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acetylglucosamine and Mucopolysaccharidoses

acetylglucosamine has been researched along with Mucopolysaccharidoses in 11 studies

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-199010 (90.91)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (9.09)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Byers, S; Derrick-Roberts, AL; Marais, W1
Caskey, CT; Di Ferrante, DT; Di Ferrante, N; Donnelly, PV; Ginsberg, LC2
Suzuki, Y1
Elliott, H; Hopwood, JJ3
Fuchs, W; Gilberg, W; Glössl, J; Holtfrerich, D; Kresse, H1
Farooqui, AA1
Fensom, AH; Marsh, J1
Kornfeld, S; Sly, WS1

Reviews

2 review(s) available for acetylglucosamine and Mucopolysaccharidoses

ArticleYear
[Mucopolysaccharidoses and disorders of glycoprotein metabolism].
    Tanpakushitsu kakusan koso. Protein, nucleic acid, enzyme, 1984, Volume: 29, Issue:14

    Topics: Acetylglucosamine; Carbohydrate Metabolism, Inborn Errors; Glycoproteins; Glycosaminoglycans; Humans; Mucopolysaccharidoses; Structure-Activity Relationship

1984
Sulfatases, sulfate esters and their metabolic disorders.
    Clinica chimica acta; international journal of clinical chemistry, 1980, Jan-31, Volume: 100, Issue:3

    Topics: Acetylgalactosamine; Acetylglucosamine; Animals; Brain; Cattle; Cerebrosides; Esters; Estrone; Female; Heparin; Humans; Iduronate Sulfatase; Leukodystrophy, Metachromatic; Liver; Male; Metabolism, Inborn Errors; Molecular Weight; Mucopolysaccharidoses; Mucopolysaccharidosis III; Mucopolysaccharidosis IV; Placenta; Rabbits; Rats; Sulfatases; Sulfates

1980

Other Studies

9 other study(ies) available for acetylglucosamine and Mucopolysaccharidoses

ArticleYear
Rhodamine B and 2-acetamido-1,3,6-tri-O-acetyl-4-deoxy-4-fluoro-D-glucopyranose (F-GlcNAc) inhibit chondroitin/dermatan and keratan sulphate synthesis by different mechanisms in bovine chondrocytes.
    Molecular genetics and metabolism, 2012, Volume: 106, Issue:2

    Topics: Acetylglucosamine; Animals; Cartilage; Cattle; Chondrocytes; Chondroitin Sulfates; Dermatan Sulfate; Gene Expression Profiling; Gene Expression Regulation; Glycosaminoglycans; Keratan Sulfate; Mucopolysaccharidoses; Proteoglycans; Rhodamines

2012
Deficiencies of glucosamine-6-sulfate or galactosamine-6-sulfate sulfatases are responsible for different mucopolysaccharidoses.
    Science (New York, N.Y.), 1978, Jan-06, Volume: 199, Issue:4324

    Topics: Acetylgalactosamine; Acetylglucosamine; Cells, Cultured; Child, Preschool; Chondroitin Sulfates; Chondroitinsulfatases; Fibroblasts; Galactitol; Heparitin Sulfate; Humans; Hydrogen-Ion Concentration; Keratan Sulfate; Male; Mucopolysaccharidoses; Mucopolysaccharidosis III; Mucopolysaccharidosis IV; Skin; Substrate Specificity; Sulfatases

1978
Isolation and characterization of N-acetylglucosamine 6-sulfate from the urine of a patient with Sanfilippo type D syndrome and its occurrence in normal urine.
    Biochemistry international, 1983, Volume: 6, Issue:6

    Topics: Acetylglucosamine; Chromatography; Galactosamine; Glucosamine; Heparitin Sulfate; Humans; Keratan Sulfate; Mucopolysaccharidoses; Mucopolysaccharidosis III; Mucopolysaccharidosis VI

1983
Liberation of N-acetylglucosamine-6-sulfate by human beta-N-acetylhexosaminidase A.
    The Journal of biological chemistry, 1981, Dec-25, Volume: 256, Issue:24

    Topics: Acetylglucosamine; beta-N-Acetylhexosaminidases; Cells, Cultured; Fibroblasts; Glucosamine; Hexosaminidases; Humans; Kinetics; Mucopolysaccharidoses; Sandhoff Disease; Skin; Substrate Specificity; Sulfur Radioisotopes; Tay-Sachs Disease; Tritium

1981
Detection of the Sanfilippo type B syndrome using radiolabelled oligosaccharides as substrates for the estimation of alpha-N-acetylglucosaminidase.
    Clinica chimica acta; international journal of clinical chemistry, 1982, Mar-26, Volume: 120, Issue:1

    Topics: Acetylglucosamine; Acetylglucosaminidase; Cells, Cultured; Disaccharides; Fibroblasts; Hexosaminidases; Humans; Leukocytes; Mucopolysaccharidoses; Mucopolysaccharidosis III; Skin; Structure-Activity Relationship; Substrate Specificity; Tritium

1982
N-acetylglucosamine-6-sulfate sulfatase in man: deficiency of the enzyme in a new mucopolysaccharidosis.
    Pediatric research, 1978, Volume: 12, Issue:7

    Topics: Acetylglucosamine; Child, Preschool; Humans; Male; Mucopolysaccharidoses; Sulfatases

1978
4-Methylumbelliferyl alpha-N-acetylglucosaminidase activity for diagnosis of Sanfilippo B disease.
    Clinical genetics, 1985, Volume: 27, Issue:3

    Topics: Acetylglucosamine; Acetylglucosaminidase; Amniotic Fluid; Chorionic Villi; Clinical Enzyme Tests; Female; Fibroblasts; Glucosamine; Hexosaminidases; Humans; Hydrogen-Ion Concentration; Hymecromone; Mucopolysaccharidoses; Mucopolysaccharidosis III; Pregnancy; Prenatal Diagnosis; Skin; Spectrometry, Fluorescence; Umbelliferones

1985
Lysosomal storage defects.
    Hospital practice (Office ed.), 1985, Aug-15, Volume: 20, Issue:8

    Topics: Acetylglucosamine; Glycoside Hydrolases; Humans; Lysosomes; Mannosephosphates; Metabolism, Inborn Errors; Mucolipidoses; Mucopolysaccharidoses

1985
Urinary excretion of sulphated N-acetylhexosamines in patients with various mucopolysaccharidoses.
    The Biochemical journal, 1985, Aug-01, Volume: 229, Issue:3

    Topics: Acetylgalactosamine; Acetylglucosamine; Amino Acids; Cells, Cultured; Chromatography, Paper; Fibroblasts; Galactosamine; Humans; Mucopolysaccharidoses; Oligosaccharides; Structure-Activity Relationship

1985