acetylcysteine has been researched along with Cystic Fibrosis in 145 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 81 (55.86) | 18.7374 |
1990's | 13 (8.97) | 18.2507 |
2000's | 23 (15.86) | 29.6817 |
2010's | 23 (15.86) | 24.3611 |
2020's | 5 (3.45) | 2.80 |
Authors | Studies |
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Brodsky, JL; Chiang, A; Chung, WJ; Denny, RA; Goeckeler-Fried, JL; Havasi, V; Hong, JS; Keeton, AB; Mazur, M; Piazza, GA; Plyler, ZE; Rasmussen, L; Rowe, SM; Sorscher, EJ; Weissman, AM; White, EL | 1 |
Chen, J; Chen, L; Chen, M; Li, W; Liao, Y; Liu, L; Qin, J; Shen, Y; Wang, T; Wen, F; Wu, Y; Xiong, S; Zhou, H; Zi, K | 1 |
Aldogan, EH; Hacioglu, M; Yilmaz, FN | 1 |
Addante, A; Charbit, A; Daniltchenko, M; Drescher, M; Duerr, J; Fahy, JV; Gitlin, I; Graeber, SY; Healy, AM; Kuppe, A; Mall, MA; Orain, X; Oscarson, S; Raymond, W; Scheffler, AW | 1 |
Emelogu, IK; Greene, WR; Novak, JD; Tran, CN | 1 |
Elgaher, WAM; Haupenthal, J; Hirsch, AKH; Lababidi, N; Ofosu Kissi, E; Rades, T; Schneider, M; Schwarz, BC; Sigal, V | 1 |
Alonso, SDV; Bujan, A; Chiaramoni, NS | 1 |
Hupp, S; Luckett, P; Papacostas, MF | 1 |
Cheung, B; Gantier, M; Graudins, A; Nejad, C; Wong, A | 1 |
Chilvers, NJ; Wheeler, J | 1 |
Boucher, RC; Delion, MF; Donaldson, SH; Ehre, C; Esther, CR; Fontana, NC; Grubb, BR; Hill, DB; Hothem, LN; Kato, T; Livraghi-Butrico, A; Markovetz, MR; Morrison, CB; Rushton, ZL; Thelin, WR; Villalon, D; Wang, B | 1 |
Aliberti, S; Blasi, F; Cannatelli, A; Cariani, L; Di Maggio, T; Di Pilato, V; Landini, G; Pallecchi, L; Pollini, S; Rossolini, GM; Sergio, F; Sottotetti, S | 1 |
Nash, EF; Ratjen, F; Stephenson, A; Tam, J; Tullis, E | 1 |
Boyle, MP; Guggino, WB; Hanes, J; Kanzawa, MM; Kays, JC; Kim, AJ; Muzyczka, N; Rowe, SM; Schuster, BS; Suk, JS | 1 |
Hussain, S; Roomans, GM; Särndahl, E; Varelogianni, G | 1 |
Antony, V; Chatfield, B; Clancy, J; Conrad, C; Davies, Z; Dunn, C; Egan, ME; Goss, CH; Herzenberg, LA; Lymp, J; Michelson, P; Moss, RB; Nichols, D; Quittell, L; Rubenstein, RC; Spahr, J; Thompson, V; Tirouvanziam, R; Vender, R | 1 |
Cantu-Gonzalez, G | 1 |
Ciofu, O; Høiby, N; Jensen, PØ; Johansen, HK; Kræmer, D; Lykkesfeldt, J; Poulsen, HE; Pressler, T; Qvist, T; Skov, M | 1 |
Carrington, SD; Daniel, BM; Dunican, EM; Erzurum, SC; Fahy, JV; Ghosh, S; Hazen, SL; Hollinger, M; Huang, X; Kerr, SC; Lachowicz-Scroggins, ME; Oscarson, S; Willard, B; Yuan, S | 1 |
Blasi, F; Cazzola, M; Matera, MG; Page, C; Pallecchi, L; Rogliani, P; Rossolini, GM | 1 |
Bartling, TR; Drumm, ML | 2 |
Cohen, R; Cooke, A; Deshpande, AV; Wong, CK | 1 |
Nash, EF; Ratjen, F; Stephenson, A; Tullis, E | 1 |
Cutz, E; Mateos-Corral, D; Ratjen, F; Solomon, M | 1 |
Aulbach, B; Bargon, J; Dauletbaev, N; Fischer, P; Gross, J; Kusche, W; Thyroff-Friesinger, U; Wagner, TO | 1 |
Legnani, D | 1 |
Johannesson, M; Oliynyk, I; Roomans, GM; Varelogianni, G | 1 |
Ballabio, A; Brunetti-Pierri, N; D'Apolito, M; Esposito, S; Gavina, M; Giardino, I; Guido, S; Luciani, A; Maiuri, L; Masliah, E; Medina, D; Pettoello-Mantovani, M; Pulze, L; Quaratino, S; Raia, V; Settembre, C; Spencer, B; Villella, VR | 1 |
Cross, CE; de Cruz, SJ; Eiserich, JP; Hayakawa, KA; Houghton, JS; Morrissey, BM; Vasu, VT | 1 |
Boylan, NJ; Boyle, MP; Dawson, MR; Hanes, J; Lai, SK; Suk, JS | 1 |
Boylan, NJ; Boyle, MP; Cooper, MJ; Hanes, J; Lai, SK; Lin, JM; Schneider, CS; Suk, JS; Tang, BC; Trehan, K; Zeitlin, PL | 1 |
Chargui, A; Cougnon, M; Duranton, C; Melis, N; Mograbi, B; Rubera, I; Tauc, M | 1 |
Osterhoudt, K; Selbst, SM | 1 |
Bear, CE | 1 |
Bange, FC; Böttger, EC | 1 |
REAS, HW | 3 |
SUDDARTH, SB | 1 |
LYNN, HB | 1 |
WEBB, WR | 1 |
MEEKER, IA | 1 |
LAWSON, D; SAGGERS, BA | 2 |
DOCTER, J; STAMM, SJ | 1 |
Jornot, L; Lacroix, JS; Rochat, T | 1 |
Boncoeur, E; Bonvin, E; Clement, A; Fritah, A; Henrion-Caude, A; Jacquot, J; Lefait, E; Muselet, C; Redeuilh, G; Tabary, O | 1 |
Bottiglieri, T; Conrad, CK; Herzenberg, LA; Moss, RB; Tirouvanziam, R | 1 |
Kamin, W; Krämer, I; Schwabe, A | 1 |
Berche, P; Fauroux, B; Ferroni, A; Gaillard, JL; Lanotte, P; Le Bourgeois, M; Marchand, S; Offredo, C; Sermet-Gaudelus, I; Varaigne, F; Vu-Thien, H | 1 |
Fayon, M | 1 |
Broughton-Head, VJ; Shur, J; Shute, JK; Smith, JR | 1 |
Atkuri, KR; Herzenberg, LA; Mantovani, JJ | 1 |
De Lisle, RC; Jansson, K; Roach, E | 1 |
Brunet, S; Comte, B; Guéraud, F; Huot, C; Jacob, SV; Krishnamoorthy, P; Lands, LC; Legault, L; Levy, E; Ntimbane, T | 1 |
Hsia, DY; O'Flynn, M; Rowley, WF | 1 |
Delaitre, R | 1 |
Denton, R; Kwart, H; Litt, M | 1 |
Hurst, GA; LeMaistre, CA; Shaw, PB | 1 |
Docter, JM; Eidelman, S; Lillibridge, CB | 1 |
Gargani, GF; Minicucci, L; Nantron, M; Romano, C | 1 |
Fitzgerald, MX; Hanly, JG | 1 |
Copeland, G; Waldron, R; Wilson, WA | 1 |
Zoirova, RR | 1 |
Böwing, B; Brandt, H; Goering, U; Hirche, H; Reinhardt, M; Stephan, U; Wiesemann, HG | 1 |
Niessen, KH; Steil, E | 1 |
Cunha, LG; Frenkiel, S; Ribeiro, TM; Santos, M | 1 |
Götz, M; Kerrebijn, KF; Kraemer, R; Popow, C | 1 |
Elliott, RB; Mitchell, EA | 1 |
Bonzet-vd Water, E; Kerrebijn, KF; Veentjer, R | 1 |
Dobrowolskaja, R; Kapranov, NJ; Rachynsky, SW; Schabalowa, L | 1 |
Berger, G; Dietzsch, HJ; Gottschalk, B; Leupold, W; Mittenzwey, KW; Rupprecht, E; Wunderlich, P | 1 |
Baker, LM; Lee, JT; Li, PK | 1 |
Goldberg, AL; Jensen, TJ; Loo, MA; Pind, S; Riordan, JR; Williams, DB | 1 |
Albelda, SM; Bavaria, JE; Engelhardt, JF; Kaiser, LR; Pilewski, JM; Wilson, JM | 1 |
Gilligan, PH; Hopfer, RL; Knowles, MR; Whittier, S | 1 |
Busch, AE; Greger, R; Hug, MJ; Köttgen, M; Kunzelmann, K | 1 |
Dasgupta, B; King, M | 1 |
Gillissen, A | 1 |
Sanchis, J; Serrano, J | 1 |
Brand, PL; Duijvestijn, YC | 1 |
Bange, FC; Böttger, EC; Kirschner, P | 1 |
Baran, D; Moës, AJ; Schoutens, A; Van Gansbeke, B; Vanderbist, F; Wery, B | 1 |
Alton, EW; Colledge, WH; Evans, MJ; Farley, R; Ferrari, S; Geddes, DM; Kitson, C; Marriott, C; Parkins, DA; Scarpa, M; Steel, R; Wainwright, B | 1 |
Cabrini, G; Melotti, P; Nicolis, E; Pavirani, A; Rolfini, R; Tamanini, A | 1 |
App, EM; Baran, D; Coffiner, M; Dab, I; King, M; Malfroot, A; Vanderbist, F | 1 |
Boehm, G; Theile, H | 1 |
Dreisin, RB; Mostow, SR | 1 |
Benghial, A | 1 |
Landman, ME; Spiro, RK | 1 |
Gaedicke, G; Koch, G; Lambrecht, W; Weinland, G | 1 |
Govan, JR | 1 |
Kulczycki, LL; Millis, RM; Young, RC | 1 |
Holsclaw, DS; Tecklin, JS | 1 |
Batten, JC; Hodson, ME; Mearns, MB | 1 |
Dietzsch, HJ; Gottschalk, B; Heyne, K; Leupoid, W; Wunderlich, P | 1 |
Mearns, MB | 1 |
Brodzińska, K; Chobot-Maciejewska, H; Gruchot, M; Kompf, E; Kosicka, M; Rafiński, R; Rafiński, T; Zabel, E | 1 |
Breslow, L; Ingal, D; Perman, J | 1 |
Ballke, EH; König, A; Mahner, B; Wiersbitzky, S | 1 |
Evans, JS; George, DE; Mollit, D | 1 |
Andersen, HO; Hjelt, K; Overgaard, K; Waever, E | 1 |
de Leval, M; Fradet, G; Helms, P; Higenbottam, TW; Scott, JP; Sharples, L; Smyth, RL; Wallwork, J; Whitehead, B | 1 |
Koch, C; Stafanger, G | 1 |
Bar-Yishay, E; Godfrey, S; Katznelson, D; Maayan, C; Marcus, Y; Yaacobi, T; Yahav, Y | 1 |
Bourke, S; Brady, HR; FitzGerald, MX; Godson, C; Ryan, MP | 1 |
Ballke, EH; Jährig, K; König, A; Wiersbitzky, S | 1 |
Garne, S; Howitz, P; Koch, C; Morkassel, E; Stafanger, G | 1 |
Bouquet, J; Neijens, HJ; Sinaasappel, M | 1 |
Weller, PH; Williams, J | 1 |
Eichler, I; Götz, M; Wagner, U | 1 |
Andres, JM; Bailey, DJ | 1 |
Bender, SW; Hofmann, D; Posselt, HG; Ratjen, F; Stöver, B; Wönne, R | 1 |
Doershuk, CF; Matthews, LW | 1 |
Cabanel, G; Rambaud, P; Voog, R | 1 |
Stephan, U | 3 |
Schumacher, H | 1 |
Kerrebijn, KF | 2 |
Reid, L; Sturgess, J | 1 |
Altman, RP; Kulczycki, LL; McClenathan, JE; Randolph, JG | 1 |
Friolet, B | 1 |
Flores, RL; Goddard, RF; Mercer, TT; O'Neill, PX; Sanchez, R | 1 |
Chiummariello, A; De Luca, L | 1 |
Kalayoglu, M; Kiesewetter, WB; Rodnan, JB; Sieber, WK | 1 |
Gottschalk, B | 2 |
Aiache, JM; Cheminat, JC; Molina, C | 1 |
Berger, G; Dietzsch, HJ; Gottschalk, B; Händel, D; Heyne, K; Wunderlich, P | 1 |
Cezeaux, G; Harrison, G; Keats, AS; Telford, J | 1 |
Gottschalk, B; Wichmann, G | 1 |
Rocchietta, S | 1 |
Hagmann, R; Rossi, E | 1 |
Busch, R | 1 |
Jodl, J; Lisá, L; Simánková, N | 1 |
Simánková, N; Stefanová, J | 1 |
Anderson, CM; Burke, V; Gracey, M | 1 |
Sitzmann, FC; Stephan, U | 1 |
Brachfeldová, J; Copová, M; Houstĕk, J; Vávrová, V | 1 |
14 review(s) available for acetylcysteine and Cystic Fibrosis
Article | Year |
---|---|
The use of pulmonary clearance medications in the acutely ill patient.
Topics: Acetylcysteine; Cystic Fibrosis; Deoxyribonuclease I; Expectorants; Heparin; Humans; Lung; Mannitol; Mucociliary Clearance; Recombinant Proteins; Saline Solution, Hypertonic; Smoke Inhalation Injury | 2017 |
Nebulized and oral thiol derivatives for pulmonary disease in cystic fibrosis.
Topics: Acetylcysteine; Administration, Inhalation; Administration, Oral; Ambroxol; Carbocysteine; Cystic Fibrosis; Expectorants; Glutathione; Humans; Lung Diseases; Mucociliary Clearance; Nebulizers and Vaporizers; Randomized Controlled Trials as Topic; Saline Solution, Hypertonic | 2013 |
The effect of N-acetylcysteine on biofilms: Implications for the treatment of respiratory tract infections.
Topics: Acetylcysteine; Administration, Inhalation; Biofilms; Bronchiectasis; Bronchitis; Bronchitis, Chronic; Cystic Fibrosis; Expectorants; Humans; Injections, Intramuscular; Pulmonary Disease, Chronic Obstructive; Respiratory Tract Infections | 2016 |
Nebulized and oral thiol derivatives for pulmonary disease in cystic fibrosis.
Topics: Acetylcysteine; Administration, Inhalation; Administration, Oral; Ambroxol; Carbocysteine; Cystic Fibrosis; Expectorants; Humans; Lung Diseases; Mucociliary Clearance; Randomized Controlled Trials as Topic | 2009 |
[Acute bacterial exacerbation of chronic obstructive pulmonary disease and biofilm].
Topics: Acetylcysteine; Anti-Infective Agents; Antioxidants; Biofilms; Bronchi; Bronchitis; Cystic Fibrosis; Humans; Lung; Pneumocystis carinii; Pneumonia, Bacterial; Pneumonia, Pneumocystis; Pneumonia, Viral; Practice Guidelines as Topic; Pulmonary Disease, Chronic Obstructive | 2009 |
Inhalation solutions: which one are allowed to be mixed? Physico-chemical compatibility of drug solutions in nebulizers.
Topics: Acetylcysteine; Administration, Inhalation; Albuterol; Anti-Asthmatic Agents; Anti-Bacterial Agents; Asthma; Bronchodilator Agents; Budesonide; Colistin; Cromolyn Sodium; Cystic Fibrosis; Deoxyribonuclease I; Drug Therapy, Combination; Expectorants; Humans; Ipratropium; Nebulizers and Vaporizers; Respiratory Therapy; Tobramycin | 2006 |
CF-Emerging therapies: Modulation inflammation.
Topics: Acetylcysteine; Anti-Inflammatory Agents, Non-Steroidal; Bronchitis; Cystic Fibrosis; Deoxyribonuclease I; Free Radical Scavengers; Glucocorticoids; Humans; Inflammation; Pancreatic Elastase; Recombinant Proteins; Treatment Outcome | 2006 |
N-Acetylcysteine--a safe antidote for cysteine/glutathione deficiency.
Topics: Acetaminophen; Acetylcysteine; Antidotes; Controlled Clinical Trials as Topic; Cysteine; Cystic Fibrosis; Free Radical Scavengers; Glutathione; HIV Infections; Humans; Prodrugs; Quality of Life | 2007 |
[New perspectives of antioxidant therapy with thiols: nacystelyn].
Topics: Acetylcysteine; Antioxidants; Cystic Fibrosis; Expectorants; Humans; Lysine; Prodrugs | 1996 |
[Usefulness of mucoactive drugs in respiratory diseases].
Topics: Acetylcysteine; Ambroxol; Bromhexine; Bronchiectasis; Bronchitis; Cystic Fibrosis; Deoxyribonuclease I; Dioxanes; Expectorants; Glycerol; Humans; Lung Diseases, Obstructive; Middle Aged; Multicenter Studies as Topic; Prospective Studies; Randomized Controlled Trials as Topic | 1998 |
Systematic review of N-acetylcysteine in cystic fibrosis.
Topics: Acetylcysteine; Administration, Inhalation; Cystic Fibrosis; Expectorants; Humans; Lung; Respiratory Function Tests | 1999 |
Immediate effect of various treatments on lung function in infants with cystic fibrosis.
Topics: Acetylcysteine; Administration, Inhalation; Albuterol; Combined Modality Therapy; Cystic Fibrosis; Humans; Infant; Methods; Physical Therapy Modalities; Respiratory Function Tests | 1989 |
[Mucoviscidosis (review of the literature)].
Topics: Acetylcysteine; Adult; Aerosols; Anti-Bacterial Agents; Bronchi; Bronchial Diseases; Bronchopneumonia; Cough; Cystic Fibrosis; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Lung Compliance; Lung Diseases; Middle Aged; Pancreas; Radiography; Sweating | 1968 |
Meconium ileus: a critical review of treatment and eventual prognosis.
Topics: Acetylcysteine; Adolescent; Autopsy; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Hydrogen Peroxide; Ileum; Infant; Infant, Newborn; Intestinal Obstruction; Intestinal Perforation; Intestine, Small; Male; Meconium; Pancreatin; Peritonitis; Prognosis; Radiography, Abdominal; Therapeutic Irrigation; Vitamin K Deficiency | 1971 |
18 trial(s) available for acetylcysteine and Cystic Fibrosis
Article | Year |
---|---|
The effect of N-acetylcysteine in patients with non-cystic fibrosis bronchiectasis (NINCFB): study protocol for a multicentre, double-blind, randomised, placebo-controlled trial.
Topics: Acetylcysteine; Anti-Bacterial Agents; Bronchiectasis; Cystic Fibrosis; Double-Blind Method; Fibrosis; Humans; Multicenter Studies as Topic; Prospective Studies; Quality of Life; Randomized Controlled Trials as Topic; RNA, Ribosomal, 16S | 2022 |
Long-term treatment with oral N-acetylcysteine: affects lung function but not sputum inflammation in cystic fibrosis subjects. A phase II randomized placebo-controlled trial.
Topics: Acetylcysteine; Administration, Oral; Adolescent; Adult; Antioxidants; Child; Cystic Fibrosis; Double-Blind Method; Drug Monitoring; Female; Humans; Inflammation; Leukocyte Elastase; Lung; Male; Oxidative Stress; Respiratory Function Tests; Sputum; Time; Treatment Outcome | 2015 |
The effect of short-term, high-dose oral N-acetylcysteine treatment on oxidative stress markers in cystic fibrosis patients with chronic P. aeruginosa infection -- a pilot study.
Topics: Acetylcysteine; Administration, Oral; Adult; Antioxidants; Ascorbic Acid; Chronic Disease; Cystic Fibrosis; Dose-Response Relationship, Drug; Drug Administration Schedule; Drug Monitoring; Female; Forced Expiratory Volume; Humans; Inflammation; Lung; Male; Middle Aged; Oxidative Stress; Pseudomonas Infections; Reactive Oxygen Species; Treatment Outcome | 2015 |
A phase II study on safety and efficacy of high-dose N-acetylcysteine in patients with cystic fibrosis.
Topics: Acetylcysteine; Adult; Cystic Fibrosis; Dose-Response Relationship, Drug; Double-Blind Method; Female; Forced Expiratory Volume; Free Radical Scavengers; Glutathione; Humans; Interleukin-8; Male; Sputum; Tumor Necrosis Factor-alpha; Young Adult | 2009 |
High-dose oral N-acetylcysteine, a glutathione prodrug, modulates inflammation in cystic fibrosis.
Topics: Acetylcysteine; Administration, Oral; Adolescent; Antioxidants; Child; Cystic Fibrosis; Female; Glutathione; Humans; Male; Neutrophils; Pancreatic Elastase; Pneumonia; Prodrugs; Treatment Outcome | 2006 |
[Controlled clinical study on the activity of a new mucoregulating drug in obstructive bronchial pathology with a marked hypersecretory feature. The pediatric experience].
Topics: Acetylcysteine; Adolescent; Ambroxol; Bromhexine; Bronchial Diseases; Child; Child, Preschool; Clinical Trials as Topic; Cystic Fibrosis; Female; Humans; Male; Mucus | 1984 |
Oral acetylcysteine in cystic fibrosis. A co-operative study.
Topics: Acetylcysteine; Administration, Oral; Adolescent; Child; Clinical Trials as Topic; Cystic Fibrosis; Double-Blind Method; Female; Humans; Male; Placebos; Respiratory Function Tests | 1980 |
Failure of oral N-acetylcysteine to improve the malabsorption of cystic fibrosis.
Topics: Acetylcysteine; Celiac Disease; Child; Clinical Trials as Topic; Cystic Fibrosis; Double-Blind Method; Female; Humans; Male | 1981 |
Systematic review of N-acetylcysteine in cystic fibrosis.
Topics: Acetylcysteine; Administration, Inhalation; Cystic Fibrosis; Expectorants; Humans; Lung; Respiratory Function Tests | 1999 |
Deposition of nacystelyn from a dry powder inhaler in healthy volunteers and cystic fibrosis patients.
Topics: Absorption; Acetylcysteine; Administration, Inhalation; Adolescent; Adult; Analysis of Variance; Child; Cystic Fibrosis; Expectorants; Female; Humans; Lung; Lysine; Male; Powders; Radionuclide Imaging; Technetium; Tissue Distribution | 2001 |
Dose-finding and 24-h monitoring for efficacy and safety of aerosolized Nacystelyn in cystic fibrosis.
Topics: Acetylcysteine; Administration, Inhalation; Adolescent; Adult; Aerosols; Cystic Fibrosis; Dose-Response Relationship, Drug; Double-Blind Method; Expectorants; Female; Humans; Lysine; Male; Nebulizers and Vaporizers; Respiratory Mechanics; Sputum; Viscosity | 2002 |
[Oral mucosolvin therapy of pulmonary symptoms of mucoviscidosis].
Topics: Acetylcysteine; Administration, Oral; Clinical Trials as Topic; Cystic Fibrosis; Humans; Infant; Lung Diseases | 1979 |
Bronchial drainage with aerosol medications in cystic fibrosis.
Topics: Acetylcysteine; Adolescent; Adult; Aerosols; Bronchi; Child; Cystic Fibrosis; Drainage; Drug Evaluation; Drug Therapy, Combination; Humans; Isoproterenol; Respiratory Function Tests | 1976 |
N-acetylcysteine in cystic fibrosis and Pseudomonas aeruginosa infection: clinical score, spirometry and ciliary motility.
Topics: Acetylcysteine; Adolescent; Adult; Child; Cilia; Clinical Trials as Topic; Cystic Fibrosis; Double-Blind Method; Female; Humans; Male; Pseudomonas Infections; Respiration; Respiratory Function Tests; Time Factors | 1989 |
Immediate effect of various treatments on lung function in infants with cystic fibrosis.
Topics: Acetylcysteine; Administration, Inhalation; Albuterol; Combined Modality Therapy; Cystic Fibrosis; Humans; Infant; Methods; Physical Therapy Modalities; Respiratory Function Tests | 1989 |
The clinical effect and the effect on the ciliary motility of oral N-acetylcysteine in patients with cystic fibrosis and primary ciliary dyskinesia.
Topics: Acetylcysteine; Adolescent; Adult; Child; Child, Preschool; Cilia; Ciliary Motility Disorders; Clinical Trials as Topic; Cystic Fibrosis; Double-Blind Method; Female; Forced Expiratory Volume; Humans; In Vitro Techniques; Infant; Male; Peak Expiratory Flow Rate; Respiratory System; Vital Capacity | 1988 |
A double-blind placebo controlled trial with oral ambroxol and N-acetylcysteine for mucolytic treatment in cystic fibrosis.
Topics: Acetylcysteine; Adolescent; Adult; Ambroxol; Bromhexine; Child; Clinical Trials as Topic; Cystic Fibrosis; Double-Blind Method; Expectorants; Female; Humans; Male; Mucus; Respiratory Function Tests | 1985 |
Bronchial lavage in cystic fibrosis. A comparison of agents.
Topics: Acetylcysteine; Clinical Trials as Topic; Cystic Fibrosis; Humans; Pneumonia; Sodium Chloride; Solutions; Therapeutic Irrigation | 1967 |
115 other study(ies) available for acetylcysteine and Cystic Fibrosis
Article | Year |
---|---|
Increasing the Endoplasmic Reticulum Pool of the F508del Allele of the Cystic Fibrosis Transmembrane Conductance Regulator Leads to Greater Folding Correction by Small Molecule Therapeutics.
Topics: Alleles; Benzoates; Cells, Cultured; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Endoplasmic Reticulum; Furans; Gene Deletion; HEK293 Cells; HeLa Cells; High-Throughput Screening Assays; Humans; Hydroxamic Acids; Microscopy, Fluorescence; Protein Folding; Protein Structure, Tertiary; Pyrazoles; RNA, Messenger; Small Molecule Libraries; Ubiquitination; Vorinostat | 2016 |
Impact of N-Acetylcysteine and Antibiotics Against Single and Dual Species Biofilms of Pseudomonas aeruginosa and Achromobacter xylosoxidans.
Topics: Acetylcysteine; Achromobacter denitrificans; Animals; Anti-Bacterial Agents; Aztreonam; Biofilms; Caenorhabditis elegans; Ciprofloxacin; Cystic Fibrosis; Humans; Pseudomonas aeruginosa; Tobramycin | 2022 |
A novel thiol-saccharide mucolytic for the treatment of muco-obstructive lung diseases.
Topics: Acetylcysteine; Adult; Animals; Carbohydrates; Cystic Fibrosis; Expectorants; Humans; Inflammation; Lung; Lung Diseases, Obstructive; Mice; Sputum; Sulfhydryl Compounds | 2023 |
Successful treatment of distal intestinal obstruction syndrome with N-acetylcysteine and polyethylene glycol via colonoscopy.
Topics: Acetylcysteine; Colonoscopy; Cystic Fibrosis; Female; Humans; Intestinal Obstruction; Middle Aged; Polyethylene Glycols | 2023 |
Spray-drying of inhalable, multifunctional formulations for the treatment of biofilms formed in cystic fibrosis.
Topics: Acetylcysteine; Administration, Inhalation; Animals; Anti-Bacterial Agents; Azithromycin; Biofilms; Ciprofloxacin; Cystic Fibrosis; Drug Stability; Drug Storage; Expectorants; Horses; Mucus; Particle Size; Pseudomonas aeruginosa; Pseudomonas Infections; Tobramycin | 2019 |
Lipopolymers and lipids from lung surfactants in association with N-acetyl-l-cysteine: Characterization and cytotoxicity.
Topics: A549 Cells; Acetylcysteine; Cell Survival; Cystic Fibrosis; Humans; Hydrophobic and Hydrophilic Interactions; Lipids; Particle Size; Polymers; Pulmonary Surfactants; Surface Properties | 2020 |
Hepatotoxicity after paracetamol overdose in a patient with cystic fibrosis despite early acetylcysteine and utility of microRNA to predict hepatotoxicity.
Topics: Acetaminophen; Acetylcysteine; Adult; Antidotes; Biomarkers; Chemical and Drug Induced Liver Injury; Cystic Fibrosis; Drug Overdose; Female; Humans; MicroRNAs; Retrospective Studies; Risk Factors; Treatment Outcome; Young Adult | 2018 |
Intraoperative intraluminal injection of N-acetylcysteine allowing treatment of distal intestinal obstruction syndrome without the need for enterotomy.
Topics: Acetylcysteine; Adolescent; Cystic Fibrosis; Digestive System Surgical Procedures; Fecal Impaction; Humans; Intestinal Obstruction; Intestine, Small; Male; Solvents; Tomography, X-Ray Computed | 2018 |
An Improved Inhaled Mucolytic to Treat Airway Muco-obstructive Diseases.
Topics: Acetylcysteine; Animals; Asthma; Cystic Fibrosis; Disease Models, Animal; Dithiothreitol; Expectorants; Humans; In Vitro Techniques; Male; Mice; Mucociliary Clearance; Mucus; Pulmonary Disease, Chronic Obstructive | 2019 |
In vitro activity of N-acetylcysteine against Stenotrophomonas maltophilia and Burkholderia cepacia complex grown in planktonic phase and biofilm.
Topics: Acetylcysteine; Biofilms; Burkholderia cepacia complex; Cystic Fibrosis; Dose-Response Relationship, Drug; Drug Resistance, Bacterial; Humans; In Vitro Techniques; Microbial Sensitivity Tests; Plankton; Stenotrophomonas maltophilia; Time Factors | 2018 |
Overcoming the cystic fibrosis sputum barrier to leading adeno-associated virus gene therapy vectors.
Topics: Acetylcysteine; Cell Line; Cystic Fibrosis; Dependovirus; Genetic Therapy; Genetic Vectors; HEK293 Cells; Humans; Microscopy, Electron, Scanning; Sputum | 2014 |
N-acetylcysteine and azithromycin affect the innate immune response in cystic fibrosis bronchial epithelial cells in vitro.
Topics: Acetylcysteine; Azithromycin; Bronchi; Cell Line; Cystic Fibrosis; Epithelial Cells; Humans; Immunity, Innate; Interleukin-6; Nod1 Signaling Adaptor Protein; Nod2 Signaling Adaptor Protein; Up-Regulation | 2015 |
50 years ago in The Journal of Pediatrics: The use of N-acetylcysteine in the treatment of cystic fibrosis.
Topics: Acetylcysteine; Administration, Oral; Aminophenols; Cell Membrane; Cystic Fibrosis; Deoxyribonuclease I; DNA; Female; History, 20th Century; Humans; Lung; Mutation; Pediatrics; Quality of Life; Quinolones; Recombinant Proteins | 2014 |
Oxidation increases mucin polymer cross-links to stiffen airway mucus gels.
Topics: Acetylcysteine; Animals; Biomechanical Phenomena; Cross-Linking Reagents; Cystic Fibrosis; Disulfides; DNA; Elasticity; Expectorants; Galactose; Gels; Humans; Lung; Mice, Inbred C57BL; Mucins; Mucus; Oxidation-Reduction; Oxidative Stress; Polymers; Reducing Agents; Sputum; Sulfhydryl Compounds | 2015 |
Oxidative stress causes IL8 promoter hyperacetylation in cystic fibrosis airway cell models.
Topics: Acetylation; Acetylcysteine; Animals; Cell Line; Cystic Fibrosis; Cytokines; Epithelial Cells; Free Radical Scavengers; Humans; Hydrogen Peroxide; Interleukin-8; Oxidants; Oxidative Stress; Promoter Regions, Genetic; Respiratory Mucosa; Transcription, Genetic | 2009 |
Hepatic derangement following N-Acetylcysteine enemas in an infant with cystic fibrosis.
Topics: Acetylcysteine; Chemical and Drug Induced Liver Injury; Cystic Fibrosis; Enema; Fecal Impaction; Free Radical Scavengers; Humans; Ileus; Infant, Newborn; Meconium | 2008 |
Loss of CFTR results in reduction of histone deacetylase 2 in airway epithelial cells.
Topics: Acetylation; Acetylcysteine; Cell Line; Cell Nucleus; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelial Cells; Gene Knockdown Techniques; Histone Deacetylase 2; Histone Deacetylases; Humans; Interleukin-8; NF-kappa B; p300-CBP Transcription Factors; Promoter Regions, Genetic; Repressor Proteins; Respiratory System; RNA Interference; RNA, Messenger; RNA, Small Interfering | 2009 |
Plastic bronchitis as an unusual cause of mucus plugging in cystic fibrosis.
Topics: Acetylcysteine; Administration, Inhalation; Bronchitis; Child, Preschool; Cystic Fibrosis; Expectorants; Humans; Male; Mucus; Pulmonary Disease, Chronic Obstructive | 2009 |
The effect of N-acetylcysteine on chloride efflux from airway epithelial cells.
Topics: Acetylcysteine; Antioxidants; Cell Line; Chlorides; Cystic Fibrosis; Epithelial Cells; Humans; Immunohistochemistry; Oxidative Stress; Respiratory Mucosa | 2010 |
Defective CFTR induces aggresome formation and lung inflammation in cystic fibrosis through ROS-mediated autophagy inhibition.
Topics: Acetylcysteine; Adaptor Proteins, Signal Transducing; Adolescent; Adult; Animals; Antioxidants; Apoptosis Regulatory Proteins; Autophagy; Beclin-1; Cell Line; Cystamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelial Sodium Channels; GTP-Binding Proteins; Heat-Shock Proteins; Humans; Inflammation; Membrane Proteins; Mice; Mice, Inbred CFTR; Mice, Inbred Strains; Mice, Transgenic; Microtubule-Associated Proteins; Models, Biological; Nasal Polyps; Organometallic Compounds; Phosphatidylinositol 3-Kinases; Phosphoinositide-3 Kinase Inhibitors; Protein Binding; Protein Glutamine gamma Glutamyltransferase 2; Protein Transport; Reactive Oxygen Species; Respiratory Mucosa; Salicylates; Sequestosome-1 Protein; Small Ubiquitin-Related Modifier Proteins; Transglutaminases; Young Adult | 2010 |
Evaluation of thiol-based antioxidant therapeutics in cystic fibrosis sputum: Focus on myeloperoxidase.
Topics: Acetylcysteine; Adult; C-Reactive Protein; Cells, Cultured; Chloramines; Cystic Fibrosis; Female; Glutathione; Humans; Inflammation; Lung; Male; Middle Aged; Neutrophils; NF-kappa B; Oxidation-Reduction; Oxidative Stress; Peroxidase; Sputum; Young Adult | 2011 |
Rapid transport of muco-inert nanoparticles in cystic fibrosis sputum treated with N-acetyl cysteine.
Topics: Acetylcysteine; Adult; Biological Transport; Cystic Fibrosis; Drug Carriers; Female; Humans; Male; Middle Aged; Nanoparticles; Polyethylene Glycols; Sputum; Young Adult | 2011 |
N-acetylcysteine enhances cystic fibrosis sputum penetration and airway gene transfer by highly compacted DNA nanoparticles.
Topics: Acetylcysteine; Adult; Animals; Biopolymers; Cystic Fibrosis; Diffusion; DNA; Expectorants; Female; Genetic Therapy; Humans; Male; Mice; Mice, Inbred C57BL; Mucins; Nanoparticles; Plasmids; Polyethylene Glycols; Polylysine; Respiratory System; Sputum; Transduction, Genetic; Viscosity; Young Adult | 2011 |
CFTR is involved in the fine tuning of intracellular redox status: physiological implications in cystic fibrosis.
Topics: Acetylcysteine; Animals; Carbonic Anhydrases; Cell Hypoxia; Cell Line; Chloride Channels; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Disease Models, Animal; Glutathione; Green Fluorescent Proteins; Humans; Hypoxia-Inducible Factor 1, alpha Subunit; Intracellular Space; Kidney Tubules, Proximal; Male; Mice; Mice, Inbred C57BL; Models, Biological; Mutation; Osmolar Concentration; Oxidation-Reduction; Protein Stability; Protein Structure, Tertiary; Reactive Oxygen Species | 2012 |
Pediatric emergency medicine: legal briefs.
Topics: Acetaminophen; Acetylcysteine; Adolescent; Adult; Aortic Aneurysm; Aortic Dissection; Appendicitis; Asthma; Child; Child, Preschool; Cystic Fibrosis; Diagnostic Errors; Drug Labeling; Drug Overdose; Emergencies; False Negative Reactions; Fatal Outcome; Female; Heart Rate, Fetal; Humans; Ibuprofen; Lymphoma, Non-Hodgkin; Male; Malpractice; Marfan Syndrome; Mediastinal Neoplasms; Medication Errors; Nuchal Cord; Patient Safety; Persistent Vegetative State; Pleurisy; Pregnancy; Respiratory Sounds; Social Media; Stevens-Johnson Syndrome; Suicide; Tomography, X-Ray Computed; Transportation of Patients; Unnecessary Procedures; Young Adult | 2012 |
50 years ago in the Journal of Pediatrics: the effect of N-acetylcysteine on the viscosity of tracheobronchial secretions in cystic fibrosis of the pancreas.
Topics: Acetylcysteine; Bronchi; Child; Cystic Fibrosis; Expectorants; Humans; Trachea; Viscosity | 2013 |
Improved decontamination method for recovering mycobacteria from patients with cystic fibrosis.
Topics: Acetylcysteine; Bacteriological Techniques; Cystic Fibrosis; Disinfection; Female; Humans; Male; Mycobacterium; Mycobacterium Infections; Respiratory System; Sodium Hydroxide | 2002 |
The effect of N-acetylcysteine on the viscosity of tracheobronchial secretions in cystic fibrosis of the pancreas.
Topics: Acetylcysteine; Bronchi; Cysteine; Cystic Fibrosis; Humans; Trachea; Viscosity | 1963 |
Acetylcysteine, a new and effective mucolytic agent.
Topics: Acetylcysteine; Bronchi; Cysteine; Cystic Fibrosis; Expectorants; Humans; Lung Diseases | 1963 |
THE USE OF N-ACETYLCYSTEINE IN THE TREATMENT OF CYSTIC FIBROSIS.
Topics: Acetylcysteine; Adolescent; Child; Cysteine; Cystic Fibrosis; Expectorants; Humans; Lung Diseases; Respiration; Respiratory Therapy | 1963 |
MECONIUM ILEUS.
Topics: Acetylcysteine; Child; Cysteine; Cystic Fibrosis; Diagnosis; Humans; Ileus; Infant; Infant Nutritional Physiological Phenomena; Infant, Newborn; Infant, Newborn, Diseases; Intestinal Obstruction; Intestinal Pseudo-Obstruction; Intussusception; Meconium; Pancreatic Extracts; Rectal Prolapse; Surgical Procedures, Operative | 1964 |
NEW MUCOLYTIC AGENTS FOR SPUTUM LIQUEFACTION.
Topics: Acetylcysteine; Asthma; Bronchial Diseases; Cysteine; Cystic Fibrosis; Expectorants; Fibrin; Humans; Lung Diseases; Mucus; Sputum; Toxicology | 1964 |
ACETYLCYSTEINE USED TO LIQUEFY INSPISSATED MECONIUM CAUSING INTESTINAL OBSTRUCTION IN THE NEWBORN.
Topics: Acetylcysteine; Cysteine; Cystic Fibrosis; Fetal Diseases; Hernia, Umbilical; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Intestinal Obstruction; Intestinal Perforation; Meconium; Peritonitis; Surgical Procedures, Operative | 1964 |
THE USE OF N-ACETYLCYSTEINE IN THE TREATMENT OF CYSTIC FIBROSIS.
Topics: Acetylcysteine; Adolescent; Child; Cysteine; Cystic Fibrosis; Humans; Infant; Klebsiella; Lung Diseases; Pneumonia; Proteus Infections; Pseudomonas Infections; Pulmonary Emphysema; Radiography, Thoracic; Respiratory Function Tests; Respiratory Therapy; Spirometry; Staphylococcal Infections | 1964 |
N.A.C. AND ANTIBIOTICS IN CYSTIC FIBROSIS.
Topics: Acetylcysteine; Ampicillin; Anti-Bacterial Agents; Antibiotics, Antitubercular; Cysteine; Cystic Fibrosis; Erythromycin; Fusidic Acid; Humans; Penicillins; Pharmacology; Protein Synthesis Inhibitors; Tetracycline | 1965 |
CLINICAL EVALUATION OF ACETYLCYSTEINE AS A MUCOLYTIC AGENT IN CYSTIC FIBROSIS.
Topics: Acetylcysteine; Adolescent; Aerosols; Blood Gas Analysis; Child; Cysteine; Cystic Fibrosis; Drug Therapy; Expectorants; Humans; Respiratory Function Tests | 1965 |
N-acetylcysteine inhibits Na+ absorption across human nasal epithelial cells.
Topics: Acetylcysteine; Amiloride; Cell Polarity; Cells, Cultured; Chlorides; Cystic Fibrosis; Diffusion Chambers, Culture; Diuretics; Epithelial Sodium Channels; Expectorants; Glutathione; Humans; Membrane Potentials; Nasal Mucosa; Potassium; RNA, Messenger; Sodium; Sodium Channels; Sodium-Potassium-Exchanging ATPase | 2004 |
Oxidative stress response results in increased p21WAF1/CIP1 degradation in cystic fibrosis lung epithelial cells.
Topics: Acetylcysteine; Annexin A5; Apoptosis; Caspase 3; Caspases; Cells, Cultured; Cyclin-Dependent Kinase Inhibitor p21; Cysteine Proteinase Inhibitors; Cystic Fibrosis; Epithelial Cells; Humans; Hyperoxia; Leupeptins; Lung; Oxidative Stress; Oxygen; Reactive Oxygen Species; S Phase | 2006 |
[Cystic fibrosis].
Topics: Acetylcysteine; Clinical Trials as Topic; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans | 2005 |
Value of the chlorhexidine decontamination method for recovery of nontuberculous mycobacteria from sputum samples of patients with cystic fibrosis.
Topics: Acetylcysteine; Chlorhexidine; Cystic Fibrosis; Decontamination; Humans; Mycobacterium; Mycobacterium Infections; Oxalic Acid; Sodium Hydroxide; Sputum | 2006 |
Actin limits enhancement of nanoparticle diffusion through cystic fibrosis sputum by mucolytics.
Topics: Acetylcysteine; Actins; Adolescent; Adult; Cystic Fibrosis; Deoxyribonucleases; Diffusion; DNA; Electrophoresis, Agar Gel; Expectorants; Gelsolin; Genetic Therapy; Humans; In Vitro Techniques; Microscopy, Atomic Force; Mucins; Nanoparticles; Particle Size; Sputum | 2007 |
Effects of laxative and N-acetylcysteine on mucus accumulation, bacterial load, transit, and inflammation in the cystic fibrosis mouse small intestine.
Topics: Acetylcysteine; Animals; Bacteria; Body Weight; Cathartics; Cystic Fibrosis; Disease Models, Animal; Expectorants; Gastric Emptying; Gastrointestinal Transit; Gene Expression Regulation; Immunity, Innate; Inflammation; Intestine, Small; Mice; Mice, Inbred CFTR; Mucus; Polyethylene Glycols; RNA, Bacterial; RNA, Ribosomal, 16S | 2007 |
Oxidative stress and cystic fibrosis-related diabetes: a pilot study in children.
Topics: Acetylcysteine; Adolescent; Analysis of Variance; Child; Cystic Fibrosis; Diabetes Mellitus; Fatty Acids; Female; Glucose Intolerance; Glucose Tolerance Test; Glutathione; Humans; Male; Membrane Proteins; Oxidative Stress; Pilot Projects; Respiratory Function Tests | 2008 |
Cystic fibrosis of the pancreas.
Topics: Acetylcysteine; Anti-Bacterial Agents; Bronchi; Bronchial Diseases; Child; Cystic Fibrosis; Digestive System; Drainage; Fecal Impaction; Humans; Hyperglycemia; Intestinal Obstruction; Liver Cirrhosis; Lung; Lung Diseases; Meconium; Mucus; Pneumatosis Cystoides Intestinalis; Respiratory Function Tests; Respiratory Insufficiency; Respiratory Therapy; Respiratory Tract Diseases; Salivary Glands; Sweat | 1966 |
[Current problems of mucoviscidosis].
Topics: Acetylcysteine; Anti-Bacterial Agents; Child; Cystic Fibrosis; Diet Therapy; Humans; Physical Therapy Modalities | 1966 |
N-acetylcysteine in cystic fibrosis. Mechanical and chemical factors in treatment by aerosol.
Topics: Acetylcysteine; Adolescent; Adult; Aerosols; Agammaglobulinemia; Bronchiectasis; Child; Child, Preschool; Cystic Fibrosis; Drug Stability; Female; Humans; Male; Masks; Mucus | 1967 |
Laboratory and clinical evaluation of the mucolytic properties of acetylcysteine.
Topics: Acetylcysteine; Adult; Bronchiectasis; Cystic Fibrosis; Deoxyribonucleases; Detergents; Humans; Male; Radiography, Thoracic; Respiratory Therapy; Sodium Chloride; Sputum; Tracheotomy; Trypsin; Viscosity | 1967 |
Oral administration of n-acetyl cysteine in the prophylaxis of "meconium ileus equivalent".
Topics: Acetylcysteine; Adult; Cystic Fibrosis; Enema; Humans; Intestinal Obstruction; Male; Meconium; Mucus; Pancreas; Pharmaceutical Vehicles | 1967 |
Meconium ileus equivalent in older patients with cystic fibrosis.
Topics: Acetylcysteine; Adolescent; Child; Child, Preschool; Cystic Fibrosis; Diatrizoate; Drug Therapy, Combination; Female; Humans; Infant; Intestinal Obstruction; Male; Recurrence | 1983 |
Meconium ileus equivalent.
Topics: Acetylcysteine; Adult; Combined Modality Therapy; Cystic Fibrosis; Female; Humans; Intestinal Obstruction; Intestine, Small; Recurrence | 1984 |
[Use of the mucolytic agent, mucosolvin, in multiple modality treatment of cystic fibrosis in children].
Topics: Acetylcysteine; Administration, Oral; Adolescent; Aerosols; Age Factors; Child; Cystic Fibrosis; Humans; Respiratory Therapy | 1983 |
Acetylcysteine in the oral mucolytic treatment of cystic fibrosis.
Topics: Acetylcysteine; Administration, Oral; Adolescent; Body Height; Body Weight; Child; Child, Preschool; Cough; Cystic Fibrosis; Female; Humans; Male; Sputum | 1980 |
Expiratory ventilatory capacity measurements in children with cystic fibrosis treated by oral acetylcysteine.
Topics: Acetylcysteine; Administration, Oral; Adolescent; Adult; Carbocysteine; Child; Cystic Fibrosis; Female; Forced Expiratory Flow Rates; Humans; Male; Peak Expiratory Flow Rate; Time Factors; Vital Capacity | 1980 |
Treatment of bronchial diseases in pediatrics. results of the use of oral acetylcysteine in 80 cases.
Topics: Acetylcysteine; Administration, Oral; Airway Obstruction; Bronchial Diseases; Bronchitis; Child; Child, Preschool; Chronic Disease; Cystic Fibrosis; Humans; Infant; Infant, Newborn; Lung Abscess | 1980 |
The immediate effect of physiotherapy and aerosol treatment on pulmonary function in children with cystic fibrosis.
Topics: Acetylcysteine; Adolescent; Aerosols; Anti-Bacterial Agents; Child; Cystic Fibrosis; Female; Forced Expiratory Flow Rates; Forced Expiratory Volume; Humans; Inspiratory Reserve Volume; Lung; Lung Volume Measurements; Male; Physical Therapy Modalities; Vital Capacity | 1982 |
[Therapy of mucoviscidosis depending on the activity of the inflammatory lung process].
Topics: Acetylcysteine; Bronchoscopy; Child; Child, Preschool; Critical Care; Cystic Fibrosis; Humans; Infant; Therapeutic Irrigation | 1982 |
[Experiences with oral N-acetyl-cysteine treatment in children suffering from cystic fibrosis (author's transl)].
Topics: Acetylcysteine; Administration, Oral; Bronchoscopy; Child; Cystic Fibrosis; Humans; Respiratory Function Tests | 1980 |
Before-assay liquification of pulmonary mucous secretions with N-acetyl-L-cysteine.
Topics: Acetylcysteine; Chemical Phenomena; Chemistry; Cystic Fibrosis; Gentamicins; Sputum | 1980 |
Multiple proteolytic systems, including the proteasome, contribute to CFTR processing.
Topics: Acetylcysteine; Animals; ATP Binding Cassette Transporter, Subfamily B, Member 1; CHO Cells; Cricetinae; Cysteine Endopeptidases; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Endopeptidases; Endoplasmic Reticulum; Humans; Leupeptins; Multienzyme Complexes; Oligopeptides; Proteasome Endopeptidase Complex; Protein Processing, Post-Translational; Recombinant Fusion Proteins; Ubiquitins | 1995 |
Adenovirus-mediated gene transfer to human bronchial submucosal glands using xenografts.
Topics: Acetylcysteine; Adenoviridae; Animals; Bronchi; Cystic Fibrosis; Fluorescence; Gene Transfer Techniques; Genetic Vectors; Humans; Immunohistochemistry; Lung; Mice; Mice, SCID; Microspheres; Submucous Plexus; Tissue Transplantation; Transplantation, Heterologous | 1995 |
Improved recovery of mycobacteria from respiratory secretions of patients with cystic fibrosis.
Topics: Acetylcysteine; Bacteriological Techniques; Cystic Fibrosis; Evaluation Studies as Topic; Humans; Lung; Mycobacterium; Oxalates; Oxalic Acid; Pseudomonas; Respiratory System; Sodium Hydroxide; Sputum; Trachea | 1993 |
N-Acetyl-L-cysteine and its derivatives activate a Cl- conductance in epithelial cells.
Topics: Acetylcysteine; Animals; Bronchi; Cells, Cultured; Chloride Channels; Colonic Neoplasms; Cystic Fibrosis; Electric Conductivity; Epithelial Cells; Humans; Hydrogen-Ion Concentration; Oocytes; Respiratory System; Tumor Cells, Cultured; Xenopus | 1996 |
Reduction in viscoelasticity in cystic fibrosis sputum in vitro using combined treatment with nacystelyn and rhDNase.
Topics: Acetylcysteine; Adolescent; Adult; Cystic Fibrosis; Deoxyribonuclease I; Elasticity; Expectorants; Humans; In Vitro Techniques; Lysine; Recombinant Proteins; Rheology; Sputum; Viscosity | 1996 |
Recovery of mycobacteria from patients with cystic fibrosis.
Topics: Acetylcysteine; Adolescent; Adult; Bacteriological Techniques; Cystic Fibrosis; Female; Humans; Male; Mycobacterium; Oxalic Acid; Prospective Studies; Pseudomonas aeruginosa; Respiratory System; Sodium Hydroxide | 1999 |
Mucus altering agents as adjuncts for nonviral gene transfer to airway epithelium.
Topics: Acetylcysteine; Animals; Chloramphenicol O-Acetyltransferase; Cholinergic Antagonists; Cystic Fibrosis; Dose-Response Relationship, Drug; Expectorants; Gene Expression; Genetic Therapy; Genetic Vectors; Glycopyrrolate; Injections, Intramuscular; Lysine; Mice; Mice, Inbred BALB C; Mice, Inbred CFTR; Models, Animal; Nasal Mucosa; Sheep; Trachea | 2001 |
Activation of NF-kB mediates ICAM-1 induction in respiratory cells exposed to an adenovirus-derived vector.
Topics: Acetylcysteine; Adenoviridae; Antioxidants; Cell Line; Chloramphenicol O-Acetyltransferase; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Gene Expression; Genetic Therapy; Genetic Vectors; Humans; Intercellular Adhesion Molecule-1; Lung; NF-kappa B; Peptides; Pyrrolidines; RNA, Messenger; Sesquiterpenes; Thiocarbamates; Translocation, Genetic | 2001 |
Sulfhydryl-mediated depression of ciliary activity: an adverse effect of acetylcysteine.
Topics: Acetylcysteine; Cilia; Cystic Fibrosis; Depression, Chemical; Sulfhydryl Compounds | 1979 |
Meconium ileus equivalent an adult: a case report.
Topics: Acetylcysteine; Adult; Cystic Fibrosis; Humans; Intestinal Obstruction; Intestine, Small; Male | 1978 |
Meconium ileus equivalent.
Topics: Acetylcysteine; Adolescent; Adult; Age Factors; Child; Child, Preschool; Cystic Fibrosis; Fecal Impaction; Humans; Ileum; Infant; Infant, Newborn; Intestinal Obstruction; Male; Meconium; Radiography; Respiration, Artificial | 1978 |
[Treatment of meconium ileus equivalent].
Topics: Acetylcysteine; Child; Cystic Fibrosis; Enema; Fecal Impaction; Humans; Intestinal Obstruction; Male | 1978 |
Mucoid strains of Pseudomonas aeruginosa: the influence of culture medium on the stability of mucus production.
Topics: Acetylcysteine; Cetrimonium Compounds; Citrates; Culture Media; Cystic Fibrosis; Deoxycholic Acid; Ferric Compounds; Humans; Lactose; Mucus; Neutral Red; Phosphatidylcholines; Polysorbates; Pseudomonas aeruginosa; Sodium Dodecyl Sulfate; Species Specificity; Surface-Active Agents; Thiosulfates | 1975 |
Validation of therapeutic bronchoscopic bronchial washing in cystic fibrosis.
Topics: Acetylcysteine; Adolescent; Adult; Age Factors; Airway Resistance; Bronchi; Bronchoscopy; Carbenicillin; Cystic Fibrosis; Gentamicins; Humans; Maximal Expiratory Flow-Volume Curves; Middle Aged; Pancreatic Extracts; Suction; Therapeutic Irrigation | 1977 |
Meconium ileus equivalent in adults with cystic fibrosis of pancreas: a report of six cases.
Topics: Acetylcysteine; Adolescent; Adult; Colon; Cystic Fibrosis; Diabetes Complications; Enema; Female; Humans; Intestinal Obstruction; Intestine, Small; Male; Radiography | 1976 |
Cystic fibrosis: comparison of two mucolytic drugs for inhalation treatment (acetylcysteine and arginine hydrochloride).
Topics: Acetylcysteine; Aerosols; Arginine; Bronchoscopy; Carbon Dioxide; Child; Child, Preschool; Cough; Cystic Fibrosis; Drug Evaluation; Expectorants; Female; Humans; Male; Mucus; Oxygen; Radionuclide Imaging; Respiration; Respiratory Function Tests; Spirometry; Sputum | 1975 |
Inhalation therapy in cystic fibrosis.
Topics: Acetylcysteine; Albuterol; Anti-Bacterial Agents; Cystic Fibrosis; Humans; Penicillins; Respiratory Therapy; Sodium Chloride | 1975 |
[Bronchial lavage in mucoviscidosis in children].
Topics: Acetylcysteine; Adolescent; Bronchi; Child, Preschool; Cystic Fibrosis; Female; Humans; Therapeutic Irrigation | 1975 |
Nonoperative treatment of meconium ileus equivalent.
Topics: Acetylcysteine; Child; Cystic Fibrosis; Enema; Feces; Female; Humans; Intestinal Obstruction; Lipase; Meconium | 1975 |
The effect of N-acetyl-cysteine (Mucosolvin) on the transmural potential difference of the mucosa in children.
Topics: Acetylcysteine; Administration, Oral; Administration, Rectal; Asthma; Child; Cystic Fibrosis; Female; Humans; Intestinal Mucosa; Male; Membrane Potentials; Mouth Mucosa; Mucous Membrane; Nasal Mucosa; Reference Values | 1992 |
Biliary infusion therapy in the inspissated bile syndrome of cystic fibrosis.
Topics: Acetylcysteine; Cholecystokinin; Cholestasis; Cystic Fibrosis; Humans; Infant; Injections, Intravenous; Liver; Male; Radiography; Therapeutic Irrigation | 1991 |
The age-related incidence of meconium ileus equivalent in a cystic fibrosis population: the impact of high-energy intake.
Topics: Acetylcysteine; Adolescent; Adult; Age Factors; Body Height; Body Weight; Child; Child, Preschool; Cystic Fibrosis; Energy Intake; Female; Humans; Infant; Infant, Newborn; Intestinal Obstruction; Male; Pancreatin | 1990 |
The use of heart-lung transplantation in management of terminal respiratory complications of cystic fibrosis.
Topics: Acetylcysteine; Adult; Constipation; Cystic Fibrosis; Follow-Up Studies; Heart-Lung Transplantation; Humans; Lung Diseases; Prognosis | 1990 |
Acute hypomagnesaemia complicating the treatment of meconium ileus equivalent in cystic fibrosis.
Topics: Acetylcysteine; Adult; Cystic Fibrosis; Diatrizoate; Fecal Impaction; Female; Humans; Intestinal Obstruction; Magnesium; Male | 1988 |
The transmural potential difference (tmpd) of the bronchial mucosa in children with chronic nonspecific respiratory diseases (CF- and non-CF-children).
Topics: Acetylcysteine; Asthma; Bronchi; Bronchitis; Child; Cystic Fibrosis; Epithelium; Humans; Membrane Potentials; Mucous Membrane | 1988 |
Malabsorption in cystic fibrosis: mechanisms and treatment.
Topics: Acetylcysteine; Adolescent; Celiac Disease; Child; Cystic Fibrosis; Drug Administration Schedule; Drug Therapy, Combination; Female; Humans; Intestinal Absorption; Intestinal Mucosa; Lipase; Lipid Metabolism; Male; Microspheres; Pancreatic Extracts; Pancreatin; Pancrelipase; Polysorbates; Random Allocation | 1988 |
Clinical features, pathogenesis and management of meconium ileus equivalent.
Topics: Acetylcysteine; Adult; Child; Cystic Fibrosis; Diatrizoate; Humans; Ileum; Intestinal Obstruction | 1986 |
[Gastrointestinal complications in cystic fibrosis: meconium ileus equivalent].
Topics: Acetylcysteine; Adolescent; Child; Child, Preschool; Cystic Fibrosis; Diagnosis, Differential; Female; Follow-Up Studies; Humans; Ileal Diseases; Intestinal Obstruction; Male; Meconium; Recurrence | 1986 |
Liver injury after oral and rectal administration of N-acetylcysteine for meconium ileus equivalent in a patient with cystic fibrosis.
Topics: Acetylcysteine; Administration, Oral; Administration, Rectal; Chemical and Drug Induced Liver Injury; Cystic Fibrosis; Humans; Infant; Intestinal Obstruction; Liver Function Tests; Male | 1987 |
Inhalation therapy and postural drainage for the treatment of cystic fibrosis.
Topics: Acetylcysteine; Aerosols; Cystic Fibrosis; Drainage; Humans; Isoproterenol; Methicillin; Neomycin; Oxygen Inhalation Therapy; Phenylephrine; Physical Therapy Modalities; Polymyxins; Propylene Glycols; Respiratory Therapy; Sodium Chloride | 1967 |
[Mucoviscidosis in adults].
Topics: Acetylcysteine; Adult; Bronchitis; Cystic Fibrosis; Duodenal Ulcer; Humans; Male; Middle Aged; Oxytetracycline; Pancreatic Juice; Sweat | 1968 |
[Physical and aerosol therapy of mucoviscidosis].
Topics: Acetylcysteine; Aerosols; Child; Cystic Fibrosis; Humans; Massage; Physical Therapy Modalities | 1972 |
[Aerosol tent and inhalation therapy of mucoviscidosis].
Topics: Acetylcysteine; Aerosols; Cystic Fibrosis; Humans; Infant; Methods; Respiratory Therapy | 1972 |
[The treatment of mucoviscidosis (pancreatic fibrosis, cystic fibrosis)].
Topics: Acetylcysteine; Aerosols; Child; Cystic Fibrosis; Diet Therapy; Humans | 1972 |
An organ culture study of the effect of drugs on the secretory activity of the human bronchial submucosal gland.
Topics: Acetylcysteine; Autoradiography; Bradykinin; Bronchi; Bronchitis; Cells, Cultured; Cystic Fibrosis; Expectorants; Glucocorticoids; Glucose; Glycoproteins; Humans; Mucous Membrane; Organ Culture Techniques; Parasympatholytics; Parasympathomimetics; Sympathomimetics; Tritium | 1972 |
Bronchoscopy and bronchial lavage (BBL) in children with cystic fibrosis.
Topics: Acetylcysteine; Adolescent; Adult; Bronchi; Bronchoscopy; Carbon Dioxide; Child; Child, Preschool; Cystic Fibrosis; Emergencies; Evaluation Studies as Topic; Humans; Hydrogen-Ion Concentration; Infant; Infant, Newborn; Oxygen; Partial Pressure; Pneumonia; Pulmonary Atelectasis; Pulmonary Emphysema; Respiratory Distress Syndrome, Newborn; Therapeutic Irrigation | 1973 |
[Current position in the diagnosis and treatment of cystic fibrosis (mucoviscidosis)].
Topics: Acetylcysteine; Breathing Exercises; Cystic Fibrosis; Humans; Infant, Newborn; Time Factors | 1974 |
Output characteristics and clinical efficacy of ultrasonic nebulizers.
Topics: Acetylcysteine; Aerosols; Asthma; Bronchial Diseases; Child; Cortisone; Cystic Fibrosis; Humans; Mucus; Pancreatic Diseases; Penicillin G; Positive-Pressure Respiration; Radioisotopes; Sarcina; Sputum; Ultrasonic Therapy; Ultrasonics | 1968 |
In vivo penetration of antibiotics into sputum in cystic fibrosis.
Topics: Acetylcysteine; Aerosols; Ampicillin; Anti-Bacterial Agents; Biological Assay; Cephaloridine; Cloxacillin; Cystic Fibrosis; Erythromycin; Gentamicins; Humans; Infection Control; Lincomycin; Methicillin; Molecular Weight; Novobiocin; Sputum; Sulfonamides | 1968 |
[Therapy of mucoviscidosis using aerosols].
Topics: Acetylcysteine; Aerosols; Anti-Bacterial Agents; Child; Child, Preschool; Cystic Fibrosis; Humans; Infant; Respiratory Therapy | 1972 |
[Liquefacients of bronchial secretion].
Topics: Acetylcysteine; Asthma; Bronchi; Bronchiectasis; Cystic Fibrosis; Expectorants; Humans; Peptide Hydrolases; Respiratory Insufficiency; Surface-Active Agents | 1971 |
[Mucoviscidosis: diagnosis and therapy].
Topics: Acetylcysteine; Aerosols; Ambulatory Care; Anti-Bacterial Agents; Bronchi; Cystic Fibrosis; Diagnosis, Differential; Diarrhea; Dispensatories as Topic | 1970 |
[Importance of bronchology in the long-time treatment of children with mucoviscidosis].
Topics: Acetylcysteine; Bronchi; Bronchitis; Bronchography; Child; Child, Preschool; Cystic Fibrosis; Humans; Infant; Sputum | 1971 |
[The treatment of cystic fibrosis with aerosols].
Topics: Acetylcysteine; Aerosols; Cystic Fibrosis; Equipment and Supplies; Humans; Ultrasonics | 1969 |
[The effect of N-acetyl-L-cystein (Mucosolvin) on different antibiotics].
Topics: Acetylcysteine; Anti-Bacterial Agents; Cystic Fibrosis; Drug Antagonism; Humans | 1970 |
Acetylcysteine--Respaire and Mucomyst.
Topics: Acetylcysteine; Cystic Fibrosis; Humans; Lung Diseases | 1970 |
[Long term therapy in cystic fibrosis].
Topics: Acetylcysteine; Aerosols; Anti-Bacterial Agents; Child; Cystic Fibrosis; Drainage; Humans; Physical Therapy Modalities; Physician-Patient Relations; Posture; Respiratory Therapy; Time Factors; Ultrasonic Therapy | 1970 |
[Mucolytic agents for inhalation].
Topics: Acetylcysteine; Aerosols; Cystic Fibrosis; Humans; Mucus; Respiratory Therapy | 1970 |
[Mucoviscidosis, current views on therapy].
Topics: Acetylcysteine; Adrenal Cortex Hormones; Adult; Aerosols; Anabolic Agents; Anti-Bacterial Agents; Anti-Inflammatory Agents; Child; Child, Preschool; Cystic Fibrosis; Diet Therapy; Digitalis Glycosides; Enzyme Therapy; Expectorants; Female; Gastrointestinal Diseases; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Lung Diseases, Obstructive; Male; Physical Therapy Modalities; Respiratory Insufficiency; Respiratory Therapy; Ultrasonic Therapy; Vaccination; Vitamins | 1971 |
[Comprehension of mucoviscidosis in the newborn].
Topics: Acetylcysteine; Cystic Fibrosis; Humans; Infant, Newborn | 1971 |
[Mucoviscidosis].
Topics: Acetylcysteine; Aerosols; Anti-Bacterial Agents; Child; Cystic Fibrosis; Drainage; Humans; Lung Diseases; Pancreatic Extracts; Radiography; Ultrasonic Therapy | 1968 |
[Therapeutic procedure in children with mucoviscidosis].
Topics: Acetylcysteine; Adolescent; Aerosols; Anti-Bacterial Agents; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Infant; Male; Prognosis; Respiratory Therapy | 1969 |
[Therapeutic rehabilitation of children afflicted with mucoviscidosis].
Topics: Acetylcysteine; Aerosols; Anti-Bacterial Agents; Child; Cystic Fibrosis; Drainage; Humans; Posture; Respiratory Therapy | 1969 |
Treatment of abdominal pain in cystic fibrosis by oral administration of n-acetyl cysteine.
Topics: Abdomen; Acetylcysteine; Adolescent; Adult; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Male; Pain | 1969 |
[On a new possibility of treating pulmonary complications of mucoviscidosis].
Topics: Acetylcysteine; Adolescent; Bronchiectasis; Child; Child, Preschool; Cystic Fibrosis; Humans | 1965 |
Mucolytic agent.
Topics: Acetylcysteine; Bronchitis; Cystic Fibrosis; Humans; Mucus; Tracheotomy | 1966 |
[The use N-acetylcysteine in the treatment of mucoviscidosis].
Topics: Acetylcysteine; Adolescent; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Infant; Male | 1966 |