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6-methoxy-n-(3-sulfopropyl)quinolinium and Cystic Fibrosis

6-methoxy-n-(3-sulfopropyl)quinolinium has been researched along with Cystic Fibrosis in 9 studies

*Cystic Fibrosis: An autosomal recessive genetic disease of the EXOCRINE GLANDS. It is caused by mutations in the gene encoding the CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR expressed in several organs including the LUNG, the PANCREAS, the BILIARY SYSTEM, and the SWEAT GLANDS. Cystic fibrosis is characterized by epithelial secretory dysfunction associated with ductal obstruction resulting in AIRWAY OBSTRUCTION; chronic RESPIRATORY INFECTIONS; PANCREATIC INSUFFICIENCY; maldigestion; salt depletion; and HEAT PROSTRATION. [MeSH]

Research

Studies (9)

TimeframeStudies, this research(%)All Research%
pre-19901 (11.11)18.7374
1990's6 (66.67)18.2507
2000's1 (11.11)29.6817
2010's1 (11.11)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Clauzure, M; Marín, MC; Santa-Coloma, TA; Valdivieso, ÁG1
Bernaudin, JF; Bresson, JL; Edelman, A; Fajac, A; Feuillet, MN; Lenoir, G; Marianovski, R; Sermet-Gaudelus, I; Torossi, T; Urbin, I; Vallée, B1
Cheng, SH; Fang, SL; Jefferson, DM; Marshall, J; Piraino, S; Schiavi, SC; Smith, AE; Welsh, MJ; Zabner, J1
Alton, EW; Caplen, NJ; Geddes, DM; Huang, L; Munkonge, FM; Sorgi, F; Stern, M1
Alton, EW; Carothers, AD; Davidson, H; Davidson-Smith, H; Dorin, JR; Greening, AP; Ho, LP; Innes, JA; Kallmeyer, G; McLachlan, G; Michaelis, U; Middleton, PG; Naujoks, K; Porteous, DJ; Samways, J; Seeber, S; Smith, SN; Stevenson, BJ1
Bonnet, N; Chinet, T; Dupuit, F; Hinnrasky, J; Kaplan, H; Pierrot, D; Puchelle, E; Zahm, JM1
Berton, G; Cabrini, G; Dechecchi, MC; Gamberi, C; Rolfini, R; Tamanini, A1
Blalock, JE; Jilling, T; Kirk, KL; LeBoeuf, RD; Sorscher, EJ; Weaver, ML1
Cabrini, G; Dechecchi, MC1

Other Studies

9 other study(ies) available for 6-methoxy-n-(3-sulfopropyl)quinolinium and Cystic Fibrosis

ArticleYear
Measurement of cystic fibrosis transmembrane conductance regulator activity using fluorescence spectrophotometry.
    Analytical biochemistry, 2011, Nov-15, Volume: 418, Issue:2

    Topics: Cells, Cultured; Chloride Channels; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Glyburide; Humans; Hypoglycemic Agents; Quartz; Quinolinium Compounds; Reproducibility of Results; Sensitivity and Specificity; Spectrometry, Fluorescence

2011
Normal function of the cystic fibrosis conductance regulator protein can be associated with homozygous (Delta)F508 mutation.
    Pediatric research, 2002, Volume: 52, Issue:5

    Topics: Chlorides; Codon; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelial Cells; Fluorescent Dyes; Homozygote; Humans; Ion Transport; Nasal Mucosa; Phenotype; Point Mutation; Quinolinium Compounds; Reverse Transcriptase Polymerase Chain Reaction; RNA, Messenger; Second Messenger Systems; Sequence Deletion

2002
Functional activation of the cystic fibrosis trafficking mutant delta F508-CFTR by overexpression.
    The American journal of physiology, 1995, Volume: 268, Issue:4 Pt 1

    Topics: Animals; Butyrates; Butyric Acid; Cell Line; Cell Membrane; Chloride Channels; Chlorides; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Fluorescent Dyes; Humans; Metallothionein; Mice; Pancreas; Promoter Regions, Genetic; Quinolinium Compounds; Recombinant Proteins; Respiratory System; Tumor Cells, Cultured

1995
Quantitative fluorescence measurements of chloride secretion in native airway epithelium from CF and non-CF subjects.
    Gene therapy, 1995, Volume: 2, Issue:10

    Topics: Adult; Aged; Bronchi; Cells, Cultured; Chlorides; Colforsin; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelium; Fluorescent Dyes; Genetic Therapy; Humans; Ionomycin; Kinetics; Middle Aged; Nasal Mucosa; Quinolinium Compounds; Reference Values; Transfection; Turbinates

1995
Laboratory and clinical studies in support of cystic fibrosis gene therapy using pCMV-CFTR-DOTAP.
    Gene therapy, 1996, Volume: 3, Issue:12

    Topics: Aerosols; Animals; Clinical Trials, Phase I as Topic; COS Cells; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Cytomegalovirus; Fatty Acids, Monounsaturated; Genetic Therapy; Genetic Vectors; Humans; Liposomes; Membrane Potentials; Mice; Nasal Mucosa; Pharmaceutical Vehicles; Quaternary Ammonium Compounds; Quinolinium Compounds; RNA, Messenger; Transfection

1996
Induction of a cAMP-stimulated chloride secretion in regenerating poorly differentiated airway epithelial cells by adenovirus-mediated CFTR gene transfer.
    Human gene therapy, 1997, Aug-10, Volume: 8, Issue:12

    Topics: Adenoviridae; Adolescent; Adult; Aged; Cell Differentiation; Cells, Cultured; Child; Child, Preschool; Chlorides; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelial Cells; Epithelium; Fluorescence; Gene Transfer Techniques; Humans; Image Processing, Computer-Assisted; Middle Aged; Patch-Clamp Techniques; Quinolinium Compounds; Respiratory System

1997
Effect of modulation of protein kinase C on the cAMP-dependent chloride conductance in T84 cells.
    FEBS letters, 1992, Oct-12, Volume: 311, Issue:1

    Topics: 8-Bromo Cyclic Adenosine Monophosphate; Biological Transport; Chloride Channels; Chlorides; Colonic Neoplasms; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Diglycerides; Down-Regulation; Electric Conductivity; Fluorescence; Fluorescent Dyes; Humans; Ionomycin; Membrane Proteins; Protein Kinase C; Protein Kinases; Quinolinium Compounds; RNA, Messenger; Tetradecanoylphorbol Acetate; Tumor Cells, Cultured

1992
Antisense oligodeoxynucleotide to the cystic fibrosis gene inhibits anion transport in normal cultured sweat duct cells.
    Proceedings of the National Academy of Sciences of the United States of America, 1991, Sep-01, Volume: 88, Issue:17

    Topics: Anions; Base Sequence; Biological Transport; Cells, Cultured; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Fluorescent Dyes; Humans; Kinetics; Membrane Proteins; Molecular Sequence Data; Oligonucleotide Probes; Oligonucleotides, Antisense; Quinolinium Compounds; Sweat Glands; Transcription, Genetic

1991
Chloride conductance in membrane vesicles from human placenta using a fluorescent probe. Implications for cystic fibrosis.
    Biochimica et biophysica acta, 1988, Nov-22, Volume: 945, Issue:2

    Topics: Biological Transport; Chlorides; Cystic Fibrosis; Electric Conductivity; Epithelium; Humans; In Vitro Techniques; Kinetics; Membrane Potentials; Placenta; Quinolinium Compounds

1988