Compounds > arginine

arginine and Porphyria, Acute Intermittent

arginine has been researched along with Porphyria, Acute Intermittent in 34 studies

Research

Studies (34)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's6 (17.65)18.2507
2000's18 (52.94)29.6817
2010's8 (23.53)24.3611
2020's2 (5.88)2.80

Authors

AuthorsStudies
Beykirch, MK; Bronisch, O; Haverkamp, T; Petrides, PE; Stauch, T1
Aarsand, AK; Aguilera, P; Brunet, M; Deulofeu, R; García-Villoria, J; Gómez-Gómez, À; Pozo, OJ; Sandberg, S; To-Figueras, J; Wijngaard, R1
Beykirch, MK; Klein, M; Loehr, C; Molitor, B; Obermeier, Z; Petrides, PE; Schuhmann, E; Torkler, H1
Deguchi, K; Ikeda, K; Kamada, M; Kokudo, Y; Kume, K; Masaki, T; Takata, T; Touge, T1
Barman-Aksözen, J; Huber, LC; Minder, E; Senn, JD1
Albertyn, CH; Bryer, A; Corrigall, A; Heckmann, JM; Meissner, P; Sonderup, M1
Hergüner, Ö; Mungan, NÖ; Nazoglu, S; Öktem, M; Turgut, M; Yildizdas, D; Yilmaz, BS1
Dosi, R; Joshi, H; Patell, R; Shah, P; Tripathi, R1
Andersson, DE; Floderus, Y; Harper, P; Sardh, E1
Cappellini, MD; Rocchi, E; Ventura, P1
Brosche, C; Doss, MO; Koszka, C; Stauch, T; Stölzel, U; Teubner, A1
Marsden, JT; Rees, DC1
Badminton, MN; Barth, JH; Cox, TM; Rees, DC; Sarkany, R; Stein, PE; Stewart, MF1
Andersson, C; Bäckström, T; Nilsson, A1
Deacon, AC; Peters, TJ1
Karpova, IV; Luchinina, IuA; Luk'ianenko, AV; Pivnik, AV; Pustovoĭt, IaS; Surin, VL1
Hasui, Y; Ikeda, M; Tanabe, H1
Hift, RJ; Meissner, PN1
Chen, WJ; Fang, CC; Lai, TI; Lien, WC; Liu, YP; Wang, HP1
Badminton, MN; Deybach, JC1
Bianketti, J; Gregor, A; Lipniacka, A; Szlendak, U1
Feder, ZM; Ignashina, EV; Karpova, IV; Kravchenko, SK; Kremenetskaia, AM; Kurtser, MA; Mironova, TS; Murashko, LE; Petrova, VI; Pustovoĭt, IaS; Pustovoĭt, LA; Shmakov, RG; Shtabnitskiĭ, AM; Sokolova, MIu1
Borie, MJ; Chauvet, MA; Corcia, P; Diot, E; Maillot, F; Zannad, N1
Bharathi, KC; Mamatha, P; Muthane, UB; Vengamma, B1
Baudry, P; Callebert, J; Deybach, JC; Nordmann, Y; Puy, H; Touitou, Y1
Mustajoki, P; Nordmann, Y1
Elder, GH; Llewellyn, DH; Whatley, S1
Deybach, JC; Doss, MO; Frank, M; Gross, U; Jacob, K; Nordmann, Y; Sassa, S1
Daimon, M; Hirata, A; Kato, T; Kitagawa, M; Manaka, H; Morita, Y; Sasaki, H; Susa, S1
Daimon, M; Igarashi, M; Kameda, W; Kato, T; Susa, S1
Hoffmann, F; Lindberg, RL; Meyer, UA; Schuurmans, MM1
Elder, GH; Hift, RJ1
Badminton, MN; Elder, GH1

Reviews

4 review(s) available for arginine and Porphyria, Acute Intermittent

ArticleYear
[CME: Acute Intermittent Porphyria: When to Think of It? What Must be Checked? How to Treat?]
    Praxis, 2018, Volume: 107, Issue:3

    Topics: Arginine; Combined Modality Therapy; Diagnosis, Differential; Female; Genetic Predisposition to Disease; Heme; Hemin; Humans; Interdisciplinary Communication; Intersectoral Collaboration; Middle Aged; Porphobilinogen; Porphyria, Acute Intermittent; Prognosis; Recurrence; Risk Factors

2018
[Porphyria].
    Ryoikibetsu shokogun shirizu, 2003, Issue:40

    Topics: 5-Aminolevulinate Synthetase; Analgesics, Opioid; Antipsychotic Agents; Arginine; Benzodiazepines; Ferrochelatase; Haloperidol; Heme; Humans; Hydroxymethylbilane Synthase; Olanzapine; Pirenzepine; Plasma Exchange; Porphyria, Acute Intermittent; Prognosis

2003
Treatment of acute porphyria.
    Hospital medicine (London, England : 1998), 2001, Volume: 62, Issue:7

    Topics: Adolescent; Adult; Analgesics, Opioid; Arginine; Clinical Trials as Topic; Dietary Carbohydrates; Female; Heme; Humans; Male; Porphobilinogen; Porphyria, Acute Intermittent; Pregnancy; Pregnancy Complications; Treatment Outcome

2001
Management of acute and cutaneous porphyrias.
    International journal of clinical practice, 2002, Volume: 56, Issue:4

    Topics: Arginine; beta Carotene; Chloroquine; Estrogens; Ethanol; Heme; Humans; Phlebotomy; Porphyria Cutanea Tarda; Porphyria, Acute Intermittent; Porphyrias; Sunlight

2002

Trials

2 trial(s) available for arginine and Porphyria, Acute Intermittent

ArticleYear
Acute porphyrias: a German monocentric study of the biochemical, molecular genetic, and clinical data of 62 families.
    Annals of hematology, 2019, Volume: 98, Issue:12

    Topics: Adult; Anxiety; Arginine; Depression; Family; Female; Germany; Heme; Hospitalization; Humans; Male; Porphyria, Acute Intermittent; Prospective Studies; Quality of Life; Surveys and Questionnaires

2019
Plasma porphobilinogen as a sensitive biomarker to monitor the clinical and therapeutic course of acute intermittent porphyria attacks.
    European journal of internal medicine, 2009, Volume: 20, Issue:2

    Topics: Acute Disease; Adult; Aminolevulinic Acid; Arginine; Biomarkers; Chromatography, Ion Exchange; Drug Monitoring; Female; Glucose; Heme; Humans; Male; Porphobilinogen; Porphyria, Acute Intermittent; Sensitivity and Specificity

2009

Other Studies

28 other study(ies) available for arginine and Porphyria, Acute Intermittent

ArticleYear
Dysregulation of homocysteine homeostasis in acute intermittent porphyria patients receiving heme arginate or givosiran.
    Journal of inherited metabolic disease, 2021, Volume: 44, Issue:4

    Topics: Acetylgalactosamine; Adult; Arginine; Cystathionine beta-Synthase; Female; Folic Acid; Heme; Homeostasis; Homocysteine; Homocystinuria; Humans; Hydroxymethylbilane Synthase; Hyperhomocysteinemia; Male; Methionine; Middle Aged; Porphyria, Acute Intermittent; Pyridoxal Phosphate; Pyrrolidines; Young Adult

2021
Severe homocysteinemia in two givosiran-treated porphyria patients: is free heme deficiency the culprit?
    Annals of hematology, 2021, Volume: 100, Issue:7

    Topics: 5-Aminolevulinate Synthetase; Acetylgalactosamine; Adult; Arginine; Colitis; Colon, Sigmoid; Controlled Clinical Trials as Topic; Drug Hypersensitivity; Female; Fibrosis; Heme; Hepatocytes; High-Throughput Nucleotide Sequencing; Homocysteine; Humans; Hydroxymethylbilane Synthase; Hyperhomocysteinemia; Male; Models, Biological; Pancreatitis; Porphyria, Acute Intermittent; Pyrrolidines

2021
Acute Intermittent Porphyria Presenting with Posterior Reversible Encephalopathy Syndrome, Accompanied by Prolonged Vasoconstriction.
    Internal medicine (Tokyo, Japan), 2017, Volume: 56, Issue:6

    Topics: Arginine; Female; Heme; Humans; Magnetic Resonance Angiography; Magnetic Resonance Imaging; Porphyria, Acute Intermittent; Posterior Leukoencephalopathy Syndrome; Young Adult

2017
Acute intermittent porphyria presenting as progressive muscular atrophy in a young black man.
    South African medical journal = Suid-Afrikaanse tydskrif vir geneeskunde, 2014, Volume: 104, Issue:4

    Topics: Arginine; Heme; Humans; Hydroxymethylbilane Synthase; Male; Muscular Atrophy, Spinal; Porphyria, Acute Intermittent; Young Adult

2014
A 17-year-old girl with chronic intermittent abdominal pain. Acute intermittent porphyria.
    Pediatric annals, 2015, Volume: 44, Issue:4

    Topics: Abdominal Pain; Adolescent; Arginine; Cholelithiasis; Chronic Disease; Diagnosis, Differential; Female; Heme; Humans; Porphyria, Acute Intermittent; Porphyrins; Tomography, X-Ray Computed

2015
Challenges in the successful management of a case of acute intermittent porphyria in India.
    Tropical doctor, 2016, Volume: 46, Issue:3

    Topics: Abdominal Pain; Administration, Intravenous; Adolescent; Arginine; Heme; Humans; India; Male; Porphobilinogen; Porphyria, Acute Intermittent; Seizures; Treatment Outcome

2016
The acute porphyrias: a diagnostic and therapeutic challenge in internal and emergency medicine.
    Internal and emergency medicine, 2009, Volume: 4, Issue:4

    Topics: Arginine; Diagnostic Errors; Emergency Medicine; Heme; Humans; Internal Medicine; Porphyria, Acute Intermittent

2009
Safe and probably safe drugs in acute hepatic porphyria.
    Cellular and molecular biology (Noisy-le-Grand, France), 2009, Jul-01, Volume: 55, Issue:2

    Topics: 5-Aminolevulinate Synthetase; Arginine; Drug-Related Side Effects and Adverse Reactions; Heme; Humans; Liver Transplantation; Porphyria, Acute Intermittent

2009
A retrospective analysis of outcome of pregnancy in patients with acute porphyria.
    Journal of inherited metabolic disease, 2010, Volume: 33, Issue:5

    Topics: Abortion, Spontaneous; Adolescent; Adult; Arginine; Child; Female; Heme; Humans; Live Birth; London; Middle Aged; Porphyria, Acute Intermittent; Pregnancy; Pregnancy Complications; Retrospective Studies; Surveys and Questionnaires; Time Factors; Treatment Outcome; Young Adult

2010
Acute intermittent porphyria: fatal complications of treatment.
    Clinical medicine (London, England), 2012, Volume: 12, Issue:3

    Topics: Abdominal Pain; Adolescent; Analgesics; Arginine; Disease Management; Fatal Outcome; Female; Hallucinations; Heme; Humans; Hyponatremia; Monitoring, Physiologic; Porphobilinogen; Porphyria, Acute Intermittent; Water-Electrolyte Balance

2012
["Acute intermittent porphyria" diagnosis. An odyssey in diagnosis].
    MMW Fortschritte der Medizin, 2002, May-23, Volume: 144, Issue:21

    Topics: Abdominal Pain; Arginine; Colic; Diagnosis, Differential; Heme; Humans; Porphyria, Acute Intermittent

2002
Atypical attack of acute intermittent porphyria--paresis but no abdominal pain.
    Journal of internal medicine, 2002, Volume: 252, Issue:3

    Topics: Abdominal Pain; Adult; Arginine; Disease Progression; Estradiol; Female; Heme; Humans; Hysterectomy; Middle Aged; Ovariectomy; Paresis; Periodicity; Porphyria, Acute Intermittent; Progesterone; Recurrence

2002
International air travel: a risk factor for attacks in acute intermittent porphyria.
    Clinica chimica acta; international journal of clinical chemistry, 2003, Volume: 335, Issue:1-2

    Topics: Abdominal Pain; Adult; Aircraft; Arginine; Female; Humans; Male; Porphyria, Acute Intermittent; Travel

2003
[Clinical manifestations of porphyrin metabolism disorders].
    Terapevticheskii arkhiv, 2003, Volume: 75, Issue:7

    Topics: Acute Disease; Adolescent; Adult; Arginine; Chronic Disease; Female; Heme; Humans; Inosine Diphosphate; Middle Aged; Octreotide; Plasmapheresis; Porphyria, Acute Intermittent; Porphyria, Erythropoietic; Porphyrias; Porphyrins

2003
An analysis of 112 acute porphyric attacks in Cape Town, South Africa: Evidence that acute intermittent porphyria and variegate porphyria differ in susceptibility and severity.
    Medicine, 2005, Volume: 84, Issue:1

    Topics: Abdominal Pain; Acute Disease; Adult; Age Factors; Arginine; Epidemiologic Methods; Female; Heme; Humans; Hypertension; Male; Porphyria, Acute Intermittent; Porphyria, Variegate; Precipitating Factors; Psychotic Disorders; Remission, Spontaneous; Sex Factors; South Africa; Tachycardia

2005
ED presentation of acute porphyria.
    The American journal of emergency medicine, 2005, Volume: 23, Issue:2

    Topics: Abdominal Pain; Adolescent; Adult; Age of Onset; Analgesia; Arginine; Diagnostic Errors; Emergency Medicine; Emergency Service, Hospital; Female; Glucose; Heme; Humans; Hyponatremia; Infusions, Intravenous; Male; Middle Aged; Porphyria, Acute Intermittent; Retrospective Studies; Seizures; Taiwan; Treatment Outcome

2005
Treatment of an acute attack of porphyria during pregnancy.
    European journal of neurology, 2006, Volume: 13, Issue:6

    Topics: Abortion, Induced; Arginine; Female; Heme; Humans; Porphyria, Acute Intermittent; Pregnancy; Pregnancy Complications, Infectious

2006
[Acute intermittent porphyria and oral contraception. Case report].
    Ginekologia polska, 2006, Volume: 77, Issue:3

    Topics: Adult; Arginine; Contraceptives, Oral, Synthetic; Desogestrel; Female; Glucose; Heme; Humans; Porphyria, Acute Intermittent; Saline Solution, Hypertonic; Treatment Outcome

2006
[Management of pregnancy in women with acute porphyria. Case reports].
    Terapevticheskii arkhiv, 2007, Volume: 79, Issue:8

    Topics: Adult; Arginine; Female; Follow-Up Studies; Heme; Humans; Infant, Newborn; Male; Porphobilinogen; Porphyria, Acute Intermittent; Porphyrins; Pregnancy; Pregnancy Complications; Pregnancy Outcome; Risk Factors

2007
[Favorable outcome of acute porphyric neuropathy after treatment with heme arginate].
    Revue neurologique, 2007, Volume: 163, Issue:11

    Topics: Adult; Arginine; Electrodiagnosis; Electrophysiology; Female; Heme; Humans; Laparoscopy; Motor Neuron Disease; Nervous System Diseases; Neural Conduction; Ovarian Cysts; Peripheral Nerves; Porphyria, Acute Intermittent; Postoperative Complications; Quadriplegia

2007
Porphyric neuropathy: prevention of progression using haeme-arginate.
    Journal of internal medicine, 1993, Volume: 234, Issue:6

    Topics: Adult; Arginine; Glucose Solution, Hypertonic; Heme; Humans; Male; Peripheral Nervous System Diseases; Porphyria, Acute Intermittent

1993
Decreased nocturnal plasma melatonin levels in patients with recurrent acute intermittent porphyria attacks.
    Life sciences, 1993, Volume: 53, Issue:8

    Topics: Adult; Arginine; Circadian Rhythm; Female; Heme; Humans; Melatonin; Porphyria, Acute Intermittent; Recurrence; Tryptophan

1993
Early administration of heme arginate for acute porphyric attacks.
    Archives of internal medicine, 1993, Sep-13, Volume: 153, Issue:17

    Topics: Adult; Aged; Arginine; Female; Heme; Humans; Length of Stay; Male; Middle Aged; Porphyria, Acute Intermittent; Time Factors; Treatment Outcome

1993
Acute intermittent porphyria caused by an arginine to histidine substitution (R26H) in the cofactor-binding cleft of porphobilinogen deaminase.
    Human molecular genetics, 1993, Volume: 2, Issue:8

    Topics: Adult; Amino Acid Sequence; Arginine; Base Sequence; Binding Sites; Conserved Sequence; DNA Primers; Erythrocytes; Female; Histidine; Humans; Hydroxymethylbilane Synthase; Male; Molecular Sequence Data; Pedigree; Point Mutation; Polymerase Chain Reaction; Porphyria, Acute Intermittent

1993
5-Aminolevulinic acid dehydratase deficiency porphyria: a twenty-year clinical and biochemical follow-up.
    Clinical chemistry, 1998, Volume: 44, Issue:9

    Topics: Adolescent; Aminolevulinic Acid; Arginine; Biomarkers; Erythrocytes; Follow-Up Studies; Glucose; Heme; Humans; Male; Mutation; Porphobilinogen Synthase; Porphyria, Acute Intermittent; Porphyrins

1998
Acute intermittent porphyria with central pontine myelinolysis and cortical laminar necrosis.
    Neuroradiology, 1999, Volume: 41, Issue:11

    Topics: Adult; Arginine; Brain; Female; Fluid Therapy; Heme; Humans; Hyponatremia; Myelinolysis, Central Pontine; Necrosis; Porphyria, Acute Intermittent; Saline Solution, Hypertonic; Seizures; Vasospasm, Intracranial

1999
Administration of heme arginate, but not hematin, caused anaphylactic shock.
    The American journal of medicine, 2001, Feb-15, Volume: 110, Issue:3

    Topics: Adult; Anaphylaxis; Arginine; Female; Heme; Hemin; Humans; Porphyria, Acute Intermittent

2001
Zinc mesoporphyrin represses induced hepatic 5-aminolevulinic acid synthase and reduces heme oxygenase activity in a mouse model of acute hepatic porphyria.
    Hepatology (Baltimore, Md.), 2001, Volume: 33, Issue:5

    Topics: 5-Aminolevulinate Synthetase; Acute Disease; Aminolevulinic Acid; Animals; Arginine; Cytosol; Drug Combinations; Female; Heme; Heme Oxygenase (Decyclizing); Injections, Intraperitoneal; Liver; Metalloporphyrins; Mice; Mice, Inbred C57BL; Mitochondria, Liver; Phenobarbital; Porphyria, Acute Intermittent; Porphyrias, Hepatic; Reference Values; RNA, Messenger

2001