androstenedione has been researched along with Adrenal Hyperplasia, Congenital in 197 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 58 (29.44) | 18.7374 |
1990's | 46 (23.35) | 18.2507 |
2000's | 28 (14.21) | 29.6817 |
2010's | 46 (23.35) | 24.3611 |
2020's | 19 (9.64) | 2.80 |
Authors | Studies |
---|---|
Auchus, RJ; Chan, JL; Davis, SM; Farber, RH; Fechner, PY; Giri, N; Imel, EA; Roberts, E; Sarafoglou, K; Sturgeon, J; Vogiatzi, MG | 1 |
Adriaansen, BPH; Bock, C; Brandt, A; Claahsen-van der Grinten, HL; Kamphuis, JS; Lentjes, EGWM; Olthaar, AJ; Schröder, MAM; Span, PN; Stikkelbroeck, NMML; Sweep, FCGJ; van Herwaarden, AE | 1 |
Chang, S; Gu, X; Guo, J; Han, L; Qiu, W; Wang, Y; Zhan, X; Zhang, H | 1 |
Gau, M; Hasegawa, T; Hashimoto, A; Ishige, N; Kashimada, K; Konishi, K; Morio, T; Nakatani, H; Sutani, A; Tajima, T; Takasawa, K; Tsuji-Hosokawa, A; Watanabe, K; Yajima, H | 1 |
Feng, D; Hu, C; Kong, H; Li, H; Shi, X; Wang, Z; Xu, G; Xu, Z; Yu, C; Zou, L | 1 |
Auchus, RJ; Chan, JL; Farber, RH; Fechner, PY; Giri, N; Jeha, GS; Newfield, RS; Nokoff, NJ; Roberts, E; Sarafoglou, K; Sturgeon, J; Vogiatzi, MG | 1 |
Matorel, E; Niño-Serna, L; Suárez, DV; Toro-Ramos, M | 1 |
Goedegebuure, WJ; Hokken-Koelega, ACS | 1 |
Baj, F; DiNardo, G; Gilardi, G; Pandey, AV; Parween, S; Zhang, C | 1 |
Auer, MK; Bidlingmaier, M; Krumbholz, A; Reisch, N; Thieme, D | 1 |
Auchus, RJ; Chang, AY; El-Maouche, D; Joyal, EG; Lin, VH; Merke, DP; Mohideen, P; Plaunt, MR; Turcu, AF; Vogiatzi, MG; Weintraub, L | 1 |
Andersson, AM; Clausen, CS; Duno, M; Frederiksen, H; Johannsen, TH; Juul, A; Ljubicic, ML; Main, KM; Petersen, JH | 1 |
Abacı, A; Acar, S; Böber, E; Can, Ş; Çatlı, G; Demir, K; Dündar, B; Egeli, T; Güleryüz, H; Öztürk, T; Tuhan, H | 1 |
Baráth, Á; Bereczki, C; Galla, Z; Grecsó, N; Monostori, P; Rácz, G; Zádori, A | 1 |
Auer, MK; Bidlingmaier, M; Hawley, J; Keevil, B; Lottspeich, C; Neuner, M; Paizoni, L; Reisch, N; Schmidt, H | 1 |
Auchus, RJ; Barnes, CN; Huang, M; Imel, EA; Madu, IJ; Merke, DP; Moriarty, D; Nakhle, S; Newfield, RS; Sarafoglou, K; Vogiatzi, MG | 1 |
Adaway, J; Auer, MK; Bidlingmaier, M; Dubinski, I; Hawley, J; Keevil, B; Lottspeich, C; Nowotny, HF; Reisch, N; Schmidt, H | 1 |
Reisch, N | 1 |
Auchus, RJ; Claahsen-van der Grinten, HL; O'Day, P; Schröder, MAM; Span, PN; Sweep, FCGJ; Turcu, AF; van Herwaarden, AE | 1 |
Barash, G; Baum, M; de Vries, L; Horovitz, M; Lazar, L; Phillip, M; Pinhas-Hamiel, O | 1 |
Auchus, RJ; Avila, NA; Elman, MS; Mallappa, A; Marko, J; Merke, DP; Rao, H; Tsodikov, A; Turcu, AF | 1 |
Charmandari, E; Chrousos, GP; Critselis, E; Farakla, I; Kolaitis, G; Koltsida, G; Kyritsi, EM; Mantzou, E; Papanikolaou, A; Zoumakis, E | 1 |
Arlt, W; Bouvattier, C; Claahsen-van der Grinten, HL; Engels, M; Falhammar, H; Gehrmann, K; Köhler, B; Kortmann, BB; Nordenström, A; Reisch, N; Richter-Unruh, A; Roeleveld, N; Rohayem, J; Span, PN; Stikkelbroeck, NMML; Sweep, FC; van Herwaarden, AE; Webb, EA | 1 |
Arlt, W; Asia, M; Elhassan, YS; Gleeson, H; Idkowiak, J; O'Reilly, MW; Smith, K; Webster, R | 1 |
Bello, R; de Vries, L; Lazar, L; Neeman, B; Phillip, M | 1 |
Avila, NA; El-Maouche, D; Hannah-Shmouni, F; Hargreaves, CJ; Mallappa, A; Merke, DP | 1 |
Chang, YS; Kim, JW; Lee, SY; Oh, HJ; Park, HD; Park, WS; Seo, JY; Yang, JS | 1 |
Fukami, M; Hasegawa, T; Hayashi, M; Homma, K; Kataoka, Y; Kato, F; Ogata, T; Oiso, Y; Sasano, H; Sugimura, Y; Tanaka, H | 1 |
Auchus, RJ; Buschur, EO; Chang, AY; Gonzalez, M; Hammer, GD; Jiao, J; Madrigal, D; Ramm, C; Smit, JW; Wang, G; Xu, XS; Yu, MK | 1 |
Claahsen-van der Grinten, HL; de Korte, CL; Dehzad, F; Kamphuis-van Ulzen, K | 1 |
Claahsen-van der Grinten, HL; de Groot, MJ; Otten, BJ; Pijnenburg-Kleizen, KJ; Stikkelbroeck, NM; Sweep, FC; Thomas, CM | 1 |
Cohen, A; Duno, M; Faurschou, S; Hougaard, DM; Johannsen, TH; Juul, A; Main, KM; Mouritsen, A | 1 |
Boonstra, T; Brundage, R; Gonzalez-Bolanos, MT; Sarafoglou, K; Yaw Addo, O; Zimmerman, CL | 1 |
Brundage, R; Gonzalez-Bolanos, MT; Sarafoglou, K; Willis, BA; Zimmerman, CL | 1 |
Ambroziak, U; Bartoszewicz, Z; Bednarczuk, T; Dadlez, M; Jaźwiec, R; Kępczyńska-Nyk, A; Kondracka, A; Kuryłowicz, A; Małunowicz, EM; Pawłowska, E; Szcześniak, M; Wysłouch-Cieszyńska, A | 1 |
Chen, L; Cheng, J; Huang, Y; Li, X; Liu, L; Lu, S; Xiao, Q; Xie, T; Zheng, J | 1 |
Bouchrit, K; Chaker, F; Chihaoui, M; Feki, M; Kanoun, F; Kharrat, M; Mizouni, H; Slimane, H; Yazidi, M | 1 |
Claahsen-van der Grinten, HL; Engels, M; Griffin, A; Krone, N; Mooij, CF; Pijnenburg-Kleizen, KJ; Span, PN; Sweep, FC; van Herwaarden, AE | 1 |
Hedderich, J; Holterhus, PM; Kulle, AE; Niermeyer, L; Riepe, FG; Schmitz, J; Sippell, WG | 1 |
Backlund, PS; Crutchfield, CA; Debono, M; Gounden, V; Harrison, RF; Mallappa, A; Merke, DP; Nella, AA; Ross, RJ; Soldin, SJ | 1 |
de Rijke, YB; Koper, JW; Noppe, G; van den Akker, EL; van Rossum, EF | 1 |
Bellincampi, L; Bernardini, S; Bizzarri, C; Cappa, M; Cualbu, A; Federici, L; Loche, S; Massimi, A; Porzio, O | 1 |
Gu, XF; Han, LS; Liang, LL; Luo, JH; Qiu, WJ; Xu, MS; Ye, J; Yu, YG; Zhang, HW; Zhou, DY | 1 |
De Mello, MP; Kater, CE; Lemos-Marini, SH; Ribeiro-Neto, LM; Tonetto-Fernandes, V | 1 |
Haslip, C; Keune, F; Liu, A; Longo, N; Murray, M; Pasquali, M; Randall, H; Schwarz, E | 1 |
Armengaud, JB; Brauner, R; Bréart, G; Chalumeau, M; Charkaluk, ML; Tardy, V; Trivin, C | 1 |
Argese, N; Borro, M; Brunetti, E; Bucci, B; Cerquetti, L; Gentile, G; Michienzi, S; Misiti, S; Simmaco, M; Stigliano, A; Toscano, V | 1 |
Singh, RJ | 1 |
Hsiao, PH; Lee, CT; Lee, JS; Tsai, WY; Tung, YC | 1 |
Claahsen-van der Grinten, HL; Kapusta, L; Mooij, CF; Otten, BJ | 1 |
Chiu, HY; Lin, SJ | 1 |
Dauber, A; Kellogg, M; Majzoub, JA | 1 |
De Jesús, VR; Hannon, WH; Kennedy, M; Mei, JV; Schiffer, J; Simms, DA | 1 |
Himes, JH; Lacey, JM; Matern, D; Netzel, BC; Sarafoglou, K; Singh, RJ | 1 |
Efstathiou, E; Kaffe, K; Neocleous, V; Phylactou, LA; Shammas, C; Skordis, N | 1 |
Kang, MJ; Kim, SM; Lee, YA; Shin, CH; Yang, SW | 1 |
Ambroziak, U; Bablok, L; Bar-Andziak, E; Bednarczuk, T; Ginalska-Malinowska, M; Grzechocińska, B; Kamiński, P; Małunowicz, EM; Przedlacki, J | 1 |
Hartmann, MF; Hochberg, Z; Kamrath, C; Remer, T; Wudy, SA | 1 |
de Jong, FH; Drop, SL; Faradz, SM; Goossens, K; Juniarto, AZ; Setyawati, BA | 1 |
Beń-Skowronek, I; Budzyńska, E | 1 |
Brack, C; Heger, S; Janzen, N; Korsch, E; Krull, F; Müller, HL; Peter, M; Riepe, FG; Sander, J; Sander, S; Steuerwald, U | 1 |
Çakir, ED; Eren, E; Mutlu, FS; Paşa, AO; Sağlam, H; Tarim, O | 1 |
Chen, HS; Chen, QL; Du, ML; Li, YH; Ma, HM; Su, Z; Xiao, HW | 1 |
Bachelot, A; Badachi, Y; Chakhtoura, Z; Charbit, B; Coudert, M; Coussieu, C; Dulon, J; Plu-Bureau, G; Touraine, P | 1 |
Backes, M; Kamp, GA; Zwaveling-Soonawala, N | 1 |
Diederich, S; Koetz, KR; Quinkler, M; van Rossum, EF; Ventz, M | 1 |
Hartmann, MF; Kamrath, C; Wudy, S | 1 |
Ksiazek, A; Oswiecimska, JM; Pys-Spychala, M; Roczniak, GR; Roczniak, W; Stojewska, M; Sygulla, K; Ziora, K | 1 |
Craviotto, C; Cutolo, M; Foppiani, L; Pizzorni, C; Prete, C; Salvarani, C; Seriolo, B; Straub, RH; Sulli, A | 1 |
Hermus, AR; Otten, BJ; Oyen, WJ; Stikkelbroeck, NM; van der Wilt, GJ | 1 |
Arleth, S; Bechtold, S; Bittmann, I; Bonfig, W; Kammer, B; Noelle, V; Raile, K; Schwarz, HP | 1 |
Braat, DD; Hermus, AR; Otten, BJ; Stikkelbroeck, NM; Sweep, CG | 1 |
Casetta, B; Hahn, SH; Lacey, JM; Lymp, J; Magera, MJ; Matern, D; McCann, M; Minutti, CZ; Rinaldo, P; Tauscher, AL | 1 |
Atabek, ME; Keskin, M; Kurtoğlu, S; Patiroglu, TE | 1 |
Hermus, AR; Jager, GJ; Otten, BJ; Stikkelbroeck, NM; Suliman, HM | 1 |
Accetta, SG; Capp, E; Di Domênico, K; Ritter, AT; Ritter, CG; Spritzer, PM | 1 |
Chace, DH; Cheillan, D; Dorche, C; Hahn, SH; Lacey, JM; Lymp, JF; Magera, MJ; Matern, D; McCann, M; Minutti, CZ; Rinaldo, P; Schulze, A; Zimmerman, D | 1 |
Johnson, DW | 1 |
David, R; Kohn, B; Rojas-Marcos, PM | 1 |
Kashiwagi, B | 1 |
Carson, KA; Malouf, MA; Migeon, CJ; Petrucci, L; Wisniewski, AB | 1 |
Claahsen-van der Grinten, HL; Hermus, AR; Hulsbergen-van de Kaa, C; Meuleman, EJ; Otten, BJ; Sweep, FC; Takahashi, S | 1 |
Holtkamp, U; Janzen, N; Peter, M; Sander, J; Sander, S; Steuerwald, U; Terhardt, M | 1 |
Claahsen-van der Grinten, HL; Hoefsloot, LH | 1 |
Claahsen-van der Grinten, HL; Hermus, AR; Meuleman, EJ; Otten, BJ; Ross, HA; Span, PN; Sweep, FC | 1 |
Blickman, JG; Claahsen-van der Grinten, HL; Hermus, AR; Otten, BJ; Sweep, FC | 1 |
Arslanoglu, I; Erguven, M; Isguven, P; Mesutoglu, N; Yildiz, M | 1 |
Atares, M; Kempken, B; Knorr-Muerset, G; Manella, B; Prader, A; Zachmann, M | 1 |
Eeckels, R; Eggermont, E; Ilondo, MM; Malvaux, P; Pizarro, M; Vanderschueren-Lodeweyckx, M; Vlietinck, R | 1 |
Canlorbe, P; Chaussain, JL; Evain, D; Roger, M; Scholler, R; Toublanc, JE | 1 |
Faredin, I; Tóth, I | 1 |
Brerault, JL; Canivet, J; Cathelineau, G; Dreux, C; Fiet, J; Julien, R | 1 |
Bouchard, P; Kuttenn, F; Mauvais-Jarvis, P; Mowszowicz, I; Raux-Eurin, MC; Schaison, G | 1 |
Angulo, M; Castro-Magana, M; Cheruvanky, T; Collipp, PJ; Ghavami-Maibodi, Z; Stewart, C | 1 |
Barboni, F; Bartolotta, E; Cacciari, E; Cassio, A; Chiumello, G; Dupont, B; Gargantini, L; Giovannelli, G; Kohn, B; Lerner, A; Levine, LS; Lorenzen, F; Mantero, F; Migliori, C; New, MI; Oberfield, SE; Pang, S; Pintor, C; Pollack, M; Rondanini, GF; Scaroni, C; Tato, L; Virdis, R | 1 |
Horrocks, PM; London, DR | 2 |
Dupont, B; Kohn, B; Lerner, AJ; Levine, LS; Levy, DJ; Lorenzen, F; New, MI; Oberfield, SE; Pang, S; Pollack, MS; Stoner, E | 1 |
Butt, WR; Holder, G; Horrocks, PM; Kandeel, FR; Logan-Edwards, R; London, DR; Lynch, SS | 1 |
Meyer-Bahlburg, HF | 2 |
Anderson, CE; Cederqvist, LL; Duchon, MA; Fuentes, M; Holcombe, JH; Levine, LS; Merkatz, I; New, MI; Nitowsky, HM; Owens, R; Pang, S; Riccardi, VM; Sachs, G | 1 |
Barboni, F; Bartolotta, E; Cacciari, E; Cassio, A; Chiumello, G; Dupont, B; Gargantini, L; Giovannelli, G; Kohn, B; Lerner, A; Levine, LS; Lorenzen, F; Mantero, F; Migliori, C; New, MI; Oberfield, S; Pang, S; Pintor, C; Pollack, M; Rondanini, GF; Scaroni, C; Tato, L; Virdis, R | 1 |
Bernick, D; Elias, AN; Grossman, MK; Meshkinpour, H; Valenta, LJ | 1 |
Kuttenn, F; Mauvais-Jarvis, P; Mowszowicz, I | 1 |
de Peretti, E; Forest, MG | 1 |
Benraad, TJ; Otten, BJ; Rijken, JC; Stoelinga, GB; Wellen, JJ | 1 |
Dhib-Jalbut, S; Hajj, H; Salti, IS | 1 |
Bougneres, P; Couzinet, B; Elkik, F; Gourmelen, M; Schaison, G | 1 |
Gutai, JP; Lee, PA; Migeon, CJ; Urban, MD | 1 |
Granoff, AB | 1 |
August, GP; Kent, SG; Larsen, JW; Migeon, CJ; Rosenbaum, KN; Schulman, JD; Warsof, SL | 1 |
Bidlingmaier, F; Knorr, D; von Schnakenburg, K | 1 |
MacGillivray, MH; Sellers, EP | 1 |
Auzéby, A; Bogdan, A; Touitou, Y | 1 |
Blades, B; Cowell, CT; Donaghue, K; Howard, NJ; Kreutzmann, DJ; Likitmaskul, S; Silink, M | 1 |
De Raeve, L; De Schepper, J; Smitz, J | 1 |
Foss, MC; Gouveia, LM; Moreira, AC; Paccola, GM; Paula, FJ; Piccinato, CE | 1 |
Calikoğlu, AS; Hatun, S; Yordam, N | 1 |
Balducci, R; Boscherini, B; Mangiantini, A; Morellini, M; Toscano, V | 1 |
Bernasconi, S; Ghizzoni, L; Giovannelli, G; Iughetti, L; Virdis, R; Volta, C; Vottero, A; Ziveri, M | 1 |
Dörr, HG; Sippell, WG | 1 |
Azziz, R; Boots, LR; Bradley, EL; Potter, HD | 1 |
Anderson, DC; O'Driscoll, JB | 1 |
Bernasconi, S; Cappa, M; Ghizzoni, L; Ibañez, L; Street, ME; Virdis, R; Vottero, A; Zampolli, M | 1 |
Herold, DA; Seely, BL; Summers, RH | 1 |
Chang, YT; Jorgensen, V; Kappy, M; Pang, S; Sakkal-Alkaddour, H; Slover, RS; Yang, X; Zhang, L | 1 |
Ayata, D; Keleştimur, F; Sahin, Y; Tutuş, A | 1 |
Eastell, R; Guo, CY; Weetman, AP | 1 |
Argenziano, A; Di Maio, S; Franzese, A; Gasparini, N; Salerno, M; Tenore, A | 1 |
Catzeflis, C; Cicotti, I; Lopes, LA; Rey, C; Sizonenko, PC | 1 |
Lee, PA; Nayak, S; Suda-Hartman, M; Witchel, SF | 1 |
Cunha, CF; Kater, CE; Silva, IN; Viana, MB | 1 |
Audí Parera, L; Foz Sala, M; Granada Ybern, ML; Lucas Martín, A; Pizarro Lozano, E; Salinas Vert, I; Sanmartí Sala, A | 1 |
Lee, PA; Nayak, S; Witchel, SF | 1 |
Djalali, M; Dörr, HG; Homoki, J; Solleder, C; Wudy, SA | 1 |
Azziz, R; Boots, LR; Decanter, C; Dewailly, D; Huerta, R; Knochenhauer, ES | 2 |
Allolio, B; Arlt, W; Callies, F; Hensen, J | 1 |
Hippeläinen, M; Jääskeläinen, J; Kiekara, O; Voutilainen, R | 1 |
Khalid, BA; Lo, MS; Ng, ML; Wu, LL | 1 |
Calis, KA; Cho, D; Chrousos, GP; Keil, MF; Merke, DP | 1 |
Chaussain, JL; Curnow, KM; Morel, Y; Mulatero, P; Pascoe, L; Portrat, S | 1 |
Hermus, AR; Jager, GJ; Noordam, K; Otten, BJ; Pasic, A; Stikkelbroeck, NM; Sweep, CG | 1 |
Azziz, R; Boots, LR; Morán, C; Ochoa, T; Reyna, R; Sánchez, LA | 1 |
Chow, DM; Korth-Schutz, S; Levine, LS; New, MI; Saenger, P; Virdis, R | 1 |
Barrett, GN; Clayton, GW; Holcombe, JH; Keenan, BS; Kirkland, RT; McNeel, R | 1 |
Chow, DM; Faiman, C; Levine, LS; New, MI; Pang, S | 1 |
Dupont, B; Gunczler, P; Levine, LS; Lorenzen, F; New, MI; Pang, S | 1 |
Achando, SS; Leme, CE; Lima, SS; Okada, H; Pieroni, RR; Shimizu, T; Wajchenberg, BL; White, A | 1 |
Bidlingmaier, F; Butenandt, O; Knorr, D; Sippell, WG; Weil, J | 1 |
Bryan, GT; Cavallo, A; Corn, C; Meyer, WJ | 1 |
Bidingmaier, F; Knorr, D; von Schnakenburg, K | 1 |
August, GP; Hung, W; Mayes, DM | 1 |
Jespersen, D; Kirschner, MA; Zucker, IR | 1 |
Akinci, A; Ersoy, F; Oğuz, H; Uluşahin, N; Yordam, N | 1 |
Perry, LA; Turner, EI; Watson, MJ; White, MC | 1 |
Borrelli, P; Cambiaso, P; Cappa, M; Danielli, E; del Balzo, P | 1 |
Augarten, A; Chayen, R; Gazit, E; Goldfarb, H; Pariente, C; Sack, J | 1 |
Carmina, E; Chang, L; Lobo, RA; Miles, RA; Stanczyk, FZ | 1 |
Clark, AT; Garibaldi, LR; Klimah, PE; Levine, LS; Oberfield, SE; Pang, SY; Riddick, LM; Senne, AR; Wang, ME | 1 |
Clark, A; Jeffries, S; MacGillivray, M; Pang, S; Riddick, L; Rosenthal, I; Wang, M; Wiegensberg, M | 1 |
Cavallo, A; Furlanetto, RW; Meyer, WJ | 1 |
Hampl, R; Stárka, L; Sulcová, J; Zwinger, A | 1 |
Azziz, R; Bradley, EL; Rafi, A; Smith, BR; Zacur, HA | 1 |
Billaud, L; Birman, P; Clair, F; Kuttenn, F; Mauvais-Jarvis, P; Mowszowicz, I; Raux-Demay, MC; Spritzer, P; Thalabard, JC | 1 |
Clayton, GW; Eberle, AE; Keenan, BS; Lin, TH | 1 |
Carmina, E; Lobo, RA | 1 |
Finegold, DN; Lanes, R; Lee, PA; Siegel, SF | 1 |
Foretová, L; Hampl, R; Stárka, L; Sulcová, J; Vána, V | 1 |
Connelly, JF; Funder, JW; Montalto, J; Whorwood, CB; Yong, AB | 1 |
Dvorák, P; Hampl, R; Lisá, L; Stárka, L; Sulcová, J | 1 |
Foretová, L; Hampl, R; Stárka, L; Sulcová, J | 1 |
Baniceviác, M; Brkljacić, L; Crawford, C; Dumić, M; Kastelan, A; Plavsić, V; Radica, A; Radmanović, S; Speiser, PW; Wood, E | 1 |
Blankstein, J; Dor, J; Geier, A; Levran, D; Lunenfeld, B; Mashiach, S; Pariente, C; Rabinovici, J; Rudak, E | 1 |
Cook, B; Thomson, S; Wallace, AM | 2 |
Chrousos, GP; Feuillan, P; Linder, B | 1 |
Hatano, M; Honda, M; Izumi, Y; Soma, M | 1 |
Tanaka, Y | 1 |
Betts, P; Egan, SM; Thomson, S; Wallace, AM; Wood, PJ | 1 |
Avgerinos, PC; Chrousos, GP; Feuillan, P; Pang, S; Schürmeyer, T | 1 |
Dewailly, D; Dufosse, F; Fossati, P; Lemaire, C; Racadot, A; Vantyghem, MC | 1 |
Gautier, T; Imperato-McGinley, J; Peterson, RE; Shackleton, C | 1 |
Ishikawa, S; Katayama, T; Kazama, T; Koike, H; Nakada, T; Yoshikawa, M | 1 |
Billaud, L; Boucekkine, C; Couillin, P; Girard, F; Kuttenn, F; Maudelonde, T; Mowszowicz, I; Spritzer, P; Thalabard, JC; Vincens, M | 1 |
Cunningham, SK; Loughlin, T; McKenna, TJ | 1 |
Lambotte, C | 1 |
New, MI; Speiser, PW | 1 |
Bongiovanni, AM; Cara, JF; Marx, BS; Moshang, T | 1 |
Hughes, IA; Riad-Fahmy, D; Walker, RF; Young, MC | 1 |
Clayton, G; Dupont, B; Green, O; Loo, M; New, MI; Nussbaum, R; Pang, S; Pollack, MS | 1 |
Forest, MG | 1 |
Bertrand, J; de Peretti, E; Forest, MG; Lecoq, A; Monneret, MP | 1 |
Sizonenko, PC; Theintz, GE | 1 |
Rosenfield, RL | 1 |
Gabrilove, JL; Nicolis, GL; Sohval, AR | 1 |
12 review(s) available for androstenedione and Adrenal Hyperplasia, Congenital
Article | Year |
---|---|
21-hydroxylase deficiency transiently mimicking combined 21- and 11beta-hydroxylase deficiency.
Topics: Adrenal Hyperplasia, Congenital; Androstenedione; Child; Cortodoxone; Diagnosis, Differential; Female; Humans; Mutation; Steroid 11-beta-Hydroxylase; Steroid 21-Hydroxylase | 2008 |
Monitoring of therapy in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Androstenedione; Biomarkers; Bone Development; Catecholamines; Glucocorticoids; Humans; Mineralocorticoids; Monitoring, Physiologic; Pregnanetriol; Saliva; Testosterone | 2010 |
Testicular adrenal rest tumours in boys with congenital adrenal hyperplasia: case report and literature review.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Age of Onset; Androstenedione; Child; Humans; Male; Risk Factors; Testicular Neoplasms; Testis; Ultrasonography | 2011 |
[The alternative androgen synthesis pathway in humans].
Topics: 17-alpha-Hydroxypregnenolone; 17-alpha-Hydroxyprogesterone; Adrenal Glands; Adrenal Hyperplasia, Congenital; Androgens; Androstenedione; Animals; Child; Child, Preschool; Dehydroepiandrosterone; Dihydrotestosterone; Female; Humans; Infant; Infant, Newborn; Male; Neoplasms, Hormone-Dependent; Orchiectomy; Pregnancy; Prostatic Neoplasms; Sex Differentiation; Steroid 21-Hydroxylase; Testis; Testosterone | 2013 |
[Androstenedione].
Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Androstenedione; Biomarkers; Cushing Syndrome; Female; Gonadal Disorders; Humans; Hypertrichosis; Male; Polycystic Ovary Syndrome; Radioimmunoassay; Specimen Handling | 2005 |
[From gene to disease: adrenogenital syndrome and the CYP21A2 gene].
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Androstenedione; Female; Humans; Male; Mutation; Steroid 21-Hydroxylase | 2007 |
[Common and uncommon forms of female sexual precocity and their biological diagnosis].
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Androstenedione; Child; Child, Preschool; Chorionic Gonadotropin; Dehydroepiandrosterone; Estradiol; Female; Fibrous Dysplasia, Polyostotic; Follicle Stimulating Hormone; Humans; Hydroxyprogesterones; Infant; Luteinizing Hormone; Male; Ovarian Neoplasms; Puberty, Precocious | 1984 |
Psychoendocrine research on sexual orientation. Current status and future options.
Topics: 3-Oxo-5-alpha-Steroid 4-Dehydrogenase; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Animals; Diethylstilbestrol; Dihydrotestosterone; Embryonic and Fetal Development; Estradiol; Estrone; Feedback; Female; Follicle Stimulating Hormone; Forecasting; Gonadal Steroid Hormones; Gonadotropin-Releasing Hormone; Homosexuality; Humans; Liver; Luteinizing Hormone; Male; Models, Biological; Pregnancy; Prenatal Exposure Delayed Effects; Progesterone; Sex Differentiation; Sexual Behavior; Sexual Behavior, Animal; Testosterone | 1984 |
Hirsutism.
Topics: 17-Ketosteroids; 3-Oxo-5-alpha-Steroid 4-Dehydrogenase; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstane-3,17-diol; Androstenedione; Cells, Cultured; Child; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Dihydrotestosterone; Estradiol; Female; Fibroblasts; Hirsutism; Humans; Liver; Male; Metabolic Clearance Rate; Ovarian Neoplasms; Polycystic Ovary Syndrome; Sebaceous Glands; Sex Hormone-Binding Globulin; Skin; Testosterone | 1981 |
The adrenal cortex and virilization.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Amenorrhea; Androgens; Androstenedione; Clomiphene; Cushing Syndrome; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Hirsutism; Humans; Hydroxyprogesterones; Infertility, Female; Obesity; Polycystic Ovary Syndrome; Testosterone; Virilism | 1985 |
[Adrenal hyperplasia as a result of 21-hydroxylase deficiency: prenatal diagnosis and treatment. Neonatal diagnosis].
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Amniotic Fluid; Androstenedione; Cytochrome P-450 Enzyme System; Dexamethasone; Female; Histocompatibility Antigens Class II; HLA Antigens; Humans; Hydroxyprogesterones; Immunoenzyme Techniques; Infant, Newborn; Male; Mass Screening; Pregnancy; Prenatal Diagnosis; Radioimmunoassay; Steroid 21-Hydroxylase; Steroid Hydroxylases | 1986 |
Relationship of androgens to female hirsutism and infertility.
Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Androstenedione; Androstenols; Dehydroepiandrosterone; Dihydrotestosterone; Female; Hirsutism; Humans; Hydroxysteroids; Infertility, Female; Ovary; Ovulation; Polycystic Ovary Syndrome; Protein Binding; Secretory Rate; Testosterone | 1973 |
14 trial(s) available for androstenedione and Adrenal Hyperplasia, Congenital
Article | Year |
---|---|
Crinecerfont Lowers Elevated Hormone Markers in Adults With 21-Hydroxylase Deficiency Congenital Adrenal Hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Administration, Oral; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Azabicyclo Compounds; Biomarkers; Dose-Response Relationship, Drug; Female; Humans; Male; Middle Aged; Oxadiazoles; Receptors, Corticotropin-Releasing Hormone; Testosterone; Treatment Outcome; Young Adult | 2022 |
A Phase 2, Multicenter Study of Nevanimibe for the Treatment of Congenital Adrenal Hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Administration, Oral; Adolescent; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Biomarkers; Cross-Over Studies; Dose-Response Relationship, Drug; Drug Therapy, Combination; Glucocorticoids; Humans; Middle Aged; Treatment Outcome; Urea; Young Adult | 2020 |
Tildacerfont in Adults With Classic Congenital Adrenal Hyperplasia: Results from Two Phase 2 Studies.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aged; Androstenedione; Biomarkers; Female; Follow-Up Studies; Humans; Male; Middle Aged; Receptors, Corticotropin-Releasing Hormone; Young Adult | 2021 |
Adrenal morphology and associated comorbidities in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Cohort Studies; Comorbidity; Cross-Sectional Studies; Female; Humans; Insulin Resistance; Male; Maryland; Obesity; Tertiary Care Centers; Tomography, X-Ray Computed; Young Adult | 2019 |
Steroid profiling for congenital adrenal hyperplasia by tandem mass spectrometry as a second-tier test reduces follow-up burdens in a tertiary care hospital: a retrospective and prospective evaluation.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Biomarkers; Chromatography, Liquid; Dried Blood Spot Testing; False Positive Reactions; Follow-Up Studies; Humans; Hydrocortisone; Infant, Newborn; Infant, Premature; Infant, Premature, Diseases; Neonatal Screening; Predictive Value of Tests; Prospective Studies; Retrospective Studies; Tandem Mass Spectrometry; Tertiary Care Centers | 2014 |
Abiraterone acetate to lower androgens in women with classic 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Abiraterone Acetate; Adrenal Hyperplasia, Congenital; Adult; Androgen Antagonists; Androgens; Androstadienes; Androstenedione; Androsterone; Desoxycorticosterone; Dose-Response Relationship, Drug; Female; Humans; Hydrocortisone; Treatment Outcome | 2014 |
Comparison of cortisol exposures and pharmacodynamic adrenal steroid responses to hydrocortisone suspension vs. commercial tablets.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Child; Child, Preschool; Humans; Hydrocortisone; Infant; Suspensions; Tablets | 2015 |
Interrelationships among cortisol, 17-hydroxyprogesterone, and androstenendione exposures in the management of children with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Child; Demography; Dose-Response Relationship, Drug; Female; Humans; Hydrocortisone; Infant; Male | 2015 |
Anthropometric and endocrine features in girls with isolated premature pubarche or non-classical congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Body Height; Body Mass Index; Body Weight; Bone Development; Brazil; Child; Child, Preschool; Dehydroepiandrosterone Sulfate; Female; Humans; Puberty, Precocious; Stimulation, Chemical; Testosterone | 2004 |
Testicular adrenal rest tumors in adult males with congenital adrenal hyperplasia: evaluation of pituitary-gonadal function before and after successful testis-sparing surgery in eight patients.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adrenocorticotropic Hormone; Adult; Androstenedione; Azoospermia; Biopsy; Estrone; Follicle Stimulating Hormone; Humans; Inhibins; Luteinizing Hormone; Magnetic Resonance Imaging; Male; Pituitary Gland; Postoperative Complications; Preoperative Care; Testicular Neoplasms; Testis; Testosterone; Treatment Outcome; Urologic Surgical Procedures, Male | 2007 |
Newborn screening for congenital adrenal hyperplasia: additional steroid profile using liquid chromatography-tandem mass spectrometry.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Calibration; Chromatography, High Pressure Liquid; Cortodoxone; False Positive Reactions; Female; Humans; Hydrocortisone; Infant, Newborn; Infant, Premature; Male; Neonatal Screening; Prospective Studies; Reproducibility of Results; Retrospective Studies; Tandem Mass Spectrometry | 2007 |
Colonic mucosal potential differences in the management of 21-hydroxylase deficiency.
Topics: Action Potentials; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Androstenedione; Clinical Trials as Topic; Colon; Dehydroepiandrosterone; Dexamethasone; Drug Therapy, Combination; Female; Humans; Hydrocortisone; Intestinal Mucosa; Mixed Function Oxygenases; Prednisone; Progesterone | 1980 |
Randomised controlled trial of growth effect of hydrocortisone in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Body Height; Child; Child, Preschool; Cross-Over Studies; Dose-Response Relationship, Drug; Female; Growth Disorders; Humans; Hydrocortisone; Infant; Male; Mixed Function Oxygenases; Prospective Studies; Testosterone | 1997 |
Cyproterone acetate versus hydrocortisone treatment in late-onset adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Cyproterone; Cyproterone Acetate; Estradiol; Female; Hirsutism; Humans; Hydrocortisone; Testosterone | 1990 |
171 other study(ies) available for androstenedione and Adrenal Hyperplasia, Congenital
Article | Year |
---|---|
Diurnal salivary androstenedione and 17-hydroxyprogesterone levels in healthy volunteers for monitoring treatment efficacy of patients with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aged; Androgens; Androstenedione; Child; Child, Preschool; Healthy Volunteers; Humans; Middle Aged; Steroids; Treatment Outcome; Young Adult | 2022 |
Steroid profile in dried blood spots by liquid chromatography tandem mass spectrometry: Application to newborn screening for congenital adrenal hyperplasia in China.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Chromatography, Liquid; Cortodoxone; Humans; Hydrocortisone; Infant, Newborn; Neonatal Screening; Steroids; Tandem Mass Spectrometry; Testosterone | 2022 |
The High Relevance of 21-Deoxycortisol, (Androstenedione + 17α-Hydroxyprogesterone)/Cortisol, and 11-Deoxycortisol/17α-Hydroxyprogesterone for Newborn Screening of 21-Hydroxylase Deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androgens; Androstenedione; Chromatography, Liquid; Cortodoxone; Endocrine System Diseases; Female; Humans; Hydrocortisone; Infant, Newborn; Male; Neonatal Screening; Steroids; Tandem Mass Spectrometry | 2022 |
Steroid profiling for the diagnosis of congenital adrenal hyperplasia by microbore ultra-performance liquid chromatography-tandem mass spectrometry.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Chromatography, Liquid; Cortodoxone; Desoxycorticosterone; Humans; Infant; Infant, Newborn; Progesterone; Steroids; Tandem Mass Spectrometry | 2023 |
Crinecerfont, a CRF1 Receptor Antagonist, Lowers Adrenal Androgens in Adolescents With Congenital Adrenal Hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androgens; Androstenedione; Female; Humans; Male; Testosterone | 2023 |
[Characterization of a cohort of pediatric patients with Congenital Adrenal Hyperplasia].
Topics: Adrenal Hyperplasia, Congenital; Androstenedione; Child; Child, Preschool; Female; Humans; Infant; Infant, Newborn; Longitudinal Studies; Male; Neonatal Screening; Testosterone | 2022 |
Aromatase Inhibitor as Treatment for Severely Advanced Bone Age in Congenital Adrenal Hyperplasia: A Case Report.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Androstadienes; Androstenedione; Aromatase Inhibitors; Body Height; Bone Development; Child; Follow-Up Studies; Gonadotropin-Releasing Hormone; Humans; Hydrocortisone; Male; Puberty; Puberty, Precocious | 2019 |
Differential effects of variations in human P450 oxidoreductase on the aromatase activity of CYP19A1 polymorphisms R264C and R264H.
Topics: Adrenal Hyperplasia, Congenital; Amino Acid Substitution; Androstenedione; Arginine; Aromatase; Cysteine; Cytochrome P-450 CYP1A1; Cytochrome P-450 Enzyme System; Enzyme Activation; Histidine; Humans; Models, Molecular; Mutation, Missense; Polymorphism, Single Nucleotide; Protein Conformation; Structure-Activity Relationship | 2020 |
Steroid 17-Hydroxyprogesterone in Hair Is a Potential Long-Term Biomarker of Androgen Control in Congenital Adrenal Hyperplasia due to 21-Hydroxylase Deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Biomarkers; Female; Hair; Humans; Male; Young Adult | 2020 |
Congenital Adrenal Hyperplasia in Children: A Pilot Study of Steroid Hormones Expressed as Sex- and Age-Related Standard Deviation Scores.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Child; Child, Preschool; Female; Humans; Hydrocortisone; Longitudinal Studies; Male; Pilot Projects; Retrospective Studies | 2020 |
The relationship of carotid intima-media thickness with anthropometric and metabolic parameters in patients with classic congenital adrenal hyperplasia
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Carotid Arteries; Carotid Intima-Media Thickness; Case-Control Studies; Child; Female; Humans; Male; Progesterone; Prospective Studies; Risk Factors; Ultrasonography | 2021 |
Comparison of different preparation techniques of dried blood spot quality controls in newborn screening for congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Cortodoxone; Dried Blood Spot Testing; Humans; Infant, Newborn; Neonatal Screening; Tandem Mass Spectrometry | 2021 |
11-oxygenated androgens and their relation to hypothalamus-pituitary-gonadal-axis disturbances in adults with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenedione; Female; Gonads; Humans; Hypogonadism; Hypothalamo-Hypophyseal System; Male; Menstruation Disturbances; Middle Aged; Testosterone; Young Adult | 2021 |
Salivary Profiles of 11-oxygenated Androgens Follow a Diurnal Rhythm in Patients With Congenital Adrenal Hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenedione; Biomarkers; Circadian Rhythm; Cross-Sectional Studies; Female; Humans; Male; Saliva; Testosterone | 2021 |
Block and Replace-a New Therapeutic Concept in Congenital Adrenal Hyperplasia?
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Humans | 2022 |
Production of 11-Oxygenated Androgens by Testicular Adrenal Rest Tumors.
Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adult; Androstenedione; Case-Control Studies; Humans; Hydroxytestosterones; Male; Middle Aged; Steroid 21-Hydroxylase; Testicular Neoplasms; Testis; Testosterone; Young Adult | 2022 |
Management of Fully Pubertal Girls With Nonclassical Congenital Adrenal Hyperplasia: Glucocorticoids Versus Oral Contraceptives.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Contraceptives, Oral; Female; Glucocorticoids; Hirsutism; Humans; Retrospective Studies | 2022 |
11-Oxygenated Androgens Are Biomarkers of Adrenal Volume and Testicular Adrenal Rest Tumors in 21-Hydroxylase Deficiency.
Topics: 17-alpha-Hydroxypregnenolone; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adult; Age Determination by Skeleton; Aged; Androgens; Androstenedione; Androstenes; Child; Child, Preschool; Cortodoxone; Cross-Sectional Studies; Female; Hirsutism; Humans; Hydroxytestosterones; Male; Menstruation Disturbances; Middle Aged; Organ Size; Pregnenolone; Testicular Neoplasms; Testosterone; Young Adult | 2017 |
Psychological vulnerability to stress in carriers of congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Anxiety; Case-Control Studies; Female; Humans; Hydrocortisone; Male; Middle Aged; Paranoid Disorders; Psychometrics; Psychotic Disorders | 2017 |
Gonadal function in adult male patients with congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adult; Aged; Androstenedione; Cross-Sectional Studies; Europe; Gonadotropins; Humans; Hydroxyprogesterones; Hypogonadism; Male; Middle Aged; Odds Ratio; Oligospermia; Prevalence; Semen Analysis; Sperm Count; Sperm Motility; Testicular Neoplasms; Testosterone; Young Adult | 2018 |
Causes, Patterns, and Severity of Androgen Excess in 1205 Consecutively Recruited Women.
Topics: Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocortical Carcinoma; Adult; Androgens; Androstenedione; Dehydroepiandrosterone Sulfate; Female; Humans; Hyperandrogenism; Middle Aged; Ovarian Diseases; Polycystic Ovary Syndrome; Postmenopause; Predictive Value of Tests; Premenopause; Reference Values; Retrospective Studies; Severity of Illness Index; Testosterone | 2018 |
Central Precocious Puberty as a Presenting Sign of Nonclassical Congenital Adrenal Hyperplasia: Clinical Characteristics.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Case-Control Studies; Child; Child, Preschool; Dehydroepiandrosterone Sulfate; Estradiol; Female; Follicle Stimulating Hormone; Gonadotropin-Releasing Hormone; Humans; Hydrocortisone; Luteinizing Hormone; Puberty, Precocious; Retrospective Studies | 2019 |
A 68-year-old phenotypically male patient with 21-hydroxylase deficiency and concomitant adrenocortical neoplasm producing testosterone and cortisol.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Aged; Androstenedione; Base Sequence; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydrocortisone; Immunohistochemistry; Japan; Magnetic Resonance Imaging; Male; Molecular Sequence Data; Pregnanetriol; Sequence Analysis, DNA; Testosterone | 2013 |
Increased prevalence of testicular adrenal rest tumours during adolescence in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Androstenedione; Child; Cross-Sectional Studies; Gonadal Steroid Hormones; Humans; Male; Prevalence; Saliva; Testicular Neoplasms; Ultrasonography; Young Adult | 2014 |
Salivary morning androstenedione and 17α-OH progesterone levels in childhood and puberty in patients with classic congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Child; Child, Preschool; Female; Glucocorticoids; Humans; Male; Puberty; Retrospective Studies; Saliva | 2015 |
Hormonal disturbances due to severe and mild forms of congenital adrenal hyperplasia are already detectable in neonatal life.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Female; Genotype; Humans; Hydrocortisone; Infant, Newborn; Male; Retrospective Studies | 2015 |
LC-MS/MS improves screening towards 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Chromatography, High Pressure Liquid; Dehydroepiandrosterone Sulfate; Diagnosis, Differential; False Positive Reactions; Female; Hospitals, University; Humans; Immunoassay; Poland; Reagent Kits, Diagnostic; Reproducibility of Results; Sensitivity and Specificity; Tandem Mass Spectrometry; Testosterone; Young Adult | 2015 |
[A novel homozygous mutation p.E25X in the HSD3B2 gene causing salt wasting 3β-hydroxysteroid dehydrogenases deficiency in a Chinese pubertal girl: a delayed diagnosis until recurrent ovary cysts].
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; China; Codon, Nonsense; Delayed Diagnosis; Female; Follicle Stimulating Hormone; Homozygote; Humans; Hydrocortisone; Luteinizing Hormone; Mutation; Ovarian Cysts; Progesterone Reductase; Recurrence; Retrospective Studies | 2014 |
Testicular adrenal rest tumours in young adult males with congenital adrenal hyperplasia: prevalence and impact on testicular function.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adult; Androstenedione; Asthenozoospermia; Azoospermia; Cohort Studies; Follicle Stimulating Hormone; Humans; Inhibins; Luteinizing Hormone; Male; Neoplasms, Multiple Primary; Oligospermia; Prevalence; Prospective Studies; Sperm Count; Sperm Motility; Testicular Neoplasms; Testosterone; Young Adult | 2016 |
Adrenal Steroid Metabolites Accumulating in Congenital Adrenal Hyperplasia Lead to Transactivation of the Glucocorticoid Receptor.
Topics: 17-alpha-Hydroxyprogesterone; Active Transport, Cell Nucleus; Adrenal Glands; Adrenal Hyperplasia, Congenital; Androstenedione; Animals; Binding, Competitive; Chlorocebus aethiops; Cortodoxone; COS Cells; Glucocorticoids; Green Fluorescent Proteins; HEK293 Cells; HeLa Cells; Humans; Microscopy, Fluorescence; Progesterone; Protein Binding; Receptors, Glucocorticoid; Steroids; Transcriptional Activation | 2015 |
LC-MS/MS based determination of basal- and ACTH-stimulated plasma concentrations of 11 steroid hormones: implications for detecting heterozygote CYP21A2 mutation carriers.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aged; Androstenedione; Case-Control Studies; Child; Chromatography, Liquid; Corticosterone; Cortisone; Cortodoxone; Desoxycorticosterone; Dihydrotestosterone; Female; Genetic Carrier Screening; Hormones; Humans; Hydrocortisone; Male; Middle Aged; Progesterone; Steroid 21-Hydroxylase; Tandem Mass Spectrometry; Testosterone; Young Adult | 2015 |
Hormonal circadian rhythms in patients with congenital adrenal hyperplasia: identifying optimal monitoring times and novel disease biomarkers.
Topics: 17-alpha-Hydroxyprogesterone; 5-alpha-Dihydroprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Androsterone; Biomarkers; Circadian Rhythm; Cross-Sectional Studies; Dehydroepiandrosterone; Dexamethasone; Female; Glucocorticoids; Hormones; Humans; Male; Prednisone; Pregnanediones; Progesterone; Testosterone; Young Adult | 2015 |
Scalp hair 17-hydroxyprogesterone and androstenedione as a long-term therapy monitoring tool in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Case-Control Studies; Child; Child, Preschool; Chromatography, Liquid; Drug Monitoring; Female; Hair; Humans; Hydrocortisone; Male; Scalp; Tandem Mass Spectrometry; Young Adult | 2016 |
A New Homozygous Frameshift Mutation in the HSD3B2 Gene in an Apparently Nonconsanguineous Italian Family.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Family; Female; Frameshift Mutation; Humans; Infant, Newborn; Italy; Male; Progesterone Reductase; Protein Domains; Renin; Structure-Activity Relationship | 2016 |
[Clinical and genetic analysis of an infant with isolated 17, 20-lyase deficiency].
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Estradiol; Follicle Stimulating Hormone; Genetic Testing; Gonadal Dysgenesis, 46,XY; High-Throughput Nucleotide Sequencing; Humans; Infant; Luteinizing Hormone; Lyases; Male; Mutation; Progesterone; Steroid 17-alpha-Hydroxylase; Testis; Testosterone | 2016 |
Use of steroid profiling by UPLC-MS/MS as a second tier test in newborn screening for congenital adrenal hyperplasia: the Utah experience.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Chromatography, High Pressure Liquid; Female; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Neonatal Screening; Tandem Mass Spectrometry; Utah | 2009 |
Precocious pubarche: distinguishing late-onset congenital adrenal hyperplasia from premature adrenarche.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenarche; Adrenocorticotropic Hormone; Androstenedione; Child; Child, Preschool; Female; Humans; Infant; Male; Puberty, Precocious; Retrospective Studies; Testosterone | 2009 |
Proteomic profiles in hyperandrogenic syndromes.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Dehydroepiandrosterone Sulfate; Electrophoresis, Gel, Two-Dimensional; Estradiol; Female; Follicle Stimulating Hormone; Humans; Hydrocortisone; Hydroxyprogesterones; Hyperandrogenism; Luteinizing Hormone; Mass Spectrometry; Polycystic Ovary Syndrome; Prolactin; Proteomics; Sex Hormone-Binding Globulin; Testosterone; Young Adult | 2010 |
Quantitation of 17-OH-progesterone (OHPG) for diagnosis of congenital adrenal hyperplasia (CAH).
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Chromatography, Liquid; Desoxycorticosterone; Humans; Molecular Structure; Progesterone; Reproducibility of Results; Tandem Mass Spectrometry | 2010 |
Clinical characteristics of Taiwanese children with congenital adrenal hyperplasia caused by 21-hydroxylase deficiency in the pre-screening era.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Dehydroepiandrosterone; Female; Genotype; Humans; Hydrocortisone; Hyponatremia; Infant, Newborn; Male; Phenotype; Pigmentation Disorders; Point Mutation; Pregnancy; Steroid 21-Hydroxylase | 2010 |
Blood pressure in the first year of life in children with congenital adrenal hyperplasia due to 21-hydroxylase deficiency: a pilot study.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Alleles; Androstenedione; Anti-Inflammatory Agents; Blood Pressure; DNA; DNA Mutational Analysis; Female; Fludrocortisone; Humans; Infant; Infant, Newborn; Male; Pilot Projects; Renin; Retrospective Studies; Steroid 21-Hydroxylase | 2010 |
Female pattern hair loss in a patient with 17alpha-hydroxylase deficiency.
Topics: Adrenal Hyperplasia, Congenital; Alopecia; Androstenedione; Biomarkers; Dehydroepiandrosterone Sulfate; Female; Hair Follicle; Humans; Steroid 17-alpha-Hydroxylase; Testosterone; Young Adult | 2010 |
Pilot proficiency testing study for second tier congenital adrenal hyperplasia newborn screening.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Humans; Hydrocortisone; Infant, Newborn; Neonatal Screening; Pilot Projects; Steroids; Tandem Mass Spectrometry | 2010 |
Comparison of multiple steroid concentrations in serum and dried blood spots throughout the day of patients with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Anti-Inflammatory Agents; Blood Specimen Collection; Child; Child, Preschool; Circadian Rhythm; Drug Monitoring; Fludrocortisone; Hormone Replacement Therapy; Humans; Hydrocortisone; Male; Reproducibility of Results | 2011 |
Endocrine profile and phenotype-genotype correlation in unrelated patients with non-classical congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Cyprus; Female; Gene Frequency; Genetic Association Studies; Haplotypes; Humans; Male; Mutation; Severity of Illness Index; Steroid 21-Hydroxylase; Testosterone | 2011 |
Relationships of basal level of serum 17-hydroxyprogesterone with that of serum androstenedione and their stimulated responses to a low dose of ACTH in young adult patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Circadian Rhythm; Female; Humans; Male; Steroid 21-Hydroxylase; Young Adult | 2011 |
[Congenital adrenal hyperplasia due to 21-hydroxylase deficiency--management in adults].
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aged; Androstenedione; Female; Genetic Predisposition to Disease; Genotype; Glucocorticoids; Humans; Male; Middle Aged; Phenotype; Quality of Life; Steroid 21-Hydroxylase; Young Adult | 2010 |
Increased activation of the alternative "backdoor" pathway in patients with 21-hydroxylase deficiency: evidence from urinary steroid hormone analysis.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Androsterone; Child; Child, Preschool; Dihydrotestosterone; Etiocholanolone; Female; Gonadal Steroid Hormones; Humans; Infant; Infant, Newborn; Male; Steroid 17-alpha-Hydroxylase | 2012 |
Correlation between androstenedione and 17-hydroxyprogesterone levels in the saliva and plasma of patients with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Child; Child, Preschool; Disorders of Sex Development; Dose-Response Relationship, Drug; Female; Glucocorticoids; Humans; Hydrocortisone; Infant; Plasma; Saliva; Time Factors | 2011 |
Neonatal screening: identification of children with 11β-hydroxylase deficiency by second-tier testing.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Cortodoxone; False Positive Reactions; Female; Humans; Hydrocortisone; Infant; Infant, Newborn; Male; Neonatal Screening; Steroid 11-beta-Hydroxylase | 2012 |
Testicular adrenal rest tumors in patients with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adrenocorticotropic Hormone; Age Determination by Skeleton; Androstenedione; Child; Child, Preschool; Follow-Up Studies; Humans; Male; Scrotum; Steroid 21-Hydroxylase; Testicular Neoplasms; Treatment Outcome; Ultrasonography | 2012 |
[Determination of serum steroids in monitoring therapy of congenital adrenal hyperplasia].
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Child, Preschool; Dehydroepiandrosterone Sulfate; Female; Humans; Hydrocortisone; Male; Progesterone; Steroid 21-Hydroxylase; Testosterone | 2012 |
Influence of hormonal control on LH pulsatility and secretion in women with classical congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenedione; Case-Control Studies; Female; Hormone Replacement Therapy; Hormones; Humans; Luteinizing Hormone; Progesterone; Testosterone; Young Adult | 2012 |
[Premature pubarche is not always an innocent phenomenon].
Topics: Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone Sulfate; Female; Humans; Hydrocortisone; Puberty, Precocious; Testosterone; Treatment Outcome | 2012 |
BclI polymorphism of the glucocorticoid receptor gene is associated with increased bone resorption in patients on glucocorticoid replacement therapy.
Topics: 17-alpha-Hydroxyprogesterone; Addison Disease; Adrenal Hyperplasia, Congenital; Adult; Aged; Androstenedione; Bone Density; Bone Resorption; Collagen; Collagen Type I; Cross-Sectional Studies; Female; Glucocorticoids; Hormone Replacement Therapy; Humans; Hydrocortisone; Male; Middle Aged; Peptides; Polymorphism, Genetic; Prospective Studies; Receptors, Glucocorticoid | 2013 |
Androgens concentrations and second-to fourth-digit ratio (2D:4D) in girls with congenital adrenal hyperplasia (21-hydroxylase deficiency).
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androgens; Androstenedione; Anti-Inflammatory Agents; Child; Child, Preschool; Dehydroepiandrosterone; Female; Fingers; Humans; Hydrocortisone; Pregnancy; Prenatal Exposure Delayed Effects; Retrospective Studies; Testosterone; Virilism; Young Adult | 2012 |
Cortisol, dehydroepiandrosterone sulfate, and androstenedione levels in patients with polymyalgia rheumatica during twelve months of glucocorticoid therapy.
Topics: Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aged; Aging; Androstenedione; Area Under Curve; Biomarkers; Blood Sedimentation; C-Reactive Protein; Corticotropin-Releasing Hormone; Dehydroepiandrosterone; Female; Humans; Hydrocortisone; Hypothalamo-Hypophyseal System; Inflammation; Interleukin-6; Male; Neuroimmunomodulation; Pituitary-Adrenal System; Polymyalgia Rheumatica; Secretory Rate; Testis | 2002 |
Normal bone mineral density and lean body mass, but increased fat mass, in young adult patients with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adipose Tissue; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Body Composition; Body Mass Index; Bone Density; Female; Glucocorticoids; Humans; Male; Saliva | 2003 |
Virilising adrenocortical tumours in children.
Topics: 17-Hydroxycorticosteroids; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocortical Adenoma; Adrenocortical Carcinoma; Adrenocorticotropic Hormone; Androstenedione; Biomarkers; Child; Child, Preschool; Dehydroepiandrosterone Sulfate; Diagnostic Errors; Disease Progression; Female; Humans; Immunohistochemistry; Infant; Ki-67 Antigen; Magnetic Resonance Imaging; Male; Mutation; Testosterone; Tomography, X-Ray Computed; Tumor Suppressor Protein p53; Ultrasonography, Interventional; Virilism | 2003 |
Monitoring of menstrual cycles, ovulation, and adrenal suppression by saliva sampling in female patients with 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Androstenedione; Female; Humans; Longitudinal Studies; Menstrual Cycle; Ovulation; Population Surveillance; Prospective Studies; Saliva; Steroid 21-Hydroxylase | 2003 |
Improved specificity of newborn screening for congenital adrenal hyperplasia by second-tier steroid profiling using tandem mass spectrometry.
Topics: Adrenal Hyperplasia, Congenital; Androstenedione; Chromatography, Liquid; False Positive Reactions; Humans; Hydrocortisone; Immunoassay; Infant, Newborn; Mass Screening; Progesterone; Sensitivity and Specificity; Spectrometry, Mass, Electrospray Ionization; Steroids | 2004 |
Adrenocortical adenoma associated with inadequately treated congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocortical Adenoma; Adrenocorticotropic Hormone; Androstenedione; Child; Dehydroepiandrosterone Sulfate; Drug Administration Schedule; Glucocorticoids; Hair; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Mixed Function Oxygenases; Patient Compliance; Steroid 21-Hydroxylase; Testosterone; Treatment Failure; Virilism | 2003 |
Asymptomatic testicular adrenal rest tumours in adolescent and adult males with congenital adrenal hyperplasia: basal and follow-up investigation after 2.6 years.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adult; Androstenedione; Dexamethasone; Dose-Response Relationship, Drug; Follicle Stimulating Hormone; Follow-Up Studies; Glucocorticoids; Humans; Hydrocortisone; Luteinizing Hormone; Male; Saliva; Testicular Neoplasms; Testosterone; Ultrasonography | 2004 |
Steroid profiling by tandem mass spectrometry improves the positive predictive value of newborn screening for congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Chromatography, Liquid; Humans; Hydrocortisone; Infant, Newborn; Mass Spectrometry; Neonatal Screening; Predictive Value of Tests; Retrospective Studies; Sensitivity and Specificity; Single-Blind Method | 2004 |
Ketosteroid profiling using Girard T derivatives and electrospray ionization tandem mass spectrometry: direct plasma analysis of androstenedione, 17-hydroxyprogesterone and cortisol.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Humans; Hydrocortisone; Radioimmunoassay; Reproducibility of Results; Spectrometry, Mass, Electrospray Ionization | 2005 |
Hormonal effects in infants conceived by assisted reproductive technology.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Androstenedione; Breast; Chorionic Gonadotropin; Chorionic Gonadotropin, beta Subunit, Human; Dehydroepiandrosterone Sulfate; Estradiol; Estrone; Female; Fertilization in Vitro; Follicle Stimulating Hormone; Hair; Humans; Infant; Infant, Newborn; Luteinizing Hormone; Male; Ovulation Induction; Pregnancy; Puberty, Precocious; Recombinant Proteins; Reproductive Techniques, Assisted; Testosterone | 2005 |
Cognitive outcome in adult women affected by congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: Adrenal Hyperplasia, Congenital; Adult; Aged; Androgens; Androstenedione; Cognition; Dehydroepiandrosterone; Female; Functional Laterality; Humans; Memory; Middle Aged; Pregnancy; Prenatal Exposure Delayed Effects; Space Perception; Steroid 21-Hydroxylase; Testosterone; Verbal Learning | 2006 |
Testicular tumors in patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency show functional features of adrenocortical tissue.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adult; Androstenedione; Cytochrome P-450 CYP11B2; Humans; Male; Middle Aged; Receptors, Angiotensin; Receptors, Corticotropin; RNA, Messenger; Steroid 11-beta-Hydroxylase; Steroid 21-Hydroxylase; Testicular Neoplasms; Testis | 2007 |
Prevalence of testicular adrenal rest tumours in male children with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Age Distribution; Age of Onset; Androstenedione; Child; Child, Preschool; Follow-Up Studies; Humans; Infant; Male; Prevalence; Retrospective Studies; Saliva; Steroid 21-Hydroxylase; Testicular Neoplasms; Testis; Ultrasonography | 2007 |
Bioelectrical impedance analysis of body fatness in childhood congenital adrenal hyperplasia and its metabolic correlates.
Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Androstenedione; Anthropometry; Child; Child, Preschool; Cholesterol; Electric Impedance; Female; Humans; Infant; Insulin; Leptin; Male; Obesity; Progesterone; Skinfold Thickness | 2008 |
Ovarian steroidogenesis in an adrenalectomized girl with 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adrenocorticotropic Hormone; Androstenedione; Depression, Chemical; Dexamethasone; Ethinyl Estradiol; Female; Hormones; Humans; Hydroxyprogesterones; Menotropins; Ovary; Steroid Hydroxylases; Testosterone | 1984 |
Plasma levels of androgens and 17 alpha-OH-progesterone as an index of the adequacy of treatment in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androgens; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Infant; Male; Testosterone | 1983 |
Metabolism and concentration of androgenic steroids in abdominal skin of hirsute women with androgenital syndrome.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Abdominal Muscles; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenediol; Androstenedione; Dehydroepiandrosterone; Female; Hirsutism; Humans; Male; Middle Aged; Pregnanetriol; Skin; Sulfates; Testosterone | 1984 |
Adrenocortical 11 beta-hydroxylation defect in adult women with postmenarchial onset of symptoms.
Topics: 17-Ketosteroids; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androgens; Androstenedione; Blood Pressure; Child; Female; Glucose Tolerance Test; Hirsutism; Humans; Menstruation; Mineralocorticoids; Steroid Hydroxylases; Steroids | 1980 |
Congenital adrenal hyperplasia due to partial 21-hydroxylase deficiency. A study of five cases.
Topics: 3-Oxo-5-alpha-Steroid 4-Dehydrogenase; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstane-3,17-diol; Androstanols; Androstenedione; Female; Hirsutism; Humans; Hydrocortisone; Hydroxyprogesterones; Steroid Hydroxylases; Testosterone | 1981 |
Transient adrenogenital syndrome due to exposure to danazol in utero.
Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Cortodoxone; Cosyntropin; Danazol; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Infant, Newborn; Infant, Premature, Diseases; Maternal-Fetal Exchange; Pregnadienes; Pregnancy; Pregnancy Trimester, First; Renin; Testosterone | 1981 |
Genetic and hormonal characterization of cryptic 21-hydroxylase deficiency.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Child; Dehydroepiandrosterone; Female; Heterozygote; HLA Antigens; Humans; Hydroxyprogesterones; Male; Middle Aged; Pedigree; Steroid 21-Hydroxylase; Steroid Hydroxylases; Testosterone | 1981 |
A comparison of three glucocorticoid suppressive regimes in adults with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Circadian Rhythm; Cortisone; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Depression, Chemical; Dexamethasone; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Pituitary-Adrenal System | 1982 |
Genotyping steroid 21-hydroxylase deficiency: hormonal reference data.
Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Female; Genotype; HLA Antigens; Humans; Hydroxyprogesterones; Kinetics; Male; Steroid 21-Hydroxylase; Steroid Hydroxylases | 1983 |
Acth function in women with the polycystic ovarian syndrome.
Topics: Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Humans; Hydrocortisone; Metyrapone; Polycystic Ovary Syndrome; Testosterone | 1983 |
Amniotic fluid concentrations of delta 5 and delta 4 steroids in fetuses with congenital adrenal hyperplasia due to 21 hydroxylase deficiency and in anencephalic fetuses.
Topics: 17-alpha-Hydroxypregnenolone; Adrenal Hyperplasia, Congenital; Amniotic Fluid; Androstenedione; Anencephaly; Dehydroepiandrosterone; Female; Fetus; Gestational Age; Humans; Hydroxyprogesterones; Male; Pregnancy; Steroid Hydroxylases; Testosterone | 1980 |
Cryptic 21-hydroxylase deficiency in families of patients with classical congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxypregnenolone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Female; HLA Antigens; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Pedigree; Steroid 21-Hydroxylase; Steroid Hydroxylases; Testosterone | 1980 |
Pitfalls in the etiological diagnosis of congenital adrenal hyperplasia in the early neonatal period.
Topics: 3-Hydroxysteroid Dehydrogenases; Adrenal Hyperplasia, Congenital; Androstenedione; Dehydroepiandrosterone; Female; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Longitudinal Studies; Male; Testosterone | 1982 |
Salivary and plasma androstenedione and 17-hydroxyprogesterone levels in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Child, Preschool; Female; Humans; Hydroxyprogesterones; Infant; Male; Saliva | 1983 |
Testicular in vitro conversion of progesterone to testosterone and androstenedione in 17 alpha-hydroxylase deficiency.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Humans; Karyotyping; Male; Progesterone; Reference Values; Sex Chromosomes; Steroid 17-alpha-Hydroxylase; Steroid Hydroxylases; Steroids; Testis; Testosterone | 1982 |
Angiotensin and adrenal steroidogenesis: study of 21-hydroxylase-deficient congenital adrenal hyperplasia.
Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Androstenedione; Angiotensin II; Diet, Sodium-Restricted; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Pregnanetriol; Renin; Steroid Hydroxylases | 1980 |
Plasma progesterone, 17-hydroxyprogesterone, androstenedione and testosterone in prepubertal, pubertal and adult subjects with congenital virilizing adrenal hyperplasia as indicators of adrenal suppression.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Age Factors; Androstenedione; Child; Child, Preschool; Circadian Rhythm; Female; Humans; Hydroxyprogesterones; Infant; Male; Pregnanetriol; Progesterone; Puberty; Sex Factors; Testosterone | 1980 |
Treatment of menstrual irregularities with dexamethasone in congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Dexamethasone; Female; Gonadal Steroid Hormones; Humans; Hydroxyprogesterones; Menstruation Disturbances; Pregnanetriol; Testosterone | 1981 |
Prenatal diagnosis of congenital adrenal hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Adult; Amniocentesis; Amniotic Fluid; Androstenedione; Diseases in Twins; Female; Humans; Hydroxyprogesterones; Karyotyping; Male; Mixed Function Oxygenases; Pregnancy; Prenatal Diagnosis; Virilism | 1980 |
17-hydroxyprogesterone, androstenedione, and testosterone in normal children and in prepubertal patients with congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Age Factors; Androstenedione; Child; Child, Preschool; Female; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Reference Values; Testosterone | 1980 |
Blunted adrenarche in patients with classical congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Humans; Hydroxyprogesterones; Male; Reference Values; Testosterone | 1995 |
An alternate pathway to androstenedione synthesis by human adrenals: evidence of a balance in 11 beta-hydroxylase and 17,20-lyase activities leading to androstenedione.
Topics: Adenoma; Adolescent; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Aged; Aldehyde-Lyases; Aminoglutethimide; Androstenedione; Carcinoma; Child; Cytochrome P-450 Enzyme System; Female; Humans; Hyperaldosteronism; Male; Metyrapone; Middle Aged; Steroid 11-beta-Hydroxylase; Steroid 17-alpha-Hydroxylase | 1995 |
'Exaggerated adrenarche' in children presenting with premature adrenarche.
Topics: 17-alpha-Hydroxypregnenolone; 17-alpha-Hydroxyprogesterone; Adrenal Cortex Diseases; Adrenal Cortex Function Tests; Adrenal Cortex Hormones; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Humans; Hydroxyprogesterones; Male; Retrospective Studies; Testosterone | 1995 |
Prepubertal acne: a cutaneous marker of androgen excess?
Topics: 17-alpha-Hydroxyprogesterone; Acne Vulgaris; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Age Determination by Skeleton; Age of Onset; Androgens; Androstenedione; Basal Metabolism; Biomarkers; Child; Child, Preschool; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Heterozygote; Humans; Hydroxyprogesterones; Male; Puberty; Sexual Maturation; Steroid 21-Hydroxylase; Testosterone | 1995 |
Androgen-related effects on peripheral glucose metabolism in women with congenital adrenal hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenedione; Blood Glucose; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Fatty Acids, Nonesterified; Female; Forearm; Glucose Tolerance Test; Humans; Insulin; Kinetics; Middle Aged; Testosterone | 1994 |
Serum 3 alpha-androstanediol glucuronide measurements in children with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstane-3,17-diol; Androstenedione; Child, Preschool; Cross-Sectional Studies; Dihydrotestosterone; Female; Follow-Up Studies; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Testosterone | 1994 |
Isolated precocious pubarche: an approach.
Topics: 17-alpha-Hydroxypregnenolone; 17-alpha-Hydroxyprogesterone; 3-Hydroxysteroid Dehydrogenases; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Child; Dehydroepiandrosterone; Diagnosis, Differential; Female; HLA-B Antigens; HLA-B14 Antigen; HLA-DR1 Antigen; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Puberty; Puberty, Precocious; Testosterone | 1994 |
Dynamics of 24-hour pulsatile cortisol, 17-hydroxyprogesterone, and androstenedione release in prepubertal patients with nonclassic 21-hydroxylase deficiency and normal prepubertal children.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aging; Androstenedione; Child; Circadian Rhythm; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Puberty; Radioimmunoassay | 1994 |
Prenatal dexamethasone treatment in pregnancies at risk for congenital adrenal hyperplasia due to 21-hydroxylase deficiency: effect on midgestational amniotic fluid steroid levels.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Aldosterone; Amniocentesis; Amniotic Fluid; Androstenedione; Corticosterone; Cortisone; Cortodoxone; Dexamethasone; Female; Gestational Age; Humans; Hydrocortisone; Hydroxyprogesterones; Pregnancy; Pregnancy Trimester, Second; Prenatal Diagnosis; Risk Factors; Steroids | 1993 |
3 beta-hydroxysteroid dehydrogenase deficiency in hyperandrogenism.
Topics: 17-alpha-Hydroxypregnenolone; 17-alpha-Hydroxyprogesterone; 3-Hydroxysteroid Dehydrogenases; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenedione; Cosyntropin; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Follicle Stimulating Hormone; Humans; Hydroxyprogesterones; Luteinizing Hormone; Prospective Studies; Sex Hormone-Binding Globulin; Testosterone | 1993 |
Untreated congenital adrenal hyperplasia presenting with severe androgenic alopecia.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Alopecia; Androstenedione; Female; Humans; Hydroxyprogesterones; Middle Aged; Testosterone; Virilism | 1993 |
Pituitary-ovarian responses to leuprolide acetate testing in patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxypregnenolone; 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Dehydroepiandrosterone; Estradiol; Female; Follicle Stimulating Hormone; Humans; Hydroxyprogesterones; Kinetics; Leuprolide; Luteinizing Hormone; Ovary; Pituitary Gland; Testosterone | 1996 |
Hormonal and genetic analysis of a patient with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Acne Vulgaris; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Clitoris; Cortodoxone; Dehydroepiandrosterone; Female; Gonadal Steroid Hormones; Hirsutism; Histocompatibility Testing; Humans; Hydroxyprogesterones; Hyperpigmentation; Testosterone; Urinary Tract Infections | 1996 |
Studies of 3 beta-hydroxysteroid dehydrogenase genes in infants and children manifesting premature pubarche and increased adrenocorticotropin-stimulated delta 5-steroid levels.
Topics: 17-alpha-Hydroxypregnenolone; 3-Hydroxysteroid Dehydrogenases; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Case-Control Studies; Child; Child, Preschool; Dehydroepiandrosterone; Female; Humans; Hydrocortisone; Infant; Male; Mutation; Polymerase Chain Reaction; Puberty, Precocious | 1996 |
The prevalence of non-classic adrenal hyperplasia due to 11 beta-hydroxylase deficiency among hirsute women in a Turkish population.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Cortodoxone; Cosyntropin; Female; Hirsutism; Humans; Prevalence; Testosterone; Turkey | 1996 |
Bone turnover and bone mineral density in patients with congenital adrenal hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Adult; Aged; Androstenedione; Bone and Bones; Bone Density; Bone Remodeling; Case-Control Studies; Dehydroepiandrosterone Sulfate; Female; Glucocorticoids; Humans; Male; Middle Aged | 1996 |
Growth pattern during the first 36 months of life in congenital adrenal hyperplasia (21-hydroxylase deficiency).
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Age Determination by Skeleton; Androstenedione; Body Height; Body Weight; Child, Preschool; Cortisone; Female; Fludrocortisone; Growth; Humans; Infant; Male | 1997 |
Plasma 3 alpha-androstanediol glucuronide in normal children and in congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Aging; Androstane-3,17-diol; Androstenedione; Child; Child, Preschool; Female; Humans; Infant; Male; Reference Values; Testosterone | 1997 |
Newborn screening for 21-hydroxylase deficiency: results of CYP21 molecular genetic analysis.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Alleles; Androstenedione; Exons; Female; Gene Conversion; Genotype; Humans; Infant, Newborn; Introns; Male; Mineralocorticoids; Molecular Biology; Mutation; Neonatal Screening; Nucleic Acid Hybridization; Phenotype; Polymerase Chain Reaction; Polymorphism, Restriction Fragment Length; Polymorphism, Single-Stranded Conformational; Progesterone; RNA Splicing; Sequence Analysis, DNA; Steroid 21-Hydroxylase; Virilism | 1997 |
[Defects of adrenal steroidogenesis in patients with hirsutism].
Topics: 17-alpha-Hydroxypregnenolone; 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Anabolic Agents; Androstenediol; Androstenedione; Cortodoxone; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Estradiol; Female; Follicle Stimulating Hormone; Hirsutism; Humans; Hydrocortisone; Hydroxysteroid Dehydrogenases; Luteinizing Hormone; Menstrual Cycle; Middle Aged; Progesterone; Prolactin; Radioimmunoassay; Testosterone | 1998 |
Variants of the type II 3beta-hydroxysteroid dehydrogenase gene in children with premature pubic hair and hyperandrogenic adolescents.
Topics: 17-alpha-Hydroxyprogesterone; 17-Hydroxycorticosteroids; 3-Hydroxysteroid Dehydrogenases; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Amino Acid Sequence; Androstenedione; Breast; Child; Female; Genetic Variation; Heterozygote; Hirsutism; Humans; Hyperandrogenism; Male; Oligomenorrhea; Pedigree; Polymorphism, Single-Stranded Conformational; Puberty, Precocious | 1998 |
Profiling steroid hormones in amniotic fluid of midpregnancy by routine stable isotope dilution/gas chromatography-mass spectrometry: reference values and concentrations in fetuses at risk for 21-hydroxylase deficiency.
Topics: Adrenal Hyperplasia, Congenital; Amniotic Fluid; Androstenedione; Female; Gas Chromatography-Mass Spectrometry; Gonadal Steroid Hormones; Humans; Male; Pregnancy; Reference Values; Risk; Sex Factors; Testosterone | 1999 |
11beta-hydroxyandrostenedione and delta5-androstenediol as markers of adrenal androgen production in patients with 21-hydroxylase-deficient nonclassic adrenal hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenedione; Biomarkers; Body Mass Index; Case-Control Studies; Female; Humans; Reproducibility of Results; Sensitivity and Specificity | 1999 |
[A hairy case].
Topics: Adrenal Hyperplasia, Congenital; Alopecia; Androstenedione; Dehydroepiandrosterone Sulfate; Dexamethasone; Diagnosis, Differential; Female; Gonadotropin-Releasing Hormone; Goserelin; Hirsutism; Humans; Hydrocortisone; Middle Aged; Polycystic Ovary Syndrome; Testosterone; Treatment Outcome | 1999 |
Pituitary gonadal axis and child rate in males with classical 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Body Height; Body Mass Index; Cross-Sectional Studies; Dehydroepiandrosterone Sulfate; Finland; Follicle Stimulating Hormone; Glucocorticoids; Humans; Inhibins; Male; Pituitary Gland; Reference Values; Testis | 2000 |
Measurement of androstenedione levels by an in-house radioimmunoassay.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Child, Preschool; Circadian Rhythm; Female; Humans; Infant; Infant, Newborn; Infant, Premature; Infant, Premature, Diseases; Male; Middle Aged; Pregnancy; Puberty; Radioimmunoassay; Reference Values; Reproducibility of Results; Sensitivity and Specificity | 1996 |
Adrenocortical hyperresponsivity to adrenocorticotropic hormone: a mechanism favoring the normal production of cortisol in 21-hydroxylase-deficient nonclassic adrenal hyperplasia.
Topics: 17-alpha-Hydroxypregnenolone; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Case-Control Studies; Cortodoxone; Dehydroepiandrosterone; Female; Hirsutism; Humans; Hydrocortisone; Pregnenolone; Progesterone; Prospective Studies; Steroid 21-Hydroxylase | 2000 |
Hydrocortisone suspension and hydrocortisone tablets are not bioequivalent in the treatment of children with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Anti-Inflammatory Agents; Child; Child, Preschool; Dose-Response Relationship, Drug; Female; Fludrocortisone; Humans; Hydrocortisone; Male; Retreatment; Suspensions; Tablets; Therapeutic Equivalency | 2001 |
Deletion hybrid genes, due to unequal crossing over between CYP11B1 (11beta-hydroxylase) and CYP11B2(aldosterone synthase) cause steroid 11beta-hydroxylase deficiency and congenital adrenal hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Androstenedione; Animals; Blotting, Southern; Child, Preschool; Cortodoxone; COS Cells; Crossing Over, Genetic; Cyproterone Acetate; Cytochrome P-450 CYP11B2; DNA, Complementary; Exons; Gene Deletion; Gene Expression; Homozygote; Humans; Male; Polymerase Chain Reaction; Promoter Regions, Genetic; Puberty, Precocious; Renin; Steroid 11-beta-Hydroxylase; Transfection | 2001 |
High prevalence of testicular adrenal rest tumors, impaired spermatogenesis, and Leydig cell failure in adolescent and adult males with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adult; Androstenedione; Follicle Stimulating Hormone; Humans; Leydig Cells; Luteinizing Hormone; Male; Oligospermia; Prevalence; Saliva; Semen; Spermatogenesis; Testicular Neoplasms; Testis; Testosterone; Ultrasonography | 2001 |
Adrenal progestogen and androgen production in 21-hydroxylase-deficient nonclassic adrenal hyperplasia is partially independent of adrenocorticotropic hormone stimulation.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androgens; Androstenedione; Dehydroepiandrosterone; Dexamethasone; Female; Glucocorticoids; Humans; Hydrocortisone; Kinetics; Leuprolide; Middle Aged; Progesterone; Progestins; Prospective Studies; Steroid 21-Hydroxylase | 2002 |
Serum androgens as a continuing index of adequacy of treatment of congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Androgens; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Female; Humans; Hydrocortisone; Infant; Male; Testosterone | 1978 |
Plasma androgens in congenital adrenal hyperplasia: androstenedione concentration as an index of adrenal androgen suppression.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Female; Glucocorticoids; Humans; Male; Pregnanetriol; Testosterone | 1979 |
Serum androgen concentrations in neonates and young infants with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
Topics: Adrenal Hyperplasia, Congenital; Age Factors; Androgens; Androstenedione; Dehydroepiandrosterone; Female; Fetal Blood; Glucocorticoids; Humans; Hydroxyprogesterones; Infant; Infant, Newborn; Male; Sex Factors; Steroid Hydroxylases; Testosterone | 1979 |
"Acquired" adrenal hyperplasia with 21-hydroxylase deficiency is not the same genetic disorders as congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Androstenedione; Dehydroepiandrosterone; Female; Histocompatibility Antigens; Humans; Hydrocortisone; Hydroxyprogesterones; Hyperplasia; Steroid Hydroxylases; Testosterone | 1979 |
Adrenal steroid dynamics in congenital adrenal hyperplasia: evaluation by simultaneous bilateral adrenal venous catheterization.
Topics: Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; Androgens; Androstenedione; Child; Child, Preschool; Dexamethasone; Dihydrotestosterone; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Progesterone; Testosterone | 1979 |
Comparison of two tests for heterozygosity in congenital adrenal hyperplasia (CAH).
Topics: Adrenal Cortex Function Tests; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Androstenedione; Dexamethasone; Evaluation Studies as Topic; Female; Heterozygote; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Pituitary-Adrenal Function Tests; Testosterone | 1979 |
Sex hormones and female homosexuality: a critical examination.
Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Androgens; Androstenedione; Animals; Estradiol; Estrogens; Estrone; Feedback; Female; Follicle Stimulating Hormone; Gonadal Steroid Hormones; Homosexuality; Humans; Luteinizing Hormone; Sex Differentiation; Sexual Behavior; Somatotypes; Testosterone; Transsexualism | 1979 |
The use of plasma androstenedione in monitoring therapy of patients with congenital adrenal hyperplasia.
Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Age Factors; Androstenedione; Child; Cortisone; Female; Humans; Infant; Longitudinal Studies; Male; Prednisone; Sex Factors; Testosterone | 1979 |
[17-hydroxyprogesterone, testosterone and androstenedione in treated congenital adrenogenital syndrome].
Topics: Adrenal Hyperplasia, Congenital; Androstenedione; Circadian Rhythm; Humans; Hydrocortisone; Hydroxyprogesterones; Testosterone | 1977 |
Plasma androgens in premature pubarche: value of 17alpha-hydroxyprogesterone in differentiation from congenital adrenal hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Androstenedione; Child; Diagnosis, Differential; Female; Humans; Hydroxyprogesterones; Male; Puberty, Precocious; Radioimmunoassay; Testosterone | 1975 |
Idiopathic hirsutism--an ovarian abnormality.
Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Androstenedione; Depression, Chemical; Dexamethasone; Diagnosis, Differential; Female; Hirsutism; Humans; Hydrocortisone; Menstruation Disturbances; Obesity; Ovary; Secretory Rate; Testosterone | 1976 |
The incidence of non-classical 21-hydroxylase deficiency in hirsute adolescent girls.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Follicle Stimulating Hormone; Hirsutism; Humans; Hydrocortisone; Hydroxyprogesterones; Luteinizing Hormone; Prolactin; Testosterone | 1992 |
Investigation of adrenal function in women with oligomenorrhoea and hirsutism (clinical PCOS) from the north-east of England using an adrenal stimulation test.
Topics: 3-Hydroxysteroid Dehydrogenases; Adrenal Cortex Function Tests; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Dehydroepiandrosterone; Dexamethasone; Female; Humans; Polycystic Ovary Syndrome; Prospective Studies; Steroid 17-alpha-Hydroxylase | 1992 |
Adrenal steroidogenic defects in children with precocious pubarche.
Topics: 17-alpha-Hydroxypregnenolone; 17-alpha-Hydroxyprogesterone; Adrenal Cortex Hormones; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Female; Humans; Hydroxyprogesterones; Infant; Male; Puberty, Precocious | 1992 |
Ambiguous genitalia due to partial activity of cytochromes P450c17 and P450c21.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Androstenedione; Chorionic Gonadotropin; Chromosomes, Human, Pair 10; Chromosomes, Human, Pair 6; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Disorders of Sex Development; Female; Histocompatibility Testing; Humans; Hydrocortisone; Hydroxyprogesterones; Infant; Male; Mutation; Pedigree; Progesterone; Sincalide; Testosterone | 1992 |
The ratio of androstenedione:11 beta-hydroxyandrostenedione is an important marker of adrenal androgen excess in women.
Topics: Adolescent; Adrenal Gland Diseases; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenedione; Biomarkers; Dexamethasone; Female; Humans; Hyperplasia; Prospective Studies; Radioimmunoassay | 1992 |
3 alpha-Androstanediol glucuronide in premature and normal pubarche.
Topics: 3-Hydroxysteroid Dehydrogenases; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androgens; Androstane-3,17-diol; Androstenedione; Child; Child, Preschool; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Humans; Infant; Male; Puberty, Precocious; Testosterone | 1991 |
3 alpha-androstanediol glucuronide in virilizing congenital adrenal hyperplasia: a useful serum metabolic marker of integrated adrenal androgen secretion.
Topics: 17-alpha-Hydroxyprogesterone; 17-Ketosteroids; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstane-3,17-diol; Androstenedione; Child; Child, Preschool; Circadian Rhythm; Cortodoxone; Dexamethasone; Female; Humans; Hydroxyprogesterones; Testosterone | 1991 |
Plasma insulin-like growth factor I levels during treatment of congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Biomarkers; Child; Child, Preschool; Female; Follow-Up Studies; Humans; Infant; Insulin-Like Growth Factor I; Male | 1990 |
11 beta-hydroxyandrostenedione in human amniotic fluid.
Topics: Adrenal Hyperplasia, Congenital; Amniotic Fluid; Androstenedione; Female; Humans; Male; Pregnancy; Prenatal Diagnosis; Reference Values | 1990 |
On the origin of the elevated 17-hydroxyprogesterone levels after adrenal stimulation in hyperandrogenism.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adult; Androgens; Androstenedione; Cosyntropin; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Humans; Hydroxyprogesterones; Middle Aged; Polycystic Ovary Syndrome; Radioimmunoassay; Testosterone | 1990 |
Inappropriate adrenal androgen secretion with once-a-day corticosteroid therapy for congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androgens; Androstenedione; Child; Cortisone; Drug Administration Schedule; Female; Humans; Hydroxyprogesterones; Male; Testosterone | 1990 |
Pituitary-adrenal responses to corticotropin-releasing factor in late onset 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Corticotropin-Releasing Hormone; Female; Hirsutism; Humans; Hydroxyprogesterones; Pituitary Gland; Steroid Hydroxylases; Testosterone | 1990 |
ACTH stimulation tests and plasma dehydroepiandrosterone sulfate levels in women with hirsutism.
Topics: 17-alpha-Hydroxypregnenolone; 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Cortodoxone; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Diagnosis, Differential; Female; Hirsutism; Humans; Hydrocortisone; Hydroxyprogesterones; Progesterone | 1990 |
[Diagnosis of the heterozygote carrier state in 21-hydroxylase deficiency using steroids].
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex Function Tests; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Female; Genetic Carrier Screening; Humans; Hydrocortisone; Hydroxyprogesterones; Male | 1990 |
Serum levels of 5-androstene-3 beta,17 beta-diol sulphate, 5 alpha-androstane-3 alpha, 17beta-diol sulphate and glucuronide, in late onset 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstane-3,17-diol; Androstenediol; Androstenedione; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Female; Glucuronates; Hirsutism; Humans; Hydroxyprogesterones; Sex Hormone-Binding Globulin; Sulfates; Testosterone | 1990 |
[Use of steroid indicators in monitoring the treatment of congenital adrenal hyperplasia].
Topics: 17-alpha-Hydroxyprogesterone; 17-Ketosteroids; Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Child, Preschool; Humans; Hydroxyprogesterones; Infant | 1990 |
Daily profiles of salivary cortisol in hydrocortisone treated children with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Case-Control Studies; Child; Child, Preschool; Circadian Rhythm; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Regression Analysis; Saliva | 1990 |
An update on the frequency of nonclassic deficiency of adrenal 21-hydroxylase in the Yugoslav population.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Glands; Adrenal Hyperplasia, Congenital; Androstenedione; Female; Gene Frequency; HLA-B Antigens; HLA-B14 Antigen; HLA-DR1 Antigen; Humans; Hydroxyprogesterones; Male; Pedigree; Steroid Hydroxylases; Yugoslavia | 1990 |
Steroid secretion by granulosa cells isolated from a woman with 17 alpha-hydroxylase deficiency.
Topics: Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Body Fluids; Cells, Cultured; Estrogens; Female; Follicular Phase; Granulosa Cells; Humans; Hydroxyprogesterones; Luteal Phase; Progesterone; Steroid 17-alpha-Hydroxylase; Steroid Hydroxylases; Testosterone | 1990 |
A 'blood spot' androstenedione radioimmunoassay able to detect congenital adrenal hyperplasia.
Topics: Adrenal Hyperplasia, Congenital; Androstenedione; Biomarkers; Blood Specimen Collection; Humans; Infant, Newborn; Infant, Premature; Radioimmunoassay | 1989 |
Alternate day prednisone therapy in congenital adrenal hyperplasia: adrenal androgen suppression and normal growth.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androgens; Androstenedione; Child; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Drug Administration Schedule; Female; Growth Disorders; Humans; Hydroxyprogesterones; Prednisone | 1989 |
[Hypertensinogenic steroid].
Topics: 17-alpha-Hydroxyprogesterone; 18-Hydroxydesoxycorticosterone; Adrenal Hyperplasia, Congenital; Androstenedione; Blood Pressure; Cushing Syndrome; Humans; Hydroxyprogesterones; Hyperaldosteronism; Hypertension | 1989 |
[Clinical significance of serum androstenedione analysis in endocrine tests of the adrenal cortex].
Topics: Adrenal Cortex Function Tests; Adrenal Hyperplasia, Congenital; Androstenedione; Female; Humans; Male; Pregnancy; Radioimmunoassay; Reference Values; Specimen Handling | 1989 |
A bloodspot androstenedione assay suitable for home-monitoring of steroid replacement therapy in congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Child, Preschool; Evaluation Studies as Topic; Female; Humans; Hydroxyprogesterones; Immunologic Techniques; Infant; Infant, Newborn; Male; Monitoring, Physiologic; Reference Values; Self Care; Sensitivity and Specificity | 1989 |
A 125I-radioimmunoassay for measuring androstenedione in serum and in blood-spot samples from neonates.
Topics: Adrenal Hyperplasia, Congenital; Adult; Aged; Androstenedione; Female; Humans; Infant, Newborn; Infant, Premature; Iodine Radioisotopes; Male; Middle Aged; Polycystic Ovary Syndrome; Radioimmunoassay; Respiratory Distress Syndrome, Newborn | 1989 |
The hypothalamic-pituitary-adrenal axis in partial (late-onset) 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Animals; Child; Child, Preschool; Circadian Rhythm; Corticotropin-Releasing Hormone; Female; Humans; Hydrocortisone; Hydroxyprogesterones; Hypothalamo-Hypophyseal System; Male; Pituitary-Adrenal System; Sheep; Steroid Hydroxylases; Time Factors | 1988 |
Screening heterozygotes for 21-hydroxylase deficiency among hirsute women: lack of utility of the adrenocorticotropin hormone test.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Dehydroepiandrosterone; Female; Genetic Carrier Screening; Hirsutism; HLA Antigens; Humans; Hydroxyprogesterones; Middle Aged; Progesterone; Steroid 21-Hydroxylase; Steroid Hydroxylases; Testosterone | 1988 |
Effects of long term dexamethasone treatment in adult patients with congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Dexamethasone; Female; Follow-Up Studies; Humans; Hydroxyprogesterones; Male; Ovulation; Time Factors | 1987 |
Male pseudohermaphroditism due to multiple defects in steroid-biosynthetic microsomal mixed-function oxidases. A new variant of congenital adrenal hyperplasia.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; 18-Hydroxycorticosterone; 18-Hydroxydesoxycorticosterone; Adrenal Hyperplasia, Congenital; Aldehyde-Lyases; Aldosterone; Androstenedione; Corticosterone; Cortodoxone; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Desoxycorticosterone; Dihydrotestosterone; Disorders of Sex Development; Humans; Hydrocortisone; Infant; Male; Mixed Function Oxygenases; Pregnenolone; Progesterone; Steroid Hydroxylases; Testosterone | 1985 |
Primary aldosteronism treated by trilostane (3 beta-hydroxysteroid dehydrogenase inhibitor).
Topics: 17-Hydroxycorticosteroids; Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androstenedione; Dehydroepiandrosterone; Desoxycorticosterone; Dihydrotestosterone; Estradiol; Female; Humans; Hydroxysteroid Dehydrogenases; Hyperaldosteronism; Male; Middle Aged; Oxidative Phosphorylation Coupling Factors; Progesterone; Radioimmunoassay; Renin-Angiotensin System; Testosterone | 1985 |
Late-onset adrenal hyperplasia in hirsutism.
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Androgens; Androstenedione; Female; Heterozygote; Hirsutism; HLA Antigens; Homozygote; Humans; Hydrocortisone; Hydroxyprogesterones | 1985 |
Genotype and hormonal phenotype in nonclassical 21-hydroxylase deficiency.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstenedione; Female; Genotype; Heterozygote; Homozygote; Humans; Hydrocortisone; Hydroxyprogesterones; Male; Phenotype; Steroid 21-Hydroxylase; Steroid Hydroxylases | 1987 |
Elevated 17-hydroxyprogesterone and testosterone in a newborn with 3-beta-hydroxysteroid dehydrogenase deficiency.
Topics: 17-alpha-Hydroxypregnenolone; 17-alpha-Hydroxyprogesterone; 20-Hydroxysteroid Dehydrogenases; Adrenal Hyperplasia, Congenital; Androstenedione; Cortisone Reductase; Dehydroepiandrosterone; Humans; Hydroxyprogesterones; Hypospadias; Infant, Newborn; Male; Testosterone | 1985 |
Androstenedione rhythms in saliva in congenital adrenal hyperplasia.
Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Child; Child, Preschool; Circadian Rhythm; Female; Humans; Male; Puberty; Saliva; Testosterone | 1988 |
Pitfalls of prenatal diagnosis of 21-hydroxylase deficiency congenital adrenal hyperplasia.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Amniotic Fluid; Androstenedione; Female; Genotype; Heterozygote; HLA Antigens; Homozygote; Humans; Hydroxyprogesterones; Male; Pregnancy; Prenatal Diagnosis; Risk; Steroid Hydroxylases | 1985 |
Pitfalls in prenatal diagnosis of 21-hydroxylase deficiency by amniotic fluid steroid analysis? A six years experience in 102 pregnancies at risk.
Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Amniotic Fluid; Androstenedione; Female; Fetal Diseases; Genetic Counseling; Histocompatibility Testing; Humans; Hydroxyprogesterones; Infant, Newborn; Karyotyping; Male; Pedigree; Pregnancy; Prenatal Diagnosis; Risk; Steroid Hydroxylases; Testosterone | 1985 |
[Kinetics of the testicular steroidogenic response to stimulation by placental gonadotropin hormone. VI. Enzyme deficiencies of testicular biosynthesis].
Topics: 17-Hydroxysteroid Dehydrogenases; 3-Hydroxysteroid Dehydrogenases; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aldehyde-Lyases; Algestone; Androstenedione; Child; Child, Preschool; Chorionic Gonadotropin; Dihydrotestosterone; Estradiol; Estrone; Humans; Infant; Kinetics; Male; Oxidoreductases; Testis; Testosterone | 1985 |
[Value of the assay of plasma steroids in the control of congenital adrenal hyperplasia].
Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Androstenedione; Body Height; Child, Preschool; Female; Follow-Up Studies; Humans; Hydrocortisone; Hydroxyprogesterones; Infant; Male; Testosterone; Time Factors | 1985 |
Non-tumorous feminizing adrenogenital syndrome in the male subject.
Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Androstenedione; Androsterone; Estrogens; Feminization; Gynecomastia; Humans; Hydrocortisone; Male; Pituitary-Adrenal Function Tests; Pregnanetriol; Sex Chromatin; Spermatogenesis; Testis; Testosterone | 1973 |