arginine and Acquired Metabolic Diseases, Brain

arginine has been researched along with Acquired Metabolic Diseases, Brain in 10 studies

Research

Studies (10)

TimeframeStudies, this research(%)All Research%
pre-19901 (10.00)18.7374
1990's1 (10.00)18.2507
2000's1 (10.00)29.6817
2010's4 (40.00)24.3611
2020's3 (30.00)2.80

Authors

AuthorsStudies
Bouchereau, J; Schiff, M1
Ando, Y; Arisaka, O; Imataka, G; Ishii, J; Nitta, A; Takagi, Y; Yoshihara, S1
Ballhausen, D; Barroso, M; Braissant, O; Caterino, M; Costanzo, M; Cudalbu, C; Cudré-Cung, HP; Feichtinger, RG; Gersting, SW; Gonzalez Melo, M; Häberle, J; Mayr, JA; Poms, M; Remacle, N; Roux, C; Rüfenacht, V; Ruoppolo, M1
Davis, MP; Sharma, P; Shinde, SS1
Blair, NF; Cremer, PD; Tchan, MC1
Hoffmann, GF; Koeller, DM; Kölker, S; Okun, JG; Opp, S; Sauer, SW1
Boy, SP; Burgard, P; Ensenauer, R; Greenberg, CR; Haege, G; Heringer, J; Hoffmann, GF; Koeller, DM; Kölker, S; Maier, EM; Mühlhausen, C; Müller, E; Schlune, A1
Cornélio, AR; Delwing, D; Wajner, M; Wannmacher, CM; Wyse, AT1
Deshmukh, DR; Shope, TC1
DeJoseph, MR; Hawkins, RA; Mans, AM1

Reviews

1 review(s) available for arginine and Acquired Metabolic Diseases, Brain

ArticleYear
Inherited Disorders of Lysine Metabolism: A Review.
    The Journal of nutrition, 2020, 10-01, Volume: 150, Issue:Suppl 1

    Topics: 2-Aminoadipic Acid; Aldehyde Dehydrogenase; Amino Acid Metabolism, Inborn Errors; Arginine; Brain; Brain Diseases, Metabolic; Brain Diseases, Metabolic, Inborn; Carnitine; Epilepsy; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Lysine; Metabolic Diseases; Pyridoxal Phosphate; Pyridoxine

2020

Other Studies

9 other study(ies) available for arginine and Acquired Metabolic Diseases, Brain

ArticleYear
Long-term survival of a patient with acute neonatal-onset metabolic encephalopathy with carbamoyl phosphate synthetase 1 deficiency.
    European review for medical and pharmacological sciences, 2020, Volume: 24, Issue:19

    Topics: Arginine; Brain Diseases, Metabolic; Carbamoyl-Phosphate Synthase I Deficiency Disease; Carnitine; Female; Humans; Hyperammonemia; Infant, Newborn; Phenylbutyrates; Renal Dialysis; Sodium Benzoate

2020
The first knock-in rat model for glutaric aciduria type I allows further insights into pathophysiology in brain and periphery.
    Molecular genetics and metabolism, 2021, Volume: 133, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Arginine; Brain; Brain Diseases, Metabolic; Creatine; Disease Models, Animal; Gene Knock-In Techniques; Gliosis; Glutaryl-CoA Dehydrogenase; Humans; Lysine; Metabolism, Inborn Errors; Rats

2021
Acute hyperammonemic encephalopathy in a non-cirrhotic patient with hepatocellular carcinoma reversed by arginine therapy.
    Journal of pain and symptom management, 2014, Volume: 47, Issue:4

    Topics: Antineoplastic Agents; Arginine; Brain Diseases, Metabolic; Carcinoma, Hepatocellular; Humans; Hyperammonemia; Indoles; Liver Neoplasms; Male; Pyrroles; Sunitinib; Young Adult

2014
Urea cycle disorders: a life-threatening yet treatable cause of metabolic encephalopathy in adults.
    Practical neurology, 2015, Volume: 15, Issue:1

    Topics: Adult; Ammonia; Arginine; Brain Diseases, Metabolic; Diet, Protein-Restricted; Fat Emulsions, Intravenous; Female; Glucose; Humans; Postpartum Period; Sodium Benzoate; Urea Cycle Disorders, Inborn

2015
Therapeutic modulation of cerebral L-lysine metabolism in a mouse model for glutaric aciduria type I.
    Brain : a journal of neurology, 2011, Volume: 134, Issue:Pt 1

    Topics: 2-Aminoadipate Transaminase; 2-Aminoadipic Acid; Amino Acid Metabolism, Inborn Errors; Analysis of Variance; Animals; Arginine; Brain; Brain Diseases, Metabolic; Carnitine; Catalase; Glutaryl-CoA Dehydrogenase; Ketoglutaric Acids; Lysine; Mice

2011
Complementary dietary treatment using lysine-free, arginine-fortified amino acid supplements in glutaric aciduria type I - A decade of experience.
    Molecular genetics and metabolism, 2012, Volume: 107, Issue:1-2

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Brain; Brain Diseases, Metabolic; Child; Child, Preschool; Dietary Supplements; Female; Glutaryl-CoA Dehydrogenase; Humans; Infant; Lysine; Male; Treatment Outcome

2012
Arginine administration reduces creatine kinase activity in rat cerebellum.
    Metabolic brain disease, 2007, Volume: 22, Issue:1

    Topics: alpha-Tocopherol; Animals; Antioxidants; Arginine; Ascorbic Acid; Brain Diseases, Metabolic; Cerebellum; Creatine Kinase; Enzyme Activation; Enzyme Inhibitors; Male; NG-Nitroarginine Methyl Ester; Rats; Rats, Wistar

2007
Arginine requirement and ammonia toxicity in ferrets.
    The Journal of nutrition, 1983, Volume: 113, Issue:8

    Topics: Ammonia; Animals; Arginine; Brain Diseases, Metabolic; Carnivora; Ferrets; Male; Nutritional Requirements; Urease

1983
Metabolic abnormalities and grade of encephalopathy in acute hepatic failure.
    Journal of neurochemistry, 1994, Volume: 63, Issue:5

    Topics: Ammonia; Animals; Arginine; Aspartic Acid; Blood Glucose; Blood-Brain Barrier; Brain Chemistry; Brain Diseases, Metabolic; Glutamic Acid; Lactates; Liver Failure, Acute; Male; Pyruvates; Rats

1994