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alpha-keto-delta-guanidinovaleric acid and Amino Acid Metabolism Disorders, Inborn

alpha-keto-delta-guanidinovaleric acid has been researched along with Amino Acid Metabolism Disorders, Inborn in 4 studies

5-guanidino-2-oxopentanoic acid : A 2-oxo monocarboxylic acid that is 2-oxopentanoic acid in which one of the methyl hydrogens is substituted by a carbamimidamido group.

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19903 (75.00)18.7374
1990's1 (25.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Marescau, B4
Lowenthal, A3
Terheggen, HG3
Esmans, E2
Alderweireldt, F2
Pintens, J2
Luyten, Y1
Lemière, G1
Dommisse, R1
Lambert, MA1
Desjardins, M1
Laberge, M1
Dhondt, JL1
Dallaire, L1
De Deyn, PP1
Qureshi, IA1

Other Studies

4 other studies available for alpha-keto-delta-guanidinovaleric acid and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Guanidino compounds in hyperargininemia.
    Advances in experimental medicine and biology, 1982, Volume: 153

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Chromatography, Liquid; Chromatography, Thin Layer;

1982
Isolation and identification of 2-oxo-5-guanidinovaleric acid in urine of patients with hyperargininaemia by chromatography and gas chromatography/mass spectrometry.
    Journal of clinical chemistry and clinical biochemistry. Zeitschrift fur klinische Chemie und klinische Biochemie, 1981, Volume: 19, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Chemical Phenomena; Chemistry; Chromatography, Liqui

1981
Excretion of alpha-keto-delta-guanidinovaleric acid and its cyclic form in patients with hyperargininemia.
    Clinica chimica acta; international journal of clinical chemistry, 1979, Oct-15, Volume: 98, Issue:1-2

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Female; Guanidines; Humans; Keto Acids; Valerates

1979
Hyperargininemia: intellectual and motor improvement related to changes in biochemical data.
    The Journal of pediatrics, 1991, Volume: 118, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Child; Female; Guanidines; Humans; Intelligence; Mot

1991