Page last updated: 2024-09-02

valerates and methylmalonic acid

valerates has been researched along with methylmalonic acid in 11 studies

Compound Research Comparison

Studies
(valerates)
Trials
(valerates)
Recent Studies (post-2010)
(valerates)
Studies
(methylmalonic acid)
Trials
(methylmalonic acid)
Recent Studies (post-2010) (methylmalonic acid)
2,2512944571,72290453

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19909 (81.82)18.7374
1990's1 (9.09)18.2507
2000's1 (9.09)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Mahoney, MJ1
Fennessey, PV; Goodman, SI; Jellum, E; Mace, JW; McCabe, ER; Miles, BS1
Amédée-Manesme, O; Besson-Leaud, M; Charpentier, C; Checouri, A; Coude, FX; Ferre, P; Lavaud, J; Leraillez, J; Mselati, JC; Ogier, H; Saudubray, JM1
Porath, U; Schreier, K1
Piccardo, M; Tassara, F; Vico, L1
Bachmann, C; Berüter, J; Colombo, JP1
Barness, LA1
Nakamura, E; Rosenberg, LE; Tanaka, K1
Buchanan, DN; Muenzer, J; Thoene, JG1
Jakobs, C; Nyhan, WL; Sweetman, L1
Carrozzo, R; Dionisi-Vici, C; Joensen, F; Kluijtmans, LA; Morava, E; Santer, R; Steuerwald, U; Wevers, RA1

Reviews

3 review(s) available for valerates and methylmalonic acid

ArticleYear
Organic acidemias.
    Clinics in perinatology, 1976, Volume: 3, Issue:1

    Topics: Acidosis, Renal Tubular; Acids; Amino Acid Metabolism, Inborn Errors; Amino Acids, Essential; Ammonia; Child; Diagnosis, Differential; Glutarates; Humans; Hydrogen-Ion Concentration; Infant; Infant, Newborn; Leucine; Ligases; Methylmalonic Acid; Prenatal Diagnosis; Propionates; Pyruvates; Urea; Valerates

1976
[Congenital metabolic acidosis in the postnatal period].
    Deutsche medizinische Wochenschrift (1946), 1978, Jun-02, Volume: 103, Issue:22

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine

1978
[Some clinical and therapeutic aspects of organico-acidemia and organico-aciduria].
    La Clinica terapeutica, 1977, Apr-15, Volume: 81, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Butyrates; Humans; Maple Syrup Urine Disease; Metabolic Diseases; Methylmalonic Acid; Propionates; Renal Aminoacidurias; Valerates

1977

Other Studies

8 other study(ies) available for valerates and methylmalonic acid

ArticleYear
Methylmalonic/beta-hydroxy-n-valeric aciduria due to methylmalonyl-CoA mutase deficiency.
    Clinica chimica acta; international journal of clinical chemistry, 1978, Aug-01, Volume: 87, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Humans; Hydroxy Acids; Infant, Newborn; Infant, Newborn, Diseases; Isomerases; Liver; Male; Malonates; Malonyl Coenzyme A; Mass Spectrometry; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Pentanoic Acids; Valerates

1978
[Emergency treatment of inborn amino errors of amino acid metabolism detected in the neonatal period].
    Archives francaises de pediatrie, 1979, Volume: 36, Issue:10

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Diuretics, Osmotic; Emergencies; Enteral Nutrition; Exchange Transfusion, Whole Blood; Humans; Infant, Newborn; Leucine; Methylmalonic Acid; Peritoneal Dialysis; Propionates; Valerates

1979
Short chain fatty acids in plasma and brain: quantitative determination by gas chromatography.
    Clinica chimica acta; international journal of clinical chemistry, 1979, Mar-01, Volume: 92, Issue:2

    Topics: Adult; Brain Chemistry; Butyrates; Chromatography, Gas; Evaluation Studies as Topic; Fatty Acids; Female; Humans; Male; Methods; Methylmalonic Acid; Middle Aged; Propionates; Valerates

1979
Organic acidosis in infants.
    South African medical journal = Suid-Afrikaanse tydskrif vir geneeskunde, 1977, May-14, Volume: 51, Issue:20

    Topics: Acidosis; Adult; Child; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Lactates; Methylmalonic Acid; Propionates; Pyruvates; Valerates

1977
Microdetermination of methylmalonic acid and other short chain dicarboxylic acids by gas chromatography: use in prenatal diagnosis of methylmalonic acidemia and in studies of isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1976, Apr-15, Volume: 68, Issue:2

    Topics: Adult; Child; Chromatography, Gas; Colorimetry; Dicarboxylic Acids; Evaluation Studies as Topic; Female; Fetus; Heterozygote; Humans; Infant, Newborn; Malonates; Metabolism, Inborn Errors; Methylmalonic Acid; Microchemistry; Pregnancy; Prenatal Diagnosis; Succinates; Valerates

1976
Positive-ion thermospray liquid chromatography-mass spectrometry: detection of organic acidurias.
    Journal of chromatography, 1990, Dec-14, Volume: 534

    Topics: Argininosuccinic Acid; Carboxylic Acids; Chromatography, Thin Layer; Female; Humans; Infant; Infant, Newborn; Male; Mass Spectrometry; Meglutol; Metabolism, Inborn Errors; Methylmalonic Acid; Sensitivity and Specificity; Valerates

1990
Hydroxy acid metabolites of branched-chain amino acids in amniotic fluid.
    Clinica chimica acta; international journal of clinical chemistry, 1984, Jul-16, Volume: 140, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Amniotic Fluid; Caproates; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydroxy Acids; Hydroxybutyrates; Maple Syrup Urine Disease; Methylmalonic Acid; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Valerates

1984
Dystonia and deafness due to SUCLA2 defect; Clinical course and biochemical markers in 16 children.
    Mitochondrion, 2009, Volume: 9, Issue:6

    Topics: Adolescent; Biomarkers; Child; Child, Preschool; Dystonia; Hearing Loss, Sensorineural; Homozygote; Humans; Infant; Lactates; Male; Metabolic Networks and Pathways; Methylmalonic Acid; Models, Biological; Succinate-CoA Ligases; Valerates; Young Adult

2009