2-methylbutanoic acid has been researched along with Amino Acid Metabolism Disorders, Inborn in 3 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 1 (33.33) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 1 (33.33) | 24.3611 |
2020's | 1 (33.33) | 2.80 |
Authors | Studies |
---|---|
Armstrong, AJ; Collado, MS; Dillberger, JE; Figler, RA; Henke, BR; Hoang, SA; Johns, BA; Olson, MW; Pourtaheri, TD; Reardon, JE; Roper, TD; Taylor, JM; Wamhoff, BR | 1 |
Alvorcem, Lde M; Grings, M; Knebel, LA; Leipnitz, G; Tonin, AM; Wajner, M; Zanatta, Â | 1 |
Gibson, KM; Iden, P; Middleton, B; Robinson, BH; Sherwood, WG; Sweetman, L; Søvik, O | 1 |
3 other study(ies) available for 2-methylbutanoic acid and Amino Acid Metabolism Disorders, Inborn
Article | Year |
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Identification of 2,2-Dimethylbutanoic Acid (HST5040), a Clinical Development Candidate for the Treatment of Propionic Acidemia and Methylmalonic Acidemia.
Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Animals; Area Under Curve; Butyrates; Cells, Cultured; Dogs; Drug Evaluation, Preclinical; Half-Life; Hepatocytes; Humans; Mice; Models, Biological; Propionic Acidemia; Rats; ROC Curve; Structure-Activity Relationship | 2021 |
2-Methylbutyrylglycine induces lipid oxidative damage and decreases the antioxidant defenses in rat brain.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Antioxidants; Butyrates; Cerebral Cortex; Glycine; Lipid Peroxidation; Male; Oxidative Stress; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances | 2012 |
3-Oxothiolase activities and [14C]-2-methylbutanoic acid incorporation in cultured fibroblasts from 13 cases of suspected 3-oxothiolase deficiency.
Topics: Acetyl-CoA C-Acyltransferase; Amino Acid Metabolism, Inborn Errors; Butyrates; Cells, Cultured; Female; Fibroblasts; Humans; Infant; Isoleucine; Male; Skin | 1990 |