2-methyl-3-oxovaleric acid has been researched along with Amino Acid Metabolism Disorders, Inborn in 3 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 3 (100.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
DelValle, JA; García, MJ; Jiménez, A; Merinero, B; Neustadt, G; Omeñaca, F; Quero, J; Ugarte, M | 1 |
Junker, A; Lehnert, W | 1 |
Böhm, N; Lehnert, W; Niederhoff, H; Schuchmann, L; Urbánek, R | 1 |
3 other study(ies) available for 2-methyl-3-oxovaleric acid and Amino Acid Metabolism Disorders, Inborn
Article | Year |
---|---|
Dietary treatment and biochemical studies on a neonatal case of propionyl-CoA carboxylase deficiency.
Topics: 3-Hydroxybutyric Acid; Amino Acid Metabolism, Inborn Errors; Amino Acids; Carboxy-Lyases; Citrates; Female; Fibroblasts; Food, Formulated; Humans; Hydroxybutyrates; Infant, Newborn; Lactates; Lactic Acid; Methylmalonyl-CoA Decarboxylase; Pentanoic Acids; Propionates | 1982 |
[2-Methyl-3-oxovaleric acid: a characteristic metabolite in propionic acidemia].
Topics: Amino Acid Metabolism, Inborn Errors; Citrates; Female; Humans; Keto Acids; Pentanoic Acids; Propionates; Valerates | 1980 |
Excretion of 2-methyl-3-oxovaleric acid in propionic acidemia.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Autopsy; Female; Humans; Hypothermia; Infant, Newborn; Keto Acids; Liver; Muscle Hypotonia; Pentanoic Acids; Propionates; Vomiting | 1978 |