Page last updated: 2024-08-23

1-deoxynojirimycin and Nerve Degeneration

1-deoxynojirimycin has been researched along with Nerve Degeneration in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's2 (66.67)29.6817
2010's1 (33.33)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Hawlitschka, A; Hovakimyan, M; Lukas, J; Maass, F; Petersen, J; Rolfs, A; Schmitt, O; Witt, M; Wree, A1
Addobbati, R; Barone, R; Bembi, B; Butters, T; Cariati, R; Ciana, G; Fernandez-Guillen, L; Grasso, D; Guerci, VI; Marchetti, F; Pittis, MG1
Baek, RC; Kasperzyk, JL; Platt, FM; Seyfried, TN1

Other Studies

3 other study(ies) available for 1-deoxynojirimycin and Nerve Degeneration

ArticleYear
Reduced cerebellar neurodegeneration after combined therapy with cyclodextrin/allopregnanolone and miglustat in NPC1: a mouse model of Niemann-Pick type C1 disease.
    Journal of neuroscience research, 2015, Volume: 93, Issue:3

    Topics: 1-Deoxynojirimycin; Animals; Cell Count; Cerebellum; Cyclodextrins; Disease Models, Animal; Disease Progression; Drug Therapy, Combination; Enzyme Inhibitors; Mice; Nerve Degeneration; Neurons; Niemann-Pick Disease, Type C; Pregnanolone

2015
Substrate reduction therapy in the infantile form of Tay-Sachs disease.
    Neurology, 2006, Jan-24, Volume: 66, Issue:2

    Topics: 1-Deoxynojirimycin; Craniofacial Abnormalities; Electroencephalography; Evoked Potentials, Auditory, Brain Stem; Evoked Potentials, Visual; Female; Humans; Infant; Nerve Degeneration; Tay-Sachs Disease

2006
N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal Sandhoff disease mice.
    Neurochemistry international, 2008, Volume: 52, Issue:6

    Topics: 1-Deoxynojirimycin; Animals; Animals, Newborn; beta-Hexosaminidase alpha Chain; Brain; Brain Chemistry; Disease Models, Animal; Down-Regulation; G(M2) Ganglioside; Gangliosides; Glycosphingolipids; Mice; Mice, Knockout; Nerve Degeneration; Neuraminidase; Sandhoff Disease; Treatment Outcome

2008