adenosine diphosphate has been researched along with Mitochondrial Myopathies in 15 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 11 (73.33) | 18.2507 |
2000's | 4 (26.67) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
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Förster, H; Fötschl, U; Houstek, J; Kurnik, P; Mayr, JA; Paul, J; Pecina, P; Sperl, W | 1 |
Kemp, GJ; Sue, CM; Thompson, CH; Trenell, MI | 1 |
Barbiroli, B; Iotti, S; Klopstock, T; Lodi, R; Medori, R; Reichmann, H; Seibel, P; Tritschler, HJ; Zaniol, P | 1 |
Kemp, GJ; Radda, GK; Taylor, DJ | 1 |
Arnold, D; Carpenter, S; Genge, A; Karpati, G; Shoubridge, EA | 1 |
Arnold, DL; De Stefano, N; Ford, B; Genge, A; Karpati, G; Matthews, PM | 1 |
Edwards, JH; Kemp, GJ; Radda, GK; Taylor, DJ; Woods, CG | 1 |
Barbiroli, B; Cortelli, P; Funicello, R; Iotti, S; Lodi, R; Martinelli, P; Montagna, P; Zaniol, P | 1 |
Abeling, NG; Bakker, HD; Dorland, B; Jeneson, JA; Ruitenbeek, W; Scholte, HR; Sengers, RC; Van den Bogert, C; Van Gennip, AH; Wanders, RJ | 1 |
Brandolin, G; Dianoux, AC; Fiore, C; Lauquin, GJ; Le Saux, A; Noel, F; Roux, P; Schwimmer, C; Trézéguet, V; Vignais, PV | 1 |
Argov, Z; Arnold, DL; Chen, JT; Kearney, RE | 1 |
Barbiroli, B; Iotti, S; Lodi, R | 1 |
Attardi, G; Elger, CE; Kudin, A; Kunz, WS; Vielhaber, S; Villani, G | 1 |
Kunz, WS | 1 |
Challiss, RA; Clark, JB; Cooper, JM; Hayes, DJ; Morgan-Hughes, JA | 1 |
2 review(s) available for adenosine diphosphate and Mitochondrial Myopathies
Article | Year |
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The mitochondrial ADP/ATP carrier: structural, physiological and pathological aspects.
Topics: Adenosine Diphosphate; Adenosine Triphosphate; Amino Acid Sequence; Animals; Cell Compartmentation; Cytosol; Eukaryotic Cells; Fluorescence; Humans; Mitochondria; Mitochondrial ADP, ATP Translocases; Mitochondrial Myopathies; Molecular Sequence Data; Mutagenesis, Site-Directed; Protein Conformation; Tissue Distribution; Transcription, Genetic | 1998 |
Control of oxidative phosphorylation in skeletal muscle.
Topics: Adenosine Diphosphate; Animals; Creatine Kinase; Diffusion; Humans; Mitochondria, Muscle; Mitochondrial Myopathies; Models, Chemical; Muscle, Skeletal; Oxidation-Reduction; Oxidative Phosphorylation; Oxygen Consumption | 2001 |
3 trial(s) available for adenosine diphosphate and Mitochondrial Myopathies
Article | Year |
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Supplemental oxygen and muscle metabolism in mitochondrial myopathy patients.
Topics: Adenosine Diphosphate; Adenosine Triphosphate; Adult; Exercise; Female; Humans; Hydrogen-Ion Concentration; Magnetic Resonance Spectroscopy; Male; Middle Aged; Mitochondria, Muscle; Mitochondrial Myopathies; Muscle Contraction; Muscle, Skeletal; Oxygen; Oxygen Inhalation Therapy; Phosphorus; Recovery of Function; Treatment Outcome | 2007 |
Bioenergetics of skeletal muscle in mitochondrial myopathy.
Topics: Adenosine Diphosphate; Adenosine Triphosphate; Adolescent; Adult; Aged; Aged, 80 and over; Child; DNA, Mitochondrial; Energy Metabolism; Exercise; Female; Humans; Hydrogen-Ion Concentration; Magnetic Resonance Imaging; Male; Middle Aged; Mitochondrial Myopathies; Muscle, Skeletal; Ophthalmoplegia, Chronic Progressive External; Phosphates; Phosphocreatine | 1994 |
Short-term dichloroacetate treatment improves indices of cerebral metabolism in patients with mitochondrial disorders.
Topics: Acetylcysteine; Adenosine Diphosphate; Adolescent; Adult; Aged; Alanine; Brain; Child; Creatine; Cross-Over Studies; Dichloroacetic Acid; Double-Blind Method; Female; Humans; Lactates; Lactic Acid; Magnetic Resonance Spectroscopy; Male; Middle Aged; Mitochondrial Myopathies; Placebos; Pyruvate Dehydrogenase Complex | 1995 |
10 other study(ies) available for adenosine diphosphate and Mitochondrial Myopathies
Article | Year |
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Reduced respiratory control with ADP and changed pattern of respiratory chain enzymes as a result of selective deficiency of the mitochondrial ATP synthase.
Topics: Adenosine Diphosphate; Cell Nucleus; Child, Preschool; Electron Transport; Female; Fibroblasts; Humans; Mitochondria, Muscle; Mitochondrial Myopathies; Mitochondrial Proton-Translocating ATPases; Oxidative Phosphorylation | 2004 |
Lipoic (thioctic) acid increases brain energy availability and skeletal muscle performance as shown by in vivo 31P-MRS in a patient with mitochondrial cytopathy.
Topics: Adenosine Diphosphate; Adult; Brain Chemistry; Chronic Disease; Energy Metabolism; Exercise; Female; Humans; Magnetic Resonance Spectroscopy; Mitochondrial Myopathies; Muscle, Skeletal; Occipital Lobe; Ophthalmoplegia; Phosphorus; Phosphorylation; Thioctic Acid | 1995 |
Familial myopathy with conspicuous depletion of mitochondria in muscle fibers: a morphologically distinct disease.
Topics: Adenosine Diphosphate; Adolescent; Adult; Biopsy; Diagnosis, Differential; DNA, Mitochondrial; Female; Humans; Immunohistochemistry; Male; Microscopy, Electron; Mitochondria; Mitochondrial Myopathies; Muscle Fibers, Skeletal; Muscle, Skeletal; Phosphocreatine; Phosphorylation | 1995 |
Skeletal muscle bioenergetics in myotonic dystrophy.
Topics: Adenosine Diphosphate; Adult; Energy Metabolism; Exercise; Female; Forearm; Humans; Hydrogen-Ion Concentration; Magnetic Resonance Spectroscopy; Male; Middle Aged; Mitochondrial Myopathies; Muscles; Myotonic Dystrophy; Phosphates; Phosphocreatine; Rest | 1993 |
Defective brain energy metabolism shown by in vivo 31P MR spectroscopy in 28 patients with mitochondrial cytopathies.
Topics: Adenosine Diphosphate; Adolescent; Adult; Aged; Brain; Child; Energy Metabolism; Female; Humans; Magnetic Resonance Spectroscopy; Male; Middle Aged; Mitochondrial Encephalomyopathies; Mitochondrial Myopathies; Ophthalmoplegia; Optic Atrophies, Hereditary; Osmolar Concentration; Phosphocreatine; Phosphorus | 1993 |
Deficiency of the adenine nucleotide translocator in muscle of a patient with myopathy and lactic acidosis: a new mitochondrial defect.
Topics: Acidosis, Lactic; Adenosine Diphosphate; Adenosine Triphosphate; Child, Preschool; Energy Metabolism; Humans; Male; Mitochondria, Muscle; Mitochondrial ADP, ATP Translocases; Mitochondrial Myopathies; Oxidative Phosphorylation; Phosphocreatine | 1993 |
Fitting cytosolic ADP recovery after exercise with a step response function.
Topics: Adenosine Diphosphate; Adult; Algorithms; Cytosol; Female; Humans; Ischemia; Linear Models; Magnetic Resonance Spectroscopy; Male; Middle Aged; Mitochondria, Muscle; Mitochondrial Myopathies; Muscle, Skeletal; Oxidation-Reduction; Oxygen Consumption; Phosphorus Isotopes; Physical Exertion; Regional Blood Flow; Time Factors | 1999 |
Improved brain and muscle mitochondrial respiration with CoQ. An in vivo study by 31P-MR spectroscopy in patients with mitochondrial cytopathies.
Topics: Adenosine Diphosphate; Adenosine Triphosphate; Adolescent; Adult; Aged; Brain; Coenzymes; Cytosol; DNA, Mitochondrial; Female; Humans; Magnesium; Magnetic Resonance Spectroscopy; Male; Middle Aged; Mitochondria; Mitochondria, Muscle; Mitochondrial Myopathies; Ophthalmoplegia, Chronic Progressive External; Optic Atrophies, Hereditary; Oxygen Consumption; Phosphates; Phosphorus; Reference Values; Ubiquinone | 1999 |
Flux control of cytochrome c oxidase in human skeletal muscle.
Topics: Adenosine Diphosphate; Adult; Blotting, Southern; Cell Membrane Permeability; DNA, Mitochondrial; Electron Transport Complex IV; Humans; Kinetics; Middle Aged; Mitochondria, Muscle; Mitochondrial Myopathies; Muscle Fibers, Skeletal; Muscle, Skeletal; Ophthalmoplegia, Chronic Progressive External; Oxygen Consumption; Potassium Cyanide; Sequence Deletion | 2000 |
Treatment of experimental NADH ubiquinone reductase deficiency with menadione.
Topics: Adenosine Diphosphate; Adenosine Triphosphate; Animals; Biphenyl Compounds; Drug Therapy, Combination; Electron Transport; Electron Transport Complex I; Hindlimb; Magnetic Resonance Spectroscopy; Male; Mitochondrial Myopathies; Muscles; NADH, NADPH Oxidoreductases; Onium Compounds; Phosphates; Phosphocreatine; Rats; Rats, Wistar; Vitamin K | 1992 |