3-hydroxyglutaric acid has been researched along with Disease Models, Animal in 12 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 8 (66.67) | 29.6817 |
| 2010's | 4 (33.33) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Amaral, AU; da Silva, JC; de Oliveira, FH; Leipnitz, G; Ribeiro, RT; Seminotti, B; Souza, DO; Wajner, M | 1 |
| Blank, AE; Burgard, P; Koeller, DM; Kölker, S; Komatsuzaki, S; Mittelbronn, M; Okun, JG; Opp, S; Sauer, SW | 1 |
| Colín-González, AL; Leipnitz, G; Paz-Loyola, AL; Ribeiro, CA; Santamaría, A; Seminotti, B; Serratos, I; Souza, DO; Wajner, M | 1 |
| Ballhausen, D; Bonafé, L; Braissant, O; Henry, H; Jafari, P; Zavadakova, P | 1 |
| de Mello, CF; Goodman, SI; Koeller, DM; Kölker, S; Mühlhausen, C; Okun, JG; Sauer, S; Wajner, M; Woontner, M | 1 |
| Del Bigio, MR; Funk, CB; Prasad, AN | 1 |
| Antonetti, DA; Cheng, KC; Connor, JR; Goodman, SI; Lazovic, J; Smith, MB; Wolpert, EB; Woontner, M; Zinnanti, WJ | 2 |
| Crnic, LR; Fricker, G; Goodman, SI; Harding, CO; Hoffmann, GF; Hörster, F; Koeller, DM; Kölker, S; Mahringer, A; Mühlhausen, C; Müller, I; Okun, JG; Sauer, SW | 1 |
| Bjugstad, KB; Crnic, LS; Freed, CR; Goodman, SI | 1 |
| Sauer, SW | 1 |
| Braulke, T; Glatzel, M; Goodman, SI; Herdering, W; Keyser, B; Koeller, DM; Kölker, S; Kortmann, B; Lukacs, Z; Mühlhausen, C; Muschol, N; Sauer, SW; Stellmer, F; Thiem, J; Ullrich, K | 1 |
12 other study(ies) available for 3-hydroxyglutaric acid and Disease Models, Animal
| Article | Year |
|---|---|
Acute lysine overload provokes marked striatum injury involving oxidative stress signaling pathways in glutaryl-CoA dehydrogenase deficient mice.
Topics: Animals; Corpus Striatum; Disease Models, Animal; Glutarates; Glutaryl-CoA Dehydrogenase; Lysine; Mice, Knockout; Neostriatum; Oxidation-Reduction; Oxidative Stress; Signal Transduction | 2019 |
Multifactorial modulation of susceptibility to l-lysine in an animal model of glutaric aciduria type I.
Topics: Aconitate Hydratase; Amino Acid Metabolism, Inborn Errors; Animals; Brain; Brain Diseases, Metabolic; Diet; Disease Models, Animal; Dose-Response Relationship, Drug; Energy Metabolism; Female; Genetic Predisposition to Disease; Glutarates; Glutaryl-CoA Dehydrogenase; Glyceraldehyde-3-Phosphate Dehydrogenases; Ketoglutarate Dehydrogenase Complex; Lysine; Male; Mice, 129 Strain; Mice, Inbred C57BL; Mice, Knockout; Risk Factors; Sex Factors; Spectrophotometry | 2015 |
Toxic synergism between quinolinic acid and organic acids accumulating in glutaric acidemia type I and in disorders of propionate metabolism in rat brain synaptosomes: Relevance for metabolic acidemias.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Brain; Brain Diseases, Metabolic; Disease Models, Animal; Glutarates; Glutaryl-CoA Dehydrogenase; Lipid Peroxidation; Male; Methylmalonic Acid; Neuroprotective Agents; Oxidative Stress; Propionates; Quinolinic Acid; Rats, Wistar; Reactive Oxygen Species; Synaptosomes | 2015 |
Ammonium accumulation and cell death in a rat 3D brain cell model of glutaric aciduria type I.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Astrocytes; Brain; Brain Diseases, Metabolic; Cell Death; Culture Media; Disease Models, Animal; Glutarates; Glutaryl-CoA Dehydrogenase; Neurons; Oligodendroglia; Quaternary Ammonium Compounds; Rats; Rats, Sprague-Dawley | 2013 |
Animal models for glutaryl-CoA dehydrogenase deficiency.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Chiroptera; Disease Models, Animal; Glutarates; Glutaryl-CoA Dehydrogenase; Injections; Mice; Mice, Knockout; Neostriatum; Oxidoreductases Acting on CH-CH Group Donors | 2004 |
Preliminary attempts to establish a rat model of striatal injury in glutaric acidaemia type I.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Disease Models, Animal; Glutarates; Injections; Lipopolysaccharides; Male; Necrosis; Neostriatum; Neurons; Rats; Rats, Sprague-Dawley | 2004 |
A diet-induced mouse model for glutaric aciduria type I.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Blood-Brain Barrier; Capillary Permeability; Corpus Striatum; Diet; Dietary Proteins; Disease Models, Animal; Female; Glutarates; Lysine; Magnetic Resonance Imaging; Male; Mice; Mice, Inbred C57BL; Neurons; Survival Analysis; Tissue Culture Techniques | 2006 |
Intracerebral accumulation of glutaric and 3-hydroxyglutaric acids secondary to limited flux across the blood-brain barrier constitute a biochemical risk factor for neurodegeneration in glutaryl-CoA dehydrogenase deficiency.
Topics: Amino Acids; Animals; Biological Transport; Blood-Brain Barrier; Blotting, Western; Brain; Carnitine; Cells, Cultured; Dicarboxylic Acids; Disease Models, Animal; Endothelial Cells; Glucose; Glutarates; Glutaryl-CoA Dehydrogenase; Heart; Liver; Mice; Mice, Inbred C57BL; Mice, Knockout; Models, Biological; Muscles; Neurodegenerative Diseases; Risk Factors; Statistics, Nonparametric; Swine; Time Factors; Tissue Distribution | 2006 |
New insights for glutaric aciduria type I.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Brain Diseases, Metabolic, Inborn; Diet; Disease Models, Animal; Glutarates; Mice | 2006 |
Infant mice with glutaric acidaemia type I have increased vulnerability to 3-nitropropionic acid toxicity.
Topics: Animals; Animals, Newborn; Brain; Brain Diseases, Metabolic, Inborn; Disease Models, Animal; Dose-Response Relationship, Drug; Glutarates; Humans; Mice; Mice, Inbred C57BL; Mice, Knockout; Mice, Transgenic; Neurodegenerative Diseases; Nitro Compounds; Propionates | 2006 |
Biochemistry and bioenergetics of glutaryl-CoA dehydrogenase deficiency.
Topics: Acyl Coenzyme A; Animals; Blood-Brain Barrier; Brain; Brain Diseases, Metabolic, Inborn; Capillary Permeability; Disease Models, Animal; Energy Metabolism; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Ketoglutarate Dehydrogenase Complex; Mice; Mice, Knockout; Neurons | 2007 |
Transport and distribution of 3-hydroxyglutaric acid before and during induced encephalopathic crises in a mouse model of glutaric aciduria type 1.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Biological Transport; Brain; Brain Diseases; Dextrans; Disease Models, Animal; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Immunohistochemistry; Intestinal Mucosa; Kidney; Mice; Mice, Inbred C57BL; Mice, Knockout | 2008 |