2-aminoadipic acid and Cerebro-Hepato-Renal Syndrome studies

2-Aminoadipic Acid: A metabolite in the principal biochemical pathway of lysine. It antagonizes neuroexcitatory activity modulated by the glutamate receptor, N-METHYL-D-ASPARTATE; (NMDA).
2-aminoadipic acid : An alpha-amino acid that is adipic acid bearing a single amino substituent at position 2. An intermediate in the formation of lysine.

Research Excerpts

Excerpt	Relevance	Reference
"L-Pipecolic acid, a cyclic imino acid produced during the degradation of lysine, accumulates in body fluids of infants with the generalized peroxisomal disorders, including Zellweger syndrome, neonatal adrenoleukodystrophy, and infantile Refsum disease."	7.67	Peroxisomal L-pipecolic acid oxidation is deficient in liver from Zellweger syndrome patients. ( Danks, DM; Mihalik, SJ; Moser, HW; Poulos, A; Rhead, WJ; Watkins, PA, 1989)
"L-Pipecolic acid, a cyclic imino acid produced during the degradation of lysine, accumulates in body fluids of infants with the generalized peroxisomal disorders, including Zellweger syndrome, neonatal adrenoleukodystrophy, and infantile Refsum disease."	3.67	Peroxisomal L-pipecolic acid oxidation is deficient in liver from Zellweger syndrome patients. ( Danks, DM; Mihalik, SJ; Moser, HW; Poulos, A; Rhead, WJ; Watkins, PA, 1989)

Research

Studies (1)

Authors

Other Studies

1 other study available for 2-aminoadipic acid and Cerebro-Hepato-Renal Syndrome

Timeframe	Studies, this research(%)	All Research%
pre-1990	1 (100.00)	18.7374
1990's	0 (0.00)	18.2507
2000's	0 (0.00)	29.6817
2010's	0 (0.00)	24.3611
2020's	0 (0.00)	2.80

Authors	Studies
Mihalik, SJ	1
Moser, HW	1
Watkins, PA	1
Danks, DM	1
Poulos, A	1
Rhead, WJ	1