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4-methylumbelliferyl-6-sulfo-2-acetamido-2-deoxy-beta-glucopyranoside and Gangliosidoses

4-methylumbelliferyl-6-sulfo-2-acetamido-2-deoxy-beta-glucopyranoside has been researched along with Gangliosidoses in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19903 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Bayleran, J; Hechtman, P; Saray, W1
Desnick, RJ; Inui, K; Okada, S; Wenger, DA; Yabuuchi, H; Yutaka, T1
Eto, Y; Gomibuchi, I; Ida, H; Maekawa, K; Ohashi, T; Umezawa, F1

Other Studies

3 other study(ies) available for 4-methylumbelliferyl-6-sulfo-2-acetamido-2-deoxy-beta-glucopyranoside and Gangliosidoses

ArticleYear
Synthesis of 4-methylumbelliferyl-beta-D-N-acetylglucosamine-6-sulfate and its use in classification of GM2 gangliosidosis genotypes.
    Clinica chimica acta; international journal of clinical chemistry, 1984, Nov-15, Volume: 143, Issue:2

    Topics: beta-N-Acetylhexosaminidases; Cell Line; Drug Stability; Fibroblasts; Gangliosidoses; Genetic Carrier Screening; Genotype; Hexosaminidase A; Hexosaminidase B; Hexosaminidases; Homozygote; Hot Temperature; Humans; Hymecromone; Kinetics; Liver; Substrate Specificity; Tay-Sachs Disease; Umbelliferones

1984
Hexosaminidase A activity in skin fibroblasts from various types of GM2 gangliosidosis using a fluorogenic sulphated substrate.
    Journal of inherited metabolic disease, 1985, Volume: 8, Issue:3

    Topics: beta-N-Acetylhexosaminidases; Catalysis; Cell Line; Fibroblasts; G(M2) Ganglioside; Gangliosidoses; Hexosaminidase A; Humans; Hymecromone; Skin

1985
Partial deficiency of beta-hexosaminidase activity in canine GM2-gangliosidosis.
    The Tohoku journal of experimental medicine, 1987, Volume: 152, Issue:4

    Topics: Animals; beta-N-Acetylhexosaminidases; Chromatography, DEAE-Cellulose; Disease Models, Animal; Dog Diseases; Dogs; G(M2) Ganglioside; Gangliosidoses; Hexosaminidase A; Hymecromone; Isoenzymes

1987