aspartic acid has been researched along with Adult Neuronal Ceroid Lipofuscinosis in 6 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 2 (33.33) | 18.2507 |
2000's | 4 (66.67) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Autti, T; Häkkinen, AM; Liewendahl, K; Nikkinen, P; Puranen, J; Raininko, R; Santavuori, P; Suominen, P; Vanhanen, SL; Vuori, K | 1 |
Autti, T; Bathen, TF; Gribbestad, IS; Häkkinen, AM; Haltia, MJ; Paetau, A; Polvikoski, T; Puranen, J; Santavuori, P; Sitter, B; Sonnewald, U; Tyynelä, J | 1 |
Cooper, JD; Griffin, JL; Mitchison, HM; Mortishire-Smith, RJ; Pearce, DA; Pears, MR | 1 |
Ballon, D; Crystal, RG; Dyke, JP; Hackett, NR; Heier, L; Hollmann, C; Kaplitt, MG; Kekatpure, MV; Kosofsky, B; Mao, X; Shungu, D; Sondhi, D; Souweidane, MM; Worgall, S | 1 |
Brockmann, K; Christen, HJ; Frahm, J; Hanefeld, F; Pouwels, PJ | 1 |
Grodd, W; Klose, U; Nägele, T; Schwab, A; Seeger, U; Seitz, D | 1 |
6 other study(ies) available for aspartic acid and Adult Neuronal Ceroid Lipofuscinosis
Article | Year |
---|---|
Neuroradiological findings (MRS, MRI, SPECT) in infantile neuronal ceroid-lipofuscinosis (infantile CLN1) at different stages of the disease.
Topics: Aspartic Acid; Brain; Child; Child, Preschool; Choline; Creatinine; Humans; Infant; Infant, Newborn; Magnetic Resonance Imaging; Magnetic Resonance Spectroscopy; Neuronal Ceroid-Lipofuscinoses; Oximes; Radiopharmaceuticals; Tomography, Emission-Computed, Single-Photon | 2004 |
High-resolution magic angle spinning and 1H magnetic resonance spectroscopy reveal significantly altered neuronal metabolite profiles in CLN1 but not in CLN3.
Topics: Adolescent; Adult; Analysis of Variance; Aspartic Acid; Brain; Brain Chemistry; Child; Child, Preschool; Choline; Creatine; Female; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Humans; Inositol; Magnetic Resonance Spectroscopy; Male; Membrane Glycoproteins; Membrane Proteins; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Neurons; Thiolester Hydrolases | 2004 |
High resolution 1H NMR-based metabolomics indicates a neurotransmitter cycling deficit in cerebral tissue from a mouse model of Batten disease.
Topics: Aging; Animals; Aspartic Acid; Brain; Cerebellum; Cerebral Cortex; Creatine; Disease Models, Animal; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Humans; Inositol; Magnetic Resonance Spectroscopy; Membrane Glycoproteins; Mice; Mice, Knockout; Models, Biological; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Neurotransmitter Agents; Phenotype; Spectrophotometry; Time Factors | 2005 |
Neurological deterioration in late infantile neuronal ceroid lipofuscinosis.
Topics: Adolescent; Age Factors; Age of Onset; Aminopeptidases; Aspartic Acid; Cerebral Cortex; Child; Child, Preschool; Dipeptidyl-Peptidases and Tripeptidyl-Peptidases; Disease Progression; DNA Mutational Analysis; Endopeptidases; Female; Humans; Magnetic Resonance Imaging; Male; Mutation, Missense; Neurologic Examination; Neuronal Ceroid-Lipofuscinoses; Nuclear Magnetic Resonance, Biomolecular; Ophthalmoscopy; Organ Size; Point Mutation; Retina; Serine Proteases; Severity of Illness Index; Siblings; Tripeptidyl-Peptidase 1 | 2007 |
Localized proton magnetic resonance spectroscopy of cerebral metabolic disturbances in children with neuronal ceroid lipofuscinosis.
Topics: Aspartic Acid; Brain; Brain Diseases, Metabolic; Brain Mapping; Child; Child, Preschool; Choline; Creatine; Energy Metabolism; Female; Humans; Infant; Inositol; Lactic Acid; Magnetic Resonance Imaging; Magnetic Resonance Spectroscopy; Male; Neurologic Examination; Neuronal Ceroid-Lipofuscinoses | 1996 |
MR imaging and localized proton MR spectroscopy in late infantile neuronal ceroid lipofuscinosis.
Topics: Aspartic Acid; Brain; Brain Diseases; Case-Control Studies; Cerebellum; Cerebral Ventricles; Child; Child, Preschool; Choline; Creatine; Diagnosis, Differential; Female; Glutamic Acid; Glutamine; Humans; Inositol; Lactates; Magnetic Resonance Imaging; Magnetic Resonance Spectroscopy; Male; Mitochondrial Encephalomyopathies; Neuronal Ceroid-Lipofuscinoses; Peroxisomal Disorders; Thalamus | 1998 |