4-methylumbelliferyl 2-acetamido-2-deoxy-beta-d-glucopyranoside has been researched along with Gangliosidoses in 2 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 1 (50.00) | 18.7374 |
1990's | 1 (50.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Hinrichs, U; Kytzia, HJ; Sandhoff, K | 1 |
Dos Santos, MR; Maia, M; Pinto, RA; Ribeiro, MG; Sá Miranda, MC | 1 |
2 other study(ies) available for 4-methylumbelliferyl 2-acetamido-2-deoxy-beta-d-glucopyranoside and Gangliosidoses
Article | Year |
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Diagnosis of infantile and juvenile forms of GM2 gangliosidosis variant 0. Residual activities toward natural and different synthetic substrates.
Topics: Acetylglucosamine; Cells, Cultured; Fibroblasts; G(M2) Ganglioside; Gangliosidoses; Genetic Variation; Glucosamine; Hexosaminidases; Humans; Hymecromone; Isoelectric Focusing; Skin; Substrate Specificity | 1984 |
Biochemical characterization of beta-hexosaminidase in different biological specimens from eleven patients with GM2-gangliosidosis B1 variant.
Topics: Acetylglucosamine; beta-N-Acetylhexosaminidases; Child; Child, Preschool; Electrophoresis, Cellulose Acetate; Fibroblasts; G(M2) Ganglioside; Gangliosidoses; Genetic Variation; Heterozygote; Homozygote; Humans; Hymecromone; Leukocytes; Lymphocytes; Portugal | 1991 |