6-methoxy-n-(3-sulfopropyl)quinolinium has been researched along with Cystic Fibrosis in 9 studies
*Cystic Fibrosis: An autosomal recessive genetic disease of the EXOCRINE GLANDS. It is caused by mutations in the gene encoding the CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR expressed in several organs including the LUNG, the PANCREAS, the BILIARY SYSTEM, and the SWEAT GLANDS. Cystic fibrosis is characterized by epithelial secretory dysfunction associated with ductal obstruction resulting in AIRWAY OBSTRUCTION; chronic RESPIRATORY INFECTIONS; PANCREATIC INSUFFICIENCY; maldigestion; salt depletion; and HEAT PROSTRATION. [MeSH]
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 1 (11.11) | 18.7374 |
1990's | 6 (66.67) | 18.2507 |
2000's | 1 (11.11) | 29.6817 |
2010's | 1 (11.11) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
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Clauzure, M; Marín, MC; Santa-Coloma, TA; Valdivieso, ÁG | 1 |
Bernaudin, JF; Bresson, JL; Edelman, A; Fajac, A; Feuillet, MN; Lenoir, G; Marianovski, R; Sermet-Gaudelus, I; Torossi, T; Urbin, I; Vallée, B | 1 |
Cheng, SH; Fang, SL; Jefferson, DM; Marshall, J; Piraino, S; Schiavi, SC; Smith, AE; Welsh, MJ; Zabner, J | 1 |
Alton, EW; Caplen, NJ; Geddes, DM; Huang, L; Munkonge, FM; Sorgi, F; Stern, M | 1 |
Alton, EW; Carothers, AD; Davidson, H; Davidson-Smith, H; Dorin, JR; Greening, AP; Ho, LP; Innes, JA; Kallmeyer, G; McLachlan, G; Michaelis, U; Middleton, PG; Naujoks, K; Porteous, DJ; Samways, J; Seeber, S; Smith, SN; Stevenson, BJ | 1 |
Bonnet, N; Chinet, T; Dupuit, F; Hinnrasky, J; Kaplan, H; Pierrot, D; Puchelle, E; Zahm, JM | 1 |
Berton, G; Cabrini, G; Dechecchi, MC; Gamberi, C; Rolfini, R; Tamanini, A | 1 |
Blalock, JE; Jilling, T; Kirk, KL; LeBoeuf, RD; Sorscher, EJ; Weaver, ML | 1 |
Cabrini, G; Dechecchi, MC | 1 |
9 other study(ies) available for 6-methoxy-n-(3-sulfopropyl)quinolinium and Cystic Fibrosis
Article | Year |
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Measurement of cystic fibrosis transmembrane conductance regulator activity using fluorescence spectrophotometry.
Topics: Cells, Cultured; Chloride Channels; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Glyburide; Humans; Hypoglycemic Agents; Quartz; Quinolinium Compounds; Reproducibility of Results; Sensitivity and Specificity; Spectrometry, Fluorescence | 2011 |
Normal function of the cystic fibrosis conductance regulator protein can be associated with homozygous (Delta)F508 mutation.
Topics: Chlorides; Codon; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelial Cells; Fluorescent Dyes; Homozygote; Humans; Ion Transport; Nasal Mucosa; Phenotype; Point Mutation; Quinolinium Compounds; Reverse Transcriptase Polymerase Chain Reaction; RNA, Messenger; Second Messenger Systems; Sequence Deletion | 2002 |
Functional activation of the cystic fibrosis trafficking mutant delta F508-CFTR by overexpression.
Topics: Animals; Butyrates; Butyric Acid; Cell Line; Cell Membrane; Chloride Channels; Chlorides; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Fluorescent Dyes; Humans; Metallothionein; Mice; Pancreas; Promoter Regions, Genetic; Quinolinium Compounds; Recombinant Proteins; Respiratory System; Tumor Cells, Cultured | 1995 |
Quantitative fluorescence measurements of chloride secretion in native airway epithelium from CF and non-CF subjects.
Topics: Adult; Aged; Bronchi; Cells, Cultured; Chlorides; Colforsin; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelium; Fluorescent Dyes; Genetic Therapy; Humans; Ionomycin; Kinetics; Middle Aged; Nasal Mucosa; Quinolinium Compounds; Reference Values; Transfection; Turbinates | 1995 |
Laboratory and clinical studies in support of cystic fibrosis gene therapy using pCMV-CFTR-DOTAP.
Topics: Aerosols; Animals; Clinical Trials, Phase I as Topic; COS Cells; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Cytomegalovirus; Fatty Acids, Monounsaturated; Genetic Therapy; Genetic Vectors; Humans; Liposomes; Membrane Potentials; Mice; Nasal Mucosa; Pharmaceutical Vehicles; Quaternary Ammonium Compounds; Quinolinium Compounds; RNA, Messenger; Transfection | 1996 |
Induction of a cAMP-stimulated chloride secretion in regenerating poorly differentiated airway epithelial cells by adenovirus-mediated CFTR gene transfer.
Topics: Adenoviridae; Adolescent; Adult; Aged; Cell Differentiation; Cells, Cultured; Child; Child, Preschool; Chlorides; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelial Cells; Epithelium; Fluorescence; Gene Transfer Techniques; Humans; Image Processing, Computer-Assisted; Middle Aged; Patch-Clamp Techniques; Quinolinium Compounds; Respiratory System | 1997 |
Effect of modulation of protein kinase C on the cAMP-dependent chloride conductance in T84 cells.
Topics: 8-Bromo Cyclic Adenosine Monophosphate; Biological Transport; Chloride Channels; Chlorides; Colonic Neoplasms; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Diglycerides; Down-Regulation; Electric Conductivity; Fluorescence; Fluorescent Dyes; Humans; Ionomycin; Membrane Proteins; Protein Kinase C; Protein Kinases; Quinolinium Compounds; RNA, Messenger; Tetradecanoylphorbol Acetate; Tumor Cells, Cultured | 1992 |
Antisense oligodeoxynucleotide to the cystic fibrosis gene inhibits anion transport in normal cultured sweat duct cells.
Topics: Anions; Base Sequence; Biological Transport; Cells, Cultured; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Fluorescent Dyes; Humans; Kinetics; Membrane Proteins; Molecular Sequence Data; Oligonucleotide Probes; Oligonucleotides, Antisense; Quinolinium Compounds; Sweat Glands; Transcription, Genetic | 1991 |
Chloride conductance in membrane vesicles from human placenta using a fluorescent probe. Implications for cystic fibrosis.
Topics: Biological Transport; Chlorides; Cystic Fibrosis; Electric Conductivity; Epithelium; Humans; In Vitro Techniques; Kinetics; Membrane Potentials; Placenta; Quinolinium Compounds | 1988 |