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2,3-diphosphoglycerate and Inborn Errors of Metabolism

2,3-diphosphoglycerate has been researched along with Inborn Errors of Metabolism in 2 studies

2,3-Diphosphoglycerate: A highly anionic organic phosphate which is present in human red blood cells at about the same molar ratio as hemoglobin. It binds to deoxyhemoglobin but not the oxygenated form, therefore diminishing the oxygen affinity of hemoglobin. This is essential in enabling hemoglobin to unload oxygen in tissue capillaries. It is also an intermediate in the conversion of 3-phosphoglycerate to 2-phosphoglycerate by phosphoglycerate mutase (EC 5.4.2.1). (From Stryer Biochemistry, 4th ed, p160; Enzyme Nomenclature, 1992, p508)
2,3-bisphosphoglyceric acid : A bisphosphoglyceric acid that is glyceric acid carrying two phospho substituents at positions 2 and 3.

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19901 (50.00)18.7374
1990's1 (50.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Staal, GE1
Jansen, G1
Roos, D1
Lakomek, M1
Neubauer, B1
von der Lühe, A1
Hoch, G1
Winkler, H1
Schröter, W1

Other Studies

2 other studies available for 2,3-diphosphoglycerate and Inborn Errors of Metabolism

ArticleYear
Pyruvate kinase and the "high ATP syndrome".
    The Journal of clinical investigation, 1984, Volume: 74, Issue:1

    Topics: 2,3-Diphosphoglycerate; Adenosine Triphosphate; Diphosphoglyceric Acids; Erythrocyte Aging; Erythroc

1984
Erythrocyte pyruvate kinase deficiency: relations of residual enzyme activity, altered regulation of defective enzymes and concentrations of high-energy phosphates with the severity of clinical manifestation.
    European journal of haematology, 1992, Volume: 49, Issue:2

    Topics: 2,3-Diphosphoglycerate; Adenosine Diphosphate; Adenosine Triphosphate; Anemia, Hemolytic, Congenital

1992