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4-methylumbelliferyl 2-acetamido-2-deoxy-beta-d-glucopyranoside and Gangliosidoses

4-methylumbelliferyl 2-acetamido-2-deoxy-beta-d-glucopyranoside has been researched along with Gangliosidoses in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19901 (50.00)18.7374
1990's1 (50.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Hinrichs, U; Kytzia, HJ; Sandhoff, K1
Dos Santos, MR; Maia, M; Pinto, RA; Ribeiro, MG; Sá Miranda, MC1

Other Studies

2 other study(ies) available for 4-methylumbelliferyl 2-acetamido-2-deoxy-beta-d-glucopyranoside and Gangliosidoses

ArticleYear
Diagnosis of infantile and juvenile forms of GM2 gangliosidosis variant 0. Residual activities toward natural and different synthetic substrates.
    Human genetics, 1984, Volume: 67, Issue:4

    Topics: Acetylglucosamine; Cells, Cultured; Fibroblasts; G(M2) Ganglioside; Gangliosidoses; Genetic Variation; Glucosamine; Hexosaminidases; Humans; Hymecromone; Isoelectric Focusing; Skin; Substrate Specificity

1984
Biochemical characterization of beta-hexosaminidase in different biological specimens from eleven patients with GM2-gangliosidosis B1 variant.
    Journal of inherited metabolic disease, 1991, Volume: 14, Issue:5

    Topics: Acetylglucosamine; beta-N-Acetylhexosaminidases; Child; Child, Preschool; Electrophoresis, Cellulose Acetate; Fibroblasts; G(M2) Ganglioside; Gangliosidoses; Genetic Variation; Heterozygote; Homozygote; Humans; Hymecromone; Leukocytes; Lymphocytes; Portugal

1991