aica ribonucleotide and Luft Disease

aica ribonucleotide has been researched along with Luft Disease in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's3 (100.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Ayalon, O; Saada, A; Soiferman, D; Weissman, S1
Arguello, T; Diaz, F; Garcia, S; Moraes, CT; Peralta, S; Yin, HY1
Brookes, P; Chang, C; Chen, LM; Chou, S; Lee, YF; Li, G; Liu, S; Massett, MP; Uno, H; Wu, Q1

Other Studies

3 other study(ies) available for aica ribonucleotide and Luft Disease

ArticleYear
The effect of small molecules on nuclear-encoded translation diseases.
    Biochimie, 2014, Volume: 100

    Topics: Acetylcysteine; Aminoimidazole Carboxamide; Bezafibrate; Cytochrome-c Oxidase Deficiency; DNA, Mitochondrial; Electron Transport; Electron Transport Complex IV; Fibroblasts; Gene Expression Regulation; Humans; Membrane Potential, Mitochondrial; Mitochondria; Mitochondrial Myopathies; Mitochondrial Proteins; Mutation; Oxidative Phosphorylation; Peptide Elongation Factor G; Primary Cell Culture; Protein Biosynthesis; Reactive Oxygen Species; Ribonucleotides; Ribosomal Proteins; Small Molecule Libraries; tRNA Methyltransferases

2014
Sustained AMPK activation improves muscle function in a mitochondrial myopathy mouse model by promoting muscle fiber regeneration.
    Human molecular genetics, 2016, 08-01, Volume: 25, Issue:15

    Topics: Alkyl and Aryl Transferases; Aminoimidazole Carboxamide; AMP-Activated Protein Kinases; Animals; Disease Models, Animal; Enzyme Activation; Membrane Proteins; Mice; Mice, Transgenic; Mitochondria, Muscle; Mitochondrial Myopathies; Muscle Fibers, Skeletal; Regeneration; Ribonucleotides

2016
Mice lacking TR4 nuclear receptor develop mitochondrial myopathy with deficiency in complex I.
    Molecular endocrinology (Baltimore, Md.), 2011, Volume: 25, Issue:8

    Topics: Adenosine Triphosphate; Aminoimidazole Carboxamide; Animals; Cells, Cultured; Electron Transport Complex I; Gene Expression Regulation; Humans; Lactic Acid; Metformin; Mice; Mitochondria; Mitochondrial Myopathies; Muscle Weakness; Muscle, Skeletal; Myoblasts; NADH Dehydrogenase; Physical Conditioning, Animal; Receptors, Steroid; Receptors, Thyroid Hormone; Ribonucleotides

2011