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2-methyl-3-oxovaleric acid and Amino Acid Metabolism Disorders, Inborn

2-methyl-3-oxovaleric acid has been researched along with Amino Acid Metabolism Disorders, Inborn in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19903 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
DelValle, JA; García, MJ; Jiménez, A; Merinero, B; Neustadt, G; Omeñaca, F; Quero, J; Ugarte, M1
Junker, A; Lehnert, W1
Böhm, N; Lehnert, W; Niederhoff, H; Schuchmann, L; Urbánek, R1

Other Studies

3 other study(ies) available for 2-methyl-3-oxovaleric acid and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Dietary treatment and biochemical studies on a neonatal case of propionyl-CoA carboxylase deficiency.
    Journal of inherited metabolic disease, 1982, Volume: 5, Issue:2

    Topics: 3-Hydroxybutyric Acid; Amino Acid Metabolism, Inborn Errors; Amino Acids; Carboxy-Lyases; Citrates; Female; Fibroblasts; Food, Formulated; Humans; Hydroxybutyrates; Infant, Newborn; Lactates; Lactic Acid; Methylmalonyl-CoA Decarboxylase; Pentanoic Acids; Propionates

1982
[2-Methyl-3-oxovaleric acid: a characteristic metabolite in propionic acidemia].
    Clinica chimica acta; international journal of clinical chemistry, 1980, May-21, Volume: 104, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Citrates; Female; Humans; Keto Acids; Pentanoic Acids; Propionates; Valerates

1980
Excretion of 2-methyl-3-oxovaleric acid in propionic acidemia.
    European journal of pediatrics, 1978, Jul-03, Volume: 128, Issue:3

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Autopsy; Female; Humans; Hypothermia; Infant, Newborn; Keto Acids; Liver; Muscle Hypotonia; Pentanoic Acids; Propionates; Vomiting

1978