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2-methylbutanoic acid and Amino Acid Metabolism Disorders, Inborn

2-methylbutanoic acid has been researched along with Amino Acid Metabolism Disorders, Inborn in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's1 (33.33)18.2507
2000's0 (0.00)29.6817
2010's1 (33.33)24.3611
2020's1 (33.33)2.80

Authors

AuthorsStudies
Armstrong, AJ; Collado, MS; Dillberger, JE; Figler, RA; Henke, BR; Hoang, SA; Johns, BA; Olson, MW; Pourtaheri, TD; Reardon, JE; Roper, TD; Taylor, JM; Wamhoff, BR1
Alvorcem, Lde M; Grings, M; Knebel, LA; Leipnitz, G; Tonin, AM; Wajner, M; Zanatta, Â1
Gibson, KM; Iden, P; Middleton, B; Robinson, BH; Sherwood, WG; Sweetman, L; Søvik, O1

Other Studies

3 other study(ies) available for 2-methylbutanoic acid and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Identification of 2,2-Dimethylbutanoic Acid (HST5040), a Clinical Development Candidate for the Treatment of Propionic Acidemia and Methylmalonic Acidemia.
    Journal of medicinal chemistry, 2021, 04-22, Volume: 64, Issue:8

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Animals; Area Under Curve; Butyrates; Cells, Cultured; Dogs; Drug Evaluation, Preclinical; Half-Life; Hepatocytes; Humans; Mice; Models, Biological; Propionic Acidemia; Rats; ROC Curve; Structure-Activity Relationship

2021
2-Methylbutyrylglycine induces lipid oxidative damage and decreases the antioxidant defenses in rat brain.
    Brain research, 2012, Oct-10, Volume: 1478

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Antioxidants; Butyrates; Cerebral Cortex; Glycine; Lipid Peroxidation; Male; Oxidative Stress; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances

2012
3-Oxothiolase activities and [14C]-2-methylbutanoic acid incorporation in cultured fibroblasts from 13 cases of suspected 3-oxothiolase deficiency.
    Pediatric research, 1990, Volume: 28, Issue:5

    Topics: Acetyl-CoA C-Acyltransferase; Amino Acid Metabolism, Inborn Errors; Butyrates; Cells, Cultured; Female; Fibroblasts; Humans; Infant; Isoleucine; Male; Skin

1990