aica ribonucleotide and Complex IV Deficiency

aica ribonucleotide has been researched along with Complex IV Deficiency in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's2 (100.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Ayalon, O; Saada, A; Soiferman, D; Weissman, S1
Bottani, E; Cerutti, R; Civiletto, G; Fagiolari, G; Lamperti, C; Moggio, M; Schon, EA; Viscomi, C; Zeviani, M1

Other Studies

2 other study(ies) available for aica ribonucleotide and Complex IV Deficiency

ArticleYear
The effect of small molecules on nuclear-encoded translation diseases.
    Biochimie, 2014, Volume: 100

    Topics: Acetylcysteine; Aminoimidazole Carboxamide; Bezafibrate; Cytochrome-c Oxidase Deficiency; DNA, Mitochondrial; Electron Transport; Electron Transport Complex IV; Fibroblasts; Gene Expression Regulation; Humans; Membrane Potential, Mitochondrial; Mitochondria; Mitochondrial Myopathies; Mitochondrial Proteins; Mutation; Oxidative Phosphorylation; Peptide Elongation Factor G; Primary Cell Culture; Protein Biosynthesis; Reactive Oxygen Species; Ribonucleotides; Ribosomal Proteins; Small Molecule Libraries; tRNA Methyltransferases

2014
In vivo correction of COX deficiency by activation of the AMPK/PGC-1α axis.
    Cell metabolism, 2011, Jul-06, Volume: 14, Issue:1

    Topics: Aminoimidazole Carboxamide; AMP-Activated Protein Kinases; Animals; Bezafibrate; Cytochrome-c Oxidase Deficiency; Disease Models, Animal; Electron Transport Complex IV; Gene Knock-In Techniques; Hypoglycemic Agents; Hypolipidemic Agents; Membrane Proteins; Mice; Mice, Knockout; Mice, Transgenic; Mitochondrial Proteins; Molecular Chaperones; Muscle, Skeletal; Oxidative Phosphorylation; Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha; Ribonucleotides; Signal Transduction; Trans-Activators; Transcription Factors

2011