Page last updated: 2024-08-23

1-deoxynojirimycin and Nervous System Diseases

1-deoxynojirimycin has been researched along with Nervous System Diseases in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's3 (42.86)29.6817
2010's3 (42.86)24.3611
2020's1 (14.29)2.80

Authors

AuthorsStudies
Brassier, A; Broué, P; Cances, C; Chabrol, B; Dahmani-Rabehi, B; Eyer, D; Freihuber, C; Héron, B; Labarthe, F; Latour, P; Levade, T; Pichard, S; Sevin, C; Vanier, MT1
Bembi, B; Hollak, CE; Hughes, D; Schwierin, B; van Schaik, IN1
Coll, MJ; de la Barca, OB; Domingo, R; Fumero, LM; Gaspar, A; Macías-Vidal, J; O'Callaghan, M; Peñas, JJ; Pérez, AV; Perez-Poyato, MS; Pineda, M; Pocovi, M; Portal, LR; Roldán, S; Silva, MT; Temudo, T; Vilaseca, MA1
Chien, YH; Huang, AC; Hwu, WL; Lee, NC; Peng, SF; Su, SC; Tsai, LK; Tseng, CC; Yang, CC1
Aryani, O; Ashrafi, MR; Ghofrani, M; Houshmand, M; Karimzadeh, P; Rahmanifar, A; Rezayi, A; Salehpour, S; Shafeghati, Y; Shiva, F; Shoar, BN; Taghdiri, MM; Tavasoli, A; Tonekaboni, SH; Zaman, T1
Groot-Loonen, JJ; Hoogerbrugge, PM; Jacobs, JF; Wevers, RA; Willemsen, MA1
Alfonso, P; Capablo, JL; de Cabezón, AS; Franco, R; Giraldo, P; Pocovi, M1

Other Studies

7 other study(ies) available for 1-deoxynojirimycin and Nervous System Diseases

ArticleYear
Effects of miglustat therapy on neurological disorder and survival in early-infantile Niemann-Pick disease type C: a national French retrospective study.
    Orphanet journal of rare diseases, 2023, 07-21, Volume: 18, Issue:1

    Topics: 1-Deoxynojirimycin; Adolescent; Adult; Child; Child, Preschool; Female; Humans; Infant; Nervous System Diseases; Niemann-Pick Disease, Type C; Pregnancy; Retrospective Studies; Young Adult

2023
Miglustat (Zavesca) in type 1 Gaucher disease: 5-year results of a post-authorisation safety surveillance programme.
    Pharmacoepidemiology and drug safety, 2009, Volume: 18, Issue:9

    Topics: 1-Deoxynojirimycin; Adolescent; Adult; Aged; Child; Child, Preschool; Enzyme Inhibitors; Europe; Female; Gaucher Disease; Humans; Male; Middle Aged; Nervous System Diseases; Retrospective Studies; Severity of Illness Index; Young Adult

2009
Clinical experience with miglustat therapy in pediatric patients with Niemann-Pick disease type C: a case series.
    Molecular genetics and metabolism, 2010, Volume: 99, Issue:4

    Topics: 1-Deoxynojirimycin; Adolescent; Adult; Age Factors; Child; Child, Preschool; Cognition; Female; Humans; Male; Nervous System Diseases; Niemann-Pick Disease, Type C

2010
Long-term efficacy of miglustat in paediatric patients with Niemann-Pick disease type C.
    Journal of inherited metabolic disease, 2013, Volume: 36, Issue:1

    Topics: 1-Deoxynojirimycin; Child; Child, Preschool; Cognition; Deglutition; Disease Progression; Drug Administration Schedule; Female; Humans; Male; Nervous System Diseases; Niemann-Pick Disease, Type C; Time; Treatment Outcome

2013
Effects of miglustat on stabilization of neurological disorder in niemann-pick disease type C: Iranian pediatric case series.
    Journal of child neurology, 2013, Volume: 28, Issue:12

    Topics: 1-Deoxynojirimycin; Adolescent; Child; Child, Preschool; Enzyme Inhibitors; Female; Humans; Infant; Iran; Male; Nervous System Diseases; Niemann-Pick Disease, Type C; Retrospective Studies; Treatment Outcome; Young Adult

2013
Allogeneic BMT followed by substrate reduction therapy in a child with subacute Tay-Sachs disease.
    Bone marrow transplantation, 2005, Volume: 36, Issue:10

    Topics: 1-Deoxynojirimycin; Bone Marrow Transplantation; Child; Female; Humans; Nervous System Diseases; Tay-Sachs Disease; Transplantation, Homologous

2005
Neurologic improvement in a type 3 Gaucher disease patient treated with imiglucerase/miglustat combination.
    Epilepsia, 2007, Volume: 48, Issue:7

    Topics: 1-Deoxynojirimycin; Adult; Comorbidity; Disease Progression; Drug Administration Schedule; Drug Therapy, Combination; Dystonia; Electroencephalography; Enzyme Inhibitors; Epilepsies, Myoclonic; Gaucher Disease; Glucosylceramidase; Humans; Male; Nervous System Diseases; Recombinant Proteins; Syndrome; Treatment Outcome

2007