2-aminoisobutyric acid has been researched along with BH4 Deficiency in 2 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 2 (100.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Arning, E; Bottiglieri, T; Gibson, KM; Vogel, KR; Wasek, BL | 2 |
2 other study(ies) available for 2-aminoisobutyric acid and BH4 Deficiency
Article | Year |
---|---|
Characterization of 2-(methylamino)alkanoic acid capacity to restrict blood-brain phenylalanine transport in Pah enu2 mice: preliminary findings.
Topics: Acids, Acyclic; Aminoisobutyric Acids; Animals; Blood-Brain Barrier; Brain; Disease Models, Animal; Humans; Isoleucine; Large Neutral Amino Acid-Transporter 1; Methylation; Mice; Mice, Transgenic; Molecular Targeted Therapy; Organ Specificity; Phenylalanine; Phenylketonurias; Protein Conformation; Protein Folding; Valine | 2013 |
Non-physiological amino acid (NPAA) therapy targeting brain phenylalanine reduction: pilot studies in PAHENU2 mice.
Topics: Amino Acids; Amino Acids, Cyclic; Aminoisobutyric Acids; Animals; Brain; Down-Regulation; Drug Evaluation, Preclinical; Female; Male; Mice; Mice, Inbred C57BL; Mice, Transgenic; Models, Biological; Molecular Targeted Therapy; Norleucine; Phenylalanine; Phenylketonurias; Pilot Projects | 2013 |