Page last updated: 2024-09-03

3,7,12-trihydroxycholestan-26-oic acid and Peroxisomal Disorders

3,7,12-trihydroxycholestan-26-oic acid has been researched along with Peroxisomal Disorders in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's1 (33.33)18.2507
2000's2 (66.67)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Denis, S; Seedorf, U; van Berkel, E; Wanders, RJ; Wirtz, KW; Wouters, F1
Jakobs, C; Johnson, DW; Schuit, RC; ten Brink, HJ1
Denis, S; Ferdinandusse, S; Overmars, H; Vreken, P; Wanders, RJ; Waterham, HR1

Other Studies

3 other study(ies) available for 3,7,12-trihydroxycholestan-26-oic acid and Peroxisomal Disorders

ArticleYear
Identification of the newly discovered 58 kDa peroxisomal thiolase SCPx as the main thiolase involved in both pristanic acid and trihydroxycholestanoic acid oxidation: implications for peroxisomal beta-oxidation disorders.
    Journal of inherited metabolic disease, 1998, Volume: 21, Issue:3

    Topics: Acetyl-CoA C-Acetyltransferase; Carrier Proteins; Cholestanols; Fatty Acids; Humans; Microbodies; Oxidation-Reduction; Peroxisomal Disorders

1998
Rapid and quantitative analysis of unconjugated C(27) bile acids in plasma and blood samples by tandem mass spectrometry.
    Journal of lipid research, 2001, Volume: 42, Issue:1

    Topics: Age Factors; Bile Acids and Salts; Child; Child, Preschool; Cholestanols; Deuterium; Fatty Acids; Humans; Infant; Infant, Newborn; Matched-Pair Analysis; Peroxisomal Disorders; Spectrometry, Mass, Electrospray Ionization

2001
Plasma analysis of di- and trihydroxycholestanoic acid diastereoisomers in peroxisomal alpha-methylacyl-CoA racemase deficiency.
    Journal of lipid research, 2001, Volume: 42, Issue:1

    Topics: Bile Acids and Salts; Child, Preschool; Cholestanols; Cholestasis, Intrahepatic; Diagnosis, Differential; Female; Humans; Infant; Male; Oxidation-Reduction; Peroxisomal Disorders; Peroxisomes; Racemases and Epimerases; Spectrometry, Mass, Electrospray Ionization; Stereoisomerism; Zellweger Syndrome

2001