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aspartic acid and Ataxias, Hereditary

aspartic acid has been researched along with Ataxias, Hereditary in 6 studies

Research

Studies (6)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's3 (50.00)18.2507
2000's3 (50.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Baracca, A; Casalena, GA; DiMauro, S; Lenaz, G; Sgarbi, G; Solaini, G1
Cai, Y; Gao, Y; Guo, X; Li, D; Liang, Y; Lim, CC; Ma, L; Yin, H1
Blaschek, A; Ebinger, F; Goebel, HH; Harting, I; Haupt, M; Rating, D; Sartor, K; Seitz, A; Wolf, NI1
Kanazawa, I1
Kish, SJ; Mastrogiacomo, F1
Bartolozzi, C; Bianchi, MC; Frontali, M; Mascalchi, M; Plasmati, R; Salvi, F; Tassinari, CA; Tessa, C; Tosetti, M; Valzania, F1

Reviews

1 review(s) available for aspartic acid and Ataxias, Hereditary

ArticleYear
[Neurochemical aspects of spinocerebellar degeneration].
    Rinsho shinkeigaku = Clinical neurology, 1993, Volume: 33, Issue:12

    Topics: Aspartic Acid; Cerebellum; gamma-Aminobutyric Acid; Glutamates; Homocysteine; Humans; Neurotransmitter Agents; Spinocerebellar Degenerations

1993

Trials

1 trial(s) available for aspartic acid and Ataxias, Hereditary

ArticleYear
Proton magnetic resonance spectroscopy in an Italian family with spinocerebellar ataxia type 1.
    Annals of neurology, 1998, Volume: 43, Issue:2

    Topics: Adult; Aspartic Acid; Brain Chemistry; Cerebellum; Choline; Chromosome Mapping; Creatine; DNA; Female; Genetic Linkage; Heterozygote; Humans; Inositol; Italy; Magnetic Resonance Imaging; Magnetic Resonance Spectroscopy; Male; Middle Aged; Neurologic Examination; Pedigree; Pons; Spinocerebellar Degenerations; Statistics, Nonparametric

1998

Other Studies

4 other study(ies) available for aspartic acid and Ataxias, Hereditary

ArticleYear
Human NARP mitochondrial mutation metabolism corrected with alpha-ketoglutarate/aspartate: a potential new therapy.
    Archives of neurology, 2009, Volume: 66, Issue:8

    Topics: Adenosine Triphosphate; Anti-Infective Agents, Local; Aspartic Acid; C-Reactive Protein; Cell Line; Cell Survival; DNA, Mitochondrial; Energy Metabolism; Gramicidin; Humans; Ketoglutaric Acids; Leigh Disease; Mitochondria; Mitochondrial Proton-Translocating ATPases; Mutation; Nerve Tissue Proteins; Oligomycins; Oxidative Phosphorylation; Retinitis Pigmentosa; Spinocerebellar Degenerations

2009
Combined MR spectroscopic imaging and diffusion tensor MRI visualizes corticospinal tract degeneration in amyotrophic lateral sclerosis.
    Journal of neurology, 2004, Volume: 251, Issue:10

    Topics: Adult; Amyotrophic Lateral Sclerosis; Aspartic Acid; Brain Mapping; Case-Control Studies; Creatine; Diffusion Magnetic Resonance Imaging; Female; Humans; Magnetic Resonance Spectroscopy; Male; Middle Aged; Pyramidal Tracts; Spinocerebellar Degenerations

2004
T2-hyperintense cerebellar cortex in Marinesco-Sjögren syndrome.
    Neurology, 2004, Dec-28, Volume: 63, Issue:12

    Topics: Aspartic Acid; Cerebellar Cortex; Cerebral Cortex; Child; Child, Preschool; Consanguinity; Diagnosis, Differential; Female; Humans; Infant; Inositol; Magnetic Resonance Imaging; Magnetic Resonance Spectroscopy; Male; Neuroaxonal Dystrophies; Spinocerebellar Degenerations

2004
Cerebellar alpha-ketoglutarate dehydrogenase activity is reduced in spinocerebellar ataxia type 1.
    Annals of neurology, 1994, Volume: 35, Issue:5

    Topics: Adult; Aspartic Acid; Cerebellum; Cerebral Cortex; Energy Metabolism; Glutamates; Glutamic Acid; Humans; Ketoglutarate Dehydrogenase Complex; Neurotransmitter Agents; Reference Values; Spinocerebellar Degenerations

1994