Page last updated: 2024-09-04

alpha-methyl-beta-hydroxybutyrate and Acidosis

alpha-methyl-beta-hydroxybutyrate has been researched along with Acidosis in 6 studies

Research

Studies (6)

TimeframeStudies, this research(%)All Research%
pre-19904 (66.67)18.7374
1990's0 (0.00)18.2507
2000's1 (16.67)29.6817
2010's1 (16.67)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Bancel, LP; Dessein, AF; Germain, N; Guemann, AS; Joncquel Chevalier Curt, M1
da C Ferreira, G; Dalcin, KB; de Assis, DR; Filho, CS; Latini, A; Leipnitz, G; Maria, RC; Perry, ML; Ribeiro, CA; Rosa, RB; Schuck, PF; Wajner, M; Wannmacher, CM; Wyse, AT1
Bennett, MJ; Littlewood, JM; MacDonald, A; Pollitt, RJ; Thompson, J1
Condado, I; DelValle, JA; Garcia, MJ; Jiménez, A; López, O; Merinero, B; Solaguren, R; Ugarte, M1
Middleton, B; Oorthuys, JW; Schutgens, RB; Tegelaers, WH; vd Blij, JF; Veder, HA; Vulsma, T1
Leonard, JV; Middleton, B; Seakins, JW1

Other Studies

6 other study(ies) available for alpha-methyl-beta-hydroxybutyrate and Acidosis

ArticleYear
Abnormal Ketone Bodies in a 22-Month-Old Boy Presenting with Recurrent Vomiting and Metabolic Acidosis.
    Clinical chemistry, 2019, Volume: 65, Issue:11

    Topics: Acetoacetates; Acetyl-CoA C-Acyltransferase; Acidosis; Amino Acid Metabolism, Inborn Errors; Glycine; Humans; Hydroxybutyrates; Infant; Ketone Bodies; Male; Vomiting

2019
Inhibition of energy metabolism by 2-methylacetoacetate and 2-methyl-3-hydroxybutyrate in cerebral cortex of developing rats.
    Journal of inherited metabolic disease, 2005, Volume: 28, Issue:4

    Topics: 3-Hydroxyacyl CoA Dehydrogenases; Acetates; Acetoacetates; Acetyl-CoA C-Acyltransferase; Acidosis; Alcohol Oxidoreductases; Animals; Brain; Carbon Dioxide; Cerebral Cortex; Citrates; Creatine Kinase; Dose-Response Relationship, Drug; Electron Transport; Energy Metabolism; Glucose; Glutathione; Glycine; Hydroxybutyrates; In Vitro Techniques; Intellectual Disability; Lactic Acid; NG-Nitroarginine Methyl Ester; Oxygen; Rats; Rats, Wistar; Time Factors

2005
A case of beta-ketothiolase deficiency.
    Journal of inherited metabolic disease, 1983, Volume: 6, Issue:4

    Topics: Acetyl-CoA C-Acyltransferase; Acidosis; Acyltransferases; Dietary Proteins; Female; Glycine; Humans; Hydroxybutyrates; Infant

1983
Late onset type of propionic acidaemia: case report and biochemical studies.
    Journal of inherited metabolic disease, 1981, Volume: 4, Issue:2

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carbon-Carbon Ligases; Female; Glycine; Humans; Hydroxybutyrates; Infant; Ketosis; Ligases; Propionates

1981
Beta-ketothiolase deficiency in a family confirmed by in vitro enzymatic assays in fibroblasts.
    European journal of pediatrics, 1982, Volume: 139, Issue:1

    Topics: Acetyl-CoA C-Acyltransferase; Acidosis; Acyltransferases; Adult; Child; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Male; Metabolism, Inborn Errors

1982
Acetoacetyl CoA thiolase deficiency presenting as ketotic hypoglycemia.
    Pediatric research, 1987, Volume: 21, Issue:2

    Topics: Acetoacetates; Acetyl-CoA C-Acetyltransferase; Acetyltransferases; Acidosis; Female; Glycine; Humans; Hydroxybutyrates; Hypoglycemia; Infant; Ketosis

1987