3-hydroxyglutaric acid has been researched along with Brain Diseases, Metabolic, Familial in 10 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 10 (100.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Barbeito, L; Casanova, G; Cassina, P; Fernandez, A; Latini, A; Olivera, S; Rosillo, JC; Wajner, M | 1 |
| Hoffmann, GF; Koeller, DM; Kölker, S; Okun, JG | 1 |
| Christensen, E; Kristensen, AS; Lund, AM; Lund, TM; Schousboe, A | 1 |
| Bührer, C; Gerstner, B; Gratopp, A; Marcinkowski, M; Obladen, M; Sifringer, M | 1 |
| Antonetti, DA; Cheng, KC; Connor, JR; Goodman, SI; Lazovic, J; Smith, MB; Wolpert, EB; Woontner, M; Zinnanti, WJ | 1 |
| Bjugstad, KB; Crnic, LS; Freed, CR; Goodman, SI | 1 |
| Sauer, SW | 1 |
| Ahlemeyer, B; Hoffmann, GF; Kölker, S; Krieglstein, J | 1 |
| Ahlemeyer, B; Hoffmann, GF; Hühne, R; Kölker, S; Krieglstein, J; Mayatepek, E | 1 |
| Ahlemeyer, B; de Mello, CF; de Souza, FR; Fighera, MR; Hoffmann, GF; Kölker, S; Krieglstein, J; Mayatepek, E; Wajner, M | 1 |
1 review(s) available for 3-hydroxyglutaric acid and Brain Diseases, Metabolic, Familial
| Article | Year |
|---|---|
Pathomechanisms of neurodegeneration in glutaryl-CoA dehydrogenase deficiency.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Brain Diseases, Metabolic, Inborn; Child, Preschool; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Infant; Models, Neurological; Nerve Degeneration; Oxidoreductases Acting on CH-CH Group Donors | 2004 |
9 other study(ies) available for 3-hydroxyglutaric acid and Brain Diseases, Metabolic, Familial
| Article | Year |
|---|---|
Astrocytic proliferation and mitochondrial dysfunction induced by accumulated glutaric acidemia I (GAI) metabolites: possible implications for GAI pathogenesis.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Animals, Newborn; Anthracenes; Antioxidants; Astrocytes; Brain; Brain Diseases, Metabolic, Inborn; Butadienes; Cell Count; Cell Proliferation; Cell Survival; Cells, Cultured; Glutarates; Immunohistochemistry; Membrane Potential, Mitochondrial; Mitochondria; Nitriles; Porphyrins; Rats; Rats, Sprague-Dawley | 2008 |
On the neurotoxicity of glutaric, 3-hydroxyglutaric, and trans-glutaconic acids in glutaric acidemia type 1.
Topics: Animals; Brain Diseases, Metabolic, Inborn; Cell Death; Cells, Cultured; Cerebral Cortex; Corpus Striatum; Fetus; Glutarates; Glutaryl-CoA Dehydrogenase; Membrane Potentials; Mice; Nerve Degeneration; Neurons; Neurotoxins; Oocytes; Oxidoreductases Acting on CH-CH Group Donors; Rats; Receptors, N-Methyl-D-Aspartate; Xenopus | 2004 |
Glutaric acid and its metabolites cause apoptosis in immature oligodendrocytes: a novel mechanism of white matter degeneration in glutaryl-CoA dehydrogenase deficiency.
Topics: Amino Acid Chloromethyl Ketones; Animals; Apoptosis; Base Sequence; Brain Diseases, Metabolic, Inborn; Caspase Inhibitors; Cell Differentiation; Cell Line; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Nerve Degeneration; Oligodendroglia; Oxidoreductases Acting on CH-CH Group Donors; Rats; Receptors, Glutamate; RNA, Messenger | 2005 |
New insights for glutaric aciduria type I.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Brain Diseases, Metabolic, Inborn; Diet; Disease Models, Animal; Glutarates; Mice | 2006 |
Infant mice with glutaric acidaemia type I have increased vulnerability to 3-nitropropionic acid toxicity.
Topics: Animals; Animals, Newborn; Brain; Brain Diseases, Metabolic, Inborn; Disease Models, Animal; Dose-Response Relationship, Drug; Glutarates; Humans; Mice; Mice, Inbred C57BL; Mice, Knockout; Mice, Transgenic; Neurodegenerative Diseases; Nitro Compounds; Propionates | 2006 |
Biochemistry and bioenergetics of glutaryl-CoA dehydrogenase deficiency.
Topics: Acyl Coenzyme A; Animals; Blood-Brain Barrier; Brain; Brain Diseases, Metabolic, Inborn; Capillary Permeability; Disease Models, Animal; Energy Metabolism; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Ketoglutarate Dehydrogenase Complex; Mice; Mice, Knockout; Neurons | 2007 |
Maturation-dependent neurotoxicity of 3-hydroxyglutaric and glutaric acids in vitro: a new pathophysiologic approach to glutaryl-CoA dehydrogenase deficiency.
Topics: Animals; Antibodies; Brain Diseases, Metabolic, Inborn; Cells, Cultured; Chick Embryo; Dizocilpine Maleate; Glutarates; Glutaryl-CoA Dehydrogenase; Neurons; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Piperidines; Rats | 2000 |
Potentiation of 3-hydroxyglutarate neurotoxicity following induction of astrocytic iNOS in neonatal rat hippocampal cultures.
Topics: Animals; Animals, Newborn; Astrocytes; Brain Diseases, Metabolic, Inborn; Cell Survival; Cells, Cultured; Cerebral Cortex; Cytokines; Drug Interactions; Enzyme Inhibitors; Glutarates; Glutaryl-CoA Dehydrogenase; Hippocampus; Interferon-gamma; Interleukin-1; Neurons; Neuroprotective Agents; Neurotoxins; Nitric Oxide; Nitric Oxide Synthase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Rats; Receptors, N-Methyl-D-Aspartate | 2001 |
Intrastriatal administration of 3-hydroxyglutaric acid induces convulsions and striatal lesions in rats.
Topics: Acyl Coenzyme A; Animals; Brain Diseases, Metabolic, Inborn; Excitatory Amino Acid Antagonists; GABA Agonists; GABA-A Receptor Agonists; Glutamic Acid; Glutarates; Male; Neostriatum; Neurotoxins; Rats; Rats, Wistar; Receptors, AMPA; Receptors, GABA-A; Receptors, N-Methyl-D-Aspartate; Seizures | 2001 |