
Rakesh, N1
LaGrant, B1
Sein, M1
Cai, Q1
Wu, C1
Xu, W1
Liang, Y1
Liao, S1
Abbatemarco, JR1
Willis, MA1
Wilson, RG1
Nagel, SJ1
Machado, AG1
Bethoux, FA1
Derksen, A1
Stettner, M1
Stöcker, W1
Seitz, RJ2
Tohid, H1
Saigal, R1
Goyal, L1
Yadav, R1
Agrawal, A1
Mital, P1
Patel, B1
Ho, BL1
Shih, PY1
Egwuonwu, S1
Chedebeau, F1
Goldkamp, J1
Blaskiewicz, R1
Myles, T1
Bardutzky, J1
Tronnier, V3
Schwab, S2
Meinck, HM4
Vogels, RL1
van Orshoven, NP1
de Koning-Tijssen, MA1
Wouda, EJ1
Weatherby, SJM1
Woolner, P1
Clarke, CE1
Hattan, E1
Angle, MR1
Chalk, C1
Vernino, S1
McEvoy, K1
Silbert, PL1
Matsumoto, JY1
McManis, PG1
Stolp-Smith, KA1
Elliott, BA1
McEvoy, KM1
Rieke, K2
Wirtz, CR1
Flügel, D1
Ford, B1
Fahn, S1
Ricker, K1
Hülser, PJ1
Schmid, E1
Peiffer, J1
Solimena, M1
Penn, RD1
Mangieri, EA1
Blank, B1
Kiwit, JC1
Benecke, R1
Diedrich, U1
Udani, VP1
Dharnidharka, VR1
Gajendragadkar, AR1
Udani, SV1
Stayer, C1
Dressnandt, J1
Mauch, E1
Marquardt, G1
Müller-Schwefe, G1
Schumm, F1
Gouider-Khouja, N1
Mekaouar, A1
Larnaout, A1
Miladi, N1
Ben Khelifa, F1
Hentati, F1
Calvet, D1
Touzé, E1
Delegue, P1
Bertherat, J1
Zuber, M1
Clifton, ER1
Subramony, SH1

Reviews

5 reviews available for baclofen and Congenital Stiff-Man Syndrome

ArticleYear
Therapies in Stiff-Person Syndrome: Advances and Future Prospects Based on Disease Pathophysiology.
    Neurology(R) neuroimmunology & neuroinflammation, 2023, Volume: 10, Issue:3

    Topics: Aged; Autoantibodies; Autoimmunity; Baclofen; Child; Female; Humans; Spasm; Stiff-Person Syndrome

2023
Anti-glutamic acid decarboxylase antibody positive neurological syndromes.
    Neurosciences (Riyadh, Saudi Arabia), 2016, Volume: 21, Issue:3

    Topics: Autoantibodies; Baclofen; Cerebellar Ataxia; Diazepam; Epilepsy; GABA Modulators; GABA-B Receptor Ag

2016
Stiff-person syndrome: a case report and review of the literature.
    Journal of the National Medical Association, 2010, Volume: 102, Issue:12

    Topics: Anemia, Pernicious; Anti-Anxiety Agents; Baclofen; Diabetes Mellitus, Type 1; Diagnosis, Differentia

2010
Stiff-person syndrome with anti-glutamic acid decarboxylase autoantibodies: complete remission of symptoms after intrathecal baclofen administration.
    Journal of neurology, 1995, Volume: 242, Issue:10

    Topics: Autoantibodies; Baclofen; Diabetes Mellitus, Type 1; Female; Glutamate Decarboxylase; Humans; Inject

1995
Sporadic Stiffman syndrome in a young girl.
    Pediatric neurology, 1997, Volume: 17, Issue:1

    Topics: Baclofen; Diagnosis, Differential; Diazepam; Drug Therapy, Combination; Female; GABA Agonists; GABA

1997

Trials

2 trials available for baclofen and Congenital Stiff-Man Syndrome

ArticleYear
Intrathecal baclofen therapy in stiff-man syndrome: a double-blind, placebo-controlled trial.
    Neurology, 1995, Volume: 45, Issue:10

    Topics: Analysis of Variance; Baclofen; Double-Blind Method; Electromyography; Humans; Injections, Spinal; R

1995
Intrathecal baclofen therapy for stiff-man syndrome and progressive encephalomyelopathy with rigidity and myoclonus.
    Neurology, 1997, Volume: 49, Issue:6

    Topics: Adult; Aged; Baclofen; Central Nervous System Diseases; Cohort Studies; Disease Progression; Female;

1997

Other Studies

21 other studies available for baclofen and Congenital Stiff-Man Syndrome

ArticleYear
Stiff limb syndrome with lower limb myoclonus: A case report.
    Medicine, 2019, Volume: 98, Issue:49

    Topics: Baclofen; Botulinum Toxins, Type A; Diagnosis, Differential; Electromyography; Humans; Immunoglobuli

2019
Advanced Progression of Scoliosis After Intrathecal Baclofen in an Adult With Stiff Person Syndrome: A Case Report.
    A&A practice, 2020, Volume: 14, Issue:6

    Topics: Adult; Baclofen; Child; Humans; Scoliosis; Stiff-Person Syndrome

2020
Stiff-person syndrome coexisting with critical illness polyneuropathy: A case report.
    Medicine, 2020, Dec-11, Volume: 99, Issue:50

    Topics: Baclofen; Clonazepam; Diagnosis, Differential; Electromyography; Humans; Immunoglobulins, Intravenou

2020
Case Series: Intrathecal Baclofen Therapy in Stiff-Person Syndrome.
    Neuromodulation : journal of the International Neuromodulation Society, 2018, Volume: 21, Issue:7

    Topics: Adult; Aged; Baclofen; Female; Follow-Up Studies; Humans; Injections, Spinal; Male; Middle Aged; Mus

2018
Antiglycine receptor-related stiff limb syndrome in a patient with chronic lymphocytic leukaemia.
    BMJ case reports, 2013, May-20, Volume: 2013

    Topics: Aged; Autoantibodies; Baclofen; Clonazepam; Electromyography; GABA Agents; Humans; Leukemia, Lymphoc

2013
Stiff Person Syndrome.
    The Journal of the Association of Physicians of India, 2015, Volume: 63, Issue:8

    Topics: Adult; Antibodies; Anticonvulsants; Autoimmunity; Baclofen; Clonazepam; Electromyography; Glutamate

2015
Successful intrathecal baclofen therapy for seronegative stiff-person syndrome: a case report.
    Acta neurologica Taiwanica, 2008, Volume: 17, Issue:3

    Topics: Adult; Autoantibodies; Baclofen; Glutamate Decarboxylase; Humans; Injections, Spinal; Male; Stiff-Pe

2008
Stiff person syndrome and pregnancy.
    Obstetrics and gynecology, 2011, Volume: 118, Issue:2 Pt 2

    Topics: Adult; Amines; Baclofen; Cesarean Section; Cyclohexanecarboxylic Acids; Diazepam; Female; Gabapentin

2011
Intrathecal baclofen for stiff-person syndrome: life-threatening intermittent catheter leakage.
    Neurology, 2003, Jun-24, Volume: 60, Issue:12

    Topics: Acute Disease; Adult; Baclofen; Catheterization; Equipment Failure; Humans; Hypertension; Infusion P

2003
['Stiff-person'-syndrome].
    Nederlands tijdschrift voor geneeskunde, 2003, Jun-21, Volume: 147, Issue:25

    Topics: Adrenal Cortex Hormones; Autoantibodies; Baclofen; Diazepam; Electromyography; Female; Glutamate Dec

2003
Pregnancy in stiff-limb syndrome.
    Movement disorders : official journal of the Movement Disorder Society, 2004, Volume: 19, Issue:7

    Topics: Adult; Anti-Inflammatory Agents; Anticonvulsants; Baclofen; Diazepam; Drug Therapy, Combination; Ext

2004
Unexpected benefit of propofol in stiff-person syndrome.
    Neurology, 2008, Apr-29, Volume: 70, Issue:18

    Topics: Aged; Autoantibodies; Baclofen; Diazepam; Drug Resistance; Female; GABA Agonists; GABA-A Receptor Ag

2008
Propofol for stiff-person syndrome: learning new tricks from an old dog.
    Neurology, 2008, Apr-29, Volume: 70, Issue:18

    Topics: Aged; Autoantibodies; Baclofen; Diazepam; Drug Resistance; Female; GABA Agonists; GABA-A Receptor Ag

2008
Intrathecal baclofen treatment for stiff-man syndrome: pump failure may be fatal.
    Neurology, 1994, Volume: 44, Issue:11

    Topics: Aged; Baclofen; Equipment Failure; Female; Humans; Infusion Pumps; Stiff-Person Syndrome

1994
Intrathecal baclofen.
    Neurology, 1994, Volume: 44, Issue:7

    Topics: Baclofen; Double-Blind Method; Female; Humans; Injections, Spinal; Middle Aged; Stiff-Person Syndrom

1994
Stiff man syndrome: clinical and laboratory findings in eight patients.
    Journal of neurology, 1994, Volume: 241, Issue:3

    Topics: Adult; Aged; Autoantibodies; Autoimmune Diseases; Baclofen; Benzodiazepines; Blood Proteins; Central

1994
Stiff-man syndrome treated with intrathecal baclofen.
    Neurology, 1993, Volume: 43, Issue:11

    Topics: Adult; Baclofen; Female; Humans; Injections, Spinal; Male; Middle Aged; Stiff-Person Syndrome

1993
[Rhythmic circulatory dysregulation in stiff man syndrome].
    Der Nervenarzt, 1996, Volume: 67, Issue:12

    Topics: Autonomic Nervous System; Baclofen; Blood Pressure; Cardiovascular System; Female; GABA Agonists; ga

1996
Progressive encephalomyelitis with rigidity presenting as a stiff-person syndrome.
    Parkinsonism & related disorders, 2002, Volume: 8, Issue:4

    Topics: Anti-Inflammatory Agents; Baclofen; Diagnosis, Differential; Diazepam; Drug Therapy, Combination; El

2002
[Stiff limb syndrome associated with Hashimoto's encephalopathy: improvement after corticotherapy].
    Revue neurologique, 2002, Volume: 158, Issue:5 Pt 1

    Topics: Aged; Antibody Specificity; Anticonvulsants; Antithyroid Agents; Autoantibodies; Autoimmune Diseases

2002
Stiff-man syndrome.
    Southern medical journal, 1992, Volume: 85, Issue:7

    Topics: Adult; Baclofen; Diazepam; Female; Humans; Male; Middle Aged; Stiff-Person Syndrome

1992