3-hydroxybutyric acid has been researched along with Electron Transfer Flavoprotein Alpha Subunit Deficiency in 3 studies
3-Hydroxybutyric Acid: BUTYRIC ACID substituted in the beta or 3 position. It is one of the ketone bodies produced in the liver.
3-hydroxybutyric acid : A straight-chain 3-hydroxy monocarboxylic acid comprising a butyric acid core with a single hydroxy substituent in the 3- position; a ketone body whose levels are raised during ketosis, used as an energy source by the brain during fasting in humans. Also used to synthesise biodegradable plastics.
| Excerpt | Relevance | Reference |
|---|---|---|
| "The strength of the current study is the international pooling of data demonstrating that D,L-3-HB treatment can be effective and safe in MADD(-like) patients." | 2.66 | Efficacy and safety of D,L-3-hydroxybutyrate (D,L-3-HB) treatment in multiple acyl-CoA dehydrogenase deficiency. ( Aktuğlu Zeybek, AÇ; Allersma, DP; Bhattacharya, K; Debray, FG; Derks, TGJ; Ellaway, CJ; Gautschi, M; Geraghty, MT; Gil-Ortega, D; Jager, EA; Larson, AA; Moore, F; Morava, E; Morris, AA; Oishi, K; Schiff, M; Scholl-Bürgi, S; Tchan, MC; Van Hove, JLK; van Rijt, WJ; van Spronsen, F; Vockley, J; Witters, P; Wortmann, SB, 2020) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 2 (66.67) | 24.3611 |
| 2020's | 1 (33.33) | 2.80 |
| Authors | Studies |
|---|---|
| van Rijt, WJ | 2 |
| Jager, EA | 1 |
| Allersma, DP | 1 |
| Aktuğlu Zeybek, AÇ | 1 |
| Bhattacharya, K | 1 |
| Debray, FG | 1 |
| Ellaway, CJ | 1 |
| Gautschi, M | 1 |
| Geraghty, MT | 1 |
| Gil-Ortega, D | 1 |
| Larson, AA | 1 |
| Moore, F | 1 |
| Morava, E | 1 |
| Morris, AA | 1 |
| Oishi, K | 1 |
| Schiff, M | 1 |
| Scholl-Bürgi, S | 1 |
| Tchan, MC | 1 |
| Vockley, J | 1 |
| Witters, P | 1 |
| Wortmann, SB | 1 |
| van Spronsen, F | 1 |
| Van Hove, JLK | 1 |
| Derks, TGJ | 1 |
| Fischer, T | 1 |
| Och, U | 1 |
| Marquardt, T | 1 |
| Heiner-Fokkema, MR | 1 |
| du Marchie Sarvaas, GJ | 1 |
| Waterham, HR | 1 |
| Blokpoel, RG | 1 |
| van Spronsen, FJ | 1 |
| Derks, TG | 1 |
1 review available for 3-hydroxybutyric acid and Electron Transfer Flavoprotein Alpha Subunit Deficiency
| Article | Year |
|---|---|
Efficacy and safety of D,L-3-hydroxybutyrate (D,L-3-HB) treatment in multiple acyl-CoA dehydrogenase deficiency.
Topics: 3-Hydroxybutyric Acid; Acyl-CoA Dehydrogenase; Cardiomyopathies; Humans; Infant; Multiple Acyl Coenz | 2020 |
2 other studies available for 3-hydroxybutyric acid and Electron Transfer Flavoprotein Alpha Subunit Deficiency
| Article | Year |
|---|---|
Long-term ketone body therapy of severe multiple acyl-CoA dehydrogenase deficiency: A case report.
Topics: 3-Hydroxybutyric Acid; Child; Dietary Supplements; Humans; Ketone Bodies; Male; Multiple Acyl Coenzy | 2019 |
Favorable outcome after physiologic dose of sodium-D,L-3-hydroxybutyrate in severe MADD.
Topics: 3-Hydroxybutyric Acid; Female; Humans; Infant, Newborn; Multiple Acyl Coenzyme A Dehydrogenase Defic | 2014 |