Page last updated: 2024-10-17

2-aminoadipic acid and Acquired Metabolic Diseases, Brain

2-aminoadipic acid has been researched along with Acquired Metabolic Diseases, Brain in 3 studies

2-Aminoadipic Acid: A metabolite in the principal biochemical pathway of lysine. It antagonizes neuroexcitatory activity modulated by the glutamate receptor, N-METHYL-D-ASPARTATE; (NMDA).
2-aminoadipic acid : An alpha-amino acid that is adipic acid bearing a single amino substituent at position 2. An intermediate in the formation of lysine.

Research Excerpts

ExcerptRelevanceReference
" Antiquitin deficiency is the most common form of pyridoxine-dependent epilepsy."5.05Inherited Disorders of Lysine Metabolism: A Review. ( Bouchereau, J; Schiff, M, 2020)

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (33.33)24.3611
2020's2 (66.67)2.80

Authors

AuthorsStudies
Leandro, J1
Dodatko, T1
DeVita, RJ1
Chen, H1
Stauffer, B1
Yu, C1
Houten, SM1
Bouchereau, J1
Schiff, M1
Sauer, SW1
Opp, S1
Hoffmann, GF1
Koeller, DM1
Okun, JG1
Kölker, S1

Reviews

1 review available for 2-aminoadipic acid and Acquired Metabolic Diseases, Brain

ArticleYear
Inherited Disorders of Lysine Metabolism: A Review.
    The Journal of nutrition, 2020, 10-01, Volume: 150, Issue:Suppl 1

    Topics: 2-Aminoadipic Acid; Aldehyde Dehydrogenase; Amino Acid Metabolism, Inborn Errors; Arginine; Brain; B

2020

Other Studies

2 other studies available for 2-aminoadipic acid and Acquired Metabolic Diseases, Brain

ArticleYear
Deletion of 2-aminoadipic semialdehyde synthase limits metabolite accumulation in cell and mouse models for glutaric aciduria type 1.
    Journal of inherited metabolic disease, 2020, Volume: 43, Issue:6

    Topics: 2-Aminoadipic Acid; Amino Acid Metabolism, Inborn Errors; Animals; Brain; Brain Diseases, Metabolic;

2020
Therapeutic modulation of cerebral L-lysine metabolism in a mouse model for glutaric aciduria type I.
    Brain : a journal of neurology, 2011, Volume: 134, Issue:Pt 1

    Topics: 2-Aminoadipate Transaminase; 2-Aminoadipic Acid; Amino Acid Metabolism, Inborn Errors; Analysis of V

2011