2-keto-4-methylvalerate has been researched along with Friedreich Disease in 1 studies
alpha-ketoisocaproic acid: RN given refers to parent cpd
4-methyl-2-oxopentanoate : A 2-oxo monocarboxylic acid anion that is the conjugate base of 4-methyl-2-oxopentanoic acid.
4-methyl-2-oxopentanoic acid : A 2-oxo monocarboxylic acid that is pentanoic acid (valeric acid) substituted with a keto group at C-2 and a methyl group at C-4. A metabolite that has been found to accumulate in maple syrup urine disease.
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 1 (100.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Bertrand, MJ | 1 |
| Bouchard, R | 1 |
| Gauthier, GL | 1 |
| Bouchard, JP | 1 |
| Barbeau, A | 1 |
1 other study available for 2-keto-4-methylvalerate and Friedreich Disease
| Article | Year |
|---|---|
Quantitative metabolic profiling of alpha-keto acids in Friedreich's ataxia.
Topics: Adult; Friedreich Ataxia; Humans; Keto Acids; Ketoglutaric Acids; Phenylpyruvic Acids; Pyruvates; Py | 1982 |