6-aminoquinolyl-n-hydroxysuccinimidyl-carbamate and Metabolism--Inborn-Errors

6-aminoquinolyl-n-hydroxysuccinimidyl-carbamate has been researched along with Metabolism--Inborn-Errors* in 1 studies

Other Studies

1 other study(ies) available for 6-aminoquinolyl-n-hydroxysuccinimidyl-carbamate and Metabolism--Inborn-Errors

ArticleYear
Determination of plasma amino acids by fluorescent derivatization and reversed-phase liquid chromatographic separation.
    Clinical laboratory, 2004, Volume: 50, Issue:3-4

    Amino acid analysis in physiological fluids remains expensive, as it usually requires a dedicated analyzer. We modified an RP-HPLC method originally devoted to peptide and protein hydrolysate analysis in order to apply it to plasma amino acid determination. The described method uses a commercial kit based on 6-aminoquinolyl-N-hydroxysuccinimidyl carbamate derivatization followed by reversed-phase high-performance liquid chromatography. The described method is easy to use and allows the determination of twelve amino acids frequently involved in aminoacidopathies, thus enabling the diagnosis and follow-up of affected patients. The results obtained by this method are comparable to those obtained with a classical amino acid analyzer.

    Topics: Amino Acids; Aminoquinolines; Carbamates; Chromatography, High Pressure Liquid; Fluorescent Dyes; Humans; Metabolism, Inborn Errors; Reagent Kits, Diagnostic; Reproducibility of Results

2004