Page last updated: 2024-11-07

aldosterone and Congenital Adrenal Hyperplasia

aldosterone has been researched along with Congenital Adrenal Hyperplasia in 205 studies

Research Excerpts

ExcerptRelevanceReference
"We investigated the changes of serum PTH levels induced by oral captopril (50 mg) administration in patients with primary essential hypertension (EH) and with primary aldosteronism (PA) caused by bilateral adrenal hyperplasia (BAH) or aldosterone-producing adenoma (APA), the latter before and after adrenalectomy."7.91PTH Modulation by Aldosterone and Angiotensin II is Blunted in Hyperaldosteronism and Rescued by Adrenalectomy. ( Iacobone, M; Lenzini, L; Lerco, S; Maiolino, G; Prisco, S; Rossi, GP; Seccia, TM; Torresan, F; Vanderriele, PE, 2019)
"In primary hyperaldosteronism, discriminating bilateral adrenal hyperplasia (BAH) from an aldosterone-producing adenoma (APA) is important because adrenalectomy, which is usually curative in APA, is seldom effective in BAH."6.69Predictive value of preoperative tests in discriminating bilateral adrenal hyperplasia from an aldosterone-producing adrenal adenoma. ( Berman, AA; Choyke, PL; Doppman, JL; Gill, JR; Linehan, WM; Pezzullo, JC; Phillips, JL; Rayford, W; Walther, MM, 2000)
"Salt wasting syndrome is caused by a congenital or acquired synthesis disorder or by the aldosterone function disorder."6.43[Salt wasting syndrome caused by congenital, insufficient synthesis or aldosterone function--etiology, diagnosis and management]. ( Basiak, A; Noczyńska, A; Wikiera, B, 2005)
"Salt wasting syndrome (hyponatremia, hyperkalemia, dehydration, metabolic acidosis) in early infancy could be caused by either mineralocorticoid deficiency as in congenital adrenal hyperplasia (CAH) and adrenal insufficiency or mineralocorticoid resistance as in pseudohypoaldosteronism (PHA)."5.46High aldosterone and cortisol levels in salt wasting congenital adrenal hyperplasia: a clinical conundrum. ( Boddu, SK; Madhavan, S, 2017)
"Primary aldosteronism (PA) may account for as much as 6-20% of cases of refractory hypertension referred to hypertension clinics."5.35The cutoff value of aldosterone-to-renin ratio for the diagnosis of primary aldosteronism in patients taking antihypertensive medicine. ( Fukuchi, K; Horio, T; Iwanaga, Y; Kamide, K; Kawano, Y; Nakahama, H; Nakamura, S; Nakata, H; Niizuma, S; Yoshihara, F, 2008)
"We have studied a patient with congenital adrenal hyperplasia and steroid 11beta-hydroxylase deficiency who was homozygous for a deletion of the CYP11B1 and CYP11B2 genes normally required for cortisol and aldosterone synthesis, respectively."5.31Deletion hybrid genes, due to unequal crossing over between CYP11B1 (11beta-hydroxylase) and CYP11B2(aldosterone synthase) cause steroid 11beta-hydroxylase deficiency and congenital adrenal hyperplasia. ( Chaussain, JL; Curnow, KM; Morel, Y; Mulatero, P; Pascoe, L; Portrat, S, 2001)
"Aldosterone and cortisol were found in plasma samples from two patients with salt-losing congenital adrenal hyperplasia caused by steroid 21-hydroxylase deficiency."5.30Aldosterone production despite absence or defectiveness of the CYP21 genes in two patients with salt-losing congenital adrenal hyperplasia caused by steroid 21-hydroxylase deficiency. ( de Muinck-Keizer-Schrama, SM; Degenhart, HJ; Drop, SL; Hoogenboezem, T; Koppens, PF, 1998)
"The data used to make the diagnosis of primary hyperaldosteronism and to assess the likelihood of the presence of an adenoma indicate that patients studied at 40 centres in the UK show results very similar to those of North American series where large numbers of patients have been described but all have been studied in the same centre."5.28Primary hyperaldosteronism in England and Wales: a review of the use of a Supraregional Assay Service laboratory for the measurement of aldosterone and plasma renin activity. ( James, VH; Short, F, 1991)
"In patients with primary aldosteronism (n = 21) elevated as well as normal values of urinary 21-deoxyaldosterone were found, indicating that in some patients aldosterone may be formed not only from corticosterone but also from the 21-deoxy compound."5.2721-Deoxyaldosterone excretion in patients with primary aldosteronism and 21-hydroxylase deficiency. ( Abdelhamid, S; Bige, K; Bokkenheuser, V; Heinrich, U; Lewicka, S; Vecsei, P; Winter, J, 1987)
"Forms of congenital adrenal hyperplasia resulting from deficient steroid hydroxylation at positions 21, 17 alpha, and 11 beta have several similar clinical and biochemical characteristics."5.27Distinctive plasma aldosterone, 18-hydroxycorticosterone, and 18-hydroxydeoxycorticosterone profile in the 21-, 17 alpha-, and 11 beta-hydroxylase deficiency types of congenital adrenal hyperplasia. ( Biglieri, EG; Kater, CE, 1983)
"Both aldosterone and 17-OHP were high in the 6 untreated non salt-losers."5.26Plasma aldosterone concentrations related to 17alpha-hydroxyprogesterone in congenital adrenal hyperplasia. ( Baron, MC; Girard, F; Gourmelen, M; Pham-Huu-Trung, MT; Raux, MC, 1976)
"The aldosterone secretion was normal and responded normally to sodium deprivation in all patients studied during suppression with carbohydrate-active steroids."5.25Aldosterone hypersecretion in "non-salt-losing" congenital adrenal hyperplasia. ( Bartter, FC; Bryan, GT; Henkin, RI, 1968)
"We investigated the changes of serum PTH levels induced by oral captopril (50 mg) administration in patients with primary essential hypertension (EH) and with primary aldosteronism (PA) caused by bilateral adrenal hyperplasia (BAH) or aldosterone-producing adenoma (APA), the latter before and after adrenalectomy."3.91PTH Modulation by Aldosterone and Angiotensin II is Blunted in Hyperaldosteronism and Rescued by Adrenalectomy. ( Iacobone, M; Lenzini, L; Lerco, S; Maiolino, G; Prisco, S; Rossi, GP; Seccia, TM; Torresan, F; Vanderriele, PE, 2019)
"The 0800 h plasma concentrations of the mineralocorticoid hormones, 18-hydroxydeoxycorticosterone (18-OHDOC), deoxycorticosterone (DOC), corticosterone, 18-hydroxycorticosterone (18-OHB), and aldosterone, in six patients with nonsalt-losing congenital adrenal hyperplasia revealed two groupings of these steroids: in one group, DOC, 18-OHB, and aldosterone were significantly elevated (P less than 0."3.66The zonal origins of the mineralocorticoid hormones in the 21-hydroxylation deficiency of congenital adrenal hyperplasia. ( Biglieri, EG; Kater, CE; Leme, CE; Malerbi, DA; Okada, H; Wajchenberg, BL, 1981)
"In 12 obligate heterozygotes for the simple virilizing form of congenital adrenal hyperplasia (21-hydroxylase deficiency), basal and ACTH-stimulated levels of aldosterone, corticosterone, deoxycorticosterone, 18-hydroxycorticosterone, and 18-hydroxydeoxycorticosterone were examined."3.66Impaired mineralocorticoid hormone responses to adrenocorticotropin stimulation: additional characterization of heterozygosity for the 21-hydroxylase deficiency type of congenital adrenal hyperplasia. ( Biglieri, EG; Kater, CE; Pardini, DP; Vieira, JG, 1983)
"Aldosterone (Ald) is a crucial factor in maintaining electrolyte and water homeostasis."3.01Aldosterone signaling defect in young infants: single-center report and review. ( Chen, Q; Du, M; Guo, S; Li, Y; Ma, H; Wijaya, M; Zhang, J, 2021)
"Aldosterone levels were low or in the reference range in 98% of the cases when available."2.8211-Deoxycorticosterone Producing Adrenal Hyperplasia as a Very Unusual Cause of Endocrine Hypertension: Case Report and Systematic Review of the Literature. ( Asla, Q; Aulinas, A; Hanzu, FA; Lerma, E; Pérez, JI; Rodrigo, MT; Sardà, H; Urgell, E; Webb, SM, 2022)
"In patients with primary aldosteronism, adrenal vein sampling (AVS) is considered the only reliable technique to distinguish between unilateral and bilateral autonomous production of aldosterone, but agreement is lacking on the best criteria indicating successful cannulation and lateralization."2.75Impact of different diagnostic criteria during adrenal vein sampling on reproducibility of subtype diagnosis in patients with primary aldosteronism. ( Bertello, C; Daunt, N; Gordon, R; Leggett, D; Mengozzi, G; Mulatero, P; Rossato, D; Stowasser, M; Sukor, N; Veglio, F, 2010)
"In primary hyperaldosteronism, discriminating bilateral adrenal hyperplasia (BAH) from an aldosterone-producing adenoma (APA) is important because adrenalectomy, which is usually curative in APA, is seldom effective in BAH."2.69Predictive value of preoperative tests in discriminating bilateral adrenal hyperplasia from an aldosterone-producing adrenal adenoma. ( Berman, AA; Choyke, PL; Doppman, JL; Gill, JR; Linehan, WM; Pezzullo, JC; Phillips, JL; Rayford, W; Walther, MM, 2000)
"Primary aldosteronism (PA), characterized by the inappropriate and abnormal adrenal secretion of aldosterone, is the most common cause of secondary hypertension."2.53Hyperaldosteronism: How to Discriminate Among Different Disease Forms? ( Buffolo, F; Burrello, J; Crudo, V; Monticone, S; Mulatero, P; Tetti, M; Veglio, F, 2016)
"Primary aldosteronism is one of the commonly identified causes of hypertension and is treatable and/or potentially curable."2.52Mineralocorticoid and apparent mineralocorticoid syndromes of secondary hypertension. ( Ardhanari, S; Chaudhary, K; Kannuswamy, R; Lockette, W; Whaley-Connell, A, 2015)
"Primary aldosteronism (PA) is the most common secondary form of arterial hypertension, with a particularly high prevalence among patients with resistant hypertension."2.49Diagnosis and management of primary aldosteronism: an updated review. ( Chang, CC; Chao, CT; Chueh, SJ; Kuo, CC; Lin, YH; Pimenta, E; Stowasser, M; Wu, KD; Wu, VC, 2013)
"Primary hyperaldosteronism (PHA) is characterized by an increased Aldosterone synthesis which is independent of the Renin-Angiotensin-Aldosterone-System (RAAS)."2.48[Primay hyperaldosteronism--diagnostic and treatment]. ( Beuschlein, F; Potthoff, SA; Vonend, O, 2012)
"Primary hyperaldosteronism has historically been underdiagnosed as a cause of hypertension, but recent reports highlight its ubiquitous nature with a prevalence of 5%-10% in screened hypertensive patients."2.46Adrenal vein sampling. ( Angle, JF; Kahn, SL, 2010)
"Salt wasting syndrome is caused by a congenital or acquired synthesis disorder or by the aldosterone function disorder."2.43[Salt wasting syndrome caused by congenital, insufficient synthesis or aldosterone function--etiology, diagnosis and management]. ( Basiak, A; Noczyńska, A; Wikiera, B, 2005)
"Mutations in CYP11B1 cause congenital adrenal hyperplasia (CAH) due to 11beta-hydroxylase deficiency."2.41Congenital adrenal hyperplasia: 11beta-hydroxylase deficiency. ( Peter, M, 2002)
"Aldosterone synthase has 11beta-hydroxylase activity as well as 18-hydroxylase activity and 18-oxidase activity."2.40Disorders of the aldosterone synthase and steroid 11beta-hydroxylase deficiencies. ( Dubuis, JM; Peter, M; Sippell, WG, 1999)
"Among 154 cases of primary aldosteronism seen in the General Clinical Research Center at San Francisco General Hospital, twelve patients did not fulfill established characteristics of an aldosterone producing adenoma (APA) or idiopathic hyperaldosteronism (IHA)."2.38Correctable subsets of primary aldosteronism. Primary adrenal hyperplasia and renin responsive adenoma. ( Biglieri, EG; Irony, I; Kater, CE; Shackleton, CH, 1990)
"Non-classic congenital adrenal hyperplasia was diagnosed initially; however, genetic testing revealed no 21-hydroxylase deficiency."1.56Adrenal Tumor Mimicking Non-Classic Congenital Adrenal Hyperplasia. ( Dai, SH; Tsai, CH; Tsai, WH; Wong, CH; Zeng, YH, 2020)
"Salt wasting syndrome (hyponatremia, hyperkalemia, dehydration, metabolic acidosis) in early infancy could be caused by either mineralocorticoid deficiency as in congenital adrenal hyperplasia (CAH) and adrenal insufficiency or mineralocorticoid resistance as in pseudohypoaldosteronism (PHA)."1.46High aldosterone and cortisol levels in salt wasting congenital adrenal hyperplasia: a clinical conundrum. ( Boddu, SK; Madhavan, S, 2017)
"Although primary aldosteronism (PA) is the most common cause of endocrine hypertension, histopathological methods to reveal the presence and sites of aldosterone overproduction remain to be established."1.39Histopathological diagnosis of primary aldosteronism using CYP11B2 immunohistochemistry. ( Katabami, T; Kawa, G; Mukai, K; Nanba, K; Naruse, M; Nishimoto, K; Okumura, A; Okuno, H; Sawai, K; Shimatsu, A; Tagami, T; Tanabe, A; Tsuiki, M; Usui, T; Yamamoto, T, 2013)
"Primary aldosteronism (PA) may account for as much as 6-20% of cases of refractory hypertension referred to hypertension clinics."1.35The cutoff value of aldosterone-to-renin ratio for the diagnosis of primary aldosteronism in patients taking antihypertensive medicine. ( Fukuchi, K; Horio, T; Iwanaga, Y; Kamide, K; Kawano, Y; Nakahama, H; Nakamura, S; Nakata, H; Niizuma, S; Yoshihara, F, 2008)
"Since 1989, neonatal mass screening for congenital adrenal hyperplasia (CAH) has been carried out in Japan."1.34Nonclassic steroid 21-hydroxylase deficiency due to a homozygous V281L mutation in CYP21A2 detected by the neonatal mass-screening program in Japan. ( Horikawa, R; Isojima, T; Katsumata, N; Naiki, Y; Shinagawa, T; Tanaka, T, 2007)
"Primary aldosteronism is an important and one of the few potentially curable forms of secondary hypertension."1.33[Endosonography -- an additional diagnostic possibility in the differentiation between the two common types of primary hyperaldosteronism]. ( Kann, PH; Klein, HH; Roggenland, D; Schneider, S, 2006)
"We have studied a patient with congenital adrenal hyperplasia and steroid 11beta-hydroxylase deficiency who was homozygous for a deletion of the CYP11B1 and CYP11B2 genes normally required for cortisol and aldosterone synthesis, respectively."1.31Deletion hybrid genes, due to unequal crossing over between CYP11B1 (11beta-hydroxylase) and CYP11B2(aldosterone synthase) cause steroid 11beta-hydroxylase deficiency and congenital adrenal hyperplasia. ( Chaussain, JL; Curnow, KM; Morel, Y; Mulatero, P; Pascoe, L; Portrat, S, 2001)
"Aldosterone and cortisol were found in plasma samples from two patients with salt-losing congenital adrenal hyperplasia caused by steroid 21-hydroxylase deficiency."1.30Aldosterone production despite absence or defectiveness of the CYP21 genes in two patients with salt-losing congenital adrenal hyperplasia caused by steroid 21-hydroxylase deficiency. ( de Muinck-Keizer-Schrama, SM; Degenhart, HJ; Drop, SL; Hoogenboezem, T; Koppens, PF, 1998)
"We report a case of congenital adrenal hyperplasia due to 17 alpha-hydroxylase deficiency in a Chinese genotypic male patient."1.2917 alpha-Hydroxylase deficiency with persistence of müllerian ducts in a genotypic male and paradoxical aldosterone secretion. ( Chan, JC; Cockram, CS; Nicholls, MG; Panesar, NS; Shek, CC; Yeung, VT, 1993)
"Prenatal diagnosis of congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency by amniotic fluid (AF) steroid analysis is not possible in those cases in which prenatal dexamethasone (DEX) therapy is initiated to prevent virilization of female CAH fetuses because AF steroid levels are suppressed if DEX therapy is continued beyond amniocentesis (AC)."1.29Prenatal dexamethasone treatment in pregnancies at risk for congenital adrenal hyperplasia due to 21-hydroxylase deficiency: effect on midgestational amniotic fluid steroid levels. ( Dörr, HG; Sippell, WG, 1993)
"We report a case of male pseudohermaphroditism with 17 alpha-hydroxylase deficiency (17OHD) who also had TALT."1.28Testicular adrenal-like tissue in a patient with 17 alpha-hydroxylase deficiency. ( Andrade Olivié, A; Fernández Martín, R; Fluiters, E; Galofré, JC; García-Mayor, RV; Páramo, C; Sopeña, B, 1992)
"Aldosterone secretion was elevated markedly with ACTH administration and with sodium deprivation and/or volume depletion during ACTH suppression by dexamethasone."1.28Siblings of 21-hydroxylase deficiency (non-salt-losing) with aldosterone hypersecretion. ( Eto, S; Kashimura, M; Morimoto, I; Nakano, Y; Tateishi, H; Toda, Y; Ueda, S; Watanabe, K; Yamamoto, S; Zeki, K, 1992)
"Late-onset congenital adrenal hyperplasia is a cause of a spectrum of clinical manifestations of postnatal androgen excess."1.28[Adrenal enzymatic block with late-onset caused by 11-hydroxylase deficiency. Apropos of 29 cases]. ( Cordray, JP; Guillerd, X; Merceron, RE; Nys, P; Rainaut, M; Reboul, P, 1992)
"The data used to make the diagnosis of primary hyperaldosteronism and to assess the likelihood of the presence of an adenoma indicate that patients studied at 40 centres in the UK show results very similar to those of North American series where large numbers of patients have been described but all have been studied in the same centre."1.28Primary hyperaldosteronism in England and Wales: a review of the use of a Supraregional Assay Service laboratory for the measurement of aldosterone and plasma renin activity. ( James, VH; Short, F, 1991)
"The male pseudohermaphroditism resulted from deficient testosterone synthesis due to deficiency of 17 alpha-hydroxylase and 17,20 desmolase."1.27Male pseudohermaphroditism due to multiple defects in steroid-biosynthetic microsomal mixed-function oxidases. A new variant of congenital adrenal hyperplasia. ( Gautier, T; Imperato-McGinley, J; Peterson, RE; Shackleton, C, 1985)
"Plasma extracts from patients with congenital adrenal hyperplasia were found to contain substances that competed with aldosterone for mineralocorticoid receptor-binding sites in a rat kidney cytosol system."1.27Evidence for the secretion of an antimineralocorticoid in congenital adrenal hyperplasia. ( Kuhnle, U; Land, M; Ulick, S, 1986)
"In patients with primary aldosteronism (n = 21) elevated as well as normal values of urinary 21-deoxyaldosterone were found, indicating that in some patients aldosterone may be formed not only from corticosterone but also from the 21-deoxy compound."1.2721-Deoxyaldosterone excretion in patients with primary aldosteronism and 21-hydroxylase deficiency. ( Abdelhamid, S; Bige, K; Bokkenheuser, V; Heinrich, U; Lewicka, S; Vecsei, P; Winter, J, 1987)
"Forms of congenital adrenal hyperplasia resulting from deficient steroid hydroxylation at positions 21, 17 alpha, and 11 beta have several similar clinical and biochemical characteristics."1.27Distinctive plasma aldosterone, 18-hydroxycorticosterone, and 18-hydroxydeoxycorticosterone profile in the 21-, 17 alpha-, and 11 beta-hydroxylase deficiency types of congenital adrenal hyperplasia. ( Biglieri, EG; Kater, CE, 1983)
"In salt-losing congenital adrenal hyperplasia (CAH), treatment with a mineralocorticoid in doses that normalized plasma renin activity (PRA) induced a marked increase in linear growth."1.27The effects of long-term normalization of sodium balance on linear growth in disorders with aldosterone deficiency. ( Gunzcler, P; Kuhnle, U; Levine, LS; New, MI; Pareira, JA; Rösler, A, 1983)
"Both aldosterone and 17-OHP were high in the 6 untreated non salt-losers."1.26Plasma aldosterone concentrations related to 17alpha-hydroxyprogesterone in congenital adrenal hyperplasia. ( Baron, MC; Girard, F; Gourmelen, M; Pham-Huu-Trung, MT; Raux, MC, 1976)
"In patients with primary aldosteronism, very low renin activities were found."1.26Enzyme immunoassay for plasma renin activity: II. Clinical application. ( Büchner, M; Dörner, G; Garten, CD; Hubl, W; Schmidt, PK, 1981)
"This hyperkalemia was due to hypoaldosteronism caused by inadequate hormone biosynthesis in the absence of 21-hydroxylase."1.26[21-hydroxylase deficit revealed by hyperkalemia in the absence of renal failure in an insulin-dependent diabetic (author's transl)]. ( Colin, JY; Conessa, JM; Godeau, P; Raux-Eurin, MG; Wechsler, B, 1981)
"In patients with primary hyperaldosteronism adrenal-vein plasma aldosterone/cortisol concentration ratios successfully lateralised all 21 adenomas."1.26The diagnosis of primary hyperaldosteronism. ( Jowett, TP; Lightman, SL; Ma, JT; Payne, NN; Slater, JD; Vaughan, NJ; Wiggins, RC, 1981)
"In the two clinical syndromes of congenital adrenal hyperplasia due to a 21-hydroxylation defect of adrenal steroidogenesis, the simple virilizing and the salt-wasting forms, the 21-hydroxylase activity was studied considering the zona fasciculata and the zona glomerulosa of the adrenal cortex as two separate glands under different regulation."1.26The 21-hydroxylase activity in the glomerulosa and fasciculata of the adrenal cortex in congenital adrenal hyperplasia. ( Chow, D; Kuhnle, U; Levine, LS; New, MI; Pang, S; Rapaport, R, 1981)
"Corticosterone levels were 70 and 92 ng/ml and rose after ACTH (110 and 180 ng/ml)."1.26Dexamethasone-suppressible hypercorticosteronism in two 46,XX subjects with ambiguous genitalia and ovarian cysts. Partial defect of 17 alpha-hydroxylase or 17-20-desmolase. ( Canlorbe, P; Dehennin, L; Girard, F; Konopka, P; Merceron, RE; Roger, M; Seneze, J; Toublanc, JE, 1982)
"The aldosterone secretion was normal and responded normally to sodium deprivation in all patients studied during suppression with carbohydrate-active steroids."1.25Aldosterone hypersecretion in "non-salt-losing" congenital adrenal hyperplasia. ( Bartter, FC; Bryan, GT; Henkin, RI, 1968)

Research

Studies (205)

TimeframeStudies, this research(%)All Research%
pre-1990128 (62.44)18.7374
1990's29 (14.15)18.2507
2000's17 (8.29)29.6817
2010's23 (11.22)24.3611
2020's8 (3.90)2.80

Authors

AuthorsStudies
Fylaktou, I1
Smyrnaki, P1
Sertedaki, A1
Dracopoulou, M1
Kanaka-Gantenbein, C1
Asla, Q1
Sardà, H1
Lerma, E1
Hanzu, FA1
Rodrigo, MT1
Urgell, E1
Pérez, JI1
Webb, SM1
Aulinas, A1
Teti, C1
Bezante, G1
Gatto, F1
Khorrami Chokami, K1
Albertelli, M1
Falchi, M1
Bovio, G1
Nati, ST1
Ferone, D1
Boschetti, M1
Charoensri, S1
Auchus, RJ3
Kamenický, P1
Blanchard, A1
Lamaziere, A1
Piedvache, C1
Donadille, B1
Duranteau, L1
Bry, H1
Gautier, JF1
Salenave, S1
Raffin-Sanson, ML1
Genc, S1
Pietri, L1
Christin-Maitre, S1
Thomas, J1
Lorthioir, A1
Azizi, M1
Chanson, P1
Le Bouc, Y1
Brailly-Tabard, S1
Young, J1
Merke, DP1
Tsai, WH1
Wong, CH1
Dai, SH1
Tsai, CH1
Zeng, YH1
Wijaya, M1
Ma, H1
Zhang, J1
Du, M1
Li, Y1
Chen, Q1
Guo, S1
Boddu, SK1
Madhavan, S1
Lenzini, L1
Prisco, S1
Vanderriele, PE1
Lerco, S1
Torresan, F1
Maiolino, G1
Seccia, TM1
Iacobone, M1
Rossi, GP1
Nanba, K1
Tsuiki, M1
Sawai, K1
Mukai, K1
Nishimoto, K1
Usui, T1
Tagami, T1
Okuno, H1
Yamamoto, T2
Shimatsu, A1
Katabami, T1
Okumura, A1
Kawa, G1
Tanabe, A1
Naruse, M1
Chao, CT1
Wu, VC1
Kuo, CC1
Lin, YH1
Chang, CC1
Chueh, SJ1
Wu, KD1
Pimenta, E1
Stowasser, M2
Tuhan, HU1
Catli, G1
Anik, A1
Onay, H1
Dundar, B1
Bober, E1
Abaci, A1
Jiang, Y2
Zhang, C2
Wang, W2
Su, T2
Zhou, W2
Jiang, L2
Zhu, W1
Xie, J1
Ning, G1
Thiel, A1
Reis, AC1
Haase, M1
Goh, G1
Schott, M1
Willenberg, HS1
Scholl, UI1
Ardhanari, S1
Kannuswamy, R1
Chaudhary, K1
Lockette, W1
Whaley-Connell, A1
Turcu, AF1
Ye, L1
Zhang, Y1
Crudo, V1
Monticone, S1
Burrello, J1
Buffolo, F1
Tetti, M1
Veglio, F2
Mulatero, P3
Vouillarmet, J1
Fernandes-Rosa, F1
Graeppi-Dulac, J1
Lantelme, P1
Decaussin-Petrucci, M1
Thivolet, C1
Peix, JL1
Boulkroun, S1
Clauser, E1
Zennaro, MC1
Niizuma, S1
Nakahama, H1
Kamide, K1
Fukuchi, K1
Iwanaga, Y1
Nakata, H1
Yoshihara, F1
Horio, T1
Nakamura, S1
Kawano, Y1
Hishiki, T1
Kazukawa, I1
Saito, T1
Terui, K1
Mitsunaga, T1
Nakata, M1
Matsuura, G1
Minagawa, M1
Kohno, Y1
Yoshida, H1
Bertello, C1
Sukor, N1
Gordon, R1
Rossato, D1
Daunt, N1
Leggett, D1
Mengozzi, G1
Kahn, SL1
Angle, JF1
Lüthi, S1
Zimmerli, L1
Suter, PM1
Battegay, E1
Bernini, G1
Bacca, A1
Carli, V1
Carrara, D1
Materazzi, G1
Berti, P1
Miccoli, P1
Pisano, R1
Tantardini, V1
Bernini, M1
Taddei, S1
Manikam, L1
Cornes, MP1
Kalra, D1
Ford, C1
Gama, R1
Tsai, LC1
Beavo, JA1
White, PC6
Pascoe, L3
Curnow, KM3
Tannin, G1
Rösler, A3
Seely, EW1
Fox, DA1
Matsell, DG1
Hursh, BE1
Mammen, C1
Harvey, A1
Pasieka, JL1
Kline, G1
So, B1
Potthoff, SA1
Beuschlein, F1
Vonend, O1
Balcells, C1
Gili, T1
Pérez, J1
Corripio, R1
Li, H1
Brochu, M1
Wang, SP1
Rochdi, L1
Côté, M1
Mitchell, G1
Gallo-Payet, N1
Rijnders, RJ1
Christiaens, GC1
Bossers, B1
van der Schoot, CE1
Peter, M2
HUDSON, JB1
CHOBANIAN, AV1
RELMAN, AS1
VEGH, P1
WEISZ, P1
GLAZ, E1
SIPOS, P1
THERIEN, B1
MELLINGER, RC1
CALDWELL, JR1
HOWARD, PJ1
MOOLENAAR, AJ1
BONOMO, L1
PERRINI, M1
TAYEAU, F1
MATTOX, VR1
HAYLES, AB1
SALASSA, RM1
DION, FR1
VISSER, HK4
COST, WS1
DEGENHART, HJ4
WILMINK, R2
CROUGHS, W2
BRYAN, GT2
KLIMAN, B1
BARTTER, FC4
KOWARSKI, A3
FINKELSTEIN, JW1
SPAULDING, JS1
HOLMAN, GH1
MIGEON, CJ5
Stratakis, CA1
Bossis, I1
Perez, MS1
Benencia, H1
Frechtel, GD1
Esteban, EO1
Gil, MC1
Targovnik, HM1
Marquez, NB1
Basiak, A1
Wikiera, B1
Noczyńska, A1
Izumi, Y1
Roggenland, D1
Schneider, S1
Klein, HH1
Kann, PH1
Nimkarn, S1
Lin-Su, K1
Berglind, N1
Wilson, RC2
New, MI12
Shinagawa, T1
Horikawa, R1
Isojima, T1
Naiki, Y1
Tanaka, T1
Katsumata, N1
Peterson, RE3
Greenberg, AJ1
McNamara, H1
McCrory, WW1
Fraser, R2
Vaughan, NJ1
Jowett, TP1
Slater, JD1
Wiggins, RC1
Lightman, SL1
Ma, JT1
Payne, NN1
Nelson, DH1
Limal, JM1
Rappaport, R2
Kuhnle, U4
Chow, D1
Rapaport, R1
Pang, S2
Levine, LS6
Saruta, T1
Kondo, K1
Saito, I1
Nagahama, S1
Suzuki, H1
Konishi, K1
Matsuki, S1
Biglieri, EG13
Wajchenberg, BL2
Malerbi, DA2
Okada, H2
Leme, CE1
Kater, CE8
Tvedegaard, E1
Frederiksen, V1
Olgaard, K1
Nielsen, MD1
Starup, J1
Roger, M2
Merceron, RE2
Girard, F3
Canlorbe, P1
Dehennin, L1
Konopka, P1
Seneze, J1
Toublanc, JE1
Ganguly, A2
de Gennes, JL1
Jambart, S1
Turpin, G1
Elkik, F2
Rosenthal, SM1
Reid, IA1
Kaplan, SL1
Grumbach, MM1
D'Armiento, M1
Reda, G1
Kater, C1
Shackleton, CH2
Stoner, E2
Opitz, JM1
Pollack, MS1
Dupont, B1
Morimoto, I2
Maeda, R1
Izumi, M1
Ishimaru, T1
Nishimori, I1
Nagataki, S1
Pardini, DP1
Vieira, JG1
Pareira, JA1
Gunzcler, P1
Achando, SS1
Batlle, DC1
Kurtzman, NA1
Watanabe, F1
Ryota, T1
Kobayashi, Y1
Günther, RW1
Kelbel, C1
Lenner, V1
Elias, AN1
Grossman, MK1
Meshkinpour, H1
Valenta, LJ1
Bernick, D1
Kondo, T1
Hattori, E1
Saito, Y1
Ueda, K1
Horiuchi, Y1
Wechsler, B1
Colin, JY1
Raux-Eurin, MG1
Conessa, JM1
Godeau, P1
Tokuhiro, E1
Suwa, S1
Maesaka, H1
Schaison, G1
Couzinet, B1
Gourmelen, M3
Bougneres, P1
Kinoshita, K1
Ishida, H1
Minowada, S1
Niijima, T1
Hubl, W1
Büchner, M1
Schmidt, PK1
Garten, CD1
Dörner, G1
DeFronzo, RA1
Bia, M1
Smith, D1
Brust, N1
Chang, B1
Hirai, J1
Schalekamp, MA1
Wenting, GJ1
Man in 't Veld, AJ1
Kuchel, O1
Buu, NT1
Vecsei, P4
Bourque, M1
Hamet, P1
Genest, J1
Holcombe, JH1
Keenan, BS1
Clayton, GW1
Ulick, S3
Eberlein, WR2
Bliffeld, AR1
Chu, MD1
Bongiovanni, AM4
Mercado, AB1
Cheng, KC1
Weber, KT1
Sun, Y1
Campbell, SE1
Slight, SH1
Ganjam, VK1
Griffing, GT1
Swinfard, RW1
Diaz-Arias, AA1
Shizuta, Y1
Kawamoto, T1
Mitsuuchi, Y1
Miyahara, K1
Imura, H1
Martin-Du Pan, RC1
Dahoun, S1
Stalberg, A1
Campana, A1
Dörr, HG1
Sippell, WG2
Panesar, NS1
Yeung, VT1
Chan, JC1
Shek, CC1
Nicholls, MG1
Cockram, CS1
Bartolucci, L1
Fioretti, M1
Rossi, G1
Commissari, R1
Valori, C1
de-Araujo, M1
Sanches, MR1
Suzuki, LA1
Guerra, G1
Farah, SB1
de-Mello, MP1
Merino Arribas, JM1
Rámila de la Torre, E1
Sánchez Martín, J1
Avellanosa Arnaiz, A1
González de la Rosa, JB1
Watanabe, N1
Tsunoda, K1
Sasano, H1
Omata, K1
Imai, Y1
Ito, S1
Abe, K1
Caron, KM1
Soo, SC1
Wetsel, WC1
Stocco, DM1
Clark, BJ1
Parker, KL1
Koppens, PF1
Hoogenboezem, T1
Drop, SL1
de Muinck-Keizer-Schrama, SM1
Dubuis, JM1
Phillips, JL1
Walther, MM1
Pezzullo, JC1
Rayford, W1
Choyke, PL1
Berman, AA1
Linehan, WM1
Doppman, JL1
Gill, JR1
Portrat, S1
Chaussain, JL1
Morel, Y1
Stikkelbroeck, MM1
Otten, BJ1
Oetliker, OH1
Zurbrügg, RP1
Maclaren, NK1
Raiti, S1
Schneider, G1
Genel, M1
Goldman, AS2
Rosenfield, RL1
Pham-Huu-Trung, MT2
Raux, MC1
Baron, MC1
Parth, K1
Zimprich, H1
Swoboda, W1
Brunel, R1
Bohrn, E1
Horner, JM1
Hintz, RL1
Luetscher, JA1
Kaplan, SA1
Koshimizu, T1
Raux-Eurin, MC1
Kumagi, R1
Honour, JW1
Shackleton, HL1
Waldhäusl, W1
Herkner, K1
Nowotny, P1
Bratusch-Marrain, P1
Edwin, C1
Lanes, R1
Lee, PA1
Plotnick, LP1
Kowarski, AA1
Vetter, H1
Brecht, G1
Glänzer, K1
Nick, C1
Siegenthaler, W2
Vetter, W1
Stubbe, P1
Manouguian, G1
Breuer, H2
García-Mayor, RV1
Sopeña, B1
Fluiters, E1
Páramo, C1
Fernández Martín, R1
Galofré, JC1
Andrade Olivié, A1
Wei, JQ1
Wei, JL1
Lucarelli, C1
Zhou, XT1
Wang, DQ1
Dai, WJ1
Li, S1
Li, SM1
Liu, RT1
Fukuchi, S2
Yamamoto, S1
Tateishi, H1
Ueda, S1
Toda, Y1
Zeki, K1
Watanabe, K1
Nakano, Y1
Kashimura, M1
Eto, S1
Moreira, AC1
Leal, AM1
Castro, M1
Reboul, P1
Cordray, JP1
Guillerd, X1
Nys, P1
Rainaut, M1
Kasatkina, EP1
Tiul'pakov, AN1
Goriaĭnova, II1
Shima, H1
Kawanaka, H1
Yabumoto, Y1
Okamoto, E1
Ikoma, F1
Short, F1
James, VH2
Speiser, PW1
Agdere, L1
Ueshiba, H1
Irony, I1
Yamakita, N1
Murase, H1
Yasuda, K1
Noritake, N1
Mercado-Asis, LB1
Miura, K2
Grankvist, K1
Bäckström, BT1
Gustavsson, G1
Holmgren, G1
Brown, JJ1
Mason, PA1
Morton, JJ1
Lever, AF1
Robertson, JI1
Lee, HA1
Miller, H1
Imperato-McGinley, J1
Gautier, T1
Shackleton, C1
Wajchenberg, B1
Land, M1
Uribarri, J1
Carroll, HJ1
Toyoda, N1
Murata, K1
Tanaka, Y1
Kawai, Y1
Nishiyama, Y1
Matsumoto, T1
Sugiyama, Y1
Ribstein, J1
Sciolla, JP1
Barjon, P1
Sultan, C1
Forest, M1
de Peretti, E1
Glass, IA1
Wallace, AM1
Beattie, TJ1
Lewicka, S3
Bige, K2
Fisher, T1
Winter, J3
Abdelhamid, S3
Heinrich, U3
Bokkenheuser, VD2
Rodríguez Portales, JA1
Arteaga, E1
López Moreno, JM1
Zachmann, M1
Dimartino-Nardi, J1
Oberfield, SE1
Bokkenheuser, V1
Takeda, R1
Scaroni, C1
Opocher, G1
Mantero, F1
Iimura, O1
Shimamoto, K1
Hotta, D1
Nakata, T1
Mito, T1
Kumamoto, Y1
Dempo, K1
Ogihara, T1
Naruse, K1
Liu, LS1
Few, JD1
Cacciari, E2
Dallera, L1
Tassoni, P1
Cicognani, A1
Miano, A1
Blunck, W2
Hall, K1
Hökfelt, B1
Henkin, RI1
Lim, NY1
Mimica, N1
Dingman, JF1
Drews, J1
Jahnecke, J1
Werning, C1
Simpoulos, AP1
Marshall, JR1
Delea, CS1
Fore, WW1
Bledsoe, T1
Weber, DM1
Akers, R1
Brooks, RT1
Beitins, IZ1
Bayard, F1
Sizonenko, PC1
Riondel, AM2
Kohlberg, IJ1
Paunier, L1
Takeuchi, T1
Miura, Y1
Shioji, T1
Furuyama, T1
Dahl, V2
Rivarola, MA1
Bergadá, C2
Graef, V1
New, M1
Seaman, MP1
Strickland, AL1
Kotchen, TA1
Osterwalder, H1
Bierich, JR1
Loras, B1
Haour, F1
Bertrand, J1
Klevit, HD1
Martoni, L1
Imai, M1
Igarashi, Y1
Sokabe, H1
Godard, C1
Veyrat, R1
Mégevand, A1
Muller, AF1
Russell, A1
Petri, G1
Julesz, M1
Kovács, K1
László, FA1
Durszt, F1
Troján, I1
Vel'tishchev, IuE1
Tabolin, VA1
Deshchekina, MF1
Lebedev, VP1
Badalov, NA1
Vodolazhskaia, EE1
Bayer, JM1
Tonutti, E1
Nocke, W1
Nocke, L1
Schriefers, H1
Smith, ER1

Clinical Trials (4)

Trial Overview

TrialPhaseEnrollmentStudy TypeStart DateStatus
Evaluation of Adrenocortical Functions by Insulin Tolerance Test and Sodium Depletion in Women With Nonclassical Congenital Adrenal Hyperplasia Due to 21-hydroxylase Deficiency in Comparison With Healthy Volunteers.[NCT01862380]41 participants (Actual)Interventional2013-02-28Active, not recruiting
Effect of Anti-hypertensive Medications on the Diagnostic Accuracy in Screening for Primary Aldosteronism:a Prospective Study[NCT04991961]330 participants (Anticipated)Observational2020-09-15Recruiting
Towards Cost-effective Management of Patients With Hypertension Due to Primary Aldosteronism: Adrenal Vein Sampling or Ct-scan?[NCT01096654]Phase 3200 participants (Actual)Interventional2010-07-31Completed
Multicenter Study on Use and Interpretation of Adrenal Vein Sampling[NCT01234220]2,604 participants (Actual)Observational2010-05-31Completed
[information is prepared from clinicaltrials.gov, extracted Sep-2024]

Reviews

43 reviews available for aldosterone and Congenital Adrenal Hyperplasia

ArticleYear
Congenital adrenal hyperplasia caused by compound heterozygosity of two novel CYP11B1 gene variants.
    Hormones (Athens, Greece), 2022, Volume: 21, Issue:1

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Aldosterone; Child; Female; Humans; Hydrocortisone; Mut

2022
11-Deoxycorticosterone Producing Adrenal Hyperplasia as a Very Unusual Cause of Endocrine Hypertension: Case Report and Systematic Review of the Literature.
    Frontiers in endocrinology, 2022, Volume: 13

    Topics: Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Carcinoma; Desoxycorti

2022
Therapeutic management of congenital forms of endocrine hypertension.
    European journal of endocrinology, 2023, Nov-08, Volume: 189, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Humans; Hyperaldosteronism; Hypertension; Mineralocort

2023
Congenital Adrenal Hyperplasia Due to 21-Hydroxylase Deficiency.
    The New England journal of medicine, 2020, 09-24, Volume: 383, Issue:13

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Aldosterone; Androgen

2020
Diagnosis and management of primary aldosteronism: an updated review.
    Annals of medicine, 2013, Volume: 45, Issue:4

    Topics: Adenoma; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adrenalectomy; Aldosterone; Humans; Hypera

2013
Mineralocorticoid and apparent mineralocorticoid syndromes of secondary hypertension.
    Advances in chronic kidney disease, 2015, Volume: 22, Issue:3

    Topics: Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocortical Adenoma; Aldosterone; Drug

2015
Adrenal steroidogenesis and congenital adrenal hyperplasia.
    Endocrinology and metabolism clinics of North America, 2015, Volume: 44, Issue:2

    Topics: Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocortical Adenoma; Aldosterone; Andr

2015
Hyperaldosteronism: How to Discriminate Among Different Disease Forms?
    High blood pressure & cardiovascular prevention : the official journal of the Italian Society of Hypertension, 2016, Volume: 23, Issue:3

    Topics: Adenoma; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Aldosterone; Biomarkers; Diagnos

2016
Adrenal vein sampling.
    Techniques in vascular and interventional radiology, 2010, Volume: 13, Issue:2

    Topics: Adrenal Cortex Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adrenocort

2010
The roles of cyclic nucleotide phosphodiesterases (PDEs) in steroidogenesis.
    Current opinion in pharmacology, 2011, Volume: 11, Issue:6

    Topics: 3',5'-Cyclic-AMP Phosphodiesterases; 3',5'-Cyclic-GMP Phosphodiesterases; Adrenal Cortex; Adrenal Hy

2011
Molecular biology of 11β-hydroxylase and 11β-hydroxysteroid dehydrogenase enzymes.
    The Journal of steroid biochemistry and molecular biology, 1992, Volume: 43, Issue:8

    Topics: 11-beta-Hydroxysteroid Dehydrogenases; Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone;

1992
[Primay hyperaldosteronism--diagnostic and treatment].
    Deutsche medizinische Wochenschrift (1946), 2012, Volume: 137, Issue:48

    Topics: Adrenal Cortex Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocortical Adenoma; A

2012
Congenital adrenal hyperplasia: 11beta-hydroxylase deficiency.
    Seminars in reproductive medicine, 2002, Volume: 20, Issue:3

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Humans; Hydrocortisone; Mutation; Prenatal Care; Prena

2002
Genetics of the adrenal gland.
    Reviews in endocrine & metabolic disorders, 2004, Volume: 5, Issue:1

    Topics: 11-beta-Hydroxysteroid Dehydrogenases; 3-Hydroxysteroid Dehydrogenases; Adrenal Gland Diseases; Adre

2004
Aldosterone synthase deficiency and related disorders.
    Molecular and cellular endocrinology, 2004, Mar-31, Volume: 217, Issue:1-2

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Cortisone; Cytochrome P-450 CYP11B2; Exons; Humans; Hy

2004
[Salt wasting syndrome caused by congenital, insufficient synthesis or aldosterone function--etiology, diagnosis and management].
    Endokrynologia, diabetologia i choroby przemiany materii wieku rozwojowego : organ Polskiego Towarzystwa Endokrynologow Dzieciecych, 2005, Volume: 11, Issue:2

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Humans; Potassium Chloride; Sodium Chloride; Steroid 2

2005
[18-hydroxycorticosterone (18-OH -B)].
    Nihon rinsho. Japanese journal of clinical medicine, 2005, Volume: 63 Suppl 8

    Topics: 18-Hydroxycorticosterone; Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Aldoste

2005
Disorders of the adrenal cortex: their effects on electrolyte metabolism.
    Clinics in endocrinology and metabolism, 1984, Volume: 13, Issue:2

    Topics: Addison Disease; Adrenal Cortex Diseases; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital;

1984
The adrenal cortex: physiological function and disease.
    Major problems in internal medicine, 1980, Volume: 18

    Topics: Addison Disease; Adrenal Cortex; Adrenal Cortex Diseases; Adrenal Cortex Hormones; Adrenal Hyperplas

1980
[Aldosterone tests in children (author's transl)].
    Annales de pediatrie, 1980, Volume: 27, Issue:2

    Topics: Adolescent; Adrenal Cortex Function Tests; Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; A

1980
Hypertension of childhood with suppressed renin.
    Endocrine reviews, 1980,Fall, Volume: 1, Issue:4

    Topics: 18-Hydroxydesoxycorticosterone; 20-alpha-Dihydroprogesterone; Adolescent; Adrenal Cortex; Adrenal Hy

1980
Enzymatic disorders and hypertension.
    Clinics in endocrinology and metabolism, 1981, Volume: 10, Issue:3

    Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Adult; A

1981
Clinical disorders of aldosterone metabolism.
    Disease-a-month : DM, 1984, Volume: 30, Issue:8

    Topics: Acidosis; Adrenal Hyperplasia, Congenital; Aldosterone; Bartter Syndrome; Cushing Syndrome; Diagnosi

1984
Congenital adrenal hyperplasia.
    Clinical biochemistry, 1981, Volume: 14, Issue:5

    Topics: 17-Hydroxysteroid Dehydrogenases; 18-Hydroxycorticosterone; 3-Hydroxysteroid Dehydrogenases; Adrenal

1981
Clinical disorders of hyperkalemia.
    Annual review of medicine, 1982, Volume: 33

    Topics: Acid-Base Imbalance; Addison Disease; Adrenal Hyperplasia, Congenital; Adult; Aged; Aldosterone; Cat

1982
Pathogenesis of mineralocorticoid hypertension.
    Clinics in endocrinology and metabolism, 1981, Volume: 10, Issue:3

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Animals; Bloo

1981
Disorders of steroid 11 beta-hydroxylase isozymes.
    Endocrine reviews, 1994, Volume: 15, Issue:4

    Topics: Adrenal Cortex; Adrenal Hyperplasia, Congenital; Aldosterone; Cytochrome P-450 CYP11B2; Cytochrome P

1994
Disorders of aldosterone biosynthesis and action.
    The New England journal of medicine, 1994, Jul-28, Volume: 331, Issue:4

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Cytochrome P-450 CYP11B2; Cytochrome P-450 Enzyme Syst

1994
Molecular analysis of CYP21 and C4 genes in Brazilian families with the classical form of steroid 21-hydroxylase deficiency.
    Brazilian journal of medical and biological research = Revista brasileira de pesquisas medicas e biologicas, 1996, Volume: 29, Issue:1

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Androgens; Blotting, Southern; Brazil; Child; Child, P

1996
[11-beta-hydroxylase deficiency and glucocorticoid-sensitive hyperaldosteronism].
    Anales espanoles de pediatria, 1996, Volume: 44, Issue:6

    Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Child, Preschool; Dexamet

1996
Inherited forms of mineralocorticoid hypertension.
    Hypertension (Dallas, Tex. : 1979), 1996, Volume: 28, Issue:6

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Animals; Humans; Hydrocortisone; Hypertension; Mineral

1996
Disorders of the aldosterone synthase and steroid 11beta-hydroxylase deficiencies.
    Hormone research, 1999, Volume: 51, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Cytochrome P-450 CYP11B2; Humans; Hydrocortisone; Muta

1999
17 alpha-hydroxylation deficiency.
    Endocrinology and metabolism clinics of North America, 1991, Volume: 20, Issue:2

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Child; Female; Humans; Hypertension

1991
Correctable subsets of primary aldosteronism. Primary adrenal hyperplasia and renin responsive adenoma.
    American journal of hypertension, 1990, Volume: 3, Issue:7

    Topics: 18-Hydroxycorticosterone; Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenal

1990
Potassium metabolism and hypertension.
    Journal of clinical hypertension, 1985, Volume: 1, Issue:4

    Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Animals; Catecholamines;

1985
Basic and clinical aspects of congenital adrenal hyperplasia.
    Journal of steroid biochemistry, 1987, Volume: 27, Issue:1-3

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Gene Frequency; Genetic Linkage; HLA Antigens; HLA-B A

1987
Adrenocorticosteroids: chemistry, synthesis and disturbances in disease.
    Clinics in endocrinology and metabolism, 1985, Volume: 14, Issue:4

    Topics: 3-Hydroxysteroid Dehydrogenases; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Aldehyde-

1985
[Some diagnostic and therapeutic aspects of adrenal disorders in childhood (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1973, Volume: 121, Issue:10

    Topics: Addison Disease; Adrenal Cortex Hormones; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; A

1973
[Adrenal cortex function tests and their interpretation].
    Nihon rinsho. Japanese journal of clinical medicine, 1969, Volume: 27, Issue:2

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aldosterone; Androg

1969
[Adrenal gland hyperfunctions].
    Wiener medizinische Wochenschrift (1946), 1970, Oct-10, Volume: 120, Issue:41

    Topics: Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfuncti

1970
[Enzyme defects in steroid hormone biosynthesis].
    Deutsche medizinische Wochenschrift (1946), 1973, Jun-29, Volume: 98, Issue:26

    Topics: Adrenal Cortex Hormones; Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Estrogens; Fe

1973
Disorders of adrenal steroid biogenesis.
    Recent progress in hormone research, 1967, Volume: 23

    Topics: Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction;

1967
[Congenital errors of adrenal cortex steroid synthesis].
    Recenti progressi in medicina, 1970, Volume: 49, Issue:2

    Topics: Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Aldosterone;

1970

Trials

5 trials available for aldosterone and Congenital Adrenal Hyperplasia

ArticleYear
Aldosterone signaling defect in young infants: single-center report and review.
    BMC endocrine disorders, 2021, Jul-09, Volume: 21, Issue:1

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Biomarkers; Child, Preschool; Cytochrome P-450 CYP11B2

2021
Impact of different diagnostic criteria during adrenal vein sampling on reproducibility of subtype diagnosis in patients with primary aldosteronism.
    Hypertension (Dallas, Tex. : 1979), 2010, Volume: 55, Issue:3

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Cath

2010
Impact of different diagnostic criteria during adrenal vein sampling on reproducibility of subtype diagnosis in patients with primary aldosteronism.
    Hypertension (Dallas, Tex. : 1979), 2010, Volume: 55, Issue:3

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Cath

2010
Impact of different diagnostic criteria during adrenal vein sampling on reproducibility of subtype diagnosis in patients with primary aldosteronism.
    Hypertension (Dallas, Tex. : 1979), 2010, Volume: 55, Issue:3

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Cath

2010
Impact of different diagnostic criteria during adrenal vein sampling on reproducibility of subtype diagnosis in patients with primary aldosteronism.
    Hypertension (Dallas, Tex. : 1979), 2010, Volume: 55, Issue:3

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Cath

2010
Colonic mucosal potential differences in the management of 21-hydroxylase deficiency.
    Archives of internal medicine, 1980, Volume: 140, Issue:12

    Topics: Action Potentials; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Androstenedione; Clinical Tr

1980
Predictive value of preoperative tests in discriminating bilateral adrenal hyperplasia from an aldosterone-producing adrenal adenoma.
    The Journal of clinical endocrinology and metabolism, 2000, Volume: 85, Issue:12

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adrenocorticotropi

2000
A method for the simultaneous determination of the secretion rates of cortisol, 11-desoxycortisol, corticosterone, 11-desoxycorticosterone and aldosterone.
    The Journal of clinical endocrinology and metabolism, 1969, Volume: 29, Issue:4

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Carbon Isotopes; Child; Child, Pres

1969

Other Studies

157 other studies available for aldosterone and Congenital Adrenal Hyperplasia

ArticleYear
An unusual cause of adrenal insufficiency with elevation of 17-hydroxyprogesterone: case report.
    BMC endocrine disorders, 2023, May-29, Volume: 23, Issue:1

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenal Insu

2023
Cortisol and Aldosterone Responses to Hypoglycemia and Na Depletion in Women With Non-Classic 21-Hydroxylase Deficiency.
    The Journal of clinical endocrinology and metabolism, 2020, 01-01, Volume: 105, Issue:1

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Biomarkers; Case-Control Studies; E

2020
Adrenal Tumor Mimicking Non-Classic Congenital Adrenal Hyperplasia.
    Frontiers in endocrinology, 2020, Volume: 11

    Topics: Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adrenocortical Adenoma; Ad

2020
High aldosterone and cortisol levels in salt wasting congenital adrenal hyperplasia: a clinical conundrum.
    Journal of pediatric endocrinology & metabolism : JPEM, 2017, Nov-27, Volume: 30, Issue:12

    Topics: Acidosis; Adrenal Hyperplasia, Congenital; Aldosterone; Child; Dehydration; Diagnosis, Differential;

2017
PTH Modulation by Aldosterone and Angiotensin II is Blunted in Hyperaldosteronism and Rescued by Adrenalectomy.
    The Journal of clinical endocrinology and metabolism, 2019, 09-01, Volume: 104, Issue:9

    Topics: Adenoma; Adrenal Hyperplasia, Congenital; Adrenalectomy; Aldosterone; Angiotensin II; Antihypertensi

2019
Histopathological diagnosis of primary aldosteronism using CYP11B2 immunohistochemistry.
    The Journal of clinical endocrinology and metabolism, 2013, Volume: 98, Issue:4

    Topics: Adenoma; Adolescent; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Adult; Aged; Aldoste

2013
Cross-reactivity of adrenal steroids with aldosterone may prevent the accurate diagnosis of congenital adrenal hyperplasia.
    Journal of pediatric endocrinology & metabolism : JPEM, 2015, Volume: 28, Issue:5-6

    Topics: Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Aged; Aldosterone; Cross Reactions; Humans

2015
Diagnostic value of ACTH stimulation test in determining the subtypes of primary aldosteronism.
    The Journal of clinical endocrinology and metabolism, 2015, Volume: 100, Issue:5

    Topics: Adenoma; Adrenal Cortex Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotro

2015
PRKACA mutations in cortisol-producing adenomas and adrenal hyperplasia: a single-center study of 60 cases.
    European journal of endocrinology, 2015, Volume: 172, Issue:6

    Topics: Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adrenocortical Adenoma; Ad

2015
Factors affecting parathyroid hormone levels in different types of primary aldosteronism.
    Clinical endocrinology, 2016, Volume: 85, Issue:2

    Topics: Adenoma; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adult; Aldosterone; Calcium; Essential Hype

2016
Aldosterone-Producing Adenoma With a Somatic KCNJ5 Mutation Revealing APC-Dependent Familial Adenomatous Polyposis.
    The Journal of clinical endocrinology and metabolism, 2016, Volume: 101, Issue:11

    Topics: Adenoma; Adenomatous Polyposis Coli; Adenomatous Polyposis Coli Protein; Adrenal Gland Neoplasms; Ad

2016
The cutoff value of aldosterone-to-renin ratio for the diagnosis of primary aldosteronism in patients taking antihypertensive medicine.
    Clinical and experimental hypertension (New York, N.Y. : 1993), 2008, Volume: 30, Issue:7

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Aged; Aldosterone; Antihypertensi

2008
Diagnosis of adrenocortical tumor in a neonate by detection of elevated blood 17-hydroxyprogesterone measured as a routine neonatal screening for congenital adrenal hyperplasia: a case report.
    Journal of pediatric surgery, 2008, Volume: 43, Issue:10

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Adrenal Ins

2008
[Primary hyperaldosteronism].
    Praxis, 2011, Mar-16, Volume: 100, Issue:6

    Topics: Adenoma; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Aged; Aldosterone; Carcinoma; Di

2011
Cardiovascular changes in patients with primary aldosteronism after surgical or medical treatment.
    Journal of endocrinological investigation, 2012, Volume: 35, Issue:3

    Topics: Adenoma; Adrenal Cortex Neoplasms; Adrenal Hyperplasia, Congenital; Adult; Aged; Aldosterone; Blood

2012
Transient pseudohypoaldosteronism masquerading as congenital adrenal hyperplasia.
    Annals of clinical biochemistry, 2011, Volume: 48, Issue:Pt 4

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Chimerism; Chromosome Aberrations; Diagnosis, Differen

2011
Editorial overview: the adrenal cortex.
    Current opinion in endocrinology, diabetes, and obesity, 2012, Volume: 19, Issue:3

    Topics: Adrenal Cortex; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; Ald

2012
A rare cause of hypertension in a healthy 2-year-old female: questions.
    Pediatric nephrology (Berlin, Germany), 2012, Volume: 27, Issue:11

    Topics: Adrenal Cortex Function Tests; Adrenal Hyperplasia, Congenital; Aldosterone; Antihypertensive Agents

2012
Modification of the protocol for selective adrenal venous sampling results in both a significant increase in the accuracy and necessity of the procedure in the management of patients with primary hyperaldosteronism.
    Surgery, 2012, Volume: 152, Issue:4

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenalectomy; Al

2012
Pseudohypoaldosteronism without nephropathy masking salt-wasting congenital adrenal hyperplasia genetically confirmed.
    BMJ case reports, 2013, Jan-30, Volume: 2013

    Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Alleles; Diagnosis, Differential; Emer

2013
Hormone-sensitive lipase deficiency in mice causes lipid storage in the adrenal cortex and impaired corticosterone response to corticotropin stimulation.
    Endocrinology, 2002, Volume: 143, Issue:9

    Topics: Adrenal Cortex; Adrenal Hyperplasia, Congenital; Adrenal Medulla; Adrenocorticotropic Hormone; Aldos

2002
[Congenital adrenal hyperplasia: clinical aspects and neonatal screening].
    Nederlands tijdschrift voor geneeskunde, 2002, Sep-07, Volume: 146, Issue:36

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Dexamethasone; Female; Humans; Infant, Newborn; Male;

2002
Hypoaldosteronism; a clinical study of a patient with an isolated adrenal mineralocorticoid deficiency, resulting in hyperkalemia and Stokes-Adams attacks.
    The New England journal of medicine, 1957, Sep-19, Volume: 257, Issue:12

    Topics: Adams-Stokes Syndrome; Adrenal Hyperplasia, Congenital; Aldosterone; Heart Block; Humans; Hyperkalem

1957
[Increased urinary aldosterone activity in adrenal carcinoma leading to virilism].
    Orvosi hetilap, 1958, Mar-30, Volume: 99, Issue:13

    Topics: Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Aldosterone; Body Fluids; Female; Humans; V

1958
Primary aldosteronism due to adrenal hyperplasia; occurrence in a boy aged 10 years.
    A.M.A. journal of diseases of children, 1959, Volume: 98, Issue:1

    Topics: Adrenal Cortex; Adrenal Cortex Diseases; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfuncti

1959
Effect of cortisone on the excretion of aldosterone in virilising adrenal hyperplasia.
    Lancet (London, England), 1960, Apr-16, Volume: 1, Issue:7129

    Topics: Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Aldosterone; Cortisone; Hyperplasia

1960
[Primary hyperaldosteronism due to unilateral adrenal hyperplasia, with diabetes].
    Il Policlinico. Sezione pratica, 1960, May-16, Volume: 67

    Topics: Adrenal Cortex; Adrenal Cortex Diseases; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Al

1960
[GENERAL CONSIDERATION ON TECHNOLOGY IN MEDICINE: ADRENAL FUNCTION TESTS; APPLICATION TO HYPERCORTICISM].
    Laval medical, 1963, Volume: 34

    Topics: 17-Ketosteroids; Adenoma; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocortical H

1963
URINARY STEROID PATTERNS AND LOSS OF SALT IN CONGENITAL ADRENAL HYPERPLASIA.
    The Journal of clinical endocrinology and metabolism, 1964, Volume: 24

    Topics: 17-Ketosteroids; Adolescent; Adrenal Cortex Hormones; Adrenal Gland Diseases; Adrenal Hyperplasia, C

1964
[A NEW HEREDITARY ENZYME DEFECT IN ALDOSTERONE SYNTHESIS (18-OXIDATION DEFECT)].
    Nederlands tijdschrift voor geneeskunde, 1964, Oct-24, Volume: 108

    Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adrenogenital Syndrome; Aldosterone; B

1964
ALDOSTERONE- AND CORTISOL SECRETION RATES IN INFANTS AND CHILDREN WITH CONGENITAL ADRENAL HYPERPLASIA SUGGESTING DIFFERENT 21-HYDROXYLATION DEFECTS IN "SALT-LOSERS" AND "NON SALT-LOSERS".
    Acta endocrinologica, 1965, Volume: 48

    Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Aldoster

1965
[PRODUCTION OF ALDOSTERONE AND HYDROCORTISONE IN CHILDREN WITH CONGENITAL ADRENAL HYPERPLASIA (21-HYDROXYLASE DEFECT), WITH AND WITHOUT "SALT-LOSING" SYNDROME].
    Nederlands tijdschrift voor geneeskunde, 1965, Jun-19, Volume: 109

    Topics: Adolescent; Adrenal Cortex Hormones; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Aldost

1965
IMPAIRED ALDOSTERONE PRODUCTION IN "SALT-LOSING" CONGENITAL ADRENAL HYPERPLASIA.
    The Journal of clinical investigation, 1965, Volume: 44

    Topics: Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Aldosterone; Child; Chromatography; Humans;

1965
ALDOSTERONE SECRETION RATE IN CONGENITAL ADRENAL HYPERPLASIA. A DISCUSSION OF THE THEORIES ON THE PATHOGENESIS OF THE SALT-LOSING FORM OF THE SYNDROME.
    The Journal of clinical investigation, 1965, Volume: 44

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Aldosterone; Bodily Secretions;

1965
17alpha-hydroxylase deficiency : biochemical and molecular findings in two sisters and their family.
    Molecular diagnosis : a journal devoted to the understanding of human disease through the clinical application of molecular biology, 2004, Volume: 8, Issue:3

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Amino Acid Sequence; Base Sequence; Corticosterone; Ex

2004
[Endosonography -- an additional diagnostic possibility in the differentiation between the two common types of primary hyperaldosteronism].
    Medizinische Klinik (Munich, Germany : 1983), 2006, Jan-15, Volume: 101, Issue:1

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenalectomy; Aged; Aldosterone;

2006
Aldosterone-to-renin ratio as a marker for disease severity in 21-hydroxylase deficiency congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 2007, Volume: 92, Issue:1

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Age Distribution; Aldosterone; Biomarkers; Child

2007
Nonclassic steroid 21-hydroxylase deficiency due to a homozygous V281L mutation in CYP21A2 detected by the neonatal mass-screening program in Japan.
    Endocrine journal, 2007, Volume: 54, Issue:6

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Base Sequence; Brazil; DNA; Female; Humans; Hydrocorti

2007
A new form of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1967, Volume: 27, Issue:2

    Topics: Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Aldosterone;

1967
Renal tubular response to aldosterone in normal infants and children with adrenal disorders.
    The Journal of clinical endocrinology and metabolism, 1967, Volume: 27, Issue:8

    Topics: Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; Aldosterone; Child; Glomerular Filtration Ra

1967
Salt-losing in an infant with congenital adrenal hyperplasia and normal aldosterone production.
    Acta paediatrica Scandinavica, 1967, Volume: 56, Issue:2

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Diet; Female; Humans; Hydrocortisone; Infant, Newborn;

1967
The diagnosis of primary hyperaldosteronism.
    Lancet (London, England), 1981, Jan-17, Volume: 1, Issue:8212

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adult; Aged; Aldosterone; Diagnos

1981
The 21-hydroxylase activity in the glomerulosa and fasciculata of the adrenal cortex in congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1981, Volume: 52, Issue:3

    Topics: Adrenal Cortex; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormon

1981
Control of aldosterone in 17 alpha-hydroxylase deficiency.
    Hormone research, 1980, Volume: 13, Issue:2

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aldosterone; Desoxy

1980
The zonal origins of the mineralocorticoid hormones in the 21-hydroxylation deficiency of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1981, Volume: 53, Issue:5

    Topics: 18-Hydroxycorticosterone; 18-Hydroxydesoxycorticosterone; Adolescent; Adrenal Cortex; Adrenal Hyperp

1981
Two cases of 17 alpha-hydroxylase deficiency--one combined with complete gonadal agenesis.
    Acta endocrinologica, 1981, Volume: 98, Issue:2

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Al

1981
Dexamethasone-suppressible hypercorticosteronism in two 46,XX subjects with ambiguous genitalia and ovarian cysts. Partial defect of 17 alpha-hydroxylase or 17-20-desmolase.
    Hormone research, 1982, Volume: 16, Issue:1

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Corticosteron

1982
New insights and questions about glucocorticoid-suppressible hyperaldosteronism.
    The American journal of medicine, 1982, Volume: 72, Issue:6

    Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Animals;

1982
17 alpha-hydroxylase deficiency syndrome associated with bilateral streak gonads and impaired development of Müllerian ducts derivatives. Report of a case.
    Acta endocrinologica, 1982, Volume: 100, Issue:1

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Amenorrhea; C

1982
Renin substrate depletion in salt-losing congenital virilizing adrenal hyperplasia: low plasma renin activity despite increased renin concentration.
    The Journal of pediatrics, 1983, Volume: 102, Issue:1

    Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Angiotensinogen; Angioten

1983
17 alpha-hydroxylase deficiency: mineralocorticoid hormone profiles in an affected family.
    The Journal of clinical endocrinology and metabolism, 1983, Volume: 56, Issue:4

    Topics: 18-Hydroxycorticosterone; 18-Hydroxydesoxycorticosterone; Adolescent; Adrenal Hyperplasia, Congenita

1983
Nonsalt-losing congenital adrenal hyperplasia due to 3 beta-hydroxysteroid dehydrogenase deficiency with normal glomerulosa function.
    The Journal of clinical endocrinology and metabolism, 1983, Volume: 56, Issue:4

    Topics: 3-Hydroxysteroid Dehydrogenases; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldos

1983
An autopsy case of 17 alpha-hydroxylase deficiency with malignant hypertension.
    The Journal of clinical endocrinology and metabolism, 1983, Volume: 56, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aldosterone; Alkalosis; Dexamet

1983
Impaired mineralocorticoid hormone responses to adrenocorticotropin stimulation: additional characterization of heterozygosity for the 21-hydroxylase deficiency type of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1983, Volume: 57, Issue:5

    Topics: 17-alpha-Hydroxyprogesterone; 18-Hydroxycorticosterone; 18-Hydroxydesoxycorticosterone; Adrenal Hype

1983
The effects of long-term normalization of sodium balance on linear growth in disorders with aldosterone deficiency.
    Acta endocrinologica, 1983, Volume: 102, Issue:4

    Topics: 17-alpha-Hydroxyprogesterone; Addison Disease; Adolescent; Adrenal Hyperplasia, Congenital; Aldoster

1983
Suppression and stimulation of mineralocorticoid hormones (MCH) in the simple virilizing form of congenital adrenal hyperplasia (CAH) evaluated by the quantitation in adrenal venous blood.
    Journal of steroid biochemistry, 1983, Volume: 19, Issue:1B

    Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Al

1983
Enzyme immunoassay for serum 18-hydroxycorticosterone and its clinical application.
    Steroids, 1984, Volume: 43, Issue:5

    Topics: 18-Hydroxycorticosterone; ACTH Syndrome, Ectopic; Addison Disease; Adenoma; Adrenal Hyperplasia, Con

1984
Real-time ultrasound of normal adrenal glands and small tumors.
    Journal of clinical ultrasound : JCU, 1984, Volume: 12, Issue:4

    Topics: Adrenal Cortex Neoplasms; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital;

1984
Distinctive plasma aldosterone, 18-hydroxycorticosterone, and 18-hydroxydeoxycorticosterone profile in the 21-, 17 alpha-, and 11 beta-hydroxylase deficiency types of congenital adrenal hyperplasia.
    The American journal of medicine, 1983, Volume: 75, Issue:1

    Topics: 18-Hydroxycorticosterone; 18-Hydroxydesoxycorticosterone; Adolescent; Adrenal Hyperplasia, Congenita

1983
[Aldosterone metabolism in dizygotic twins with simple masculinizing-type adrenal gland hyperplasia due to 21-hydroxylase deficiency].
    Horumon to rinsho. Clinical endocrinology, 1983, Volume: 31 Suppl

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Child, Preschool; Diseases in Twins; Female; Humans; M

1983
[21-hydroxylase deficit revealed by hyperkalemia in the absence of renal failure in an insulin-dependent diabetic (author's transl)].
    Annales de medecine interne, 1981, Volume: 132, Issue:4

    Topics: Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Diabetes Mellitus, Type 1; Female; Humans; Hype

1981
[Clinical use of fludrocortisone acetate in congenital adrenal hyperplasia. Effect on plasma renin activity and aldosterone (author's transl)].
    Horumon to rinsho. Clinical endocrinology, 1980, Volume: 28, Issue:3

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Child, Preschool; Drug Therapy, Combination; Female; F

1980
Angiotensin and adrenal steroidogenesis: study of 21-hydroxylase-deficient congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1980, Volume: 51, Issue:6

    Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Androstenedione; Angiotensin II

1980
Dissociation of plasma renin activity and plasma aldosterone level during dexamethasone suppression test in non-salt-losers with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
    Endocrinologia japonica, 1980, Volume: 27, Issue:6

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Dexamethasone; Female; Humans;

1980
Enzyme immunoassay for plasma renin activity: II. Clinical application.
    Endokrinologie, 1981, Volume: 78, Issue:1

    Topics: Addison Disease; Adrenal Hyperplasia, Congenital; Aldosterone; Anovulation; Child; Contraceptives, O

1981
The unique patterns of plasma aldosterone and 18-hydroxycorticosterone concentrations in the 17 alpha-hydroxylase deficiency syndrome.
    The Journal of clinical endocrinology and metabolism, 1982, Volume: 55, Issue:2

    Topics: 18-Hydroxycorticosterone; 18-Hydroxydesoxycorticosterone; Adrenal Hyperplasia, Congenital; Adult; Al

1982
Are plasma aldosterone surges in primary aldosteronism due to a loss of an inhibitory dopaminergic control?
    The Journal of clinical endocrinology and metabolism, 1980, Volume: 51, Issue:2

    Topics: Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenalectomy; Adult; Aldosterone; Circ

1980
Plasma 17 alpha-hydroxyprogesterone and aldosterone concentrations in infants and children with congenital adrenal hyperplasia--the role of salt-losing hormones in salt wasting.
    The Journal of pediatrics, 1981, Volume: 98, Issue:4

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Child, Preschool; Female; Humans; Hydroxyprogesterones

1981
Evidence for an aldosterone biosynthetic defect in congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1980, Volume: 51, Issue:6

    Topics: 18-Hydroxycorticosterone; Adolescent; Adrenal Hyperplasia, Congenital; Aldosterone; Child; Child, Pr

1980
Steroid 21-hydroxylase deficiency: genotype may not predict phenotype.
    The Journal of clinical endocrinology and metabolism, 1995, Volume: 80, Issue:8

    Topics: Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Alleles; Child, Preschool; Female; Genotype; Hu

1995
Chronic mineralocorticoid excess and cardiovascular remodeling.
    Steroids, 1995, Volume: 60, Issue:1

    Topics: 11-beta-Hydroxysteroid Dehydrogenases; Adenoma; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyp

1995
Inborn errors of aldosterone biosynthesis in humans.
    Steroids, 1995, Volume: 60, Issue:1

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Amino Acid Sequence; Base Sequence; Cytochrome P-450 C

1995
[Primary amenorrhea and arterial hypertension in a case of 17 alpha-hydroxylase deficiency].
    Journal de gynecologie, obstetrique et biologie de la reproduction, 1994, Volume: 23, Issue:2

    Topics: Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Amenorrhea; Corticosterone; Desoxycorticosteron

1994
Prenatal dexamethasone treatment in pregnancies at risk for congenital adrenal hyperplasia due to 21-hydroxylase deficiency: effect on midgestational amniotic fluid steroid levels.
    The Journal of clinical endocrinology and metabolism, 1993, Volume: 76, Issue:1

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Aldosterone; Amniocentesis; Amniotic

1993
17 alpha-Hydroxylase deficiency with persistence of müllerian ducts in a genotypic male and paradoxical aldosterone secretion.
    Postgraduate medical journal, 1993, Volume: 69, Issue:808

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Aldosterone; Disorders of Sex Development; Female; Geno

1993
[Male pseudohermaphroditism due to 17-alpha-hydroxylase deficiency].
    Minerva endocrinologica, 1995, Volume: 20, Issue:4

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Aldosterone; Diagnosis, Differential; Disorders of Sex

1995
Bilateral aldosterone-producing adenomas in two patients diagnosed by immunohistochemical analysis of steroidogenic enzymes.
    The Tohoku journal of experimental medicine, 1996, Volume: 179, Issue:2

    Topics: 3-Hydroxysteroid Dehydrogenases; Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital;

1996
Targeted disruption of the mouse gene encoding steroidogenic acute regulatory protein provides insights into congenital lipoid adrenal hyperplasia.
    Proceedings of the National Academy of Sciences of the United States of America, 1997, Oct-14, Volume: 94, Issue:21

    Topics: Adrenal Cortex Hormones; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormon

1997
Aldosterone production despite absence or defectiveness of the CYP21 genes in two patients with salt-losing congenital adrenal hyperplasia caused by steroid 21-hydroxylase deficiency.
    Clinical endocrinology, 1998, Volume: 49, Issue:6

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Child, Preschool; Chromatography, High Pressure Liquid

1998
Deletion hybrid genes, due to unequal crossing over between CYP11B1 (11beta-hydroxylase) and CYP11B2(aldosterone synthase) cause steroid 11beta-hydroxylase deficiency and congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 2001, Volume: 86, Issue:7

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Androstenedione; Animals; Blotting, Southern; Child, P

2001
Distinguishing unilateral aldosteronoma from bilateral disease.
    The Journal of clinical endocrinology and metabolism, 2001, Volume: 86, Issue:8

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldo

2001
[Congenital adrenal hyperplasia: clinical aspects and neonatal screening].
    Nederlands tijdschrift voor geneeskunde, 2002, Feb-09, Volume: 146, Issue:6

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Female; Humans; Hydrocortisone; Infant, Newborn; Infer

2002
Renal regulation of fluid, electrolyte, and acid-base homeostasis in the salt-losing syndrome of congenital adrenal hyperplasia (SL-CAH). ECF volume: a compensating factor in aldosterone deficiency.
    The Journal of clinical endocrinology and metabolism, 1978, Volume: 46, Issue:4

    Topics: Acid-Base Imbalance; Adolescent; Adrenal Hyperplasia, Congenital; Aldosterone; Blood; Body Water; Ch

1978
Gynecomastia with congenital virilizing adrenal hyperplasia (11-beta-hydroxylase deficiency).
    The Journal of pediatrics, 1975, Volume: 86, Issue:4

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Cortex Function Tests; Adrenal Hyperplasia, Cong

1975
Persistent testicular delta5-isomerase-3beta-hydroxysteroid dehydrogenase (delta5-3beta-HSD) deficiency in the delta5-3beta-HSD form of congenital adrenal hyperplasia.
    The Journal of clinical investigation, 1975, Volume: 55, Issue:4

    Topics: 17-alpha-Hydroxypregnenolone; Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocor

1975
Plasma aldosterone concentrations related to 17alpha-hydroxyprogesterone in congenital adrenal hyperplasia.
    Acta endocrinologica, 1976, Volume: 82, Issue:3

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormo

1976
Congenital adrenal hyperplasia: simultaneous determination of plasma aldosterone and 17-hydroxyprogesterone.
    Acta endocrinologica, 1978, Volume: 87, Issue:1

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenoco

1978
The role of renin and angiotensin in salt-losing, 21-hydroxylase-deficient congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1979, Volume: 48, Issue:5

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenoco

1979
Diseases of the adrenal cortex. II. Congenital adrenal hyperplasia.
    Pediatric clinics of North America, 1979, Volume: 26, Issue:1

    Topics: Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocortic

1979
Plasma renin activity and aldosterone concentration in normal subjects and patients with salt-losing type of congenital adrenal hyperplasia during infancy.
    Clinical endocrinology, 1979, Volume: 10, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Adrenocorticotropic Hormone; Aldoster

1979
Mechanisms establishing the mineralocorticoid hormone patterns in the 17 alpha-hydroxylase deficiency syndrome.
    Journal of steroid biochemistry, 1979, Volume: 11, Issue:1B

    Topics: 18-Hydroxycorticosterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aldos

1979
Pituitary-adrenal axis activity in treated congenital adrenal hyperplasia: static and dynamic studies.
    The Journal of clinical endocrinology and metabolism, 1978, Volume: 47, Issue:2

    Topics: 17-alpha-Hydroxyprogesterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldoster

1978
[17 alpha-hydroxylase deficiency].
    Nihon rinsho. Japanese journal of clinical medicine, 1977,Spring, Volume: 35 Suppl 1

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Female; Humans; Hypertension; Hypogonadism; Male; Ster

1977
Differences in metabolism of corticosterone by the newborn and adult human.
    Biochemical Society transactions, 1978, Volume: 6, Issue:4

    Topics: Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Corticosterone; Humans; Infant, Newborn; Steroi

1978
Combined 17 alpha- and 18-hydroxylase deficiency associated with complete male pseudohermaphroditism and hypoaldosteronism.
    The Journal of clinical endocrinology and metabolism, 1978, Volume: 46, Issue:2

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Corticosterone; Desoxycorticosterone; Disorders of Sex

1978
Persistence of the enzymatic block in adolescent patients with salt-losing congenital adrenal hyperplasia.
    The Journal of pediatrics, 1979, Volume: 95, Issue:4

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Child; Glucocorticoids; Humans; Hyd

1979
[Aldosterone in the blood of the adrenal vein in primary aldosteronism].
    Schweizerische medizinische Wochenschrift, 1979, Dec-08, Volume: 109, Issue:47

    Topics: Adenoma; Adrenal Gland Neoplasms; Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Huma

1979
An approach to mineralocorticoid hormone hypertension.
    Cardiovascular clinics, 1978, Volume: 9, Issue:1

    Topics: Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Aldosterone; Cushing Syndrome; Desoxy

1978
[Pseudohypoaldsteronism. A further case report (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1977, Volume: 125, Issue:4

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Aldosterone; Diagnosis, Differential; Humans; Hydr

1977
[Proceedings: Normal values and samples of findings in diseases of the hypophysis and the adrenal cortex].
    Medizinische Klinik, 1975, Jun-06, Volume: 70, Issue:23

    Topics: Adrenal Cortex Diseases; Adrenal Cortex Neoplasms; Adrenal Gland Diseases; Adrenal Hyperplasia, Cong

1975
Testicular adrenal-like tissue in a patient with 17 alpha-hydroxylase deficiency.
    Hormone research, 1992, Volume: 38, Issue:5-6

    Topics: Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Disorders of Sex Developme

1992
Serum steroid hormonal profiles by reversed-phase liquid chromatography in patients with 17-hydroxylase deficiency and in an affected family.
    Clinical chemistry, 1992, Volume: 38, Issue:1

    Topics: Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; A

1992
[Diagnosis and therapy of hypercorticism].
    Nihon Naika Gakkai zasshi. The Journal of the Japanese Society of Internal Medicine, 1992, Mar-10, Volume: 81, Issue:3

    Topics: 17-Hydroxycorticosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone

1992
Siblings of 21-hydroxylase deficiency (non-salt-losing) with aldosterone hypersecretion.
    Internal medicine (Tokyo, Japan), 1992, Volume: 31, Issue:5

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aldosterone; Dexame

1992
Adrenocorticotropin-corticosterone relationship during dexamethasone therapy in 17 alpha-hydroxylase deficiency.
    Hormone and metabolic research = Hormon- und Stoffwechselforschung = Hormones et metabolisme, 1992, Volume: 24, Issue:7

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Corticosteron

1992
[Adrenal enzymatic block with late-onset caused by 11-hydroxylase deficiency. Apropos of 29 cases].
    Annales d'endocrinologie, 1992, Volume: 53, Issue:5-6

    Topics: 3-Hydroxysteroid Dehydrogenases; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; An

1992
[State of the renin-angiotensin system in children with different clinical variants of congenital adrenal cortex hyperplasia caused by 21-hydroxylase deficiency].
    Pediatriia, 1992, Issue:2

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Aldosterone; Child; Child, Preschool; Cortisone; Female

1992
A case of 17 alpha-hydroxylase deficiency with chromosomal karyotype 46,XY and high plasma aldosterone concentration.
    International urology and nephrology, 1991, Volume: 23, Issue:6

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Aldosterone; Female; Humans; Male; Orchiectomy; Phenoty

1991
Primary hyperaldosteronism in England and Wales: a review of the use of a Supraregional Assay Service laboratory for the measurement of aldosterone and plasma renin activity.
    Annals of clinical biochemistry, 1991, Volume: 28 ( Pt 3)

    Topics: Adenoma; Adrenal Hyperplasia, Congenital; Aldosterone; Clinical Laboratory Techniques; Electrolytes;

1991
Aldosterone synthesis in salt-wasting congenital adrenal hyperplasia with complete absence of adrenal 21-hydroxylase.
    The New England journal of medicine, 1991, Jan-17, Volume: 324, Issue:3

    Topics: Adolescent; Adrenal Cortex Hormones; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Aldoste

1991
Possible hyperaldosteronism and discrepancy in enzyme activity deficiency in adrenal and gonadal glands in Japanese patients with 17 alpha-hydroxylase deficiency.
    Endocrinologia japonica, 1989, Volume: 36, Issue:4

    Topics: Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Ald

1989
On the prenatal diagnosis of congenital adrenal hyperplasia (CAH) by measurement of amniotic fluid 17-alpha-hydroxyprogesterone, aldosterone and cortisol.
    Acta obstetricia et gynecologica Scandinavica, 1989, Volume: 68, Issue:1

    Topics: Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Amniocentesis; Female; Humans; Hydrocortisone;

1989
Severe hypertension with absent secondary sex characteristics due to partial deficiency of steroid 17 alpha-hydroxylase activity.
    Journal of human hypertension, 1987, Volume: 1, Issue:1

    Topics: Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aldost

1987
Male pseudohermaphroditism due to multiple defects in steroid-biosynthetic microsomal mixed-function oxidases. A new variant of congenital adrenal hyperplasia.
    The New England journal of medicine, 1985, Nov-07, Volume: 313, Issue:19

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; 18-Hydroxycorticosterone; 18-Hydroxydesoxycorticosterone

1985
Effects of continued adrenocorticotropin stimulation on the mineralocorticoid hormones in classical and nonclassical simple virilizing types of 21-hydroxylase deficiency.
    The Journal of clinical endocrinology and metabolism, 1985, Volume: 60, Issue:6

    Topics: 18-Hydroxycorticosterone; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Aldos

1985
Evidence for the secretion of an antimineralocorticoid in congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1986, Volume: 62, Issue:5

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Animals; Bind

1986
[A case of male pseudohermaphroditism due to 17 alpha-hydroxylase deficiency with high levels of plasma aldosterone and angiotensin II].
    Nihon Sanka Fujinka Gakkai zasshi, 1986, Volume: 38, Issue:7

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Aldosterone; Angiotensin II; Desoxycorticosterone; Diso

1986
[Malignant arterial hypertension disclosing late congenital adrenal hyperplasia due to 17 alpha-hydroxylase deficiency].
    Archives des maladies du coeur et des vaisseaux, 1988, Volume: 81 Spec No

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Androgens; Antihypertensive Agents; Dexamethasone; Fem

1988
Aldosterone deficiency in infancy.
    Scottish medical journal, 1988, Volume: 33, Issue:3

    Topics: Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Aldosterone; Diagnosis, Differential; Fema

1988
Urinary excretion of aldosterone metabolite Kelly-M1 in patients with adrenal dysfunction.
    Journal of steroid biochemistry, 1988, Volume: 29, Issue:3

    Topics: Adrenal Gland Diseases; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Aldosterone; Cysti

1988
Zona glomerulosa function after life-long suppression in two siblings with the hypertensive virilizing form of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1988, Volume: 66, Issue:2

    Topics: 18-Hydroxycorticosterone; Adolescent; Adrenal Cortex; Adrenal Hyperplasia, Congenital; Aldosterone;

1988
Radioimmunoassay of urinary 21-deoxytetrahydroaldosterone in primary aldosteronism and 21-hydroxylase deficiency.
    Journal of steroid biochemistry, 1986, Volume: 24, Issue:2

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Child; Female; Humans; Hyperaldosteronism; Male; Radio

1986
[Hirsutism and light forms of congenital adrenogenital syndrome with 21- and 11-beta hydroxylase defect].
    Schweizerische medizinische Wochenschrift, 1986, Mar-29, Volume: 116, Issue:13

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Aldosterone; Androgens; Child; Child, Preschool; Cortic

1986
Is salt-wasting in congenital adrenal hyperplasia due to the same gene as the fasciculata defect?
    Clinical endocrinology, 1986, Volume: 24, Issue:1

    Topics: 17-alpha-Hydroxyprogesterone; Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Child

1986
21-Deoxyaldosterone excretion in patients with primary aldosteronism and 21-hydroxylase deficiency.
    The Journal of clinical endocrinology and metabolism, 1987, Volume: 64, Issue:4

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Chromatography, High Pressure Liqui

1987
Clinical aspects of hyper- and hypo-mineralocorticoidism.
    Japanese journal of medicine, 1987, Volume: 26, Issue:1

    Topics: Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Female; Humans; Hyperaldosteronism; Japan; Kana

1987
Renin-angiotensin-aldosterone system: a long-term follow-up study in 17 alpha-hydroxylase deficiency syndrome (17OHDS).
    Clinical and experimental hypertension. Part A, Theory and practice, 1986, Volume: 8, Issue:4-5

    Topics: Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Female; Glucocortic

1986
A case of adrenal tumor producing renin, aldosterone, and sex steroid hormones.
    Hypertension (Dallas, Tex. : 1979), 1986, Volume: 8, Issue:10

    Topics: Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Carcinoma; Female; Gon

1986
[Plasma renin activity, plasma aldosterone concentration in the differential diagnosis of curable forms of secondary hypertension].
    Zhonghua nei ke za zhi, 1985, Volume: 24, Issue:1

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Angiotensin II; Diagnosis, Differential; Humans; Hyper

1985
[Various aspects of steroidogenesis in congenital adrenogenital syndrome with or without salt loss (determination of the urinary excretion of aldosterone, androsterone, etiocholanolone, dehydroisoandrosterone, 17-hydroxy-11-desoxycorticosterone, pregnaned
    Minerva pediatrica, 1969, May-26, Volume: 21, Issue:21

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Androgens; Androsterone; Child; Child, Preschool; Dehy

1969
Clinical and steroid metabolic studies in four siblings with congenital virilizing adrenal hyperplasia.
    Acta endocrinologica, 1966, Volume: 52, Issue:4

    Topics: 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Adult; Al

1966
Aldosterone hypersecretion in "non-salt-losing" congenital adrenal hyperplasia.
    The Journal of clinical investigation, 1968, Volume: 47, Issue:8

    Topics: Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; A

1968
Salt-losers and non salt-losers in congenital adrenal hyperplasia.
    Archives of disease in childhood, 1969, Volume: 44, Issue:233

    Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Humans; Hydrocortisone; H

1969
Hyperaldosteronism in hypertensive congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1969, Volume: 29, Issue:12

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adr

1969
[Endocrine hypertension].
    Munchener medizinische Wochenschrift (1950), 1970, Nov-20, Volume: 112, Issue:47

    Topics: Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Aldosterone;

1970
The etiopathology of hypertension.
    Internationale Zeitschrift fur klinische Pharmakologie, Therapie, und Toxikologie. International journal of clinical pharmacology, therapy, and toxicology, 1970, Volume: 4, Issue:1

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Angiotensin II; Blood Pressure; Blood Volume; Cardiac

1970
Studies on the deficiency of 21-hydroxylation in patients with congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1971, Volume: 32, Issue:3

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Child; Humans

1971
Cortisol production by testicular tumors in adrenogenital syndrome.
    Archives of internal medicine, 1972, Volume: 130, Issue:1

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hor

1972
The effect of ACTH administration on aldosterone production in non salt-losing congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1972, Volume: 35, Issue:4

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Adrenocorti

1972
11-beta-hydrosylase deficiency: steroid response to sodium restriction and ACTH stimulation.
    The Journal of clinical endocrinology and metabolism, 1972, Volume: 35, Issue:2

    Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Carbon Is

1972
[Etiology of hyperaldosteronemia in adrenogenital syndrome].
    Horumon to rinsho. Clinical endocrinology, 1972, Volume: 20, Issue:10

    Topics: Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Aldosterone; Angiotensin II; Child; Fe

1972
Aldosterone secretion rate in the simple virilizing form of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1972, Volume: 34, Issue:4

    Topics: 17-Ketosteroids; Adolescent; Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Aldost

1972
A study of the renin-aldosterone system in congenital adrenal hyperplasia.
    The Journal of pediatrics, 1972, Volume: 81, Issue:5

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Aldosterone; Blood Pres

1972
[Juxtaglomerular cells in the virilizing congenital adrenogenital syndrome, with and without the salt-loss syndrome].
    Schweizerische medizinische Wochenschrift, 1971, Sep-11, Volume: 101, Issue:36

    Topics: Adrenal Cortex Hormones; Adrenal Hyperplasia, Congenital; Adult; Age Factors; Aldosterone; Autopsy;

1971
[Excretion of labile acid aldosterone in congenital adrenal hypertrophy].
    Revista argentina de endocrinologia y metabolismo, 1969, Volume: 15, Issue:1

    Topics: Adolescent; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adult; Aldosterone; Child; Huma

1969
[Diagnosis and therapy of the salt-losing syndrome].
    Monatsschrift fur Kinderheilkunde, 1969, Volume: 117, Issue:5

    Topics: Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; Aldosterone; Deficiency Diseases; Desoxycort

1969
Exchangeable sodium and aldosterone secretion in children with congenital adrenal hyperplasia due to 21-hydroxylase deficiency.
    Pediatric research, 1970, Volume: 4, Issue:2

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfunction; Aldosterone; Child; Child

1970
Corticosteroid therapy in the neonatal period.
    Pediatric clinics of North America, 1970, Volume: 17, Issue:4

    Topics: Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; Aldosterone; Communi

1970
Renin activity, aldosterone secretion, and congenital adrenal hyperplasia.
    Pediatrics, 1968, Volume: 41, Issue:5

    Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Humans; Renin

1968
Plasma renin activity in congenital virilizing adrenal hyperplasia.
    Pediatrics, 1968, Volume: 41, Issue:5

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenocortical Hyperfun

1968
Plasma renin activity and aldosterone secretion in congenital adrenal hyperplasia.
    Pediatrics, 1968, Volume: 41, Issue:5

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenoc

1968
Aldosterone secretion rate in the hypertensive form of congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1968, Volume: 28, Issue:10

    Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Cortisone; Diet; Disorders of Sex Deve

1968
Surgical treatment of adrenal disorders associated with increased hormone production.
    Acta chirurgica Academiae Scientiarum Hungaricae, 1968, Volume: 9, Issue:2

    Topics: Adolescent; Adrenal Cortex Hormones; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adult;

1968
[On the problem of hypoaldosteronism in children].
    Voprosy okhrany materinstva i detstva, 1968, Volume: 13, Issue:9

    Topics: Adrenal Hyperplasia, Congenital; Adrenal Insufficiency; Aldosterone; Diagnosis, Differential; Humans

1968
Medical treatment of Cushing's disease.
    The New England journal of medicine, 1969, Oct-09, Volume: 281, Issue:15

    Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Aldosterone; Animals; Cushing Syndrome; Dichlorodip

1969
[Physiopathology of the salt-losing syndrome during congenital adrenal hyperplasia related to a 21-hydroxylation defect].
    Annales de pediatrie, 1965, Dec-02, Volume: 12, Issue:12

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Humans; Infant; Infant, Newborn; Sodium Chloride

1965
[Clinical, morphologic and biochemical studies on an androgen-producing testicular tumor].
    Klinische Wochenschrift, 1965, Oct-01, Volume: 43, Issue:19

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Aldosterone; Child; Chi

1965