ammonium hydroxide has been researched along with Phenylketonurias in 21 studies
azane : Saturated acyclic nitrogen hydrides having the general formula NnHn+2.
Phenylketonurias: A group of autosomal recessive disorders marked by a deficiency of the hepatic enzyme PHENYLALANINE HYDROXYLASE or less frequently by reduced activity of DIHYDROPTERIDINE REDUCTASE (i.e., atypical phenylketonuria). Classical phenylketonuria is caused by a severe deficiency of phenylalanine hydroxylase and presents in infancy with developmental delay; SEIZURES; skin HYPOPIGMENTATION; ECZEMA; and demyelination in the central nervous system. (From Adams et al., Principles of Neurology, 6th ed, p952).
| Excerpt | Relevance | Reference |
|---|---|---|
| "Today we know a great number of inborn errors of metabolism which can be treated by a special diet." | 1.27 | [Nutrition in congenital metabolic diseases]. ( Plöchl, E, 1984) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 21 (100.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| HARRIS, MM | 1 |
| ROTH, RT | 1 |
| HARRIS, RS | 1 |
| TSUKADA, Y | 2 |
| Efron, ML | 1 |
| Plöchl, E | 1 |
| Giovannini, M | 1 |
| Stival, G | 1 |
| Riva, E | 1 |
| Motta, G | 1 |
| Fumero, S | 1 |
| Chang, TM | 1 |
| Peterson, K | 1 |
| Slover, R | 1 |
| Gass, S | 1 |
| Seltzer, WK | 1 |
| McCabe, LL | 1 |
| McCabe, ER | 1 |
| Kolodny, EH | 1 |
| Yatziv, S | 1 |
| Holtzman, NA | 1 |
| Rett, A | 2 |
| Stöckl, W | 1 |
| Ampola, MG | 1 |
| Frézal, J | 1 |
| Menne, F | 1 |
| O'Reilly, S | 1 |
| D'iachkova, AIa | 1 |
| Lebedev, BV | 1 |
| Menkes, JH | 1 |
| Martin, JJ | 1 |
| Schlote, W | 1 |
| Moya, G | 1 |
| Giménez Roldán, S | 1 |
| McKean, CM | 1 |
| Peterson, NA | 1 |
4 reviews available for ammonium hydroxide and Phenylketonurias
| Article | Year |
|---|---|
Dietary treatment of inborn errors of metabolism.
Topics: Ammonia; Carbohydrate Metabolism, Inborn Errors; Diet Therapy; Female; Fructose; Galactosemias; Glyc | 1970 |
Phenylketonuria and other disorders of amino acid metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Child, Preschool; Counseling; Cystathionine; C | 1973 |
[Feeble mindedness caused by genetic disorders of amino acid metabolism].
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Glycine; Hartnup Disease; Histi | 1968 |
[Mental retardation and hereditary enzymopathy (review)].
Topics: Ammonia; Carboxy-Lyases; Child; Child, Preschool; Eye Diseases; Galactosemias; Growth Disorders; Har | 1971 |
17 other studies available for ammonium hydroxide and Phenylketonurias
| Article | Year |
|---|---|
Studies regarding glutamine and ammonia in the cerebrospinal fluid of patients with nervous and mental diseases (with some observations on insulin hypoglycemic shock and oligophrenia phenylpyruvica).
Topics: Ammonia; Cerebrospinal Fluid; Glutamine; Humans; Hypoglycemic Agents; Insulin; Intellectual Disabili | 1945 |
[AMINO ACID METABOLISM IN THE BRAIN AND BEHAVIORAL CHANGES].
Topics: Amino Acids; Aminobutyrates; Ammonia; Animals; Aspartic Acid; Behavior, Animal; Brain; Carbon Isotop | 1964 |
Diet therapy for inborn errors of amino acid metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child, Preschool; Coenzymes; Cystinuria; Diet Therapy | 1967 |
[Nutrition in congenital metabolic diseases].
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Carbohydrate Metabolism, Inborn Errors; | 1984 |
[Blood ammonia and blood levels of various amino acids in phenylketonuria].
Topics: Amino Acids; Ammonia; Child; Child, Preschool; Humans; Infant; Phenylketonurias | 1977 |
Medical applications of artificial cells in transfusion, phenylketonuria, essential amino acid production, and liver support.
Topics: Amino Acids, Essential; Ammonia; Artificial Organs; Biomedical Engineering; Blood Substitutes; Blood | 1988 |
Blood phenylalanine estimation for the patient with phenylketonuria using a portable device.
Topics: Ammonia; Blood Specimen Collection; Colorimetry; Humans; Monitoring, Physiologic; Phenylalanine; Phe | 1988 |
Laboratory approaches for inherited neurometabolic diseases.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Galactosemias; Homocystinuria; Humans; Lactates; Lact | 1985 |
[Studies on the ammonia content in the serum of children with brain damage with special reference to hyperammonemia].
Topics: Ammonia; Athetosis; Birth Injuries; Brain; Brain Damage, Chronic; Child; Child, Preschool; Down Synd | 1968 |
Medical physiopathology, enzymology and diagnosis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Homocystinuria; Humans; Intellectual Disability; Mapl | 1972 |
Amino acid metabolism and its relation to brain functions.
Topics: Amino Acids; Ammonia; Animals; Brain; Brain Chemistry; Conditioning, Classical; Electric Stimulation | 1966 |
Neurologic disorders and liver disease.
Topics: Adipose Tissue; Ammonia; Brain Diseases; Citrulline; Fatty Liver; Galactosemias; Hepatic Encephalopa | 1971 |
Biochemical approaches to the nosology of nervous system defects, III.
Topics: Ammonia; Biopsy; Brain; Brain Chemistry; Brain Diseases; Cells, Cultured; Chromatography; Fabry Dise | 1971 |
Central nervous system lesions in disorders of amino-acid metabolism. A neuropathological study.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Brain; Central Nervous System; Chi | 1972 |
[Aminoacidurias. 3. A case of phenylketonuria with involuntary movements].
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Humans; Male; Movement Disorders; Pedigre | 1969 |
Absence of high blood ammonia in experimental and genetic phenylketonuria.
Topics: Adolescent; Adult; Ammonia; Animals; Humans; Phenylalanine; Phenylketonurias; Rats | 1968 |
[On the diagnosis and therapy of metabolic brain damage in childhood].
Topics: Ammonia; Brain Damage, Chronic; Child; Child, Preschool; Diet Therapy; Female; Humans; Male; Metabol | 1969 |