ammonium hydroxide has been researched along with Deficiency, Muscle Phosphorylase in 20 studies
azane : Saturated acyclic nitrogen hydrides having the general formula NnHn+2.
| Excerpt | Relevance | Reference |
|---|---|---|
| "To examine metabolism during exercise in 2 patients with muscle phosphorylase kinase (PHK) deficiency and to further define the phenotype of this rare glycogen storage disease (GSD)." | 3.78 | Muscle phosphorylase kinase deficiency: a neutral metabolic variant or a disease? ( Akman, HO; Dimauro, S; Doutreleau, S; Echaniz-Laguna, A; Geny, B; Laforet, P; Lonsdorfer-Wolf, E; Orngreen, MC; Preisler, N; Vissing, J, 2012) |
| "Patients with muscle phosphofructokinase deficiency are unable to achieve a spontaneous second wind under conditions that consistently produce one in patients with McArdle's disease." | 2.71 | No spontaneous second wind in muscle phosphofructokinase deficiency. ( Haller, RG; Vissing, J, 2004) |
| "Nine patients with McArdle disease, one with the partial glycolytic defect phosphoglycerate mutase deficiency, and nine matched, healthy subjects performed the classic ischemic forearm protocol and an identical protocol without ischemia." | 2.70 | A nonischemic forearm exercise test for McArdle disease. ( Haller, RG; Jensen, TD; Kazemi-Esfarjani, P; Skomorowska, E; Vissing, J, 2002) |
| "Patients with McArdle's disease (myophosphorylase deficiency) cannot use muscle glycogen as an energy source during exercise." | 2.38 | Metabolism of branched-chain amino acids and ammonia during exercise: clues from McArdle's disease. ( Coakley, JH; Edwards, RH; Wagenmakers, AJ, 1990) |
| "1." | 1.31 | The exercise metaboreflex is maintained in the absence of muscle acidosis: insights from muscle microdialysis in humans with McArdle's disease. ( Haller, RG; MacLean, DA; Saltin, B; Sander, M; Vissing, J; Vissing, SF, 2001) |
| "Patients with McArdle's disease have previously been reported to exhibit a steepened ventilatory response relative to VCO2, despite an inability to produce lactate." | 1.29 | Respiratory gas exchange and metabolic responses during exercise in McArdle's disease. ( Bell, N; Davies, PM; Nicholls, DP; Nugent, AM; Patterson, VH; Riley, M; Stanford, CF; Steele, IC, 1993) |
| "Five patients with McArdle's disease and five patients with mitochondrial myopathies performed the same incremental maximal exercise test." | 1.28 | Exercise intolerance in patients with McArdle's disease or mitochondrial myopathies. ( Camus, F; Chaussain, M; Defoligny, C; Eymard, B; Fardeau, M, 1992) |
| "Two patients with muscle phosphorylase deficiency [McArdle's disease (McA)] were studied during bicycle exercise at 40 (n = 2) and 60 W (n = 1)." | 1.28 | Impaired oxidative metabolism increases adenine nucleotide breakdown in McArdle's disease. ( Areskog, NH; Haller, RG; Henriksson, KG; Jorfeldt, L; Lewis, SF; Sahlin, K, 1990) |
| "A 23-year-old woman with McArdle's disease performed mild leg exercise on a bicycle ergometer." | 1.28 | Glucose infusion abolishes the excessive ATP degradation in working muscles of a patient with McArdle's disease. ( Hamaguchi, T; Hara, N; Kawachi, M; Kiyokawa, H; Kono, N; Kuwajima, M; Mineo, I; Nakajima, H; Yamada, Y; Yamasaki, T, 1990) |
| "Three patients with McArdle's disease exercised for 2 h at 30% VO2max." | 1.27 | The second wind phenomenon in McArdle's disease. ( Binkhorst, RA; Braakhekke, JP; de Bruin, MI; Joosten, EM; Stegeman, DF; Wevers, RA, 1986) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 5 (25.00) | 18.7374 |
| 1990's | 8 (40.00) | 18.2507 |
| 2000's | 6 (30.00) | 29.6817 |
| 2010's | 1 (5.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Preisler, N | 1 |
| Orngreen, MC | 1 |
| Echaniz-Laguna, A | 1 |
| Laforet, P | 1 |
| Lonsdorfer-Wolf, E | 1 |
| Doutreleau, S | 1 |
| Geny, B | 1 |
| Akman, HO | 1 |
| Dimauro, S | 1 |
| Vissing, J | 4 |
| Kazemi-Esfarjani, P | 1 |
| Skomorowska, E | 1 |
| Jensen, TD | 1 |
| Haller, RG | 4 |
| Lindner, A | 1 |
| Livingstone, C | 1 |
| Al Riyami, S | 1 |
| Wilkins, P | 1 |
| Ferns, GA | 1 |
| Rubio, JC | 1 |
| Pérez, M | 1 |
| Maté-Muñoz, JL | 1 |
| García-Consuegra, I | 1 |
| Chamorro-Viña, C | 1 |
| Fernández del Valle, M | 1 |
| Andreu, AL | 1 |
| Martín, MA | 1 |
| Arenas, J | 1 |
| Lucia, A | 1 |
| Rumpf, KW | 1 |
| Wagner, H | 1 |
| Kaiser, H | 1 |
| Meinck, HM | 1 |
| Goebel, HH | 1 |
| Scheler, F | 1 |
| Riley, M | 1 |
| Nicholls, DP | 1 |
| Nugent, AM | 1 |
| Steele, IC | 1 |
| Bell, N | 1 |
| Davies, PM | 1 |
| Stanford, CF | 1 |
| Patterson, VH | 1 |
| Vanuxem, D | 1 |
| Delpierre, S | 1 |
| Fauvelle, E | 1 |
| Guillot, C | 1 |
| Vanuxem, P | 1 |
| MacLean, DA | 1 |
| Vissing, SF | 1 |
| Sander, M | 1 |
| Saltin, B | 1 |
| Chaussain, M | 1 |
| Camus, F | 1 |
| Defoligny, C | 1 |
| Eymard, B | 1 |
| Fardeau, M | 1 |
| Coakley, JH | 2 |
| Wagenmakers, AJ | 2 |
| Edwards, RH | 2 |
| Wagner, DR | 1 |
| Zöllner, N | 1 |
| Sahlin, K | 1 |
| Areskog, NH | 1 |
| Henriksson, KG | 1 |
| Jorfeldt, L | 1 |
| Lewis, SF | 1 |
| Mineo, I | 3 |
| Kono, N | 3 |
| Yamada, Y | 3 |
| Hara, N | 3 |
| Kiyokawa, H | 2 |
| Hamaguchi, T | 1 |
| Kawachi, M | 2 |
| Yamasaki, T | 1 |
| Nakajima, H | 1 |
| Kuwajima, M | 1 |
| Braakhekke, JP | 1 |
| de Bruin, MI | 1 |
| Stegeman, DF | 1 |
| Wevers, RA | 1 |
| Binkhorst, RA | 1 |
| Joosten, EM | 1 |
| Shimizu, T | 2 |
| Wang, YL | 1 |
| Tarui, S | 2 |
| Heller, SL | 1 |
| Kaiser, KK | 1 |
| Planer, GJ | 1 |
| Hagberg, JM | 1 |
| Brooke, MH | 1 |
| Sumi, S | 1 |
| Nonaka, K | 1 |
1 review available for ammonium hydroxide and Deficiency, Muscle Phosphorylase
| Article | Year |
|---|---|
Metabolism of branched-chain amino acids and ammonia during exercise: clues from McArdle's disease.
Topics: Amino Acids, Branched-Chain; Ammonia; Animals; Deamination; Exercise; Glycogen Storage Disease Type | 1990 |
2 trials available for ammonium hydroxide and Deficiency, Muscle Phosphorylase
| Article | Year |
|---|---|
A nonischemic forearm exercise test for McArdle disease.
Topics: Adult; Ammonia; Exercise; Exercise Test; Female; Forearm; Glycogen Storage Disease Type V; Hand Stre | 2002 |
No spontaneous second wind in muscle phosphofructokinase deficiency.
Topics: Adolescent; Adult; Ammonia; Child; Exercise Test; Fasting; Female; Glycogen Storage Disease Type V; | 2004 |
17 other studies available for ammonium hydroxide and Deficiency, Muscle Phosphorylase
| Article | Year |
|---|---|
Muscle phosphorylase kinase deficiency: a neutral metabolic variant or a disease?
Topics: Adult; Aged; Ammonia; Biopsy; Carbohydrate Metabolism; Creatine Kinase; Exercise; Exercise Test; For | 2012 |
[The lactate-ischemia test: efficient for diagnosis of myopathy?].
Topics: Adult; Ammonia; Diagnosis, Differential; Female; Glycogen Storage Disease Type V; Humans; Ischemia; | 2002 |
McArdle's disease diagnosed following statin-induced myositis.
Topics: Aged; Ammonia; Anticholesteremic Agents; Creatine Kinase; Glycogen Storage Disease Type V; Humans; L | 2004 |
AMPD1 genotypes and exercise capacity in McArdle patients.
Topics: Adult; Alleles; Ammonia; AMP Deaminase; Ergometry; Exercise Tolerance; Female; Genotype; Glycogen St | 2008 |
Increased ammonia production during forearm ischemic work test in McArdle's disease.
Topics: Ammonia; Forearm; Glycogen; Glycogen Storage Disease; Glycogen Storage Disease Type V; Humans; Ische | 1981 |
Respiratory gas exchange and metabolic responses during exercise in McArdle's disease.
Topics: Adolescent; Adult; Aged; Ammonia; Anaerobic Threshold; Carbon Dioxide; Exercise; Exercise Test; Fema | 1993 |
Blood ammonia and ventilation at maximal exercise.
Topics: Adult; Ammonia; Exercise; Female; Glycogen Storage Disease Type V; Glycolysis; Humans; Lactic Acid; | 1998 |
The exercise metaboreflex is maintained in the absence of muscle acidosis: insights from muscle microdialysis in humans with McArdle's disease.
Topics: Acidosis; Adult; Ammonia; Arm; Cardiovascular System; Exercise; Female; Glycogen Storage Disease Typ | 2001 |
Exercise intolerance in patients with McArdle's disease or mitochondrial myopathies.
Topics: Adult; Alanine; Ammonia; Energy Metabolism; Exercise Test; Exercise Tolerance; Female; Glycogen Stor | 1992 |
Relationship between ammonia, heart rate, and exertion in McArdle's disease.
Topics: Adolescent; Adult; Amino Acids, Branched-Chain; Ammonia; Drug Combinations; Exercise Test; Female; G | 1992 |
McArdle's disease: successful symptomatic therapy by high dose oral administration of ribose.
Topics: Administration, Oral; Adult; Ammonia; Dose-Response Relationship, Drug; Glycogen Storage Disease Typ | 1991 |
Impaired oxidative metabolism increases adenine nucleotide breakdown in McArdle's disease.
Topics: Acetylcarnitine; Adenine Nucleotides; Adenosine Triphosphate; Adult; Ammonia; Exercise; Fatigue; Fem | 1990 |
Glucose infusion abolishes the excessive ATP degradation in working muscles of a patient with McArdle's disease.
Topics: Adenosine Triphosphate; Adult; Ammonia; Creatine Kinase; Exercise Test; Female; Glucose; Glycogen St | 1990 |
The second wind phenomenon in McArdle's disease.
Topics: Adaptation, Physiological; Adult; Ammonia; Blood Glucose; Cardiac Output; Electromyography; Fatigue; | 1986 |
Myogenic hyperuricemia. A common pathophysiologic feature of glycogenosis types III, V, and VII.
Topics: Adult; Ammonia; Glycogen Storage Disease; Glycogen Storage Disease Type III; Glycogen Storage Diseas | 1987 |
McArdle's disease with myoadenylate deaminase deficiency: observations in a combined enzyme deficiency.
Topics: Adult; Ammonia; AMP Deaminase; Female; Glycogen Storage Disease; Glycogen Storage Disease Type V; Hu | 1987 |
Excess purine degradation in exercising muscles of patients with glycogen storage disease types V and VII.
Topics: Adult; Ammonia; Female; Glycogen Storage Disease; Glycogen Storage Disease Type V; Glycogen Storage | 1985 |