2-aminoadipic acid has been researched along with Acquired Metabolic Diseases, Brain in 3 studies
2-Aminoadipic Acid: A metabolite in the principal biochemical pathway of lysine. It antagonizes neuroexcitatory activity modulated by the glutamate receptor, N-METHYL-D-ASPARTATE; (NMDA).
2-aminoadipic acid : An alpha-amino acid that is adipic acid bearing a single amino substituent at position 2. An intermediate in the formation of lysine.
Excerpt | Relevance | Reference |
---|---|---|
" Antiquitin deficiency is the most common form of pyridoxine-dependent epilepsy." | 5.05 | Inherited Disorders of Lysine Metabolism: A Review. ( Bouchereau, J; Schiff, M, 2020) |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 1 (33.33) | 24.3611 |
2020's | 2 (66.67) | 2.80 |
Authors | Studies |
---|---|
Leandro, J | 1 |
Dodatko, T | 1 |
DeVita, RJ | 1 |
Chen, H | 1 |
Stauffer, B | 1 |
Yu, C | 1 |
Houten, SM | 1 |
Bouchereau, J | 1 |
Schiff, M | 1 |
Sauer, SW | 1 |
Opp, S | 1 |
Hoffmann, GF | 1 |
Koeller, DM | 1 |
Okun, JG | 1 |
Kölker, S | 1 |
1 review available for 2-aminoadipic acid and Acquired Metabolic Diseases, Brain
Article | Year |
---|---|
Inherited Disorders of Lysine Metabolism: A Review.
Topics: 2-Aminoadipic Acid; Aldehyde Dehydrogenase; Amino Acid Metabolism, Inborn Errors; Arginine; Brain; B | 2020 |
2 other studies available for 2-aminoadipic acid and Acquired Metabolic Diseases, Brain
Article | Year |
---|---|
Deletion of 2-aminoadipic semialdehyde synthase limits metabolite accumulation in cell and mouse models for glutaric aciduria type 1.
Topics: 2-Aminoadipic Acid; Amino Acid Metabolism, Inborn Errors; Animals; Brain; Brain Diseases, Metabolic; | 2020 |
Therapeutic modulation of cerebral L-lysine metabolism in a mouse model for glutaric aciduria type I.
Topics: 2-Aminoadipate Transaminase; 2-Aminoadipic Acid; Amino Acid Metabolism, Inborn Errors; Analysis of V | 2011 |