Page last updated: 2024-08-17

2-aminoisobutyric acid and BH4 Deficiency

2-aminoisobutyric acid has been researched along with BH4 Deficiency in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's2 (100.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Arning, E; Bottiglieri, T; Gibson, KM; Vogel, KR; Wasek, BL2

Other Studies

2 other study(ies) available for 2-aminoisobutyric acid and BH4 Deficiency

ArticleYear
Characterization of 2-(methylamino)alkanoic acid capacity to restrict blood-brain phenylalanine transport in Pah enu2 mice: preliminary findings.
    Molecular genetics and metabolism, 2013, Volume: 110 Suppl

    Topics: Acids, Acyclic; Aminoisobutyric Acids; Animals; Blood-Brain Barrier; Brain; Disease Models, Animal; Humans; Isoleucine; Large Neutral Amino Acid-Transporter 1; Methylation; Mice; Mice, Transgenic; Molecular Targeted Therapy; Organ Specificity; Phenylalanine; Phenylketonurias; Protein Conformation; Protein Folding; Valine

2013
Non-physiological amino acid (NPAA) therapy targeting brain phenylalanine reduction: pilot studies in PAHENU2 mice.
    Journal of inherited metabolic disease, 2013, Volume: 36, Issue:3

    Topics: Amino Acids; Amino Acids, Cyclic; Aminoisobutyric Acids; Animals; Brain; Down-Regulation; Drug Evaluation, Preclinical; Female; Male; Mice; Mice, Inbred C57BL; Mice, Transgenic; Models, Biological; Molecular Targeted Therapy; Norleucine; Phenylalanine; Phenylketonurias; Pilot Projects

2013