Page last updated: 2024-08-22

ammonium chloride and Amino Acid Metabolism Disorders, Inborn

ammonium chloride has been researched along with Amino Acid Metabolism Disorders, Inborn in 8 studies

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19904 (50.00)18.7374
1990's3 (37.50)18.2507
2000's0 (0.00)29.6817
2010's1 (12.50)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Arend, J; Barbosa, S; do Nascimento, PS; Dos Santos, ARS; Fighera, MR; Furian, AF; Gabbi, P; Haupental, F; Nogueira, V; Oliveira, MS; Rodrigues, FS; Royes, LFF1
Ameen, M; Palmer, T1
Katsunuma, T; Kusumi, K; Saheki, T; Takada, S; Tsuda, M1
Batshaw, M; Daikhin, Y; Jawad, A; Nissim, I; Wilson, J; Yudkoff, M1
Batshaw, ML; Daikhin, Y; Wilson, JM; Ye, X; Yudkoff, M1
Fukushige, T; Kobayashi, K; Li, MX; Nakajima, T; Saheki, T; Seiler, N1
Kurihara, T; Matsukura, S; Shioya, K; Yamamura, Y1
Kiyose, H; Shimizu, J; Tagawa, K; Takeuchi, H; Unuma, T; Yamakado, M1

Other Studies

8 other study(ies) available for ammonium chloride and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Ammonia role in glial dysfunction in methylmalonic acidemia.
    Toxicology letters, 2018, Oct-01, Volume: 295

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Ammonium Chloride; Animals; Behavior, Animal; Brain; Cell Proliferation; Disease Models, Animal; Fluoresceins; Hyperammonemia; Interleukin-1beta; Male; Malonates; Maze Learning; Memory Disorders; Memory, Short-Term; Mice; Neuroglia; Quaternary Ammonium Compounds; Time Factors; Tumor Necrosis Factor-alpha

2018
Enzyme inhibition as a possible cause of secondary increases in metabolite levels in patients with inborn errors of metabolism.
    Journal of inherited metabolic disease, 1980, Volume: 3, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonium Chloride; Ammonium Sulfate; Animals; Arginine; Argininosuccinate Lyase; Argininosuccinate Synthase; Argininosuccinic Acid; Cattle; Citrulline; Ligases; Liver; Lyases; Lysine; Rats; Swine

1980
Role of argininosuccinate synthetase in the regulation of urea synthesis in the rat and argininosuccinate synthetase-associated metabolic disorder in man.
    Advances in enzyme regulation, 1980, Volume: 18

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonium Chloride; Animals; Argininosuccinate Synthase; Citrulline; Dietary Proteins; Female; Glutamates; Humans; Ligases; Liver; Male; Middle Aged; Ornithine; Rats; Urea

1980
In vivo nitrogen metabolism in ornithine transcarbamylase deficiency.
    The Journal of clinical investigation, 1996, Nov-01, Volume: 98, Issue:9

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonium Chloride; Child; Female; Glutamine; Heterozygote; Humans; Male; Middle Aged; Nitrogen; Ornithine Carbamoyltransferase Deficiency Disease; Phenylbutyrates; Urea

1996
In vivo measurement of ureagenesis with stable isotopes.
    Journal of inherited metabolic disease, 1998, Volume: 21 Suppl 1

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonium Chloride; Breath Tests; Carbon Dioxide; Carbon Isotopes; Female; Gas Chromatography-Mass Spectrometry; Genetic Carrier Screening; Glutamine; Humans; Infant, Newborn; Male; Mass Spectrometry; Nitrogen Isotopes; Ornithine Carbamoyltransferase Deficiency Disease; Sodium Acetate; Urea

1998
Aberrations of ammonia metabolism in ornithine carbamoyltransferase-deficient spf-ash mice and their prevention by treatment with urea cycle intermediate amino acids and an ornithine aminotransferase inactivator.
    Biochimica et biophysica acta, 1999, Sep-20, Volume: 1455, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Ammonium Chloride; Animals; Arginine; Citrulline; Enzyme Inhibitors; Injections, Intraperitoneal; Liver; Male; Mice; Mice, Transgenic; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Perfusion; Urea

1999
[A case of combined lysinuric protein intolerance and hypoactivity of argininosuccinate synthetase (citrullinemia)].
    Nihon Naika Gakkai zasshi. The Journal of the Japanese Society of Internal Medicine, 1988, Volume: 77, Issue:5

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Ammonium Chloride; Citrulline; Female; Humans; Lysine; Renal Tubular Transport, Inborn Errors

1988
[An adult case of familial ornithine transcarbamylase deficiency].
    Nihon Naika Gakkai zasshi. The Journal of the Japanese Society of Internal Medicine, 1988, Volume: 77, Issue:12

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Ammonium Chloride; Female; Humans; Liver; Ornithine Carbamoyltransferase; Proteins

1988