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2-keto-4-methylvalerate and Metabolism, Inborn Errors

2-keto-4-methylvalerate has been researched along with Metabolism, Inborn Errors in 1 studies

alpha-ketoisocaproic acid: RN given refers to parent cpd
4-methyl-2-oxopentanoate : A 2-oxo monocarboxylic acid anion that is the conjugate base of 4-methyl-2-oxopentanoic acid.
4-methyl-2-oxopentanoic acid : A 2-oxo monocarboxylic acid that is pentanoic acid (valeric acid) substituted with a keto group at C-2 and a methyl group at C-4. A metabolite that has been found to accumulate in maple syrup urine disease.

Metabolism, Inborn Errors: Errors in metabolic processes resulting from inborn genetic mutations that are inherited or acquired in utero.

Research

Studies (1)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's1 (100.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Hagen, T1
Korson, MS1
Sakamoto, M1
Evans, JE1

Other Studies

1 other study available for 2-keto-4-methylvalerate and Metabolism, Inborn Errors

ArticleYear
A GC/MS/MS screening method for multiple organic acidemias from urine specimens.
    Clinica chimica acta; international journal of clinical chemistry, 1999, Volume: 283, Issue:1-2

    Topics: Acids; Adipates; Automation; Biomarkers; Caprylates; Decanoic Acids; Dicarboxylic Acids; Fumarates;

1999