arginine and Cystic Fibrosis of Pancreas

arginine has been researched along with Cystic Fibrosis of Pancreas in 77 studies

Research

Studies (77)

Timeframe	Studies, this research(%)	All Research%
pre-1990	33 (42.86)	18.7374
1990's	16 (20.78)	18.2507
2000's	12 (15.58)	29.6817
2010's	14 (18.18)	24.3611
2020's	2 (2.60)	2.80

Authors

Authors	Studies
D'Alessio, DA; De Leon, DD; Doliba, A; Eiel, JN; Flatt, AJ; Gallagher, K; Gallop, R; Hadjiliadis, D; Kelly, A; Nyirjesy, SC; Peleckis, AJ; Rickels, MR; Rubenstein, RC; Sheikh, S; Stefanovski, D; Tami, A	1
Beigverdi, R; Emaneini, M; Halimi, S; Jabalameli, F; Siroosi, M	1
Ahmadi, S; Bartlett, C; Bear, CE; Gonska, T; Ip, W; Jiang, J; Laselva, O; Lew, A; Moraes, TJ; Ouyang, H; Wellhauser, L; Wu, YS; Xia, S	1
De Biase, RV; Gnessi, L; Isidori, AM; Lenzi, A; Lubrano, C; Pascucci, C; Quattrucci, S; Savi, D	1
Ahmadi, S; Bear, CE; Di Paola, M; Khursigara, CM; Lam, JS; Park, AJ; Roach, EJ; Struder-Kypke, M; Wu, YS	1
Cardona, ST; Kumar, B; Sorensen, JL	1
Ahmadi, S; Bear, CE; Bozoky, Z; Di Paola, M; Du, K; Forman-Kay, J; Gonska, T; Ip, W; Lew, A; Li, M; Lloyd-Kuzik, A; Wu, YS; Xia, S	1
Com, G; Deutz, NE; Engelen, MP; Luiking, YC	1
Grasemann, H; Pencharz, PB	1
Elborn, JS; Ferguson, TE; Hamilton, RA; Harvey, BJ; Hendrick, SM; Martin, SL; Reihill, JA; Saint-Criq, V; Stutts, MJ; Walker, B	1
Baraldi, E; Da Dalt, L; Giordano, G; Gucciardi, A; Lucca, F; Naturale, M; Perilongo, G; Pirillo, P; Ros, M	1
Elnazir, B; Greally, P; Kerley, CP; Kilbride, E	1
Bazer, FW; Carey Satterfield, M; Davis, TA; Kim, SW; Li, P; Marc Rhoads, J; Smith, SB; Spencer, TE; Wu, G; Yin, Y	1
Bassas, L; Casals, T; Domingo, C; Farré, A; Giménez, J; Masvidal, L; Ramos, MD	1
Bienvenu, T; Blayau, M; Cabet-Bey, F; Claustres, M; Costa, C; Feldmann, D; Georges, Md; Girodon, E; Guittard, C; Iron, A; Lalau, G; Leclerc, J; Mittre, H; Paulet, D; René, C	1
Al-Saleh, S; Amin, R; Belik, J; Grasemann, H; Mehl, A; Pencharz, P; Rafii, M; Ratjen, F; Scott, JA; Shehnaz, D	1
Grasemann, H; Ratjen, F	1
Grasemann, H; Ratjen, F; Tullis, E	1
Grasemann, C; Grasemann, H; Kurtz, F; Ratjen, F; Tietze-Schillings, G; Vester, U	1
Donnelly, D; Everard, ML	1
Grasemann, H; Kurtz, F; Ratjen, F	1
Comeau, AM; Dorkin, HL; O'Sullivan, BP; Parad, R; Zwerdling, RG	1
Aznarez, I; Blencowe, BJ; Rommens, JM; Tsui, LC; Zielenski, J	1
Maarsingh, H; Meurs, H; Pera, T	1
Applegarth, DA; Bridges, MA; Davidson, AG; Johannson, J; Wong, LT	1
Berry, HK; Hsieh, MC	1
Nadler, HL; Rao, GJ; Walsh, MM	1
Culler, FL; Meacham, LR	1
Bocian, RC; Chao, AC; Dong, YJ; Gardner, P; Hsu, YP; Kouyama, K; Moss, RB	1
Adjiman, M; Beldjord, C; Bienvenu, T; Kaplan, JC	1
Chang, XB; Hanrahan, JW; Hou, YX; Riordan, JR; Rommens, JM; Tabcharani, JA; Tsui, LC	1
Dapena, J; Estivill, X; Ferrer, J; Giménez, J; Llevadot, R; Nunes, V; Ortigosa, L; Peña, L; Pérez-Frias, J	1
Adkins, S; Gan, KN; La Du, BN; Mody, M	1
Carson, MR; Teem, JL; Welsh, MJ	1
Harris, A; Hill, DF; Tebbutt, SJ	1
Bartholomew, DW; Fujita, J; Hojo, S; Miyawaki, H; Obayashi, Y; Takahara, J	1
Cotten, JF; Welsh, MJ	1
Koch, C; Lanng, S; Laursen, EM; Müller, J; Rasmussen, MH; Skakkebaek, NE	1
Eto, Y; Iizuka, S; Katsube, A; Morokawa, N; Muraji, T; Tanano, A; Yoshimura, K	1
Gärtig, SS; Grasemann, H; Konietzko, N; Ratjen, F; Teschler, H; Wiesemann, HG	1
Jorissen, M; Lefevere, L; Lindberg, S; Willems, T	1
Barbarotto, GM; Desai, TK; Feldman, GL; Manji, S; Monaghan, KG; Snow, K	1
Dreshaj, IA; Ferkol, T; Haxhiu, MA; Kelley, TJ; Martin, RJ; Mhanna, MJ; van Heeckeren, AM	1
Callahan, JW; Leung, A	1
Butterworth, J; Duncan, JJ	1
Nadler, NL; Rao, GJ; Shapira, E; Wessel, HU	1
Blau, K; Dann, LG	2
Blessing-Moore, J; Bossen, A; Cavalli-Sforza, LL; Parsons, M; Romeo, G	1
Dooley, RR; Lippe, BM; Sperling, MA	1
Calvo Manuel, E; Espinos Pérez, D; Rubio Pérez, P; Sánchez Sánchez, ML; Vila Canella, T	2
Nadler, HL; Platt, MW; Rao, GJ	1
Goldsmith, GH; Ratnoff, OD; Saito, H; Stern, RC	1
Buchanan, KD; Redmond, AO; Trimble, ER	1
Dietzsch, HJ; Gottschalk, B; Heyne, K; Leupoid, W; Wunderlich, P	1
Nadler, HL; Rao, GJ	2
Busch-Petersen, D; Güloz, HU; Hein, J	1
Solomons, C	1
Marchi, AG; Nordio, S	1
Hodson, ME; Pitt, TL; Taylor, RF	1
Dallapiccola, B; Murru, S; Novelli, G; Sangiuolo, F	1
Diem, P; Klein, DJ; Levitt, MD; Moran, A; Robertson, RP	1
Coburn, LA; Coburn, MD; Solomons, CC	1
Nadler, HL; Posner, LA; Rao, GJ	1
Girard, J; Ronen, G; Rutishauser, M; Stahl, M	1
Cotton, EK; Dubois, R; Solomons, CC	2
Gács, G; Hervei, C; Kerpel-Fronius, E	1
Lieberman, J	1
Girard, J; Nars, PW; Rutishauser, M; Stahl, M; Zuppinger, K	1
Agus, SG; Di Sant'Agnese, PA; Kattwinkel, J; Laster, L; Taussig, LM	1
Cotton, E; Hathaway, W; Solomons, C	1
Graham, GG; Solomons, CC	1
Mangos, JA; McSherry, NR	1
Gururangan, S; Horner, M; Marina, NM; Rodman, JH	1

Reviews

4 review(s) available for arginine and Cystic Fibrosis of Pancreas

Article	Year
Arginine metabolism and nutrition in growth, health and disease. Amino acids, 2009, Volume: 37, Issue:1 Topics: Animals; Arginine; Cystic Fibrosis; Fetal Development; Humans; Metabolic Syndrome; Muscle, Skeletal; Neoplasms; Nutritional Requirements; Obesity; Reproduction; Wounds and Injuries	2009
Nitric oxide and L-arginine deficiency in cystic fibrosis. Current pharmaceutical design, 2012, Volume: 18, Issue:5 Topics: Animals; Arginine; Cystic Fibrosis; Humans; Nitric Oxide; Nitric Oxide Synthase	2012
Arginase and pulmonary diseases. Naunyn-Schmiedeberg's archives of pharmacology, 2008, Volume: 378, Issue:2 Topics: Animals; Arginase; Arginine; Asthma; Cystic Fibrosis; Disease Models, Animal; Humans; Hypertension, Pulmonary; Lung; Lung Diseases; Nitric Oxide; Nitric Oxide Synthase; Ornithine; Pulmonary Disease, Chronic Obstructive; Pulmonary Fibrosis; Urea	2008
Nasal nitric oxide. Acta oto-rhino-laryngologica Belgica, 2000, Volume: 54, Issue:3 Topics: Arginine; Asthma; Child; Child, Preschool; Ciliary Motility Disorders; Cystic Fibrosis; Female; Humans; Infant; Luminescent Measurements; Male; Nasal Polyps; Nitric Oxide; Paranasal Sinuses; Respiratory Mucosa; Respiratory Tract Infections; Rhinitis, Allergic, Perennial; Sinusitis; Smoking	2000

Trials

4 trial(s) available for arginine and Cystic Fibrosis of Pancreas

Article	Year
Effects of GLP-1 and GIP on Islet Function in Glucose-Intolerant, Pancreatic-Insufficient Cystic Fibrosis. Diabetes, 2022, 10-01, Volume: 71, Issue:10 Topics: Adult; Arginine; Blood Glucose; Cystic Fibrosis; Gastric Inhibitory Polypeptide; Glucagon; Glucagon-Like Peptide 1; Glucose; Humans; Incretins; Insulin; Proinsulin	2022
A randomized controlled trial of inhaled L-arginine in patients with cystic fibrosis. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2013, Volume: 12, Issue:5 Topics: Administration, Inhalation; Adolescent; Adult; Arginine; Cross-Over Studies; Cystic Fibrosis; Double-Blind Method; Female; Humans; Male; Middle Aged; Nitric Oxide; Respiratory Function Tests; Young Adult	2013
Oral L-arginine supplementation in cystic fibrosis patients: a placebo-controlled study. The European respiratory journal, 2005, Volume: 25, Issue:1 Topics: Adolescent; Adult; Arginine; Cross-Over Studies; Cystic Fibrosis; Dose-Response Relationship, Drug; Double-Blind Method; Drug Administration Schedule; Female; Follow-Up Studies; Humans; Male; Nitric Oxide; Pilot Projects; Probability; Reference Values; Respiratory Function Tests; Severity of Illness Index; Treatment Outcome	2005
Normal spontaneous and stimulated GH levels despite decreased IGF-I concentrations in cystic fibrosis patients. European journal of endocrinology, 1999, Volume: 140, Issue:4 Topics: Adolescent; Adult; Arginine; Body Mass Index; Cystic Fibrosis; Diabetes Mellitus; Female; Glucose Tolerance Test; Human Growth Hormone; Humans; Insulin-Like Growth Factor Binding Protein 3; Insulin-Like Growth Factor I; Male; Middle Aged	1999

Other Studies

69 other study(ies) available for arginine and Cystic Fibrosis of Pancreas

Article	Year
Determining effects of nitrate, arginine, and ferrous on antibiotic recalcitrance of clinical strains of Pseudomonas aeruginosa in biofilm-inspired alginate encapsulates. Annals of clinical microbiology and antimicrobials, 2023, Jul-20, Volume: 22, Issue:1 Topics: Alginates; Amikacin; Anti-Bacterial Agents; Arginine; Biofilms; Ciprofloxacin; Cystic Fibrosis; Humans; Microbial Sensitivity Tests; Nitrates; Pseudomonas aeruginosa; Pseudomonas Infections; Tobramycin	2023
ORKAMBI-Mediated Rescue of Mucociliary Clearance in Cystic Fibrosis Primary Respiratory Cultures Is Enhanced by Arginine Uptake, Arginase Inhibition, and Promotion of Nitric Oxide Signaling to the Cystic Fibrosis Transmembrane Conductance Regulator Channe Molecular pharmacology, 2019, Volume: 96, Issue:4 Topics: Aminophenols; Aminopyridines; Animals; Arginase; Arginine; Benzodioxoles; Bronchi; Cells, Cultured; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Cytosol; Drug Combinations; Humans; Intestinal Mucosa; Mice; Mutation; Nitric Oxide; Nose; Quinolones	2019
Deregulation of the growth hormone/insulin-like growth factor-1 axis in adults with cystic fibrosis. Journal of endocrinological investigation, 2018, Volume: 41, Issue:5 Topics: Adolescent; Adult; Arginine; Biomarkers; Cystic Fibrosis; Female; Follow-Up Studies; Growth Disorders; Human Growth Hormone; Humans; Insulin-Like Growth Factor I; Male; Middle Aged; Prognosis; Young Adult	2018
mBio, 2017, 12-19, Volume: 8, Issue:6 Topics: Amino Acid Transport Systems; Amino Acid Transport Systems, Neutral; Animals; Arginine; Bacterial Adhesion; Cystic Fibrosis; Epithelial Cells; Humans; Mice, Knockout; Plasma Membrane Neurotransmitter Transport Proteins; Pseudomonas aeruginosa; Pseudomonas Infections	2017
A c-di-GMP-Modulating Protein Regulates Swimming Motility of Frontiers in cellular and infection microbiology, 2018, Volume: 8 Topics: Amino Acid Sequence; Amino Acids; Arginine; Bacterial Proteins; Biofilms; Burkholderia cenocepacia; Burkholderia Infections; Cloning, Molecular; Cyclic GMP; Cystic Fibrosis; Escherichia coli Proteins; Flagellin; Gene Expression Regulation, Bacterial; Glutamic Acid; Locomotion; Lung; Mutagenesis, Insertional; Peptide Hydrolases; Phosphoric Diester Hydrolases; Phosphorus-Oxygen Lyases; Sequence Alignment; Sputum	2018
Augmentation of Cystic Fibrosis Transmembrane Conductance Regulator Function in Human Bronchial Epithelial Cells via SLC6A14-Dependent Amino Acid Uptake. Implications for Treatment of Cystic Fibrosis. American journal of respiratory cell and molecular biology, 2019, Volume: 61, Issue:6 Topics: Amino Acid Transport Systems; Arginine; Biological Transport; Bronchi; Cells, Cultured; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelial Cells; Genes, Reporter; Humans; Nitric Oxide; Nitric Oxide Synthase Type II; Recombinant Proteins; Surface Properties; Transduction, Genetic; Tryptophan	2019
Stimulated nitric oxide production and arginine deficiency in children with cystic fibrosis with nutritional failure. The Journal of pediatrics, 2013, Volume: 163, Issue:2 Topics: Adolescent; Arginine; Child; Child Nutrition Disorders; Cystic Fibrosis; Female; Humans; Male; Nitric Oxide; Young Adult	2013
Arginine metabolism in patients with cystic fibrosis. The Journal of pediatrics, 2013, Volume: 163, Issue:2 Topics: Arginine; Child Nutrition Disorders; Cystic Fibrosis; Female; Humans; Male; Nitric Oxide	2013
Inhibition of Protease-Epithelial Sodium Channel Signaling Improves Mucociliary Function in Cystic Fibrosis Airways. American journal of respiratory and critical care medicine, 2016, 09-15, Volume: 194, Issue:6 Topics: Arginine; Cells, Cultured; Cystic Fibrosis; Humans; Mucociliary Clearance; Organophosphonates; Respiratory Mucosa; Serine Endopeptidases; Sodium Channel Blockers; Sodium Channels	2016
Asymmetric dimethylarginine and related metabolites in exhaled breath condensate of children with cystic fibrosis. The clinical respiratory journal, 2018, Volume: 12, Issue:1 Topics: Adolescent; Arginine; Biomarkers; Breath Tests; Child; Chromatography, High Pressure Liquid; Cystic Fibrosis; Disease Progression; Exhalation; Female; Follow-Up Studies; Forced Expiratory Volume; Humans; Male; Mass Spectrometry; Prospective Studies	2018
Dietary Nitrate Acutely and Markedly Increased Exhaled Nitric Oxide in a Cystic Fibrosis Case. Clinical medicine & research, 2016, Volume: 14, Issue:3-4 Topics: Arginine; Child; Cystic Fibrosis; Diet; Exhalation; Humans; Inflammation; Iron; Male; Nitrates; Nitric Oxide; Nitrites; Placebos; Respiratory Function Tests; Treatment Outcome	2016
The p.Arg258Gly mutation in intracellular loop 2 of CFTR is associated with CFTR-related disorders. Genetic testing and molecular biomarkers, 2009, Volume: 13, Issue:6 Topics: Adult; Aged; Amino Acid Sequence; Amino Acid Substitution; Arginine; Cohort Studies; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Glycine; Humans; Male; Middle Aged; Molecular Sequence Data; Mutation, Missense	2009
p.Ser1235Arg should no longer be considered as a cystic fibrosis mutation: results from a large collaborative study. European journal of human genetics : EJHG, 2011, Volume: 19, Issue:1 Topics: Amino Acid Sequence; Arginine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Heterozygote; Humans; Male; Male Urogenital Diseases; Models, Molecular; Molecular Epidemiology; Molecular Sequence Data; Mutation, Missense; Pregnancy; Prenatal Diagnosis; Serine; Urogenital Abnormalities; Vas Deferens	2011
Asymmetric dimethylarginine contributes to airway nitric oxide deficiency in patients with cystic fibrosis. American journal of respiratory and critical care medicine, 2011, May-15, Volume: 183, Issue:10 Topics: Adolescent; Airway Obstruction; Arginine; Child; Chromatography, Liquid; Cystic Fibrosis; Female; Humans; Lung; Male; Nitric Oxide; Respiratory System; Sputum; Tandem Mass Spectrometry	2011
A pilot study of oral L-arginine in cystic fibrosis. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2005, Volume: 4, Issue:1 Topics: Administration, Oral; Adolescent; Arginine; Breath Tests; Child; Cystic Fibrosis; Female; Follow-Up Studies; Forced Expiratory Volume; Humans; Male; Nerve Tissue Proteins; Nitric Oxide; Nitric Oxide Synthase; Nitric Oxide Synthase Type I; Nitric Oxide Synthase Type III; Pilot Projects; Treatment Outcome; Vital Capacity	2005
Inhaled L-arginine improves exhaled nitric oxide and pulmonary function in patients with cystic fibrosis. American journal of respiratory and critical care medicine, 2006, Jul-15, Volume: 174, Issue:2 Topics: Administration, Inhalation; Adolescent; Adult; Arginine; Breath Tests; Citrulline; Cystic Fibrosis; Female; Forced Expiratory Volume; Humans; Lung; Male; Middle Aged; Nitric Oxide; Ornithine; Pilot Projects; Respiratory System Agents	2006
Early pulmonary manifestation of cystic fibrosis in children with the DeltaF508/R117H-7T genotype. Pediatrics, 2006, Volume: 118, Issue:3 Topics: Age of Onset; Arginine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; DNA Mutational Analysis; Female; Genotype; Histidine; Humans; Infant, Newborn; Lung Diseases; Male; Mutation, Missense; Neonatal Screening; Point Mutation; Pseudomonas aeruginosa; Pseudomonas Infections	2006
Exon skipping through the creation of a putative exonic splicing silencer as a consequence of the cystic fibrosis mutation R553X. Journal of medical genetics, 2007, Volume: 44, Issue:5 Topics: Alternative Splicing; Arginine; Base Sequence; Cell Line; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; DNA Mutational Analysis; Exons; Humans; Molecular Sequence Data; Mutation; RNA Splice Sites; RNA, Messenger	2007
Protease binding by alpha 2 macroglobulin in cystic fibrosis. Clinica chimica acta; international journal of clinical chemistry, 1982, Jan-05, Volume: 118, Issue:1 Topics: Adolescent; alpha-Macroglobulins; Anthraquinones; Arginine; Child; Coloring Agents; Cystic Fibrosis; Female; Humans; Kinetics; Macromolecular Substances; Male; Peptide Hydrolases; Trypsin; Trypsin Inhibitor, Kunitz Soybean	1982
Measurement of trypsin-like activity of saliva, serum and meconium by a synthetic substrate carbobenzoxy-L-arginine-7-amino-4-methylcoumarin amide (CAMCA). Clinica chimica acta; international journal of clinical chemistry, 1984, Apr-13, Volume: 138, Issue:2 Topics: Adult; Arginine; Child; Coumarins; Cystic Fibrosis; Humans; Infant, Newborn; Meconium; Saliva; Trypsin	1984
Reaction of 4-methylumbelliferylguanidinobenzoate with proteases in human amniotic fluid. Pediatric research, 1980, Volume: 14, Issue:4 Pt 1 Topics: Amniotic Fluid; Arginine; Chloroform; Cystic Fibrosis; Ellagic Acid; Female; Guanidines; Humans; Hydrolysis; Hymecromone; Peptide Hydrolases; Pregnancy; Pregnancy Trimester, Second; Pregnancy Trimester, Third; Prenatal Diagnosis; Umbelliferones	1980
Effect of hypersomatostatinemia on growth hormone secretion in cystic fibrosis patients with diabetes. Neuroendocrinology, 1993, Volume: 58, Issue:4 Topics: Adult; Arginine; Body Mass Index; Carrier Proteins; Cystic Fibrosis; Diabetes Complications; Diabetes Mellitus; Growth Hormone; Humans; Insulin-Like Growth Factor Binding Proteins; Insulin-Like Growth Factor I; Male; Reference Values; Somatomedins; Somatostatin	1993
Activation of CFTR chloride current by nitric oxide in human T lymphocytes. The EMBO journal, 1995, Jun-15, Volume: 14, Issue:12 Topics: Aminoquinolines; Arginine; CD4-Positive T-Lymphocytes; Chloride Channels; Clone Cells; Cyclic GMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Guanylate Cyclase; Humans; Membrane Proteins; Nitric Oxide; Patch-Clamp Techniques; Penicillamine; S-Nitroso-N-Acetylpenicillamine; Signal Transduction	1995
Male infertility as the only presenting sign of cystic fibrosis when homozygous for the mild mutation R117H. Journal of medical genetics, 1993, Volume: 30, Issue:9 Topics: Adult; Arginine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Homozygote; Humans; Infertility, Male; Male; Membrane Proteins; Point Mutation; Vas Deferens	1993
Multi-ion pore behaviour in the CFTR chloride channel. Nature, 1993, Nov-04, Volume: 366, Issue:6450 Topics: Amino Acid Sequence; Animals; Anions; Arginine; Chloride Channels; Chlorides; CHO Cells; Cricetinae; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Ion Channels; Membrane Potentials; Membrane Proteins; Molecular Sequence Data; Mutagenesis, Site-Directed; Thiocyanates	1993
Clinical characteristics of 16 cystic fibrosis patients with the missense mutation R334W, a pancreatic insufficiency mutation with variable age of onset and interfamilial clinical differences. Human genetics, 1995, Volume: 95, Issue:3 Topics: Age of Onset; Arginine; Child; Child, Preschool; Cystic Fibrosis; Exocrine Pancreatic Insufficiency; Female; Forced Expiratory Volume; Genotype; Humans; Intestinal Obstruction; Lung; Male; Phenotype; Point Mutation; Tryptophan; Vital Capacity	1995
Molecular basis for the polymorphic forms of human serum paraoxonase/arylesterase: glutamine or arginine at position 191, for the respective A or B allozymes. American journal of human genetics, 1993, Volume: 52, Issue:3 Topics: Amino Acid Sequence; Arginine; Aryldialkylphosphatase; Base Sequence; Chromosomes, Human, Pair 7; Cloning, Molecular; Cystic Fibrosis; DNA; Female; Gene Library; Glutamine; Humans; Isoenzymes; Liver; Male; Molecular Sequence Data; Pedigree; Phosphoric Monoester Hydrolases; Polymerase Chain Reaction; Polymorphism, Genetic	1993
Mutation of R555 in CFTR-delta F508 enhances function and partially corrects defective processing. Receptors & channels, 1996, Volume: 4, Issue:1 Topics: Amino Acid Sequence; Arginine; ATP-Binding Cassette Transporters; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Electric Conductivity; Fungal Proteins; Humans; Ion Channel Gating; Lysine; Molecular Sequence Data; Mutagenesis, Site-Directed; Protein Processing, Post-Translational; Recombinant Fusion Proteins; Suppression, Genetic; Yeasts	1996
An ovine CFTR variant as a putative cystic fibrosis causing mutation. Journal of medical genetics, 1996, Volume: 33, Issue:7 Topics: Animals; Arginine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; DNA Primers; Glutamine; Lymphocytes; Mutation; Pedigree; Polymerase Chain Reaction; Polymorphism, Single-Stranded Conformational; Sequence Analysis; Sheep	1996
Severe cystic fibrosis associated with a deltaF508/R347H + D979A compound heterozygous genotype. Clinical genetics, 1998, Volume: 53, Issue:1 Topics: Adult; Alanine; Arginine; Asparagine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Genotype; Heterozygote; Histidine; Humans; Male; Point Mutation; Severity of Illness Index	1998
Cystic fibrosis-associated mutations at arginine 347 alter the pore architecture of CFTR. Evidence for disruption of a salt bridge. The Journal of biological chemistry, 1999, Feb-26, Volume: 274, Issue:9 Topics: Amino Acid Substitution; Arginine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Hydrogen-Ion Concentration; Membrane Potentials; Mutagenesis, Site-Directed; Patch-Clamp Techniques; Phenotype; Protein Conformation; Salts; Static Electricity	1999
Severe cystic fibrosis in a Japanese girl caused by two novel CFTR (ABCC7) gene mutations: M152R and 1540del10. Human mutation, 2000, Volume: 15, Issue:5 Topics: Amino Acid Substitution; Arginine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Frameshift Mutation; Gene Deletion; Humans; Methionine; Mutation, Missense	2000
Effect of L-arginine infusion on airway NO in cystic fibrosis and primary ciliary dyskinesia syndrome. The European respiratory journal, 1999, Volume: 13, Issue:1 Topics: Adolescent; Adult; Arginine; Breath Tests; Child; Ciliary Motility Disorders; Cystic Fibrosis; Female; Humans; Infusions, Intravenous; Male; Nitric Oxide; Syndrome	1999
Frequency and clinical significance of the S1235R mutation in the cystic fibrosis transmembrane conductance regulator gene: results from a collaborative study. American journal of medical genetics, 2000, Dec-11, Volume: 95, Issue:4 Topics: Adolescent; Adult; Aged; Amino Acid Substitution; Arginine; Child; Child, Preschool; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Gene Frequency; Humans; Infant; Infant, Newborn; Male; Middle Aged; Mutation, Missense; Pregnancy; Serine	2000
Nitric oxide deficiency contributes to impairment of airway relaxation in cystic fibrosis mice. American journal of respiratory cell and molecular biology, 2001, Volume: 24, Issue:5 Topics: Animals; Arginine; Bronchoconstriction; Cystic Fibrosis; Dinoprostone; Disease Models, Animal; Electric Stimulation; Enzyme Inhibitors; Female; In Vitro Techniques; Male; Mice; Mice, Inbred CFTR; Muscle Relaxation; Nitric Oxide; Nitric Oxide Synthase; Nitroarginine; Substance P; Trachea	2001
Arginine esterase and lysosomal hydrolases in liver from cystic fibrosis subjects. Pediatric research, 1977, Volume: 11, Issue:11 Topics: Adolescent; Adult; Arginine; Cathepsins; Child; Child, Preschool; Cystic Fibrosis; Esterases; Female; Humans; Hydrogen-Ion Concentration; Hydrolases; Isoelectric Focusing; Liver; Lysosomes; Male	1977
Carboxypeptidase B activity of cultured skin fibroblasts and relationship to cystic fibrosis. Clinica chimica acta; international journal of clinical chemistry, 1979, Sep-15, Volume: 97, Issue:1 Topics: Arginine; Carboxypeptidases; Cells, Cultured; Cystic Fibrosis; Dithiothreitol; Fibroblasts; Hippurates; Humans; Hydrogen-Ion Concentration; Subcellular Fractions	1979
Absence of an alpha two-macroglobulin-protease complex in cystic fibrosis. Pediatric research, 1976, Volume: 10, Issue:9 Topics: alpha-Macroglobulins; Animals; Arginine; Cystic Fibrosis; Esterases; Humans; Hydrolysis; Immune Sera; Immunoelectrophoresis; Immunologic Techniques; Rabbits	1976
Exocrine-gland function and the basic biochemical defect in cystic fibrosis. Lancet (London, England), 1978, Aug-19, Volume: 2, Issue:8086 Topics: Absorption; Arginine; Calcium; Cell Membrane; Chlorine; Cystic Fibrosis; Esterases; Humans; Kinins; Models, Biological; Salivary Glands; Sodium	1978
Arginine esterase in amniotic fluid: possible marker for cystic fibrosis. Lancet (London, England), 1979, Oct-27, Volume: 2, Issue:8148 Topics: Amniotic Fluid; Arginine; Benzoates; Carboxylic Ester Hydrolases; Coumarins; Cystic Fibrosis; Esterases; Female; Genetic Markers; Humans; Methods; Pregnancy	1979
Binding of 125I-labeled proteinases to plasma proteins in cystic fibrosis. Pediatric research, 1979, Volume: 13, Issue:9 Topics: alpha-Macroglobulins; Arginine; Blood Proteins; Cystic Fibrosis; Electrophoresis, Polyacrylamide Gel; Endopeptidases; Esterases; Humans; Immunoelectrophoresis; Immunoglobulin G; Iodine Radioisotopes; Protein Binding; Trypsin	1979
Pancreatic alpha and beta cell functions in cystic fibrosis. The Journal of pediatrics, 1977, Volume: 90, Issue:5 Topics: Adolescent; Adult; Arginine; Child; Cystic Fibrosis; Female; Glucagon; Glucose Tolerance Test; Humans; Insulin; Insulin Secretion; Islets of Langerhans; Male; Prediabetic State	1977
[Blood insulin levels and incidence of diabetes mellitus in patients with cystic fibrosis]. Revista clinica espanola, 1978, Apr-30, Volume: 149, Issue:2 Topics: Adolescent; Adult; Arginine; Child; Cystic Fibrosis; Diabetes Complications; Diabetes Mellitus; Female; Glucose Tolerance Test; Humans; Insulin; Islets of Langerhans; Male	1978
[Levels of somatotropic hormone in plasma and growth changes in patients with cystic fibrosis]. Revista clinica espanola, 1978, May-15, Volume: 149, Issue:3 Topics: Adolescent; Adult; Arginine; Body Height; Body Weight; Child; Cystic Fibrosis; Female; Growth Disorders; Growth Hormone; Humans; Male; Pituitary Gland; Stimulation, Chemical	1978
Reaction of 4-methylumbelliferylguanidinobenzoate with proteases in plasma of patients with cystic fibrosis. Enzyme, 1978, Volume: 23, Issue:5 Topics: Adolescent; Arginine; Binding Sites; Child; Child, Preschool; Cystic Fibrosis; Guanidines; Humans; Hymecromone; In Vitro Techniques; Isoelectric Focusing; Molecular Weight; Peptide Hydrolases; Umbelliferones	1978
Normal plasma arginine esterase and the Hageman factor (factor XII) -prekallikrein-kininogen system in cystic fibrosis. The Journal of laboratory and clinical medicine, 1977, Volume: 89, Issue:1 Topics: Adolescent; Adult; Arginine; Child; Cystic Fibrosis; Esterases; Factor XII; Humans; Kallikreins; Kininogens; Prekallikrein; Tosylarginine Methyl Ester	1977
Insulin and glucagon response to arginine infusion in cystic fibrosis. Acta paediatrica Scandinavica, 1977, Volume: 66, Issue:2 Topics: Arginine; Blood Glucose; Body Height; Body Weight; Child; Child, Preschool; Cystic Fibrosis; Fasting; Female; Glucagon; Humans; Injections, Intravenous; Insulin; Insulin Secretion; Male	1977
Cystic fibrosis: comparison of two mucolytic drugs for inhalation treatment (acetylcysteine and arginine hydrochloride). Pediatrics, 1975, Volume: 55, Issue:1 Topics: Acetylcysteine; Aerosols; Arginine; Bronchoscopy; Carbon Dioxide; Child; Child, Preschool; Cough; Cystic Fibrosis; Drug Evaluation; Expectorants; Female; Humans; Male; Mucus; Oxygen; Radionuclide Imaging; Respiration; Respiratory Function Tests; Spirometry; Sputum	1975
Deficiency of arginine esterase in cystic fibrosis of the pancreas: demonstration of the proteolytic nature of the activity. Pediatric research, 1975, Volume: 9, Issue:9 Topics: Adolescent; Arginine; Carboxylic Ester Hydrolases; Child; Child, Preschool; Cystic Fibrosis; Enzyme Inhibitors; Esterases; Heterozygote; Humans; Hydrolysis; Hydroxymercuribenzoates; Lung Diseases; Pancreatic Diseases; Peptides; Protamines; Tosyllysine Chloromethyl Ketone; Trypsin Inhibitors	1975
[Inhalations with L-arginine in the treatment of cystic fibrosis (author's transl)]. Zeitschrift fur Erkrankungen der Atmungsorgane, 1975, Volume: 143, Issue:2 Topics: Adolescent; Aerosols; Alanine Transaminase; Arginine; Aspartate Aminotransferases; Blood Glucose; Child; Child, Preschool; Creatinine; Cystic Fibrosis; Female; Follow-Up Studies; Humans; Male; Radiography; Viscosity	1975
Letter: Questions regarding arginine hydrochloride inhalation. Pediatrics, 1976, Volume: 57, Issue:1 Topics: Arginine; Cystic Fibrosis; Humans	1976
[Therapy of cystic fibrosis]. Minerva pediatrica, 1976, Jan-28, Volume: 28, Issue:2 Topics: Anti-Bacterial Agents; Arginine; Bicarbonates; Cysteine; Cystic Fibrosis; Humans; Infant	1976
Auxotrophy of Pseudomonas aeruginosa in cystic fibrosis. FEMS microbiology letters, 1992, May-01, Volume: 71, Issue:3 Topics: Amino Acids; Arginine; Bronchiectasis; Cystic Fibrosis; Humans; Methionine; Proline; Pseudomonas aeruginosa; Sputum; Thiamine	1992
A serine-to-arginine (AGT-to-CGT) mutation in codon 549 of the CFTR gene in an Italian patient with severe cystic fibrosis. Genomics, 1991, Volume: 9, Issue:4 Topics: Arginine; Base Sequence; Codon; Cystic Fibrosis; DNA; Exons; Female; Humans; Male; Molecular Sequence Data; Mutation; Serine	1991
Pancreatic endocrine function in cystic fibrosis. The Journal of pediatrics, 1991, Volume: 118, Issue:5 Topics: Adult; Arginine; C-Peptide; Cystic Fibrosis; Fasting; Glucagon; Glucose Tolerance Test; Humans; Hyperglycemia; Hypoglycemia; Insulin; Pancreas; Pancreatic Polypeptide; Time Factors	1991
Letter: Plasma arginine esterase activity in cystic fibrosis. The American review of respiratory disease, 1974, Volume: 110, Issue:3 Topics: Adult; Arginine; Child; Cystic Fibrosis; Electrophoresis, Polyacrylamide Gel; Esterases; Humans; Proteins	1974
Deficiency of kallikrein activity in plasma of patients with cystic fibrosis. Science (New York, N.Y.), 1972, Aug-18, Volume: 177, Issue:4049 Topics: Adult; Aprotinin; Arginine; Child; Cystic Fibrosis; Esterases; Heterozygote; Humans; Kallikreins	1972
[Arginine test for the examination of endocrine pancreatic function in childhood]. Monatsschrift fur Kinderheilkunde, 1974, Volume: 122, Issue:7 Topics: Adolescent; Anorexia Nervosa; Arginine; Blood Glucose; Child; Child, Preschool; Cystic Fibrosis; Fasting; Female; Glucagon; Humans; Injections, Intravenous; Insulin; Islets of Langerhans; Methods; Pancreatic Diseases	1974
L-arginine and cystic fibrosis. Pediatrics, 1973, Volume: 51, Issue:3 Topics: Adolescent; Amylases; Arginine; Child; Cystic Fibrosis; Humans; Lipase; Pancreas; Trypsin	1973
Growth hormone in marasmus die to cerebral disease. American journal of diseases of children (1960), 1973, Volume: 126, Issue:3 Topics: Adolescent; Arginine; Astrocytoma; Birth Injuries; Blood Glucose; Brain Diseases; Brain Neoplasms; Celiac Disease; Child; Child, Preschool; Cystic Fibrosis; Dehydration; Depression, Chemical; Fatty Acids, Nonesterified; Female; Glucose; Growth Hormone; Humans; Hydrocephalus; Hypoglycemia; Hypoproteinemia; Infant; Insulin; Male; Nutrition Disorders; Radioimmunoassay; Stimulation, Chemical	1973
Plasma arginine esterase activity in cystic fibrosis. The American review of respiratory disease, 1974, Volume: 109, Issue:3 Topics: Acids; Adolescent; Adult; Arginine; Chloroform; Cystic Fibrosis; Enzyme Activation; Esterases; Humans; Middle Aged; Trypsin Inhibitors	1974
Endocrine function of the pancreas in cystic fibrosis: evidence for an impaired glucagon and insulin response following arginine infusion. The Journal of pediatrics, 1974, Volume: 84, Issue:6 Topics: Adolescent; Antigens; Arginine; Blood Glucose; Child; Child, Preschool; Cystic Fibrosis; Female; Glucagon; Humans; Insulin; Insulin Secretion; Male; Pancreas	1974
Arginine esterase in cystic fibrosis of the pancreas. Pediatric research, 1974, Volume: 8, Issue:6 Topics: Arginine; Blood; Chromatography, DEAE-Cellulose; Chromatography, Ion Exchange; Cystic Fibrosis; Electrophoresis, Polyacrylamide Gel; Esterases; Humans; Hydrogen-Ion Concentration; Trypsin Inhibitors	1974
The use of L-arginine and sodium bicarbonate in the treatment of malabsorption due to cystic fibrosis. Pediatrics, 1972, Volume: 50, Issue:1 Topics: Adolescent; Adult; Arginine; Bicarbonates; Body Weight; Carotenoids; Child; Cystic Fibrosis; Duodenum; Fats; Feces; Humans; Intestinal Secretions; Malabsorption Syndromes; Nitrogen; Pancreatic Extracts; Peptide Hydrolases; Sodium	1972
L-arginine, the sickling phenomenon, and cystic fibrosis. Pediatrics, 1972, Volume: 49, Issue:6 Topics: Aerosols; Anemia, Sickle Cell; Arginine; Cystic Fibrosis; Fever; Humans	1972
Buffered L-arginine as treatment of cystic fibrosis: state of the evidence. Pediatrics, 1972, Volume: 49, Issue:3 Topics: Adolescent; Aerosols; Arginine; Buffers; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Infant; Infant, Newborn; Lipid Metabolism; Pregnancy; Sputum; Structure-Activity Relationship	1972
The use of buffered L-arginine in the treatment of cystic fibrosis. Pediatrics, 1971, Volume: 47, Issue:2 Topics: Adolescent; Arginine; Body Weight; Buffers; Child; Child, Preschool; Cystic Fibrosis; Humans	1971
Studies on the mechanism of inhibition of sodium transport in cystic fibrosis of the pancreas. Pediatric research, 1968, Volume: 2, Issue:5 Topics: Animals; Arginine; Biological Transport; Cell Membrane Permeability; Cystic Fibrosis; Heparin; Humans; Imines; Lysine; Macromolecular Substances; Male; Parotid Gland; Rats; Saliva; Sodium	1968
Successful treatment of acute lymphoblastic leukemia in a child with cystic fibrosis. Medical and pediatric oncology, 1994, Volume: 22, Issue:6 Topics: Antineoplastic Combined Chemotherapy Protocols; Asparaginase; Child, Preschool; Cystic Fibrosis; Cytarabine; Daunorubicin; Female; Humans; Mercaptopurine; Methotrexate; Precursor B-Cell Lymphoblastic Leukemia-Lymphoma; Precursor Cell Lymphoblastic Leukemia-Lymphoma; Prednisone; Remission Induction; Teniposide; Vincristine	1994