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3-hydroxybutyric acid and Cardiomyopathies, Primary

3-hydroxybutyric acid has been researched along with Cardiomyopathies, Primary in 3 studies

3-Hydroxybutyric Acid: BUTYRIC ACID substituted in the beta or 3 position. It is one of the ketone bodies produced in the liver.
3-hydroxybutyric acid : A straight-chain 3-hydroxy monocarboxylic acid comprising a butyric acid core with a single hydroxy substituent in the 3- position; a ketone body whose levels are raised during ketosis, used as an energy source by the brain during fasting in humans. Also used to synthesise biodegradable plastics.

Research Excerpts

ExcerptRelevanceReference
"The strength of the current study is the international pooling of data demonstrating that D,L-3-HB treatment can be effective and safe in MADD(-like) patients."2.66Efficacy and safety of D,L-3-hydroxybutyrate (D,L-3-HB) treatment in multiple acyl-CoA dehydrogenase deficiency. ( Aktuğlu Zeybek, AÇ; Allersma, DP; Bhattacharya, K; Debray, FG; Derks, TGJ; Ellaway, CJ; Gautschi, M; Geraghty, MT; Gil-Ortega, D; Jager, EA; Larson, AA; Moore, F; Morava, E; Morris, AA; Oishi, K; Schiff, M; Scholl-Bürgi, S; Tchan, MC; Van Hove, JLK; van Rijt, WJ; van Spronsen, F; Vockley, J; Witters, P; Wortmann, SB, 2020)

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (33.33)24.3611
2020's2 (66.67)2.80

Authors

AuthorsStudies
van Rijt, WJ1
Jager, EA1
Allersma, DP1
Aktuğlu Zeybek, AÇ1
Bhattacharya, K1
Debray, FG1
Ellaway, CJ1
Gautschi, M1
Geraghty, MT1
Gil-Ortega, D1
Larson, AA1
Moore, F1
Morava, E1
Morris, AA1
Oishi, K1
Schiff, M1
Scholl-Bürgi, S1
Tchan, MC1
Vockley, J1
Witters, P1
Wortmann, SB1
van Spronsen, F1
Van Hove, JLK1
Derks, TGJ1
Song, JP1
Chen, L1
Chen, X1
Ren, J1
Zhang, NN1
Tirasawasdichai, T1
Hu, ZL1
Hua, W1
Hu, YR1
Tang, HR1
Chen, HV1
Hu, SS1
Valayannopoulos, V1
Bajolle, F1
Arnoux, JB1
Dubois, S1
Sannier, N1
Baussan, C1
Petit, F1
Labrune, P1
Rabier, D1
Ottolenghi, C1
Vassault, A1
Broissand, C1
Bonnet, D1
de Lonlay, P1

Reviews

1 review available for 3-hydroxybutyric acid and Cardiomyopathies, Primary

ArticleYear
Efficacy and safety of D,L-3-hydroxybutyrate (D,L-3-HB) treatment in multiple acyl-CoA dehydrogenase deficiency.
    Genetics in medicine : official journal of the American College of Medical Genetics, 2020, Volume: 22, Issue:5

    Topics: 3-Hydroxybutyric Acid; Acyl-CoA Dehydrogenase; Cardiomyopathies; Humans; Infant; Multiple Acyl Coenz

2020

Other Studies

2 other studies available for 3-hydroxybutyric acid and Cardiomyopathies, Primary

ArticleYear
Elevated plasma β-hydroxybutyrate predicts adverse outcomes and disease progression in patients with arrhythmogenic cardiomyopathy.
    Science translational medicine, 2020, 02-12, Volume: 12, Issue:530

    Topics: 3-Hydroxybutyric Acid; Cardiomyopathies; Disease Progression; Heart Ventricles; Humans; Myocytes, Ca

2020
Successful treatment of severe cardiomyopathy in glycogen storage disease type III With D,L-3-hydroxybutyrate, ketogenic and high-protein diet.
    Pediatric research, 2011, Volume: 70, Issue:6

    Topics: 3-Hydroxybutyric Acid; Blood Glucose; Cardiomyopathies; Creatine Kinase; Diet, Ketogenic; Dietary Pr

2011