2-hydroxy-3-methylvaleric acid has been researched along with Maple Syrup Urine Disease in 2 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 1 (50.00) | 18.7374 |
| 1990's | 1 (50.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Jakobs, C; Nyhan, WL; Sweetman, L | 1 |
| Mamer, OA; Reimer, ML | 1 |
2 other study(ies) available for 2-hydroxy-3-methylvaleric acid and Maple Syrup Urine Disease
| Article | Year |
|---|---|
Hydroxy acid metabolites of branched-chain amino acids in amniotic fluid.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Amniotic Fluid; Caproates; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydroxy Acids; Hydroxybutyrates; Maple Syrup Urine Disease; Methylmalonic Acid; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Valerates | 1984 |
On the mechanisms of the formation of L-alloisoleucine and the 2-hydroxy-3-methylvaleric acid stereoisomers from L-isoleucine in maple syrup urine disease patients and in normal humans.
Topics: Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Humans; Isoleucine; Magnetic Resonance Spectroscopy; Maple Syrup Urine Disease; Pentanoic Acids; Stereoisomerism | 1992 |