Page last updated: 2024-10-16

ammonium hydroxide and Cystinuria

ammonium hydroxide has been researched along with Cystinuria in 12 studies

azane : Saturated acyclic nitrogen hydrides having the general formula NnHn+2.

Cystinuria: An inherited disorder due to defective reabsorption of CYSTINE and other BASIC AMINO ACIDS by the PROXIMAL RENAL TUBULES. This form of aminoaciduria is characterized by the abnormally high urinary levels of cystine; LYSINE; ARGININE; and ORNITHINE. Mutations involve the amino acid transport protein gene SLC3A1.

Research Excerpts

ExcerptRelevanceReference
"The infant developed severe mental retardation, athetosis, and spasticity."1.25Familial hyperargininaemia. ( Colombo, JP; Lavinha, F; Lowenthal, A; Terheggen, HG, 1975)

Research

Studies (12)

TimeframeStudies, this research(%)All Research%
pre-199012 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
HOCKADAY, TD1
SMITH, LH1
Efron, ML1
Kato, T2
Mizutani, N1
Ban, M1
Joost, J1
Jarosch, E1
Miyagi, K1
Nakada, F1
Ohshiro, S1
Marshall, RW1
Robertson, WG1
Tanaka, E1
Horisawa, S1
Terheggen, HG1
Lowenthal, A1
Lavinha, F1
Colombo, JP1
Mel'k, MV1
Shcheglova, SA1
Volkova, ZA1
Gundalakh, AI1
Hook, EW1
Ampola, MG1
Zweig, JI1

Reviews

3 reviews available for ammonium hydroxide and Cystinuria

ArticleYear
RENAL CALCULI.
    Disease-a-month : DM, 1963, Volume: 127

    Topics: Ammonia; Calcium Metabolism Disorders; Chemistry Techniques, Analytical; Cystinuria; Diagnosis; Huma

1963
Phenylketonuria and other disorders of amino acid metabolism.
    Pediatric clinics of North America, 1973, Volume: 20, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Child, Preschool; Counseling; Cystathionine; C

1973
Effects of lysine on ammonia formation, hydrogen ion, and potassium ion balance: a review and an hypothesis.
    Clinical chemistry, 1973, Volume: 19, Issue:9

    Topics: Acid-Base Equilibrium; Adolescent; Adult; Ammonia; Animals; Arginine; Biological Transport; Cystinur

1973

Other Studies

9 other studies available for ammonium hydroxide and Cystinuria

ArticleYear
Diet therapy for inborn errors of amino acid metabolism.
    Journal of the American Dietetic Association, 1967, Volume: 51, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child, Preschool; Coenzymes; Cystinuria; Diet Therapy

1967
Hyperammonemia in lysinuric protein intolerance.
    Pediatrics, 1984, Volume: 73, Issue:4

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child; Cystinuria; Humans; Lysi

1984
Glutamine: a new anticystinuric drug?
    European urology, 1981, Volume: 7, Issue:6

    Topics: Adult; Ammonia; Cystinuria; Drug Combinations; Female; Glutamine; Humans; Time Factors; Tiopronin

1981
Effect of glutamine on cystine excretion in a patient with cystinuria.
    The New England journal of medicine, 1979, Jul-26, Volume: 301, Issue:4

    Topics: Administration, Oral; Aged; Ammonia; Cystinuria; Glutamine; Humans; Infusions, Parenteral; Male

1979
Nomograms for the estimation of the saturation of urine with calcium oxalate, calcium phosphate, magnesium ammonium phosphate, uric acid, sodium acid urate, ammonium acid urate and cystine.
    Clinica chimica acta; international journal of clinical chemistry, 1976, Oct-15, Volume: 72, Issue:2

    Topics: Ammonia; Calcium; Calcium Phosphates; Computers; Cystinuria; Humans; Kinetics; Magnesium; Mathematic

1976
Hyperdibasicaminoaciduria and hyperammonemia in familial protein intolerance.
    American journal of diseases of children (1960), 1976, Volume: 130, Issue:12

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Diamino; Ammonia; Arginine; Child, Preschool; Cys

1976
Familial hyperargininaemia.
    Archives of disease in childhood, 1975, Volume: 50, Issue:1

    Topics: Amino Acids; Ammonia; Arginine; Athetosis; Child, Preschool; Chromatography; Cystinuria; Dietary Pro

1975
[Some indices of nitrogen metabolism in patients with viral hepatitis].
    Terapevticheskii arkhiv, 1975, Volume: 47, Issue:8

    Topics: Adolescent; Adult; Alanine; Ammonia; Asparagine; Chronic Disease; Cysteine; Cystinuria; Glutamates;

1975
Medical Grand Rounds: from the Department of Medicine, University of Virginia Medical Center: Nephrolithiasis.
    Virginia medical monthly, 1974, Volume: 101, Issue:9

    Topics: Adolescent; Adult; Aged; Ammonia; Calcium; Cystinuria; Female; Humans; Kidney Calculi; Magnesium; Ma

1974