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adenosine diphosphate and Electron Transport Chain Deficiencies, Mitochondrial

adenosine diphosphate has been researched along with Electron Transport Chain Deficiencies, Mitochondrial in 11 studies

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's7 (63.64)29.6817
2010's4 (36.36)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Abdollahi, M; Azizi, E; Fouladdel, S; Ghahramani, MH; Hadian, MR; Hosseini, R; Karami-Mohajeri, S1
Hall, ED; Miller, DM; Singh, IN; Wang, JA1
Alston, CL; Barbosa, IA; Bonnen, PE; Dallabona, C; Deshpande, C; Elpeleg, O; Fattal-Valevski, A; Ferrero, I; Fraenkel, ND; Haham, A; He, L; Isohanni, P; Jones, SA; King, MS; Kunji, ER; Lodi, T; Majd, H; McFarland, R; Õunap, K; Puusepp, S; Reinson, K; Rodenburg, RJ; Saada, A; Simpson, MA; Suomalainen, A; Taylor, RW; Thompson, K; Vara, R1
Cheshchevik, VT; Dremza, IK; Kujawa, J; Lapshina, EA; Zabrodskaya, SV; Zavodnik, IB1
Gottlieb, RA; Gustafsson, AB; Molkentin, JD; Sayen, MR; Sussman, MA1
Araki, T; Koshino, T; Nakai, A; Taniuchi, Y1
Fischer, JH; Hayashi, J; Schauen, M; Schubert, J; Spitkovsky, D; Wiesner, RJ1
Currin, RT; Holmuhamedov, E; Lemasters, JJ; Pediaditakis, P; Ramshesh, VK; Theruvath, TP; Tikunov, A; Zhong, Z1
De Feyter, HM; Nicolay, K; Praet, SF; Prompers, JJ; van den Broek, NM; van Loon, LJ1
Amâncio, RT; Bozza, FA; d'Avila, JC; Galina, A; Oliveira, MF; Santiago, AP1
Bendahan, D; Cea, G; Hilton-Jones, D; Lodi, R; Manners, D; Styles, P; Taylor, DJ1

Trials

1 trial(s) available for adenosine diphosphate and Electron Transport Chain Deficiencies, Mitochondrial

ArticleYear
Reduced oxidative phosphorylation and proton efflux suggest reduced capillary blood supply in skeletal muscle of patients with dermatomyositis and polymyositis: a quantitative 31P-magnetic resonance spectroscopy and MRI study.
    Brain : a journal of neurology, 2002, Volume: 125, Issue:Pt 7

    Topics: Adenosine Diphosphate; Adenosine Triphosphate; Adult; Aged; Capillaries; Dermatomyositis; Exercise Test; Female; Humans; Magnetic Resonance Imaging; Magnetic Resonance Spectroscopy; Male; Middle Aged; Mitochondria; Mitochondrial Diseases; Muscle, Skeletal; Oxidative Phosphorylation; Phosphocreatine; Phosphorus Isotopes; Physical Exertion; Polymyositis; Protons; Reference Values; Rest; Water

2002

Other Studies

10 other study(ies) available for adenosine diphosphate and Electron Transport Chain Deficiencies, Mitochondrial

ArticleYear
Mechanisms of muscular electrophysiological and mitochondrial dysfunction following exposure to malathion, an organophosphorus pesticide.
    Human & experimental toxicology, 2014, Volume: 33, Issue:3

    Topics: 8-Hydroxy-2'-Deoxyguanosine; Adenosine Diphosphate; Adenosine Triphosphate; Animals; Apoptotic Protease-Activating Factor 1; bcl-2-Associated X Protein; Caspase 9; Cell Death; Cytochromes c; Deoxyguanosine; Electron Transport Complex I; Electron Transport Complex II; Electron Transport Complex IV; Glycogen; Insecticides; Lactic Acid; Malathion; Mitochondria, Muscle; Mitochondrial Diseases; Muscle, Skeletal; Proto-Oncogene Proteins c-bcl-2; Rats; Reactive Oxygen Species

2014
Nrf2-ARE activator carnosic acid decreases mitochondrial dysfunction, oxidative damage and neuronal cytoskeletal degradation following traumatic brain injury in mice.
    Experimental neurology, 2015, Volume: 264

    Topics: Abietanes; Adenosine Diphosphate; Aldehydes; Analysis of Variance; Animals; Antioxidants; Brain; Brain Injuries; Cytoskeleton; Disease Models, Animal; Dose-Response Relationship, Drug; Lipid Peroxidation; Male; Mice; Mitochondrial Diseases; Oxidative Stress; Plant Extracts; Succinic Acid

2015
Recurrent De Novo Dominant Mutations in SLC25A4 Cause Severe Early-Onset Mitochondrial Disease and Loss of Mitochondrial DNA Copy Number.
    American journal of human genetics, 2016, 10-06, Volume: 99, Issue:4

    Topics: Adenine Nucleotide Translocator 1; Adenosine Diphosphate; Adenosine Triphosphate; Age of Onset; Arylamine N-Acetyltransferase; Child; Child, Preschool; DNA Copy Number Variations; DNA, Mitochondrial; Electron Transport; Exome; Female; Genes, Dominant; Humans; Infant; Infant, Newborn; Isoenzymes; Male; Mitochondrial Diseases; Muscle, Skeletal; Mutation

2016
Corrections by melatonin of liver mitochondrial disorders under diabetes and acute intoxication in rats.
    Cell biochemistry and function, 2011, Volume: 29, Issue:6

    Topics: Adenosine Diphosphate; Animals; Carbon Tetrachloride; Diabetes Mellitus, Experimental; Male; Melatonin; Mitochondria, Liver; Mitochondrial Diseases; Oxidative Phosphorylation; Rats; Rats, Wistar; Respiratory Rate

2011
Calcineurin transgenic mice have mitochondrial dysfunction and elevated superoxide production.
    American journal of physiology. Cell physiology, 2003, Volume: 284, Issue:2

    Topics: Adenosine Diphosphate; Animals; Animals, Newborn; Calcineurin; Cardiomegaly; Cell Respiration; Cells, Cultured; Electron Transport; Ethidium; Genetic Vectors; Heart Failure; Mice; Mice, Transgenic; Mitochondria; Mitochondrial Diseases; Myocardium; Myocytes, Cardiac; Oxidative Stress; Reperfusion Injury; Superoxides

2003
Maternal treatment with alpha-phenyl-N-tert-butylnitrone attenuates secondary mitochondrial dysfunction after transient intrauterine asphyxia in the fetal rat brain.
    Gynecologic and obstetric investigation, 2003, Volume: 55, Issue:3

    Topics: Adenosine Diphosphate; Animals; Arteries; Asphyxia; Brain Ischemia; Constriction; Cyclic N-Oxides; Female; Fetal Diseases; Maternal-Fetal Exchange; Mitochondrial Diseases; Nitrogen Oxides; Oxygen Consumption; Pregnancy; Rats; Rats, Wistar; Uterus

2003
Respiratory chain deficiency slows down cell-cycle progression via reduced ROS generation and is associated with a reduction of p21CIP1/WAF1.
    Journal of cellular physiology, 2006, Volume: 209, Issue:1

    Topics: Adenosine Diphosphate; Adenosine Triphosphate; Cell Cycle; Cell Cycle Proteins; Cell Enlargement; Cell Proliferation; Cyclin-Dependent Kinase Inhibitor p21; Down-Regulation; Ethidium; Extracellular Signal-Regulated MAP Kinases; HeLa Cells; Heme; Humans; Mitochondrial Diseases; Proto-Oncogene Proteins c-akt; Reactive Oxygen Species; Signal Transduction; Uridine; Uridine Triphosphate

2006
Minocycline and N-methyl-4-isoleucine cyclosporin (NIM811) mitigate storage/reperfusion injury after rat liver transplantation through suppression of the mitochondrial permeability transition.
    Hepatology (Baltimore, Md.), 2008, Volume: 47, Issue:1

    Topics: Adenosine Diphosphate; Alanine Transaminase; Animals; Anti-Bacterial Agents; Apoptosis; Calcium; Cyclosporine; Graft Survival; Liver; Liver Transplantation; Male; Minocycline; Mitochondria; Mitochondrial Diseases; Mitochondrial Membrane Transport Proteins; Mitochondrial Permeability Transition Pore; Necrosis; Rats; Rats, Inbred Lew; Reperfusion Injury; Tetracycline

2008
Early or advanced stage type 2 diabetes is not accompanied by in vivo skeletal muscle mitochondrial dysfunction.
    European journal of endocrinology, 2008, Volume: 158, Issue:5

    Topics: Adenosine Diphosphate; Blood Glucose; Diabetes Mellitus, Type 2; Glucose Intolerance; Humans; Insulin Resistance; Magnetic Resonance Spectroscopy; Middle Aged; Mitochondrial Diseases; Models, Biological; Muscle, Skeletal; Phosphocreatine; Phosphorus Isotopes; Prediabetic State; Severity of Illness Index

2008
Sepsis induces brain mitochondrial dysfunction.
    Critical care medicine, 2008, Volume: 36, Issue:6

    Topics: Adenosine Diphosphate; Animals; Brain; Disease Models, Animal; Electron Transport; Electron Transport Complex IV; Energy Metabolism; Hydrogen Peroxide; Male; Mice; Mitochondria; Mitochondrial Diseases; Mitochondrial Membranes; Oxidative Phosphorylation; Oxygen Consumption; Sepsis

2008