anandamide and Hermanski-Pudlak-Syndrome

anandamide has been researched along with Hermanski-Pudlak-Syndrome* in 1 studies

Other Studies

1 other study(ies) available for anandamide and Hermanski-Pudlak-Syndrome

ArticleYear
CB
    Clinical and translational medicine, 2021, Volume: 11, Issue:7

    Hermansky-Pudlak syndrome (HPS) is a rare genetic disorder which, in its most common and severe form, HPS-1, leads to fatal adult-onset pulmonary fibrosis (PF) with no effective treatment. We evaluated the role of the endocannabinoid/CB

    Topics: Adult; Animals; Antifibrotic Agents; Arachidonic Acids; Bleomycin; Bronchoalveolar Lavage Fluid; Disease Models, Animal; Endocannabinoids; Female; Fibroblasts; Hermanski-Pudlak Syndrome; Humans; Interleukin-11; Lung; Male; Mice, Inbred C57BL; Middle Aged; Nitric Oxide Synthase Type II; Polyunsaturated Alkamides; Pulmonary Fibrosis; Receptor, Cannabinoid, CB1; Transforming Growth Factor beta1

2021