arginine and Aminoaciduria, Renal

arginine has been researched along with Aminoaciduria, Renal in 34 studies

Research

Studies (34)

TimeframeStudies, this research(%)All Research%
pre-199032 (94.12)18.7374
1990's0 (0.00)18.2507
2000's2 (5.88)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
BEER, S; FISCHL, J; WALLIS, K1
ARMSTRONG, MD; STEMMERMANN, MG; YATES, KN1
Mann, GV; Perry, N1
COFFEY, VP1
HAMBRAEUS, L1
LEDERER, J1
DEHEVESY, G; HAMBRAEUS, L1
TOMLINSON, S; WESTALL, RG1
VOLKOV, VP1
GROSS, JB; JONES, JD; MAHER, FT; ULRICH, JA1
GROSS, JB; JONES, JD; ULRICH, JA1
DAMBORENEA, RG; PINTO, B; VAZQUEZ, J1
Fujii, J; Kawata, S; Saito, K; Saito, T; Takasago, Y; Takeda, H; Takeda, T; Togashi, H; Watanabe, H1
Kekomäki, M; Perheentupa, J; Saxén, L; Visakorpi, JK1
Kekomäki, M; Perheentupa, J; Räihä, NC1
Engerman, RL; Kern, TS1
González-Noriega, A; Prieto, E; Velázquez, A; Verduzco, J1
Ban, M; Kato, T; Mizutani, N1
Atienza, FC; Hsia, YE; Kennaway, NG; Perry, TL; Uemura, HS; Wirtz, ML1
Potter, JL; Silvidi, AA; Timmons, GD1
Andria, G; Bussolati, O; Dall'Asta, V; Gazzola, GC; Rotoli, BM; Sala, R; Sebastio, G; Sperandeo, MP1
Endres, W; Schaub, J; Zoulek, G1
Segal, S1
Horisawa, S; Kato, T; Tanaka, E1
Eskelin, LE; Perheentupa, J; Rapola, J; Simell, O; Visakorpi, JK1
Best, JB; Burger, HG; Connelly, JF; Davies, HE1
Fluharty, AL; Kihara, H; Porter, MT; Valente, M1
Perheentupa, J; Visakorpi, JK1
Burgess, EA; Oberholzer, VG; Palmer, T; Wagstaff, TI1
Perheentupa, J; Simell, O1
Clark, WT; Cuddeford, D1
Miura, R; Oyanagi, K; Yamanouchi, T1
Genel, M; Holtzapple, P; Rea, C; Segal, S1
Jones, JD; Ulrich, JA; Winkelmann, RK1

Trials

1 trial(s) available for arginine and Aminoaciduria, Renal

ArticleYear
Renal handling of diamino acids in lysinuric protein intolerance.
    The Journal of clinical investigation, 1974, Volume: 54, Issue:1

    Topics: Adolescent; Adult; Amino Acids, Diamino; Arginine; Child; Child, Preschool; Clinical Trials as Topic; Dietary Proteins; Fasting; Female; Genes, Recessive; Glomerular Filtration Rate; Humans; Infant; Kidney Tubules; Lysine; Male; Ornithine; Renal Aminoacidurias; Urea

1974

Other Studies

33 other study(ies) available for arginine and Aminoaciduria, Renal

ArticleYear
A FAMILY AFFECTED BY ARGININO-SUCCINIC ACIDURIA.
    Helvetica paediatrica acta, 1963, Volume: 18

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Child; Electrophoresis; Genetics, Medical; Kidney; Metabolic Diseases; Renal Aminoacidurias; Succinates; Urine

1963
AN OCCURRENCE OF ARGININOSUCCINIC ACIDURIA.
    Pediatrics, 1964, Volume: 33

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Arginine; Argininosuccinic Aciduria; Child; Humans; Infant; Infant, Newborn; Kidney; Renal Aminoacidurias; Succinates; Urine; Urologic Diseases

1964
AMINOACIDURIA AFTER DIETARY LOADING IN HUMAN SUBJECTS.
    The American journal of clinical nutrition, 1964, Volume: 14

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Cystine; Diet; Dietary Proteins; Humans; Kidney; Lysine; Nitrogen; Ornithine; Proteins; Renal Aminoacidurias; Sulfur; Urine

1964
MENTAL RETARDATION AND THE INBORN ERRORS OF METABOLISM.
    Journal of the Irish Medical Association, 1964, Volume: 54

    Topics: Alkaptonuria; Amino Acid Metabolism, Inborn Errors; Arginine; Citrulline; Fructose; Galactosemias; Histidine; Homocysteine; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Intellectual Disability; Maple Syrup Urine Disease; Metabolic Diseases; Phenylketonurias; Renal Aminoacidurias; Vitamin B 6 Deficiency

1964
CYSTINURIA IN SWEDEN. X. QUANTITATIVE STUDIES ON THE URINARY AMINO ACID EXCRETION IN CYSTINURICS.
    Acta Societatis Medicorum Upsaliensis, 1964, Volume: 69

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Arginine; Child; Chromatography; Cystinuria; Geriatrics; Humans; Lysine; Nephrectomy; Ornithine; Renal Aminoacidurias; Sulfhydryl Compounds; Sweden; Taurine; Urinary Calculi

1964
[DISEASES CAUSED BY METABOLIC DISORDER OF THE KREBS-HENSELEIT CYCLE].
    Le Scalpel, 1964, Mar-21, Volume: 117

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Blood Chemical Analysis; Child; Dietary Proteins; Humans; Infant; Kidney; Liver; Metabolic Diseases; Renal Aminoacidurias; Succinates

1964
CYSTINURIA IN SWEDEN. VIII. A CASE OF COELIAC DISEASE ASSOCIATED WITH CYSTINE-LYSINURIA.
    Acta paediatrica, 1964, Volume: 53

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Ataxia; Celiac Disease; Chromatography; Creatine; Creatinine; Cystinuria; Electrophoresis; Glucose Tolerance Test; Humans; Infant; Intestine, Small; Intestines; Lysine; Muscle Spasticity; Ornithine; Proteins; Psychomotor Disorders; Renal Aminoacidurias; Sweden; Urine; Vitamin A; Xylose

1964
ARGININOSUCCINIC ACIDURIA. ARGININOSUCCINASE AND ARGINASE IN HUMAN BLOOD CELLS.
    Clinical science, 1964, Volume: 26

    Topics: Amino Acid Metabolism, Inborn Errors; Arginase; Arginine; Argininosuccinate Lyase; Argininosuccinic Aciduria; Blood Cells; Blood Chemical Analysis; Erythrocytes; Genetics, Medical; Humans; Leukocytes; Lyases; Renal Aminoacidurias

1964
[FREE AMINO ACIDS IN THE BLOOD AND URINE OF PATIENTS WITH SOME FORMS OF DERMATOSIS].
    Vestnik dermatologii i venerologii, 1964, Volume: 38

    Topics: Alanine; Amino Acids; Arginine; Aspartic Acid; Blood; Cystine; Dermatitis; Eczema; Erythema Multiforme; Glutamates; Glycine; Histidine; Lupus Erythematosus, Systemic; Lysine; Proteins; Psoriasis; Renal Aminoacidurias; Serine; Skin Diseases; Taurine; Threonine; Toxicology; Tryptophan; Urticaria

1964
ENDOGENOUS RENAL CLEARANCES OF 12 INDIVIDUAL AMINO ACIDS IN FOUR APPARENTLY HEALTHY SUBJECTS AND IN FOUR AMINOACIDURIC PERSONS OF A KINDRED WITH HEREDITARY PANCREATITIS.
    The Journal of laboratory and clinical medicine, 1964, Volume: 63

    Topics: Amino Acids; Arginine; Biomedical Research; Cystine; Genetics, Medical; Glutamates; Healthy Volunteers; Histidine; Isoleucine; Kidney; Leucine; Lysine; Methionine; Pancreatitis; Pancreatitis, Chronic; Phenylalanine; Physiology; Renal Aminoacidurias; Threonine; Tryptophan; Tyrosine; Valine

1964
URINARY EXCRETION OF AMINO ACIDS IN A KINDRED WITH HEREDITARY PANCREATITIS AND AMINOACIDURIA.
    Gastroenterology, 1964, Volume: 47

    Topics: Amino Acids; Arginine; Biomedical Research; Child; Cystine; Genetics, Medical; Humans; Kidney; Kidney Tubules; Lysine; Pancreatitis; Pancreatitis, Chronic; Renal Aminoacidurias; Urine

1964
[ACQUIRED RENAL GLYCINURIA (REPORT OF 2 CASES WITH ARTERIAL HYPERTENSION)].
    Revista clinica espanola, 1964, Oct-31, Volume: 95

    Topics: Arginine; Glycine; Humans; Hypertension; Kidney; Kidney Calculi; Kidney Diseases; Pathology; Proline; Renal Aminoacidurias

1964
Impaired portal circulation resulting from L-arginine deficiency in patients with lysinuric protein intolerance.
    Gut, 2006, Volume: 55, Issue:10

    Topics: Adolescent; Adult; Aged; Arginine; Child; Female; Humans; Liver Circulation; Male; Middle Aged; Mucoproteins; Renal Aminoacidurias

2006
Familial protein intolerance with deficient transport of basic amino acids. An analysis of 10 patients.
    Acta paediatrica Scandinavica, 1967, Volume: 56, Issue:6

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Blood Proteins; Child; Child, Preschool; Dietary Proteins; Female; Growth; Hepatomegaly; Humans; Infant; Leukopenia; Liver; Male; Renal Aminoacidurias; Splenomegaly; Urea

1967
Enzymes of urea synthesis in familial protein intolerance with deficient transport of basic amino acids.
    Acta paediatrica Scandinavica, 1967, Volume: 56, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Arginase; Arginine; Child; Dietary Proteins; Humans; Ligases; Liver; Lyases; Lysine; Ornithine Carbamoyltransferase; Renal Aminoacidurias; Urea

1967
Abnormal amino acid concentrations in plasma and urine of experimentally diabetic dogs.
    Research in experimental medicine. Zeitschrift fur die gesamte experimentelle Medizin einschliesslich experimenteller Chirurgie, 1983, Volume: 182, Issue:3

    Topics: Amino Acids; Amino Acids, Branched-Chain; Animals; Arginine; Diabetes Mellitus, Experimental; Dogs; Female; Glutamates; Glutamic Acid; Histidine; Male; Phenylalanine; Renal Aminoacidurias; Tryptophan; Tyrosine

1983
Argininosuccinic acid synthetase deficiency in a hamster cell line and its complementation of argininosuccinic aciduria human fibroblasts.
    Journal of inherited metabolic disease, 1980, Volume: 3, Issue:2

    Topics: Animals; Arginine; Argininosuccinate Lyase; Argininosuccinate Synthase; Argininosuccinic Acid; Cell Line; Citrulline; Cricetinae; Female; Fibroblasts; Genes, Recessive; Genetic Complementation Test; HeLa Cells; Humans; Hybrid Cells; Ligases; Liver; Lyases; Male; Renal Aminoacidurias

1980
Renal transport of lysine and arginine in lysinuric protein intolerance.
    European journal of pediatrics, 1982, Volume: 139, Issue:3

    Topics: Adolescent; Ammonia; Arginine; Biological Transport; Humans; Kidney Tubules; Lysine; Male; Ornithine; Renal Aminoacidurias

1982
Amino acid and enzyme studies of brain and other tissues in an infant with argininosuccinic aciduria.
    Clinica chimica acta; international journal of clinical chemistry, 1980, Aug-04, Volume: 105, Issue:2

    Topics: Amino Acids; Arginine; Argininosuccinate Lyase; Argininosuccinic Acid; Brain; Cells, Cultured; Humans; Infant; Kidney; Liver; Lyases; Male; Renal Aminoacidurias; Skin

1980
Argininosuccinicaciduria: the hair abnormality revisited.
    American journal of diseases of children (1960), 1980, Volume: 134, Issue:11

    Topics: Amino Acids; Arginine; Argininosuccinic Acid; Child; Cystine; Female; Hair; Hair Diseases; Humans; Renal Aminoacidurias

1980
Arginine transport through system y(+)L in cultured human fibroblasts: normal phenotype of cells from LPI subjects.
    American journal of physiology. Cell physiology, 2000, Volume: 279, Issue:6

    Topics: Adolescent; Amino Acid Transport Systems, Basic; Amino Acids, Diamino; Anion Transport Proteins; Antiporters; Arginine; Biological Transport; Carrier Proteins; Cations; Cells, Cultured; DNA Primers; Enzyme Inhibitors; Ethylmaleimide; Fibroblasts; Humans; Leucine; Membrane Proteins; Nitric Oxide; Phenotype; Renal Aminoacidurias; Skin; SLC4A Proteins; Sodium

2000
Hyperdibasicaminoaciduria in a Turkish infant without evident protein intolerance.
    European journal of pediatrics, 1979, Apr-25, Volume: 131, Issue:1

    Topics: Arginine; Diarrhea; Humans; Infant; Intestinal Absorption; Lysine; Male; Ornithine; Renal Aminoacidurias; Turkey

1979
Inherited disorders of transport: aminoacidurias.
    Monographs in human genetics, 1978, Volume: 9

    Topics: Arginine; Biological Transport; Carrier Proteins; Cystinuria; Humans; Kidney; Lysine; Microvilli; Ornithine; Renal Aminoacidurias

1978
Hyperdibasicaminoaciduria and hyperammonemia in familial protein intolerance.
    American journal of diseases of children (1960), 1976, Volume: 130, Issue:12

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Diamino; Ammonia; Arginine; Child, Preschool; Cystinuria; Humans; Intestinal Absorption; Intestinal Mucosa; Lysine; Male; Ornithine; Renal Aminoacidurias

1976
Lysinuric protein intolerance.
    The American journal of medicine, 1975, Volume: 59, Issue:2

    Topics: Adolescent; Adult; Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Birth Weight; Child; Child, Preschool; Dietary Proteins; Eye Diseases; Female; Humans; Infant; Intellectual Disability; Intestinal Absorption; Liver; Lysine; Male; Nitrogen; Ornithine; Proteins; Renal Aminoacidurias; Urea

1975
Iatrogenic aminoaciduria.
    Lancet (London, England), 1970, Dec-12, Volume: 2, Issue:7685

    Topics: Arginine; Chromatography, Paper; Cystinuria; Humans; Iatrogenic Disease; Infusions, Parenteral; Lysine; Ornithine; Renal Aminoacidurias

1970
Hyperdibasicaminoaciduria in a mentally retarded homozygote with a peculiar response to phenothiazines.
    Pediatrics, 1973, Volume: 51, Issue:2

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Antipsychotic Agents; Arginine; Chlorpromazine; Cystinuria; Female; Fluphenazine; Humans; Intellectual Disability; Intestinal Absorption; Kidney Tubules; Lysine; Movement Disorders; Ornithine; Pedigree; Renal Aminoacidurias; Thioridazine; Trihexyphenidyl

1973
Protein intolerance with deficient transport of basic aminoacids. Another inborn error of metabolism.
    Lancet (London, England), 1965, Oct-23, Volume: 2, Issue:7417

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Biological Transport; Child, Preschool; Cystinuria; Female; Humans; Infant; Intestines; Lysine; Male; Renal Aminoacidurias; Urine

1965
Argininosuccinic aciduria: antenatal investigations in an affected family.
    American journal of obstetrics and gynecology, 1974, Oct-15, Volume: 120, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Amniotic Fluid; Arginine; Chromosome Aberrations; Chromosome Disorders; Genes, Recessive; Humans; Infant; Intellectual Disability; Lyases; Male; Renal Aminoacidurias; Succinates

1974
A study of the amino-acids in urine from dogs with cystine urolithiasis.
    The Veterinary record, 1971, Apr-17, Volume: 88, Issue:16

    Topics: Animals; Arginine; Chromatography; Cystinuria; Dog Diseases; Dogs; Lysine; Male; Nitrogen; Ornithine; Renal Aminoacidurias; Serine; Threonine; Urinary Calculi

1971
Congenital lysinuria: a new inherited transport disorder of dibasic amino acids.
    The Journal of pediatrics, 1970, Volume: 77, Issue:2

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Arginine; Biological Transport; Child; Chromatography, Thin Layer; Consanguinity; Cystine; Cystinuria; Diarrhea; Female; Growth; Humans; Intellectual Disability; Lysine; Malabsorption Syndromes; Ornithine; Renal Aminoacidurias; Vomiting

1970
Cycloleucine inhibition of amino acid transport in human and rat kidney cortex.
    The Journal of laboratory and clinical medicine, 1970, Volume: 75, Issue:5

    Topics: Absorption; Amino Acids; Aminobutyrates; Animals; Arginine; Biological Assay; Biological Transport; Carbon Isotopes; Cystinuria; Extracellular Space; Glycine; Humans; Inulin; Kidney Tubules; Leucine; Lysine; Radiometry; Rats; Renal Aminoacidurias; Valine

1970
Urinary amino acid excretion in patients with scleroderma.
    Mayo Clinic proceedings, 1971, Volume: 46, Issue:2

    Topics: Arginine; Aspartic Acid; Chelating Agents; Female; Glutamates; Histidine; Humans; Isoleucine; Leucine; Lysine; Male; Methionine; Phenylalanine; Renal Aminoacidurias; Scleroderma, Systemic; Threonine; Tyrosine; Valine

1971