6-hexadecanoylamino-4-methylumbelliferyl-galactopyranoside has been researched along with Classic Globoid Cell Leukodystrophy in 4 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 1 (25.00) | 18.7374 |
| 1990's | 2 (50.00) | 18.2507 |
| 2000's | 1 (25.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Kolodny, EH; Krivit, W; Kurtzberg, J; Pastores, GM; Raghavan, S; Torres, PA; Zeng, B | 1 |
| Kolodny, E; Raghavan, S; Wiederschain, G | 1 |
| Grimm, U; Machill, G; Seidlitz, G; Widerschain, G; Zschiesche, M | 1 |
| Kozlova, IK; Petushkova, NA; Tsvetkova, IV; Vidershaĭn, GIa | 1 |
4 other study(ies) available for 6-hexadecanoylamino-4-methylumbelliferyl-galactopyranoside and Classic Globoid Cell Leukodystrophy
| Article | Year |
|---|---|
Globoid cell leukodystrophy (Krabbe disease): normal umbilical cord blood galactocerebrosidase activity and polymorphic mutations.
Topics: Alleles; Central Nervous System; Cryopreservation; DNA, Complementary; Fetal Blood; Galactosides; Galactosylceramidase; Hematopoietic Stem Cell Transplantation; Heterozygote; HLA Antigens; Homozygote; Humans; Hymecromone; Leukodystrophy, Globoid Cell; Lysosomes; Mutation; Polymorphism, Genetic | 2005 |
Characterization of 6-hexadecanoylamino-4-methylumbelliferyl-beta-D- galactopyranoside as fluorogenic substrate of galactocerebrosidase for the diagnosis of Krabbe disease.
Topics: Animals; Brain; Carbohydrate Sequence; Cells, Cultured; Clinical Enzyme Tests; Dose-Response Relationship, Drug; Female; Fibroblasts; Fluorescent Dyes; Galactosides; Galactosylceramidase; Galactosylceramides; Humans; Hydrolysis; Hymecromone; Leukocytes; Leukodystrophy, Globoid Cell; Male; Mice; Mice, Inbred C57BL; Molecular Sequence Data; Oleic Acid; Oleic Acids; Substrate Specificity; Taurocholic Acid | 1992 |
Use of a fluorogenic substrate, 6-hexadecanoylamino-4-methylumbelliferyl-beta-D-galactopyranoside, in the diagnosis of Krabbe disease.
Topics: Cells, Cultured; Fibroblasts; Fluorescent Dyes; Galactosides; Galactosylceramidase; Humans; Hymecromone; Leukodystrophy, Globoid Cell | 1991 |
[A study of various properties of beta-galactocerebrosidase from human chorion using synthetic fluorescent substrates].
Topics: Cells, Cultured; Chorion; Fibroblasts; Fluorescent Dyes; Galactosidases; Galactosides; Galactosylceramidase; Glycosides; Humans; Hydrogen-Ion Concentration; Hymecromone; Kinetics; Leukodystrophy, Globoid Cell; Substrate Specificity; Umbelliferones | 1988 |