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adenosine diphosphate and Anemia, Congenital Nonspherocytic Hemolytic

adenosine diphosphate has been researched along with Anemia, Congenital Nonspherocytic Hemolytic in 8 studies

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19906 (75.00)18.7374
1990's1 (12.50)18.2507
2000's1 (12.50)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Fujii, H; Igarashi, T; Miwa, S; Takahashi, K; Takizawa, T; Tani, K1
Lakomek, M; Schröter, W; Winkler, H1
Acan, NL; Ozer, N1
Konrad, PN; Paglia, DE; Valentine, WN; Wolff, JA1
Hoch, G; Lakomek, M; Neubauer, B; Schröter, W; von der Lühe, A; Winkler, H1
Buss, D; Gerth, C; Grieger, M; Günther, I; Jacobasch, G1
Boivin, P; Galand, C1
Anderson, HM; Harris, SR; Jaffé, ER; Konrad, PN; Paglia, DE; Valentine, WN1

Other Studies

8 other study(ies) available for adenosine diphosphate and Anemia, Congenital Nonspherocytic Hemolytic

ArticleYear
Red cell adenylate kinase deficiency associated with hereditary nonspherocytic hemolytic anemia: clinical and biochemical studies.
    American journal of hematology, 1983, Volume: 14, Issue:4

    Topics: Adenosine Diphosphate; Adenosine Triphosphate; Adenylate Kinase; Anemia, Hemolytic, Congenital; Anemia, Hemolytic, Congenital Nonspherocytic; Child; Consanguinity; Erythrocyte Aging; Erythrocytes; Female; Glutathione; Humans; Phosphotransferases

1983
Red cell pyruvate kinase deficiency: an optimised assay.
    Clinica chimica acta; international journal of clinical chemistry, 1980, Nov-20, Volume: 108, Issue:1

    Topics: Adenosine Diphosphate; Anemia, Hemolytic, Congenital Nonspherocytic; Erythrocytes; Fructosediphosphates; Humans; Magnesium; Phosphoenolpyruvate; Potassium; Pyruvate Kinase; Sodium; Spectrophotometry, Ultraviolet

1980
Modification of human erythrocyte pyruvate kinase by an active site-directed reagent: bromopyruvate.
    Journal of enzyme inhibition, 2001, Volume: 16, Issue:5

    Topics: Adenosine Diphosphate; Anemia, Hemolytic, Congenital Nonspherocytic; Binding Sites; Enzyme Inhibitors; Erythrocytes; Fructosediphosphates; Humans; Kinetics; Phosphoenolpyruvate; Pyruvate Kinase; Pyruvates; Structure-Activity Relationship

2001
Biphasic reaction kinetics in an anomalous isozyme of erythrocyte pyruvate kinase.
    Clinica chimica acta; international journal of clinical chemistry, 1976, Volume: 73, Issue:3

    Topics: Adenosine Diphosphate; Anemia, Hemolytic, Congenital Nonspherocytic; Drug Stability; Erythrocytes; Fructosephosphates; Heterozygote; Hexosediphosphates; Humans; Isoenzymes; Kinetics; Mutation; Pyruvate Kinase

1976
Erythrocyte pyruvate kinase deficiency: relations of residual enzyme activity, altered regulation of defective enzymes and concentrations of high-energy phosphates with the severity of clinical manifestation.
    European journal of haematology, 1992, Volume: 49, Issue:2

    Topics: 2,3-Diphosphoglycerate; Adenosine Diphosphate; Adenosine Triphosphate; Anemia, Hemolytic, Congenital Nonspherocytic; Diphosphoglyceric Acids; Discriminant Analysis; Erythrocyte Count; Erythrocytes; Female; Glucose-6-Phosphate; Glucosephosphates; Hemoglobins; Humans; Male; Metabolism, Inborn Errors; Phosphoenolpyruvate; Pyruvate Kinase

1992
[Metabolic abnormality in erthyrocytes with atypical pyruvate kinase and potassium deficiency].
    Haematologia, 1972, Volume: 6, Issue:4

    Topics: Acid Phosphatase; Adenosine Diphosphate; Adenosine Triphosphate; Adult; Anemia, Hemolytic, Congenital; Anemia, Hemolytic, Congenital Nonspherocytic; Child, Preschool; Chromium Radioisotopes; Cyclic AMP; Erythrocytes; Female; Glucosephosphate Dehydrogenase; Glutathione Reductase; Glycolysis; Humans; Infant; Infant, Newborn; Male; Metabolism, Inborn Errors; Pedigree; Phosphogluconate Dehydrogenase; Potassium; Pregnancy; Pyruvate Kinase; Splenectomy

1972
A mutant of human red cell pyruvate kinase with high affinity for phosphoenolpyruvate.
    Enzyme, 1974, Volume: 18, Issue:1

    Topics: Adenosine Diphosphate; Adenosine Triphosphate; Adult; Anemia, Hemolytic, Congenital Nonspherocytic; Erythrocytes; Fructosephosphates; Genes; Hemolysis; Humans; Hydrogen-Ion Concentration; Kinetics; Mutation; Phosphoenolpyruvate; Pyruvate Kinase; Temperature; Urea

1974
Studies on human erythrocyte nucleotide metabolism. II. Nonspherocytic hemolytic anemia, high red cell ATP, and ribosephosphate pyrophosphokinase (RPK, E.C.2.7.6.1) deficiency.
    Blood, 1972, Volume: 39, Issue:5

    Topics: Adenosine Diphosphate; Adenosine Monophosphate; Adenosine Triphosphate; Adult; Anemia, Hemolytic, Congenital Nonspherocytic; Black People; Blood Protein Electrophoresis; Erythrocyte Aging; Erythrocytes; Female; Fetal Hemoglobin; Glutathione; Glycolysis; Hemoglobins; Hemolysis; Humans; Lactates; Metabolism, Inborn Errors; Nucleotides; Phosphotransferases; Pyruvates; Reticulocytes

1972