Page last updated: 2024-09-02

valerates and leucine

valerates has been researched along with leucine in 177 studies

Compound Research Comparison

Studies
(valerates)
Trials
(valerates)
Recent Studies (post-2010)
(valerates)
Studies
(leucine)
Trials
(leucine)
Recent Studies (post-2010) (leucine)
2,25129445728,5157444,178

Research

Studies (177)

TimeframeStudies, this research(%)All Research%
pre-1990120 (67.80)18.7374
1990's11 (6.21)18.2507
2000's6 (3.39)29.6817
2010's34 (19.21)24.3611
2020's6 (3.39)2.80

Authors

AuthorsStudies
Mahoney, MJ1
Blaskovics, ME; Donnell, GN; Ng, WG1
Amédée-Manesme, O; Besson-Leaud, M; Charpentier, C; Checouri, A; Coude, FX; Ferre, P; Lavaud, J; Leraillez, J; Mselati, JC; Ogier, H; Saudubray, JM1
Landaas, S1
Porath, U; Schreier, K1
Blum, JJ; Borowitz, M; Liang, T; Raugi, G1
Lehnert, W; Niederhoff, H; Schenck, W1
Cohn, RM; Puschak, R; Rothman, R; Segal, S; Yudkoff, M1
Owen, OE; Patel, MS1
Elsden, SR; Hilton, MG1
Hidaka, T1
Goodman, HM2
Di Campo-Rougerie, C; Mahmoud, F; Ramahandridona, G; Vague, P1
Doolittle, WF; Singer, RA1
Dogen, M; Higashi, T; Kawamata, F1
Chawla, RK; Khatra, BS; Rudman, D; Wadsworth, AD1
Mandell, R; Shih, VE; Tanaka, K2
Charpentier, C; Depondt, E; Herouin, C; Pousset, JL; Saudubray, JM; Sorin, M1
Oxender, DL; Quay, SC; Tsuyumu, S; Umbarger, HE1
Geier, MR; Kamerow, HN; LaPolla, RJ; Merril, CR; Trigg, ME1
Bogair, N; Charles, R; Gil-Av, E; Legum, C; Spirer, Z; Swirsky-Fein, S; Zakut, V1
Higashi, T; Kawamata, F; Sakurai, T1
Blailock, TT; Blomquist, GJ1
Mock, DM; Mock, NI1
Chalmers, RA; Halliday, D; Thompson, GN1
Nissen, S; Van Koevering, M1
Inoue, Y; Iwasaki, R; Kuhara, T; Matsumoto, I; Morimoto, S; Yu, WM1
Nissen, S; Van Koevering, M; Webb, D1
Beaudet, AL; Craigen, WJ; Gibson, KM; Johnston, K; Kamali, V; Lee, CF; Powell, BR; Schwartz, R; Tsai, MY; Tuchman, M1
Tanaka, K1
Dembure, P; Elsas, L; Madsen, K; Naglak, M; Salvo, R1
Elsas, LJ; Naglak, M1
Flakoll, PJ; Kuhlman, G; Nissen, S; Roth, JA; Vandehaar, MJ1
Hyman, D; Ikeda, Y; Matsubara, Y; Tanaka, K1
Herbertz, L; Langer, K; Schauder, P1
Ruchim, MA; Zarling, EJ1
Pollitt, RJ1
Hyman, DB; Tanaka, K1
Inoue, F; Maltby, DA; Millington, DS; Roe, CR1
Draffan, GH; Gompertz, D; Hull, D; Watts, JL1
Erickson, AM; Kurtz, DJ; Levy, HL; Lott, IT1
Conrad, RS; Massey, LK; Sokatch, JR1
Christians, J; Hasselblatt, A; Panten, U; Poser, W; von Kriegstein, E1
Adair, R; Davidoff, RA1
Callaghan, P; Newman, CG; Wilson, BD; Young, L1
Fujii, Y; Kodama, H; Mizuhara, S; Tanaka, K1
Yamaguchi, T1
Misono, H; Mori, K; Sakato, H; Soda, K1
Markau, K; Steinhübel, I1
Markau, K1
Kohlhaw, GB; Ryan, ED; Tracy, JW1
Berg, CP; Cruz, LJ; Glesne, LB1
Borison, HL; McCarthy, LE; Pendleton, J1
Kline, EL1
Chibata, I; Kisumi, M; Komatsubara, S1
Amzallag, A; Middleton, RB; Somers, JM1
Kohlhaw, GB; Teng-Leary, E1
Kessler, DP; Yang, HL1
Calvo, JM; Friedberg, D; Jones, J; Mikulka, TW1
Kemper, J1
Gompertz, D1
McGilvray, D; Umbarger, HE1
Lönnberg, H; Nurmikko, V; Puukka, M1
Lönnberg, H; Mäntsälä, P; Nurmikko, V; Pajula, R; Puukka, M1
Ridge, B; Rydon, HN; Snell, CR1
Daron, HH1
Bartlett, K; Blair, D; Gompertz, D; Stern, CM1
Angielski, SA; Lysiak, W; Pieńkowska-Vogel, M; Szutowicz, A1
Engel, PC1
Kaplan, JG; McDonald, RA; Satyanarayana, T1
Gross, SR; Olshan, AR1
Calvo, JM; Stieglitz, BI1
Bensch, KG; Bissell, MG; Herman, MM1
Boatman, G; Kohlhaw, G1
Bartholomew, JC; Calvo, JM2
Kohlhaw, G; Leary, TR; Umbarger, HE1
Hildesheim, R; Kunesch, G; Polonsky, J1
Hill, F; Schlegel, HG1
Demny, TC; Pruess, DL; Scannell, JP; Weiss, F; Williams, T1
Pardee, AB; Willecke, K1
Isselbacher, KJ; Shih, V; Tanaka, K1
Prescott, JM; Wagner, FW; Wilkes, SH1
Erickson, AM; Levy, HL; Lott, IT1
Mangan, JL1
Eldjarn, L; Jellum, E; Pande, H; Stokke, O; Waaler, PE1
Malins, DC; Robisch, PA; Varanasi, U1
Goedde, HW; Langenbeck, U; Rüdiger, HW1
Böhme, R; Kohlhaw, G; Ulm, EH1
Achari, RG; Court, WE; Newcombe, F1
Kishimoto, Y; Kurtz, DJ; Levy, HL; Plotkin, W1
Lahoud, H; McManus, WR; Prichard, PK; Schofield, PJ1
Budd, MA; Efron, ML; Isselbacher, KJ; Tanaka, K1
Isselbacher, KJ; Miller, EM; Tanaka, K1
Burns, RO; Calvo, J; Margolin, P; Umbarger, HE1
Bussey, H1
Malins, DC; Varanasi, U1
Ormerod, JG; Sirevåg, R1
Jenkins, WT; Shakespeare, V; Taylor, RT1
Angielski, S; Lysiak, W; Stepiński, J1
Kaneda, T1
McFarlane, IG; Von Holt, C1
Drapanas, T; McMenamy, RH; Vang, J1
Allison, MJ; Bucklin, JA; Robinson, IM1
Orlova, IG; Shaposhnikov, VN1
Isselbacher, KJ; Tanaka, K1
Blanco, A; Domenech, CE1
Cann, HM; Gibson, KM; Greene, CL; Holm, J; Nyhan, WL; Robinson, BH; Sweetman, L1
Prieto, EC; Velazquez, A1
Beemer, FA; Bruinvis, L; Duran, M; Ketting, D; Tibosch, AS; Wadman, SK1
Jakobs, C; Nyhan, WL; Packman, S; Sweetman, L1
Goldstein, F; Norton, PM; Sansaricq, C; Snyderman, SE1
Hine, DG; Tanaka, K1
Hokland, B; Spydevold, O1
Duran, M; Houstková, H; Hyánek, J; Kozich, V; Pĕtová, J; Pisacka, M; Rubín, A; Wadman, SK; Zapadlo, M; Zeman, J1
Britz, ML; Wilkinson, RG1
French, NP; Grauaug, A; Wysocki, SJ1
Duran, M; Kamerling, JP; Wadman, SK1
Berry, HK; Denton, MD; Norman, EJ1
Baker, DH; Boebel, KP1
Inoue, Y; Kameyama, J; Momoi, T; Shigematsu, Y; Sudo, M; Suzuki, Y1
Bakkeren, JA; Houben, ML; Ruitenbeek, W; Sengers, RC; Trijbels, JM; Van der Zeè, SP1
Lehnert, W; Niederhoff, H1
August, CS; Cohn, RM; Hutchinson, R; Kelleher, JF; Yudkoff, M1
Hoffer, LJ; Mamer, OA; Reimer, ML; Robitaille, L; Taveroff, A1
Bain, MS; Burns, SP; Chalmers, RA; Holmes, HC; Iles, RA1
Abumrad, N; Connelly, AS; Fuller, JC; Nissen, S; Rathmacher, JA; Ray, M; Rice, D; Sharp, R1
Kreider, RB1
Dreifort, GD; Vukovich, MD1
de Almeida, IT; Duran, M; Maya, M; Overmars, H; Selhorst, J; Silva, MF; van Gennip, AH; Wanders, RJ1
Bode, HB; Höfle, G; Kroppenstedt, RM; Mahmud, T; Müller, R; Nordhoff, S; Silakowski, B; Xu, M1
Carnell, N; Henrich, CL; Mock, DM; Mock, NI1
Engelke, UF; Kluijtmans, LA; Kremer, B; Loss, S; Loupatty, FJ; Morava, E; Moskau, D; van den Bergh, E; van der Graaf, M; Wanders, RJ; Wevers, RA1
Espinosa-Artiles, P; Kithsiri Wijeratne, EM; Leslie Gunatilaka, AA; Molnár, I; Orozco, R; Patricia Stock, S; Xu, Y1
Amaral, AU; Fernandes, CG; Leipnitz, G; Schuck, PF; Seminotti, B; Wajner, M1
de Siqueira Filho, MA; Felitti, V; Gerlinger-Romero, F; Guimarães-Ferreira, L; Lancha, AH; Lira, FS; Seelaender, M; Zanchi, NE1
Holecek, M; Kovarik, M; Muthny, T; Sispera, L1
Bogusiewicz, A; Boysen, G; Dawson, AM; Henrich, CL; Horvath, TD; Matthews, NI; Mock, DM; Moran, JH; Owen, SN; Spencer, HJ; Stratton, SL1
de Almeida, IT; Diogo, L; Duran, M; Garcia, P; IJlst, L; Luís, PB; Ruiter, JP; Silva, MF; Wanders, RJ1
Atherton, PJ; Breen, L; Churchward-Venne, TA; Crossland, H; Etheridge, T; Hill, DS; Hossain, T; Loughna, P; Phillips, BE; Phillips, SM; Rathmacher, JA; Smith, K; Szewczyk, NJ; Wilkinson, DJ; Williams, J1
Barillaro, C; Landi, F; Liperoti, R; Martone, AM; Onder, G1
Aoki, MS; Artioli, GG; Baptista, IL; Guilherme, JP; Leal, ML; Miyabara, EH; Moriscot, AS; Silva, WJ1
Boutry, C; Davis, SR; Davis, TA; El-Kadi, SW; Nguyen, HV; Orellana, RA; Suryawan, A; Wheatley, SM1
Bruckbauer, A; Zemel, MB1
Barranco, A; Navalón, A; Ramírez, M; Rueda, R; Santos-Fandila, A; Zafra-Gómez, A1
Brett, SJ; Frost, G; Hickson, M; Wandrag, L1
Caudill, MA; Gayle, A; Jiang, X; Lucas, LK; Malysheva, O; Perry, CA; West, AA; Yan, J1
Beno, DW; Edens, NK; Lee, AJ; Mason, M; Mason-Bright, T; Shapiro, R; Surber, B; Zhang, X1
Mizuno, S; Saika, A; Tsuge, T; Ushimaru, K1
Bueno-Vargas, P; López-Pedrosa, JM; Ramírez, M; Santos-Fandila, A; Zafra-Gómez, A1
Phillips, SM1
Balakrishnan, G; Pereira, SL; Puthan, JK; Ramesh, S; Reddy, MT; Shreeram, S; Subramanian, R1
Jayakumar, J; Kuriyan, R; Kurpad, AV; Lokesh, DP; Philip, MG; Selvam, S; Shreeram, S1
Bach, E; Hansen, J; Jensen, E; Jessen, N; Johannsen, M; Jørgensen, JO; Møller, AB; Møller, N; Richelsen, B; Rittig, N; Serena, A; Thomsen, HH1
Bacci, ML; Barone, F; Elmi, A; Laghi, L; Romagnoli, N; Ventrella, D1
Gerlinger-Romero, F; Guimarães-Ferreira, L; Nunes, MT; Salgueiro, RB; Yonamine, CY1
Cruz-Jentoft, AJ1
Brown, AD; Close, GL; Sharples, AP; Stewart, CE1
Chen, X; Duan, Y; Guo, Q; Li, F; Wang, W; Wen, C; Yin, Y; Zhang, L1
Buddington, KK; Buddington, RK; Howard, SC; Lee, HW1
Duan, YH; Guo, QP; Kong, XF; Li, FN; Wang, WL; Xu, K; Zeng, LM; Zhang, LY1
Jakubowski, JS; McGlory, C; Morton, RW; Murphy, KT; Noguchi, KS; Nunes, EA; Phillips, SM; Vandeweerd, JK; Wong, EPT1
Calvani, R; Landi, F; Marzetti, E; Picca, A1
Deng, J; Duan, Y; Li, F; Zeng, L; Zhong, Y1
Deng, J; Duan, Y; Kong, X; Li, F; Song, B; Zheng, C; Zhong, Y1
Alves, F; Matias, CN; Monteiro, CP; Morton, RW; Phillips, SM; Reis, JF; Sardinha, LB; Teixeira, FJ; Valamatos, MJ1
Holeček, M; Vodeničarovová, M1
Duan, Y; Kong, X; Li, F; Song, B; Xu, K; Zheng, C; Zhong, Y1
Banfield, L; Jakubowski, JS; Morton, RW; Nunes, EA; Phillips, SM; Teixeira, FJ; Vescio, V1
Bautmans, I; Beckwée, D; De Breucker, S; Delaere, A; Gielen, E; Vandewoude, M1
Baganz, F; Gao, M; Gu, J; Hao, J; Kostas, ET; Lu, X; Lye, GJ; Shi, J; Sun, S; Wang, Y; Yang, Y; Zhang, Z1
Gao, R; Li, Z1
Bear, DE; Rooyackers, O1
Atherton, PJ; Chew, STH; Gonzalez, MC; Landi, F; Molinger, J; Prado, CM; Ruck, T1

Reviews

15 review(s) available for valerates and leucine

ArticleYear
Organic acidemias.
    Clinics in perinatology, 1976, Volume: 3, Issue:1

    Topics: Acidosis, Renal Tubular; Acids; Amino Acid Metabolism, Inborn Errors; Amino Acids, Essential; Ammonia; Child; Diagnosis, Differential; Glutarates; Humans; Hydrogen-Ion Concentration; Infant; Infant, Newborn; Leucine; Ligases; Methylmalonic Acid; Prenatal Diagnosis; Propionates; Pyruvates; Urea; Valerates

1976
[Congenital metabolic acidosis in the postnatal period].
    Deutsche medizinische Wochenschrift (1946), 1978, Jun-02, Volume: 103, Issue:22

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine

1978
Molecular basis of isovaleric acidemia and the study of the acyl-CoA dehydrogenase family.
    Advances in neurology, 1988, Volume: 48

    Topics: Acyl-CoA Dehydrogenases; Animals; DNA; Hemiterpenes; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Leucine; Mitochondria, Liver; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Phenotype; Protein Biosynthesis; Protein Processing, Post-Translational; Rats; Valerates

1988
Inborn errors of organic acid metabolism.
    Clinics in endocrinology and metabolism, 1974, Volume: 3, Issue:1

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Biotin; Carboxylic Acids; Chromatography, Gas; Coenzyme A; Crotonates; Female; Gestational Age; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Infant, Newborn; Isomerases; Leucine; Male; Malonates; Metabolism, Inborn Errors; Pedigree; Pregnancy; Prenatal Diagnosis; Propionates; Pyrrolidonecarboxylic Acid; Valerates; Vitamin B 12

1974
Dietary supplements and the promotion of muscle growth with resistance exercise.
    Sports medicine (Auckland, N.Z.), 1999, Volume: 27, Issue:2

    Topics: Anabolic Agents; Boron; Chromium; Creatine; Dehydroepiandrosterone; Dietary Carbohydrates; Dietary Proteins; Dietary Supplements; Glutamine; Humans; Leucine; Muscle Development; Muscle, Skeletal; Nutritional Physiological Phenomena; Protein Biosynthesis; Testosterone; Valerates; Vanadium Compounds; Weight Lifting

1999
HMB supplementation: clinical and athletic performance-related effects and mechanisms of action.
    Amino acids, 2011, Volume: 40, Issue:4

    Topics: Administration, Oral; Adult; Athletic Performance; Body Composition; Dietary Supplements; Humans; Keto Acids; Leucine; Male; Muscle Strength; Muscle, Skeletal; Resistance Training; Signal Transduction; Valerates

2011
The new metabolic treatments for sarcopenia.
    Aging clinical and experimental research, 2013, Volume: 25, Issue:2

    Topics: Animals; Humans; Leucine; Sarcopenia; Valerates; Vitamin D

2013
Impact of supplementation with amino acids or their metabolites on muscle wasting in patients with critical illness or other muscle wasting illness: a systematic review.
    Journal of human nutrition and dietetics : the official journal of the British Dietetic Association, 2015, Volume: 28, Issue:4

    Topics: Aged; Amino Acids; Amino Acids, Essential; Body Composition; Creatine; Critical Illness; Diet; Dietary Supplements; Enteral Nutrition; Female; Humans; Intensive Care Units; Leucine; Male; MEDLINE; Muscular Atrophy; Nutritional Status; Valerates

2015
Nutritional supplements in support of resistance exercise to counter age-related sarcopenia.
    Advances in nutrition (Bethesda, Md.), 2015, Volume: 6, Issue:4

    Topics: Aged; Aging; Creatine; Diet; Dietary Proteins; Dietary Supplements; Fatty Acids, Omega-3; Female; Humans; Leucine; Male; Muscle Strength; Muscle, Skeletal; Quality of Life; Resistance Training; Sarcopenia; Valerates

2015
Beta-Hydroxy-Beta-Methyl Butyrate (HMB): From Experimental Data to Clinical Evidence in Sarcopenia.
    Current protein & peptide science, 2018, Volume: 19, Issue:7

    Topics: Aged; Aged, 80 and over; Aging; Apoptosis; Cell Survival; Dietary Supplements; Frailty; Humans; Leucine; Middle Aged; Muscle Strength; Muscle, Skeletal; Muscular Atrophy; Sarcopenia; Valerates

2018
Beta-hydroxy-beta-methylbutyrate and sarcopenia: from biological plausibility to clinical evidence.
    Current opinion in clinical nutrition and metabolic care, 2019, Volume: 22, Issue:1

    Topics: Aged; Dietary Supplements; Frail Elderly; Humans; Leucine; Muscle Proteins; Muscle, Skeletal; Physical Functional Performance; Sarcopenia; Valerates

2019
Supplementation with the Leucine Metabolite β-hydroxy-β-methylbutyrate (HMB) does not Improve Resistance Exercise-Induced Changes in Body Composition or Strength in Young Subjects: A Systematic Review and Meta-Analysis.
    Nutrients, 2020, May-23, Volume: 12, Issue:5

    Topics: Adolescent; Adult; Body Composition; Body Mass Index; Databases, Factual; Dietary Supplements; Female; Humans; Leucine; Male; Muscle Strength; Muscle, Skeletal; Randomized Controlled Trials as Topic; Resistance Training; Sensitivity and Specificity; Valerates; Young Adult

2020
Nutritional interventions to improve muscle mass, muscle strength, and physical performance in older people: an umbrella review of systematic reviews and meta-analyses.
    Nutrition reviews, 2021, 01-09, Volume: 79, Issue:2

    Topics: Aged; Aged, 80 and over; Amino Acids, Essential; Creatine; Dietary Supplements; Exercise; Humans; Leucine; Muscle Strength; Muscle, Skeletal; Physical Functional Performance; Sarcopenia; Valerates

2021
HMB and leucine supplementation during critical illness and recovery.
    Current opinion in clinical nutrition and metabolic care, 2022, 03-01, Volume: 25, Issue:2

    Topics: Critical Illness; Dietary Supplements; Humans; Leucine; Muscle Strength; Muscle, Skeletal; Muscular Atrophy; Valerates

2022
Advances in muscle health and nutrition: A toolkit for healthcare professionals.
    Clinical nutrition (Edinburgh, Scotland), 2022, Volume: 41, Issue:10

    Topics: Adult; Amino Acids; Amino Acids, Branched-Chain; COVID-19; Creatine; Delivery of Health Care; Dietary Supplements; Fatty Acids, Omega-3; Fatty Acids, Unsaturated; Hand Strength; Humans; Leucine; Malnutrition; Muscle Strength; Muscle, Skeletal; Valerates; Vitamin D

2022

Trials

7 trial(s) available for valerates and leucine

ArticleYear
Effect of leucine metabolite beta-hydroxy-beta-methylbutyrate on muscle metabolism during resistance-exercise training.
    Journal of applied physiology (Bethesda, Md. : 1985), 1996, Volume: 81, Issue:5

    Topics: Adult; Body Composition; Body Weight; Diet; Dietary Fats; Dietary Proteins; Energy Metabolism; Humans; Leucine; Male; Methylhistidines; Muscle Proteins; Muscle, Skeletal; Physical Education and Training; Valerates; Weight Lifting

1996
Effect of beta-hydroxy beta-methylbutyrate on the onset of blood lactate accumulation and V(O)(2) peak in endurance-trained cyclists.
    Journal of strength and conditioning research, 2001, Volume: 15, Issue:4

    Topics: Adult; Anaerobic Threshold; Analysis of Variance; Bicycling; Blood Glucose; Cross-Over Studies; Dietary Supplements; Double-Blind Method; Exercise; Hematocrit; Hemoglobins; Humans; Lactates; Leucine; Male; Oxygen Consumption; Physical Education and Training; Physical Endurance; Time Factors; Valerates

2001
Pregnancy and lactation alter biomarkers of biotin metabolism in women consuming a controlled diet.
    The Journal of nutrition, 2014, Volume: 144, Issue:12

    Topics: Adult; Biomarkers; Biotin; Carbon-Carbon Ligases; Carnitine; Choline; Chromatography, Liquid; Diet; Dietary Supplements; Female; Humans; Lactation; Leucine; Milk, Human; New York; Patient Compliance; Pregnancy; Tandem Mass Spectrometry; Valerates; Young Adult

2014
Anabolic effects of leucine-rich whey protein, carbohydrate, and soy protein with and without β-hydroxy-β-methylbutyrate (HMB) during fasting-induced catabolism: A human randomized crossover trial.
    Clinical nutrition (Edinburgh, Scotland), 2017, Volume: 36, Issue:3

    Topics: Adaptor Proteins, Signal Transducing; Adult; Anabolic Agents; Body Mass Index; Cell Cycle Proteins; Cross-Over Studies; Dietary Carbohydrates; Fasting; Glucagon; Humans; Leucine; Male; Muscle, Skeletal; Phosphoproteins; Phosphorylation; Ribosomal Protein S6 Kinases, 90-kDa; Signal Transduction; Soybean Proteins; TOR Serine-Threonine Kinases; Valerates; Whey Proteins; Young Adult

2017
Equivalent Hypertrophy and Strength Gains in β-Hydroxy-β-Methylbutyrate- or Leucine-supplemented Men.
    Medicine and science in sports and exercise, 2019, Volume: 51, Issue:1

    Topics: Adult; Biopsy; Body Composition; Creatine Kinase; Dietary Supplements; Double-Blind Method; Human Growth Hormone; Humans; Hydrocortisone; Insulin-Like Growth Factor I; Leucine; Male; Muscle Strength; Muscle, Skeletal; Performance-Enhancing Substances; Resistance Training; Testosterone; Ultrasonography; Valerates; Young Adult

2019
α-Ketoisocaproate and β-hydroxy-β-methyl butyrate regulate fatty acid composition and lipid metabolism in skeletal muscle of growing pigs.
    Journal of animal physiology and animal nutrition, 2019, Volume: 103, Issue:3

    Topics: AMP-Activated Protein Kinases; Animal Feed; Animal Nutritional Physiological Phenomena; Animals; Diet; Fatty Acids; Gene Expression Regulation; Keto Acids; Leucine; Lipid Metabolism; Muscle, Skeletal; Random Allocation; RNA, Messenger; Swine; TOR Serine-Threonine Kinases; Transcription Factors; Valerates

2019
Leucine metabolites do not attenuate training-induced inflammation in young resistance trained men.
    Journal of sports sciences, 2019, Volume: 37, Issue:17

    Topics: Adult; Biomarkers; Body Composition; C-Reactive Protein; Calcium; Caproates; Dietary Supplements; Double-Blind Method; Humans; Inflammation; Interleukin-6; Leucine; Male; Muscle Strength; Muscle, Skeletal; Resistance Training; Sports Nutritional Physiological Phenomena; Tumor Necrosis Factor-alpha; Valerates; Young Adult

2019

Other Studies

155 other study(ies) available for valerates and leucine

ArticleYear
Prenatal diagnosis and a case report of isovaleric acidaemia.
    Journal of inherited metabolic disease, 1978, Volume: 1, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Chromatography, Gas; Female; Humans; Leucine; Male; Pedigree; Pregnancy; Prenatal Diagnosis; Valerates

1978
[Emergency treatment of inborn amino errors of amino acid metabolism detected in the neonatal period].
    Archives francaises de pediatrie, 1979, Volume: 36, Issue:10

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Diuretics, Osmotic; Emergencies; Enteral Nutrition; Exchange Transfusion, Whole Blood; Humans; Infant, Newborn; Leucine; Methylmalonic Acid; Peritoneal Dialysis; Propionates; Valerates

1979
Accumulation of 3-hydroxyisobutyric acid, 2-methyl-3-hydroxybutyric acid and 3-hydroxyisovaleric acid in ketoacidosis.
    Clinica chimica acta; international journal of clinical chemistry, 1975, Oct-15, Volume: 64, Issue:2

    Topics: Acetates; Acidosis; Animals; Child; Child, Preschool; Chromatography, Gas; Diabetes Mellitus; Diabetic Ketoacidosis; Glutarates; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Isoleucine; Leucine; Male; Mass Spectrometry; Rats; Streptozocin; Valerates; Valine

1975
Leucine catabolism and CO2 fixation into fatty acids by Tetrahymena: evidence for two pools of CO2.
    The Journal of biological chemistry, 1977, May-25, Volume: 252, Issue:10

    Topics: Acetates; Bicarbonates; Carbon Dioxide; Coenzyme A; Crotonates; Fatty Acids; Glycogen; Leucine; Ligases; Pyruvates; Tetrahymena pyriformis; Valerates

1977
[Isovaleric acidemia combined with hypertrophic pylorstenosis (author's transl)].
    Klinische Padiatrie, 1979, Volume: 191, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Humans; Hypertrophy; Infant; Infant, Newborn; Leucine; Male; Pyloric Stenosis; Valerates

1979
Glycine therapy in isovaleric acidemia.
    The Journal of pediatrics, 1978, Volume: 92, Issue:5

    Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Drug Administration Schedule; Female; Glycine; Humans; Keto Acids; Ketone Bodies; Lactates; Leucine; Pyruvates; Valerates

1978
The metabolism of leucine by developing rat brain: effect of leucine and 2-oxo-4-methylvalerate on lipid synthesis from glucose and ketone bodies.
    Journal of neurochemistry, 1978, Volume: 30, Issue:4

    Topics: Aging; Animals; Animals, Newborn; Brain; Cerebral Cortex; Female; Glucose; Keto Acids; Ketone Bodies; Leucine; Lipids; Male; Pregnancy; Rats; Valerates

1978
Volatile acid production from threonine, valine, leucine and isoleucine by clostridia.
    Archives of microbiology, 1978, May-30, Volume: 117, Issue:2

    Topics: Acetates; Butyrates; Caproates; Clostridium; Fatty Acids, Volatile; Isoleucine; Leucine; Propionates; Species Specificity; Threonine; Valerates; Valine

1978
[Isovaleric acidemia and beta-hydroxyisovaleric aciduria].
    Nihon rinsho. Japanese journal of clinical medicine, 1978, Volume: Suppl

    Topics: Amino Acid Metabolism, Inborn Errors; Humans; Infant; Infant, Newborn; Leucine; Valerates

1978
The effects of growth hormone on the utilization of L-leucine in adipose tissue.
    Endocrinology, 1978, Volume: 102, Issue:1

    Topics: Adipose Tissue; Animals; Cycloheximide; Dactinomycin; Glucose; Growth Hormone; Hypophysectomy; Leucine; Male; Rats; Time Factors; Valerates

1978
Kinetics of the early insulin response of the perfused rat pancreas to various metabolites and tolbutamide.
    Diabete & metabolisme, 1975, Volume: 1, Issue:3

    Topics: Animals; Caproates; Glucose; Glyceraldehyde; Insulin; Insulin Secretion; Islets of Langerhans; Leucine; Male; Rats; Stimulation, Chemical; Time Factors; Tolbutamide; Valerates

1975
Leucine biosynthesis in the blue-green bacterium Anacystis nidulans.
    Journal of bacteriology, 1975, Volume: 124, Issue:2

    Topics: 2-Isopropylmalate Synthase; Alcohol Oxidoreductases; Cell-Free System; Cyanobacteria; Dicarboxylic Acids; Hydro-Lyases; Leucine; Mutation; Valerates

1975
Biosynthesis of rat kidney catalase. Double-labeling by [14C]leucine and delta-amino[3H]levulinic acid.
    Journal of biochemistry, 1976, Volume: 80, Issue:2

    Topics: Aminolevulinic Acid; Animals; Carbon Radioisotopes; Catalase; Enzyme Induction; Immunodiffusion; Isotope Labeling; Kidney; Kinetics; Leucine; Precipitin Tests; Rats; Subcellular Fractions; Tritium; Urea; Valerates

1976
Effect of dietary branched-chain alpha-keto acids on hepatic branched-chain alpha-keto acid dehydrogenase in the rat.
    The Journal of nutrition, 1977, Volume: 107, Issue:8

    Topics: Animals; Body Weight; Caproates; Keto Acids; Ketone Oxidoreductases; Kidney; Leucine; Liver; Male; Muscles; Organ Size; Organ Specificity; Rats; Structure-Activity Relationship; Valerates; Valine

1977
Site of action of insulin in promoting leucine utilization in adipose tissue.
    The American journal of physiology, 1977, Volume: 233, Issue:2

    Topics: Adipose Tissue; Animals; Carbon Dioxide; Chloramphenicol; Cycloheximide; Glucose; In Vitro Techniques; Insulin; Keto Acids; Leucine; Lipid Metabolism; Male; Oxidation-Reduction; Protein Biosynthesis; Puromycin; Rats; Valerates

1977
Metabolism of [1-(14)C] and [2-(14)C] leucine in cultured skin fibroblasts from patients with isovaleric acidemia. Characterization of metabolic defects.
    The Journal of clinical investigation, 1976, Volume: 58, Issue:1

    Topics: 2-Methyl-4-chlorophenoxyacetic Acid; Amino Acid Metabolism, Inborn Errors; Carbon Dioxide; Cell Line; Cells, Cultured; Depression, Chemical; Fibroblasts; Flavin-Adenine Dinucleotide; Glycine; Humans; Leucine; Maple Syrup Urine Disease; Oxidation-Reduction; Skin; Succinates; Valerates; Valine

1976
[Isovaleric acidemia. Study and treatment in 3 brothers].
    Archives francaises de pediatrie, 1976, Volume: 33, Issue:8

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Fatty Acids, Volatile; Female; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidoreductases; Peritoneal Dialysis; Sweat; Valerates

1976
Separate regulation of transport and biosynthesis of leucine, isoleucine, and valine in bacteria.
    Journal of bacteriology, 1975, Volume: 122, Issue:3

    Topics: Acetolactate Synthase; Alcohol Oxidoreductases; Biological Transport, Active; Cell-Free System; Dicarboxylic Acids; Enzyme Repression; Escherichia coli; Genes, Regulator; Isoleucine; Leucine; Mutation; Protein Binding; Salmonella typhimurium; Valerates; Valine

1975
Addition of leucine precursors to the diet of leucine-starved mice.
    The American journal of clinical nutrition, 1975, Volume: 28, Issue:9

    Topics: Animals; Bacteria; Caproates; Deficiency Diseases; Leucine; Mice; Structure-Activity Relationship; Valerates

1975
Acute neonatal isovaleric acidemia. A report of two cases.
    Israel journal of medical sciences, 1975, Volume: 11, Issue:10

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Diagnosis, Differential; Female; Humans; Infant, Newborn; Infant, Newborn, Diseases; Leucine; Male; Pedigree; Valerates

1975
Biosynthesis of liver catalase in rats treated with allylisopropylacetylcarbamide. II. Double-labeling of catalase with (14C)leucine and delta-(3H)aminolevulinic acid.
    Journal of biochemistry, 1975, Volume: 78, Issue:5

    Topics: Aminolevulinic Acid; Animals; Catalase; Leucine; Levulinic Acids; Liver; Microbodies; Microsomes, Liver; Rats; Ribosomes; Urea; Valerates

1975
Biosynthesis of 2-methylalkanes in the crickets Nemobius fasciatus and Gryllus pennsylvanicus.
    Biochemical and biophysical research communications, 1976, Feb-09, Volume: 68, Issue:3

    Topics: Acetates; Alkanes; Animals; Butyrates; Chromatography, Gas; Leucine; Orthoptera; Species Specificity; Valerates; Valine

1976
Biotin deficiency in rats: disturbances of leucine metabolism are detectable early.
    The Journal of nutrition, 1992, Volume: 122, Issue:7

    Topics: Animals; Biotin; Gas Chromatography-Mass Spectrometry; Leucine; Male; Rats; Rats, Inbred Strains; Valerates

1992
The contribution of protein catabolism to metabolic decompensation in 3-hydroxy-3-methylglutaric aciduria.
    European journal of pediatrics, 1990, Volume: 149, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Diseases in Twins; Female; Glutarates; Humans; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Phenylalanine; Proteins; Valerates

1990
Oxidation of leucine and alpha-ketoisocaproate to beta-hydroxy-beta-methylbutyrate in vivo.
    The American journal of physiology, 1992, Volume: 262, Issue:1 Pt 1

    Topics: Animals; Female; Keto Acids; Leucine; Male; Osmolar Concentration; Oxidation-Reduction; Sheep; Swine; Valerates

1992
Increased urinary excretion of beta-hydroxyisovaleric acid in ketotic and non-ketotic type II diabetes mellitus.
    Clinica chimica acta; international journal of clinical chemistry, 1990, Apr-30, Volume: 188, Issue:2

    Topics: Adult; Blood Glucose; Diabetes Mellitus, Type 2; Diabetic Ketoacidosis; Female; Gas Chromatography-Mass Spectrometry; Glycosuria; Humans; Leucine; Male; Middle Aged; Trimethylsilyl Compounds; Valerates

1990
Analysis of beta-hydroxy-beta-methyl butyrate in plasma by gas chromatography and mass spectrometry.
    Analytical biochemistry, 1990, Volume: 188, Issue:1

    Topics: Animals; Buffers; Caproates; Gas Chromatography-Mass Spectrometry; Leucine; Reference Standards; Sheep; Valerates

1990
3-Hydroxy-3-methylglutaryl-CoA lyase deficiency as detected by radiochemical assay in cell extracts by thin-layer chromatography, and identification of three new cases.
    Clinical chemistry, 1990, Volume: 36, Issue:2

    Topics: Cells, Cultured; Chromatography, Thin Layer; Dicarboxylic Acids; Fibroblasts; Humans; Infant; Infant, Newborn; Leucine; Lymphocytes; Male; Oxidation-Reduction; Oxo-Acid-Lyases; Radiochemistry; Valerates

1990
Isovaleric acidemia: personal history, clinical survey and study of the molecular basis.
    Progress in clinical and biological research, 1990, Volume: 321

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Cell Line; Child, Preschool; Female; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Prognosis; Valerates

1990
The treatment of isovaleric acidemia with glycine supplement.
    Pediatric research, 1988, Volume: 24, Issue:1

    Topics: Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
Acute and chronic-intermittent isovaleric acidemia: diagnosis and glycine therapy.
    Acta paediatrica Japonica : Overseas edition, 1988, Volume: 30, Issue:4

    Topics: Acute Disease; Child; Child, Preschool; Chronic Disease; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
Effects of dietary leucine, alpha-ketoisocaproate and isovalerate on antibody production and lymphocyte blastogenesis in growing lambs.
    The Journal of nutrition, 1988, Volume: 118, Issue:12

    Topics: Animals; Antibody Formation; Diet; Immunity, Cellular; Keto Acids; Leucine; Lymphocyte Activation; Lymphocytes; Sheep; Valerates

1988
[Plasma level of branched-chain amino and keto acids in healthy subjects after an intravenous dose of MCT/LCT or LCT].
    Beitrage zu Infusionstherapie und klinische Ernahrung, 1988, Volume: 20

    Topics: Adult; Amino Acids, Branched-Chain; Caproates; Fasting; Fat Emulsions, Intravenous; Female; Hemiterpenes; Humans; Infusions, Intravenous; Insulin; Isoleucine; Keto Acids; Leucine; Male; Middle Aged; Random Allocation; Triglycerides; Valerates; Valine

1988
Protein origin of the volatile fatty acids isobutyrate and isovalerate in human stool.
    The Journal of laboratory and clinical medicine, 1987, Volume: 109, Issue:5

    Topics: Albumins; Butyrates; Fatty Acids, Volatile; Feces; Hemiterpenes; Humans; Hydrogen-Ion Concentration; Isobutyrates; Leucine; Male; Pentanoic Acids; Proteins; Valerates; Valine

1987
Endogenous catabolism as source of toxic metabolites in isovaleric acidemia.
    The Journal of pediatrics, 1987, Volume: 111, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Dietary Proteins; Hemiterpenes; Humans; Leucine; Pentanoic Acids; Valerates

1987
Isovaleryl-CoA dehydrogenase activity in isovaleric acidemia fibroblasts using an improved tritium release assay.
    Pediatric research, 1986, Volume: 20, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Fibroblasts; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Kinetics; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Skin; Tritium; Valerates

1986
Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia.
    The Journal of pediatrics, 1987, Volume: 110, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Proteins; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates

1987
Biotin-responsive beta-methylcrotonylglycinuria.
    Lancet (London, England), 1971, Jul-03, Volume: 2, Issue:7714

    Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Chromatography, Gas; Fatty Acids; Glycine; Humans; Infant; Leucine; Male; Partial Pressure; Valerates; Valine; Vomiting

1971
Isovaleric acidemia: results of family study and dietary treatment.
    Pediatrics, 1973, Volume: 52, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Child; Child, Preschool; Developmental Disabilities; Diet Therapy; Fatty Acids; Female; Glycine; Humans; Infant, Newborn; Intellectual Disability; Intelligence Tests; Leucine; Male; Odorants; Pedigree; Valerates

1973
Regulation of leucine catabolism in Pseudomonas putida.
    Journal of bacteriology, 1974, Volume: 118, Issue:1

    Topics: Alcohol Oxidoreductases; Cell-Free System; Chromatography, Paper; D-Amino-Acid Oxidase; Enzyme Induction; Enzyme Repression; Glucose; Glutamates; Isoleucine; Ketones; Leucine; Ligases; Mutation; Oxidation-Reduction; Oxo-Acid-Lyases; Pseudomonas; Spectrophotometry; Stereoisomerism; Succinates; Transaminases; Valerates; Valine

1974
Studies on the mechanism of L-leucine-and alpha-ketoisocaproic acid-induced insulin release from perifused isolated pancreatic islets.
    Diabetologia, 1974, Volume: 10, Issue:2

    Topics: Animals; Caproates; Chemical Phenomena; Chemistry; Female; Glucose; Hyperglycemia; In Vitro Techniques; Insulin; Insulin Secretion; Islets of Langerhans; Keto Acids; Leucine; Male; Mice; NADP; Obesity; Spectrometry, Fluorescence; Structure-Activity Relationship; Valerates

1974
High-affinity uptake of (3H)gamma-aminobutyric acid into frog spinal cord slices.
    Brain research, 1974, Aug-23, Volume: 76, Issue:3

    Topics: Absorption; Alanine; Amines; Amino Acids, Diamino; Aminobutyrates; Animals; Anura; Dinitrophenols; Guanidines; Hydroxybutyrates; In Vitro Techniques; Iodoacetates; Kinetics; Leucine; Neurotransmitter Agents; Ouabain; Rana pipiens; Sodium; Spinal Cord; Sulfonic Acids; Synaptic Transmission; Temperature; Time Factors; Tritium; Valerates

1974
Neonatal death associated with isovalericacidaemia.
    Lancet (London, England), 1967, Aug-26, Volume: 2, Issue:7513

    Topics: Acidosis; Bicarbonates; Chromatography; Chromatography, Gas; Coenzyme A; Electrolytes; Fatty Acids; Fatty Acids, Nonesterified; Glucose; Hemorrhage; Humans; Hypocalcemia; Infant Mortality; Infant, Newborn; Leucine; Male; Metabolism, Inborn Errors; Valerates

1967
No evidence of isovalthinuria in isovaleric acidemia-- brief note.
    Acta medicinae Okayama, 1970, Volume: 24, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Autoanalysis; Child, Preschool; Electrophoresis; Filtration; Humans; Leucine; Valerates

1970
Regulation of glutamate dehydrogenase by histidine.
    Biochimica et biophysica acta, 1971, Feb-10, Volume: 227, Issue:2

    Topics: Acetates; Adenine Nucleotides; Amino Acids; Animals; Binding Sites; Cattle; Chemical Phenomena; Chemistry; Dipeptides; Enzyme Activation; Fluorescence; Glutamate Dehydrogenase; Histidine; Kinetics; Leucine; Liver; Methylation; NAD; Urea; Valerates

1971
Crystalline L-leucine dehydrogenase.
    Biochemical and biophysical research communications, 1971, Aug-20, Volume: 44, Issue:4

    Topics: Alanine; Amino Acid Oxidoreductases; Amino Acids; Aminocaproates; Ammonium Sulfate; Bacillus; Chemical Precipitation; Chromatography; Chromatography, DEAE-Cellulose; Crystallization; Electrophoresis, Disc; Glutamates; Hydroxyapatites; Isoleucine; Leucine; Molecular Weight; NAD; Stereoisomerism; Ultracentrifugation; Valerates; Valine

1971
Kinetic measurements with monocarboxylic acids as substrates and effectors of glutamate dehydrogenase.
    FEBS letters, 1972, Nov-15, Volume: 28, Issue:1

    Topics: Acetates; Alanine; Animals; Binding Sites; Carboxylic Acids; Cattle; Enzyme Activation; Glutamate Dehydrogenase; Glutamates; Kinetics; Leucine; Liver; NAD; Protein Binding; Ultracentrifugation; Valerates

1972
[Kinetic studies on binding of effectors to glutamate-dehydrogenase].
    Hoppe-Seyler's Zeitschrift fur physiologische Chemie, 1972, Volume: 353, Issue:10

    Topics: Adenosine Diphosphate; Binding Sites; Chemical Phenomena; Chemistry; Glutamate Dehydrogenase; Glutamates; Glutarates; Guanosine Triphosphate; Hydrogen-Ion Concentration; Kinetics; Leucine; NAD; Ultracentrifugation; Valerates

1972
Subcellular localization of the leucine biosynthetic enzymes in yeast.
    Journal of bacteriology, 1973, Volume: 116, Issue:1

    Topics: Acyltransferases; Cell-Free System; Centrifugation, Density Gradient; Dicarboxylic Acids; Electron Transport Complex IV; Glucosephosphate Dehydrogenase; Isomerases; Leucine; Mitochondria; Osmosis; Oxidoreductases; Oxo-Acid-Lyases; Saccharomyces cerevisiae; Solubility; Spectrophotometry; Spheroplasts; Transaminases; Valerates

1973
Mutual antagonism in the metabolism of D-valine and D-leucine and antagonism by their analogs.
    Archives of biochemistry and biophysics, 1969, Volume: 135, Issue:1

    Topics: Amino Acids; Animals; Caproates; D-Amino-Acid Oxidase; Depression, Chemical; Diet; Growth; Keto Acids; Leucine; Male; Rats; Stereoisomerism; Stimulation, Chemical; Valerates; Valine

1969
Central vs. systemic neurotoxicity of hypoglycin (ackee toxin) and related substance in the cat.
    The Journal of pharmacology and experimental therapeutics, 1974, Volume: 190, Issue:2

    Topics: Acetates; Animals; Blood Pressure; Butyrates; Carbon Dioxide; Cats; Cerebral Ventricles; Chemoreceptor Cells; Emetics; Hydrogen-Ion Concentration; Injections; Injections, Intravenous; Leucine; Medulla Oblongata; Plants; Pyruvates; Respiration; Syncope; Toxins, Biological; Valerates; Vomiting

1974
New amino acid regulatory locus having unusual properties in heterozygous merodiploids.
    Journal of bacteriology, 1972, Volume: 110, Issue:3

    Topics: Acyltransferases; Alleles; Amino Acids; Cell-Free System; Chromosome Mapping; Chromosomes, Bacterial; Culture Media; Dicarboxylic Acids; Diploidy; Drug Resistance, Microbial; Escherichia coli; Fluorine; Genes; Heterozygote; Hydro-Lyases; Leucine; Lyases; Mutation; Pyruvates; Recombination, Genetic; Threonine; Transduction, Genetic; Valerates

1972
Leucine accumulation by isoleucine revertants of Serratia marcescens resistant to -aminobutyric acid: lack of both feedback inhibition and repression.
    Journal of biochemistry, 1973, Volume: 73, Issue:1

    Topics: Acetyltransferases; Aminobutyrates; Dicarboxylic Acids; Enzyme Repression; Feedback; Hydro-Lyases; Isoleucine; Leucine; Mutation; Serratia marcescens; Valerates; Valine

1973
Genetic fine structure of the leucine operon of Escherichia coli K-12.
    Journal of bacteriology, 1973, Volume: 113, Issue:3

    Topics: Alcohol Oxidoreductases; Arabinose; Cell-Free System; Chromosome Mapping; Crosses, Genetic; Dicarboxylic Acids; Escherichia coli; Genetic Complementation Test; Leucine; Mutagens; Mutation; Nitrosoguanidines; Operon; Oxo-Acid-Lyases; Recombination, Genetic; Salmonella typhimurium; Transduction, Genetic; Valerates

1973
Mechanism of feedback inhibition by leucine. Binding of leucine to wild-type and feedback-resistant alpha-isopropylmalate synthases and its structural consequences.
    Biochemistry, 1973, Jul-31, Volume: 12, Issue:16

    Topics: Acetyl Coenzyme A; Binding Sites; Binding, Competitive; Caproates; Carbon Isotopes; Chromatography, Gel; Dialysis; Electrophoresis, Polyacrylamide Gel; Feedback; Hydrogen-Ion Concentration; Keto Acids; Kinetics; Leucine; Malates; Mutation; Oxo-Acid-Lyases; Protein Binding; Protein Conformation; Salmonella typhimurium; Spectrophotometry; Spectrophotometry, Ultraviolet; Valerates

1973
Genetic analysis of the leucine region in Escherichia coli B-r: gene-enzyme assignments.
    Journal of bacteriology, 1974, Volume: 117, Issue:1

    Topics: Acyltransferases; Arabinose; Cell-Free System; Chromosome Mapping; Conjugation, Genetic; Dicarboxylic Acids; Escherichia coli; Genes; Genetic Complementation Test; Isomerases; Leucine; Mutation; Oxidoreductases; Spectrophotometry; Stereoisomerism; Transduction, Genetic; Valerates

1974
flrB, a regulatory locus controlling branched-chain amino acid biosynthesis in Salmonella typhimurium.
    Journal of bacteriology, 1974, Volume: 118, Issue:3

    Topics: Amino Acids; Amino Acyl-tRNA Synthetases; Autoanalysis; Cell-Free System; Chromatography; Chromosome Mapping; Dicarboxylic Acids; Genes, Regulator; Hydro-Lyases; Isoleucine; Leucine; Lyases; Mutation; Oxo-Acid-Lyases; Pyruvates; RNA, Bacterial; RNA, Transfer; Salmonella typhimurium; Temperature; Threonine; Transduction, Genetic; Valerates; Valine

1974
Evolution of a new gene substituting for the leuD gene of Salmonella typhimurium: characterization of supQ mutations.
    Journal of bacteriology, 1974, Volume: 119, Issue:3

    Topics: Chromosome Mapping; Crosses, Genetic; Dicarboxylic Acids; Genes; Isomerases; Leucine; Models, Biological; Mutagens; Mutation; Nitrites; Proline; Salmonella; Salmonella typhimurium; Suppression, Genetic; Temperature; Transduction, Genetic; Valerates

1974
Regulation of transaminase C synthesis in Escherichia coli: conditional leucine auxotrophy.
    Journal of bacteriology, 1974, Volume: 120, Issue:2

    Topics: Culture Media; Escherichia coli; Genetic Linkage; Genetics, Microbial; Isoleucine; Leucine; Molecular Biology; Recombination, Genetic; Spectrophotometry, Infrared; Time Factors; Transaminases; Transduction, Genetic; Valerates

1974
Regulation of branched chain amino acid transaminase formation during the growth of Pseudomonas fluorescens UK-1.
    Acta chemica Scandinavica, 1972, Volume: 26, Issue:3

    Topics: Butyrates; Caproates; Glutamates; Isoleucine; Leucine; Propionates; Pseudomonas; Pseudomonas fluorescens; Transaminases; Valerates; Valine

1972
Formation of 2-oxoisovalerate dehydrogenase in Pseudomonas fluorescens.
    Acta chemica Scandinavica, 1972, Volume: 26, Issue:3

    Topics: Carbon Isotopes; Isoleucine; Keto Acids; Ketone Oxidoreductases; Leucine; Pseudomonas; Pseudomonas fluorescens; Valerates; Valine

1972
Polypeptides. XXI. Synthesis of some sequential macromolecular polypeptolides of L-leucine and L-2-hydroxy-4-methylpentanoic acid.
    Journal of the Chemical Society. Perkin transactions 1, 1972, Volume: 16

    Topics: Amino Acid Sequence; Hydroxylation; Leucine; Methylation; Oligopeptides; Valerates

1972
Nutritional alteration of the fatty acid composition of a thermophilic Bacillus species.
    Journal of bacteriology, 1973, Volume: 116, Issue:3

    Topics: Acetates; Bacillus; Butyrates; Chromatography, Gas; Culture Media; Fatty Acids; Hot Temperature; Isoleucine; Isomerism; Leucine; Valerates; Valine

1973
Diagnosis of isovaleric acidemia in cultured fibroblasts.
    Clinica chimica acta; international journal of clinical chemistry, 1973, Nov-15, Volume: 48, Issue:4

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carbon Radioisotopes; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Heterozygote; Humans; Infant, Newborn; Leucine; Pregnancy; Prenatal Diagnosis; Skin; Valerates

1973
Child with a defect in leucine metabolism associated with beta-hydroxyisovaleric aciduria and beta-methylcrotonylglycinuria.
    Archives of disease in childhood, 1973, Volume: 48, Issue:12

    Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Creatinine; Crotonates; Glycine; Humans; Infant; Leucine; Male; Pentanols; Pneumonia; Valerates

1973
Inhibition of alanine and aspartate aminotransferases by alpha-oxoderivatives of the branched-chain amino acids.
    Journal of neurochemistry, 1974, Volume: 22, Issue:1

    Topics: Alanine Transaminase; Amino Acids; Animals; Aspartate Aminotransferases; Azoles; Binding Sites; Brain; Caproates; Humans; Keto Acids; Kinetics; Leucine; Liver; Maple Syrup Urine Disease; Organ Specificity; Protein Binding; Pyridoxamine; Rats; Spectrophotometry, Ultraviolet; Transaminases; Valerates

1974
Possibility of inborn defect in isovalericacidaemia involving altered enzyme specificity rather than total inactivity.
    Nature, 1974, Mar-08, Volume: 248, Issue:5444

    Topics: Alanine; Butyrates; Coenzyme A; Cyclopropanes; Humans; Kinetics; Leucine; Lipid Metabolism, Inborn Errors; Oxidoreductases; Plants; Toxins, Biological; Valerates

1974
Biosynthesis of branched-chain amino acids in Schizosaccharomyces pombe: regulation of the enzymes involved in isoleucine, valine, and leucine synthesis.
    Canadian journal of biochemistry, 1974, Volume: 52, Issue:1

    Topics: Alcohol Oxidoreductases; Ascomycota; Cell-Free System; Chromatography, Gel; Culture Media; Hydro-Lyases; Hydrogen-Ion Concentration; Hydroxybutyrates; Isoleucine; Isomerases; Keto Acids; Kinetics; Lactates; Leucine; Malates; Oxo-Acid-Lyases; Pyruvates; Spectrophotometry; Spectrophotometry, Ultraviolet; Threonine; Transaminases; Valerates; Valine

1974
Role of the leu-3 cistron in the regulation of the synthesis of isoleucine and valine biosynthetic enzymes of Neurospora.
    Journal of bacteriology, 1974, Volume: 118, Issue:2

    Topics: Alcohol Oxidoreductases; Cell-Free System; Dicarboxylic Acids; Enzyme Repression; Feedback; Genes; Hydro-Lyases; Isoleucine; Leucine; Mutation; Neurospora; Oxo-Acid-Lyases; Threonine; Valerates; Valine

1974
Distribution of the isopropylmalate pathway to leucine among diverse bacteria.
    Journal of bacteriology, 1974, Volume: 118, Issue:3

    Topics: Alcohol Oxidoreductases; Bacteria; Cell-Free System; Dicarboxylic Acids; Leucine; Oxo-Acid-Lyases; Species Specificity; Valerates

1974
Effects of maple syrup urine disease metabolites on mouse L-fibroblasts in vitro: a fine structural and biochemical study.
    Journal of neurochemistry, 1974, Volume: 22, Issue:6

    Topics: Animals; Caprylates; Carbon Radioisotopes; Cell Count; Cell Division; Chromatography, Thin Layer; Humans; Hydrogen-Ion Concentration; Isoleucine; Keto Acids; L Cells; Leucine; Maple Syrup Urine Disease; Mice; Microscopy, Electron; Time Factors; Tritium; Valerates

1974
Cross-linking of Salmonella isopropylmalate synthesis with dimethyl suberimidate: evidence for antagonistic effects of leucine and acetyl-CoA on the guaternary structure.
    Biochemical and biophysical research communications, 1971, May-21, Volume: 43, Issue:4

    Topics: Acyltransferases; Chemical Phenomena; Chemistry; Coenzyme A; Detergents; Dicarboxylic Acids; Electrophoresis; Imides; Kinetics; Leucine; Macromolecular Substances; Malates; Molecular Weight; Nitriles; Protein Denaturation; Salmonella typhimurium; Sulfuric Acids; Valerates

1971
Alpha-isopropylmalate synthase from Salmonella typhimurium. Carboxypeptidase digestion studies of parent and feedback-insensitive enzymes.
    Biochimica et biophysica acta, 1971, Dec-15, Volume: 250, Issue:3

    Topics: Acyltransferases; Amino Acid Sequence; Amino Acids; Ammonium Sulfate; Arginine; Carboxypeptidases; Chemical Precipitation; Chromatography; Chromatography, Gel; Chromosome Mapping; Dicarboxylic Acids; Feedback; Genetics, Microbial; Hydroxyapatites; Leucine; Mutation; Salmonella typhimurium; Transduction, Genetic; Valerates; Valine

1971
Alpha-isopropylmalate synthase from Salmonella typhimurium--amino acid composition, NH 2 -terminal analysis, and fingerprint analysis.
    Biochimica et biophysica acta, 1971, Dec-15, Volume: 250, Issue:3

    Topics: Acyltransferases; Amino Acids; Ammonium Sulfate; Carbon Isotopes; Chemical Precipitation; Chromatography; Chromatography, Gel; Chromatography, Paper; Cyanates; Dicarboxylic Acids; Electrophoresis, Disc; Electrophoresis, Paper; Hydroxyapatites; Isotope Labeling; Kinetics; Leucine; Peptides; Salmonella typhimurium; Serine; Sulfhydryl Compounds; Trypsin; Valerates

1971
Alpha-isopropylmalate synthase from Salmonella typhimurium. Purification and properties.
    The Journal of biological chemistry, 1969, Apr-25, Volume: 244, Issue:8

    Topics: Binding Sites; Caproates; Chemical Phenomena; Chemistry; Chromatography, Gel; Chromatography, Ion Exchange; Dialysis; Edetic Acid; Electrophoresis, Disc; Feedback; Filtration; Hydrogen-Ion Concentration; Keto Acids; Kinetics; Leucine; Ligases; Mercury; Methods; Models, Biological; Salmonella typhimurium; Ultracentrifugation; Valerates

1969
[On the biogenetic origin of the isovaleryl group of mammeisin (4-phenyl coumarin)].
    Comptes rendus hebdomadaires des seances de l'Academie des sciences. Serie D: Sciences naturelles, 1969, Apr-21, Volume: 268, Issue:16

    Topics: Carbon Isotopes; Chromatography, Thin Layer; Coumarins; Crystallization; Leucine; Plants; Valerates

1969
[The alpha-isopropylmalate synthetase of Hydrogenomonas H 16].
    Archiv fur Mikrobiologie, 1969, Volume: 68, Issue:1

    Topics: Acetates; Acyltransferases; Carbon Isotopes; Catalysis; Chromatography, Paper; Coenzyme A; Culture Media; Dicarboxylic Acids; Fluorometry; Hydrogen-Ion Concentration; Isoenzymes; Isoleucine; Keto Acids; Leucine; Mutation; Pseudomonas; Valerates; Valine

1969
Antimetabolites produced by microorganisms. II. L-2-amino-4-pentynoic acid.
    The Journal of antibiotics, 1971, Volume: 24, Issue:4

    Topics: Amino Acids; Antimetabolites; Bacillus subtilis; Chromatography, Ion Exchange; Chromatography, Thin Layer; Culture Media; Depression, Chemical; Fermentation; Hydrolysis; Leucine; Magnetic Resonance Spectroscopy; Methionine; Oxidation-Reduction; Spectrophotometry; Streptomyces; Valerates

1971
Fatty acid-requiring mutant of bacillus subtilis defective in branched chain alpha-keto acid dehydrogenase.
    The Journal of biological chemistry, 1971, Sep-10, Volume: 246, Issue:17

    Topics: Bacillus subtilis; Butyrates; Caproates; Carbon Isotopes; Carboxylic Acids; Chemical Phenomena; Chemistry; Chromatography, Gas; Fatty Acids; Fluorine; Genetics, Microbial; Isoleucine; Keto Acids; Leucine; Mass Spectrometry; Mutation; Nitriles; Oxidoreductases; Valerates; Valine

1971
Isovaleric and -methylbutyric acidemias induced by hypoglycin A: mechanism of Jamaican vomiting sickness.
    Science (New York, N.Y.), 1972, Jan-07, Volume: 175, Issue:4017

    Topics: Animals; Blood Glucose; Butyrates; Cyclopropanes; Fruit; Glutarates; Glycine; Leucine; Male; Plant Extracts; Rats; Valerates

1972
Specificity of Aeromonas aminopeptidase toward amino acid amides and dipeptides.
    The Journal of biological chemistry, 1972, Feb-25, Volume: 247, Issue:4

    Topics: Aeromonas; Alanine; Amides; Amino Acids; Aminocaproates; Aminopeptidases; Dipeptides; Glycine; Isoleucine; Kinetics; Leucine; Methionine; Phenylalanine; Structure-Activity Relationship; Tryptophan; Tyrosine; Valerates; Valine

1972
Dietary treatment of an infant with isovaleric acidemia.
    Pediatrics, 1972, Volume: 49, Issue:4

    Topics: Acidosis; Diet Therapy; Fatty Acids; Humans; Infant; Leucine; Male; Valerates

1972
Quantitative studies on nitrogen metabolism in the bovine rumen. The rate of proteolysis of casein and ovalbumin and the release and metabolism of free amino acids.
    The British journal of nutrition, 1972, Volume: 27, Issue:2

    Topics: Amino Acids; Ammonia; Animals; Autoanalysis; Caseins; Cattle; Electrophoresis; Female; Half-Life; Isoleucine; Leucine; Lithium; Lysine; Nitrogen; Ovalbumin; Rumen; Valerates; Valine

1972
Beta-methylcrotonyl-CoA carboxylase deficiency: a new metabolic error in leucine degradation.
    Pediatrics, 1972, Volume: 49, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Bronchopneumonia; Butyrates; Carbon Dioxide; Carbon-Carbon Ligases; Chromatography, Gas; Diet Therapy; Female; Glycine; Humans; Infant; Leucine; Ligases; Mass Spectrometry; Neurologic Manifestations; Odorants; Pentanols; Valerates

1972
Biosynthesis of triacylglycerols containing isovaleric acid.
    Biochemical and biophysical research communications, 1972, Jul-25, Volume: 48, Issue:2

    Topics: Animals; Carbon Dioxide; Carbon Isotopes; Chromatography, Gas; Chromatography, Thin Layer; Coenzyme A; Dolphins; Fatty Acids; Kinetics; Leucine; Lipids; Stereoisomerism; Triglycerides; Valerates

1972
A simplified method for the preparation of 14 C-labelled branched-chain -oxo acids.
    The Biochemical journal, 1972, Volume: 126, Issue:2

    Topics: Amino Acid Oxidoreductases; Caproates; Carbon Isotopes; Catalase; Chromatography, Thin Layer; Isoleucine; Isotope Labeling; Keto Acids; Leucine; Methods; Valerates; Valine

1972
Alpha-isopropylmalate synthase from yeast: purification, kinetic studies, and effect of ligands on stability.
    Journal of bacteriology, 1972, Volume: 110, Issue:3

    Topics: Acyltransferases; Cell Fractionation; Chemical Precipitation; Chromatography; Chromatography, Gel; Coenzyme A; Dicarboxylic Acids; Enzyme Activation; Feedback; Glycols; Hot Temperature; Hydrogen-Ion Concentration; Hydroxyapatites; Keto Acids; Kinetics; Leucine; Molecular Weight; Saccharomyces; Streptomycin; Sulfates; Valerates

1972
Biosynthesis of the isovaleryl and senecioyl moieties of tropane alkaloids.
    Planta medica, 1972, Volume: 22, Issue:1

    Topics: Alkaloids; Datura stramonium; Leucine; Plants; Plants, Medicinal; Plants, Toxic; Tropanes; Valerates; Valine

1972
A rapid method for the quantitative analysis of short-chain fatty acids in serum or plasma.
    Clinica chimica acta; international journal of clinical chemistry, 1971, Volume: 34, Issue:3

    Topics: Acetates; Amino Acid Metabolism, Inborn Errors; Butyrates; Caproates; Chromatography, Gas; Fatty Acids; Leucine; Methods; Propionates; Time Factors; Valerates

1971
The dissimilation of leucine, isoleucine and valine to volatile fatty acids by adult Fasciola hepatica.
    International journal for parasitology, 1971, Volume: 1, Issue:3

    Topics: Acetates; Butyrates; Carbon Isotopes; Fasciola hepatica; Fatty Acids, Volatile; Glucose; Isoleucine; Leucine; Propionates; Valerates; Valine

1971
Isovaleric acidemia: a new genetic defect of leucine metabolism.
    Proceedings of the National Academy of Sciences of the United States of America, 1966, Volume: 56, Issue:1

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Butyrates; Caproates; Child, Preschool; Chromatography, Gas; Coenzyme A; Fatty Acids; Female; Humans; Leucine; Male; Propionates; Valerates

1966
Hypoglycin A: a specific inhibitor of isovaleryl CoA dehydrogenase.
    Proceedings of the National Academy of Sciences of the United States of America, 1971, Volume: 68, Issue:1

    Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Animals; Butyrates; Caproates; Carbon Dioxide; Carbon Isotopes; Carnitine; Chromatography, Gas; Coenzyme A; Cyclopropanes; In Vitro Techniques; Isoleucine; Leucine; Male; Oxidoreductases; Plant Poisoning; Rats; Valerates; Vomiting

1971
Expression of the leucine operon.
    Journal of bacteriology, 1966, Volume: 91, Issue:4

    Topics: Genes; In Vitro Techniques; Isomerases; Leucine; Ligases; Mutation; Oxidoreductases; Salmonella typhimurium; Valerates

1966
Simple selection for end-product inhibitor-insensitive mutants in yeast.
    Journal of bacteriology, 1970, Volume: 101, Issue:3

    Topics: Acyltransferases; Crosses, Genetic; Dicarboxylic Acids; Diploidy; Drug Resistance, Microbial; Genetics, Microbial; Leucine; Ligases; Mutation; Saccharomyces; Valerates

1970
Ester and ether-linked lipids in the mandibular canal of a porpoise (Phocoena phocoena). Occurrence of isovaleric acid in glycerolipids.
    Biochemistry, 1970, Nov-10, Volume: 9, Issue:23

    Topics: Animals; Chromatography, Gas; Chromatography, Thin Layer; Dolphins; Esters; Ethers; Glycerol; Leucine; Lipid Metabolism; Mandible; Valerates

1970
Carbon dioxide fixation in green sulphur bacteria.
    The Biochemical journal, 1970, Volume: 120, Issue:2

    Topics: Acetates; Bacteria; Carbon Dioxide; Citric Acid Cycle; Fluoroacetates; Glutarates; Glycolysis; Iodoacetates; Isoleucine; Leucine; Metabolism; Photosynthesis; Polysaccharides, Bacterial; Pyruvates; Quaternary Ammonium Compounds; Valerates; Valine

1970
Branched chain amino acid aminotransferase. IV. Kinetics of the transamination reactions.
    The Journal of biological chemistry, 1970, Oct-10, Volume: 245, Issue:19

    Topics: Amines; Animals; Caproates; Caprylates; Dicarboxylic Acids; Enzyme Activation; Hydrogen-Ion Concentration; Ketoglutaric Acids; Kinetics; Leucine; Mercaptoethanol; Myocardium; Picolines; Swine; Transaminases; Valerates

1970
Inhibition of alpha-oxoglutarate and pyruvate oxidation by alpha-oxoderivatives of leucine and valine in rat tissues.
    Acta biochimica Polonica, 1970, Volume: 17, Issue:2

    Topics: Animals; Brain; Caproates; Citrates; Coenzyme A; Humans; Keto Acids; Ketoglutaric Acids; Kidney; Kinetics; Leucine; Malates; Maple Syrup Urine Disease; Metabolism; Mitochondria; Mitochondria, Liver; Mitochondria, Muscle; Myocardium; Oxidoreductases; Pyruvates; Rats; Valerates; Valine; Vibration

1970
Biosynthesis of long-chain hydrocarbons. II. Studies on the biosynthetic pathway in tobacco.
    Biochemistry, 1968, Volume: 7, Issue:3

    Topics: Acetates; Butyrates; Caproates; Caprylates; Carbon Isotopes; Chromatography, Thin Layer; Fatty Acids; Hydrocarbons; Isoleucine; Leucine; Lipid Metabolism; Nicotiana; Plants, Toxic; Valerates; Valine

1968
Metabolism of amino acids in protein-calorie-deficient rats.
    The Biochemical journal, 1969, Volume: 111, Issue:4

    Topics: Alanine; Amino Acids; Animals; Caproates; Carbon Isotopes; Caseins; Coenzyme A; Deficiency Diseases; Glutamates; Leucine; Liver; Phenylalanine; Protein Biosynthesis; Protein Deficiency; Rats; Valerates

1969
Amino acid and alpha-keto acid concentrations in plasma and blood of the liverless dog.
    The American journal of physiology, 1965, Volume: 209, Issue:5

    Topics: Amino Acids; Aminobutyrates; Animals; Blood; Caproates; Chromatography, Paper; Dogs; Hepatectomy; Isoleucine; Keto Acids; Ketoglutaric Acids; Lactates; Leucine; Methionine; Pyruvates; Valerates; Valine

1965
Importance of the isovalerate carboxylation pathway of leucine biosynthesis in the rumen.
    Applied microbiology, 1966, Volume: 14, Issue:5

    Topics: Animals; Carbon Isotopes; Cattle; Leucine; Oxidoreductases; Rumen; Valerates

1966
[Accumulation of free extracellular amino acids by Pseudomonas liquefaciens].
    Doklady Akademii nauk SSSR, 1966, Apr-01, Volume: 167, Issue:4

    Topics: Acids; Alanine; Amino Acids; Aminobutyrates; Ammonium Chloride; Chromatography; Fumarates; Lactates; Leucine; Levulinic Acids; Malates; Propionates; Pseudomonas; Succinates; Valerates; Valine

1966
The isolation and identification of N-isovalerylglycine from urine of patients with isovaleric acidemia.
    The Journal of biological chemistry, 1967, Jun-25, Volume: 242, Issue:12

    Topics: Acidosis; Amino Acids; Chemistry, Clinical; Child; Child, Preschool; Chromatography, Gas; Coenzyme A; Female; Humans; In Vitro Techniques; Leucine; Magnetic Resonance Spectroscopy; Male; Spectrum Analysis; Valerates

1967
Alpha-hydroxy acid oxidases in subcellular fractions from rat kidney.
    Biochemical and biophysical research communications, 1967, Jul-21, Volume: 28, Issue:2

    Topics: Amino Acids; Animals; Electrophoresis; Hydroxybutyrates; In Vitro Techniques; Isoleucine; Kidney; Lactates; Leucine; Methionine; Mitochondria; Oxidoreductases; Rats; Valerates

1967
Isovaleric acidemia.
    Canadian Medical Association journal, 1967, Nov-11, Volume: 97, Issue:20

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Humans; Infant, Newborn; Leucine; Odorants; Valerates

1967
3-Hydroxy-3-methylglutaric aciduria.
    Journal of neurogenetics, 1984, Volume: 1, Issue:2

    Topics: Cells, Cultured; Female; Fibroblasts; Follow-Up Studies; Glutarates; Humans; Infant, Newborn; Leucine; Meglutol; Oxo-Acid-Lyases; Skin; Valerates

1984
Glycine in acute management of isovalericacidaemia.
    Lancet (London, England), 1980, Feb-09, Volume: 1, Issue:8163

    Topics: Amino Acid Metabolism, Inborn Errors; Female; Glycine; Humans; Infant; Leucine; Oxidoreductases; Valerates

1980
Inherited 3-methylglutaconic aciduria in two brothers--another defect of leucine metabolism.
    The Journal of pediatrics, 1982, Volume: 101, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Glutarates; Humans; Hydro-Lyases; Leucine; Male; Meglutol; Speech Disorders; Valerates

1982
Stable isotope dilution analysis of 3-hydroxyisovaleric acid in amniotic fluid: contribution to the prenatal diagnosis of inherited disorders of leucine catabolism.
    Journal of inherited metabolic disease, 1984, Volume: 7, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Amniocentesis; Amniotic Fluid; Carboxy-Lyases; Female; Humans; Leucine; Pregnancy; Prenatal Diagnosis; Valerates

1984
The relationship between the branched chain amino acids and their alpha-ketoacids in maple syrup urine disease.
    Pediatric research, 1984, Volume: 18, Issue:9

    Topics: Amino Acids, Branched-Chain; Caproates; Child; Child, Preschool; Female; Hemiterpenes; Humans; Infant; Infant, Newborn; Keto Acids; Leucine; Male; Maple Syrup Urine Disease; Valerates; Valine

1984
The identification and the excretion pattern of isovaleryl glucuronide in the urine of patients with isovaleric acidemia.
    Pediatric research, 1984, Volume: 18, Issue:6

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Glucuronates; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates

1984
Release of leucine and isoleucine metabolites by perfused skeletal muscle and liver of rat.
    The International journal of biochemistry, 1983, Volume: 15, Issue:8

    Topics: 3-Hydroxybutyric Acid; Acetoacetates; Animals; Female; Hydroxybutyrates; Isoleucine; Keto Acids; Lactates; Lactic Acid; Leucine; Liver; Muscles; Rats; Rats, Inbred Strains; Valerates

1983
[Isovaleric aciduria].
    Casopis lekaru ceskych, 1983, Sep-02, Volume: 122, Issue:35

    Topics: Amino Acid Metabolism, Inborn Errors; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Pentanoic Acids; Valerates

1983
Partial purification and characterization of two enzymes involved in isovaleric acid synthesis in Clostridium bifermentans.
    Journal of general microbiology, 1983, Volume: 129, Issue:10

    Topics: Carboxy-Lyases; Chromatography, Gel; Chromatography, Ion Exchange; Clostridium; Deamination; Flavin-Adenine Dinucleotide; Hemiterpenes; Hydrogen-Ion Concentration; Keto Acids; Leucine; Molecular Weight; Pentanoic Acids; Transaminases; Valerates

1983
Organic aciduria associated with isovaleric acidemia.
    Clinical chemistry, 1983, Volume: 29, Issue:5

    Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant; Leucine; Pentanoic Acids; Valerates

1983
Organic acidurias: approach, results and clinical relevance.
    Ciba Foundation symposium, 1982, Volume: 87

    Topics: Child; Child, Preschool; Crotonates; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Infant; Keto Acids; Leucine; Ligases; Male; Metabolism, Inborn Errors; Oxidoreductases; Oxo-Acid-Lyases; Pregnancy; Prenatal Diagnosis; Valerates

1982
Gas-chromatographic/mass spectrometric detection of 3-hydroxy-3-methylglutaryl-CoA lyase deficiency in double first cousins.
    Clinical chemistry, 1982, Volume: 28, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Hydroxy Acids; Infant; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Valerates

1982
Comparative utilization of the alpha-keto and D- and L-alpha-hydroxy analogs of leucine, isoleucine and valine by chicks and rats.
    The Journal of nutrition, 1982, Volume: 112, Issue:10

    Topics: Animals; Caproates; Chickens; Hemiterpenes; Isoleucine; Keto Acids; Leucine; Male; Pentanoic Acids; Rats; Species Specificity; Structure-Activity Relationship; Valerates; Valine

1982
Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
    Pediatric research, 1982, Volume: 16, Issue:9

    Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Hydroxybutyrates; Leucine; Pentanoic Acids; Valerates

1982
[Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
    Tijdschrift voor kindergeneeskunde, 1982, Volume: 50, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidation-Reduction; Pentanoic Acids; Valerates

1982
4-hydroxyisovaleric acid: a new metabolite in isovaleric acidemia.
    European journal of pediatrics, 1981, Volume: 136, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Humans; Leucine; Valerates

1981
The pancytopenia of isovaleric acidemia.
    Pediatrics, 1980, Volume: 65, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Bone Marrow Examination; Female; Hematopoietic Stem Cells; Hemiterpenes; Humans; Infant, Newborn; Leucine; Male; Pancytopenia; Pentanoic Acids; Valerates

1980
Alpha-keto and alpha-hydroxy branched-chain acid interrelationships in normal humans.
    The Journal of nutrition, 1993, Volume: 123, Issue:9

    Topics: Adult; Amino Acids, Branched-Chain; Dietary Proteins; Evaluation Studies as Topic; Fasting; Female; Hemiterpenes; Humans; Isoleucine; Keto Acids; Leucine; Male; Mass Spectrometry; Oxidation-Reduction; Protein Binding; Time Factors; Valerates; Valine

1993
Ketogenic flux from lipids and leucine, assessment in 3-hydroxy-3-methylglutaryl CoA lyase deficiency.
    Biochemical Society transactions, 1995, Volume: 23, Issue:3

    Topics: Carnitine; Child; Humans; Ketone Bodies; Leucine; Lipid Metabolism; Magnetic Resonance Spectroscopy; Male; Oxo-Acid-Lyases; Valerates

1995
Characterization of plasma acylcarnitines in patients under valproate monotherapy using ESI-MS/MS.
    Clinical biochemistry, 2001, Volume: 34, Issue:8

    Topics: Adolescent; Adult; Aged; Anticonvulsants; Carnitine; Female; Humans; Leucine; Male; Middle Aged; Mitochondrial Trifunctional Protein; Multienzyme Complexes; Spectrometry, Mass, Electrospray Ionization; Valerates; Valproic Acid

2001
A novel biosynthetic pathway providing precursors for fatty acid biosynthesis and secondary metabolite formation in myxobacteria.
    The Journal of biological chemistry, 2002, Sep-06, Volume: 277, Issue:36

    Topics: Bacterial Proteins; Cloning, Molecular; Coenzyme A; DNA; Fatty Acids; Leucine; Magnetic Resonance Spectroscopy; Methacrylates; Models, Chemical; Stigmatella aurantiaca; Thiazoles; Valerates

2002
Indicators of marginal biotin deficiency and repletion in humans: validation of 3-hydroxyisovaleric acid excretion and a leucine challenge.
    The American journal of clinical nutrition, 2002, Volume: 76, Issue:5

    Topics: Adult; Biotin; Diet; Dose-Response Relationship, Drug; Egg White; Female; Humans; Leucine; Male; Time Factors; Valerates

2002
NMR spectroscopic studies on the late onset form of 3-methylglutaconic aciduria type I and other defects in leucine metabolism.
    NMR in biomedicine, 2006, Volume: 19, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Brain; Female; Glutarates; Humans; Leucine; Magnetic Resonance Spectroscopy; Meglutol; Middle Aged; Valerates

2006
Biosynthesis of the cyclooligomer depsipeptide bassianolide, an insecticidal virulence factor of Beauveria bassiana.
    Fungal genetics and biology : FG & B, 2009, Volume: 46, Issue:5

    Topics: Amino Acid Sequence; Animals; Beauveria; Catalytic Domain; Cloning, Molecular; Depsipeptides; Fungal Proteins; Gene Silencing; Gene Targeting; Insecta; Insecticides; Leucine; Molecular Sequence Data; Peptide Synthases; Peptides, Cyclic; Protein Structure, Tertiary; Sequence Analysis; Survival Analysis; Valerates; Virulence Factors

2009
Alpha-ketoisocaproic acid and leucine provoke mitochondrial bioenergetic dysfunction in rat brain.
    Brain research, 2010, Apr-09, Volume: 1324

    Topics: Animals; Brain; Central Nervous System Agents; Electron Transport; Homeostasis; Keto Acids; Ketoglutarate Dehydrogenase Complex; Leucine; Maple Syrup Urine Disease; Membrane Potential, Mitochondrial; Mitochondrial Diseases; Mitochondrial Swelling; NADP; Oxygen Consumption; Prosencephalon; Rats; Rats, Wistar; Valerates

2010
Effects of β-hydroxy-β-methylbutyrate treatment in different types of skeletal muscle of intact and septic rats.
    Journal of physiology and biochemistry, 2010, Volume: 66, Issue:4

    Topics: Animals; Cathepsin B; Cathepsin L; Leucine; Lysosomes; Male; Muscle, Skeletal; Oxygen; Proteasome Endopeptidase Complex; Rats; Rats, Wistar; Sepsis; Time Factors; Valerates

2010
Urinary excretion of 3-hydroxyisovaleric acid and 3-hydroxyisovaleryl carnitine increases in response to a leucine challenge in marginally biotin-deficient humans.
    The Journal of nutrition, 2011, Volume: 141, Issue:11

    Topics: Adult; Biotin; Carnitine; Cohort Studies; Female; Humans; Leucine; Male; Valerates

2011
Inhibition of 3-methylcrotonyl-CoA carboxylase explains the increased excretion of 3-hydroxyisovaleric acid in valproate-treated patients.
    Journal of inherited metabolic disease, 2012, Volume: 35, Issue:3

    Topics: Biotinidase; Carbon-Carbon Ligases; Case-Control Studies; Chromatography, High Pressure Liquid; Enzyme Inhibitors; Gas Chromatography-Mass Spectrometry; Humans; Inhibitory Concentration 50; Kinetics; Leucine; Liver; Metabolomics; Models, Chemical; Valerates; Valproic Acid

2012
Effects of leucine and its metabolite β-hydroxy-β-methylbutyrate on human skeletal muscle protein metabolism.
    The Journal of physiology, 2013, Jun-01, Volume: 591, Issue:11

    Topics: Administration, Oral; Humans; Leucine; Male; Muscle, Skeletal; Protein Biosynthesis; Proteolysis; Tissue Distribution; Valerates; Young Adult

2013
Leucine and HMB differentially modulate proteasome system in skeletal muscle under different sarcopenic conditions.
    PloS one, 2013, Volume: 8, Issue:10

    Topics: Animals; Dietary Supplements; Hindlimb Suspension; Leucine; Male; Muscle, Skeletal; Organ Size; Phosphatidylinositol 3-Kinases; Proteasome Endopeptidase Complex; Proto-Oncogene Proteins c-akt; Rats; Sarcopenia; Valerates

2013
Protein synthesis in skeletal muscle of neonatal pigs is enhanced by administration of β-hydroxy-β-methylbutyrate.
    American journal of physiology. Endocrinology and metabolism, 2014, Jan-01, Volume: 306, Issue:1

    Topics: Animals; Animals, Newborn; Autophagy; Leucine; Muscle Proteins; Muscle, Skeletal; Peptide Initiation Factors; Phosphorylation; Protein Biosynthesis; Signal Transduction; Sus scrofa; TOR Serine-Threonine Kinases; Valerates

2014
Synergistic effects of polyphenols and methylxanthines with Leucine on AMPK/Sirtuin-mediated metabolism in muscle cells and adipocytes.
    PloS one, 2014, Volume: 9, Issue:2

    Topics: 3T3-L1 Cells; Adipocytes; AMP-Activated Protein Kinases; Animals; Caffeic Acids; Chlorogenic Acid; Ellagic Acid; Fatty Acids; Humans; Leucine; Mice; Muscle Cells; NAD; Oxidation-Reduction; Phosphodiesterase Inhibitors; Polyphenols; Protein Kinase Inhibitors; Resveratrol; Sirtuin 1; Stilbenes; Valerates; Xanthines

2014
Quantitative determination of β-hydroxymethylbutyrate and leucine in culture media and microdialysates from rat brain by UHPLC-tandem mass spectrometry.
    Analytical and bioanalytical chemistry, 2014, Volume: 406, Issue:12

    Topics: Animals; Blood-Brain Barrier; Brain; Brain Chemistry; Cattle; Chromatography, High Pressure Liquid; Culture Media; Leucine; Microdialysis; Rats; Rats, Sprague-Dawley; Tandem Mass Spectrometry; Valerates

2014
A (14)C-leucine absorption, distribution, metabolism and excretion (ADME) study in adult Sprague-Dawley rat reveals β-hydroxy-β-methylbutyrate as a metabolite.
    Amino acids, 2015, Volume: 47, Issue:5

    Topics: Animals; Biological Transport; Carbon Radioisotopes; Chromatography, High Pressure Liquid; Dipeptides; Intestinal Absorption; Keto Acids; Leucine; Male; Mass Spectrometry; Oxidation-Reduction; Rats; Rats, Sprague-Dawley; Valerates

2015
Genome-based analysis and gene dosage studies provide new insight into 3-hydroxy-4-methylvalerate biosynthesis in Ralstonia eutropha.
    Journal of bacteriology, 2015, Volume: 197, Issue:8

    Topics: Bacterial Proteins; Cupriavidus necator; Gene Dosage; Gene Expression Regulation, Bacterial; Genome, Bacterial; Leucine; Valerates; Valine

2015
Quantification of β-hydroxymethylbutyrate and leucine by ultrahigh performance liquid chromatography tandem mass spectrometry at different situations and stages of a rodent life.
    Journal of chromatography. B, Analytical technologies in the biomedical and life sciences, 2015, Jul-15, Volume: 995-996

    Topics: Animals; Animals, Newborn; Brain Chemistry; Chromatography, High Pressure Liquid; Fasting; Female; Lactation; Leucine; Limit of Detection; Male; Milk; Rats; Rats, Sprague-Dawley; Reproducibility of Results; Tandem Mass Spectrometry; Valerates

2015
Age associated decline in the conversion of leucine to β-Hydroxy-β-Methylbutyrate in rats.
    Experimental gerontology, 2016, Volume: 80

    Topics: 4-Hydroxyphenylpyruvate Dioxygenase; Aging; Animals; Dietary Supplements; Humans; Keto Acids; Leucine; Liver; Male; Muscle, Skeletal; Rats; Rats, Sprague-Dawley; Valerates

2016
The relationship of endogenous plasma concentrations of β-Hydroxy β-Methyl Butyrate (HMB) to age and total appendicular lean mass in humans.
    Experimental gerontology, 2016, Volume: 81

    Topics: Absorptiometry, Photon; Adolescent; Adult; Age Factors; Aged; Anthropometry; Body Composition; Child; Dietary Supplements; Female; Hand Strength; Humans; India; Leucine; Male; Middle Aged; Muscle, Skeletal; Valerates

2016
Age-Related 1H NMR Characterization of Cerebrospinal Fluid in Newborn and Young Healthy Piglets.
    PloS one, 2016, Volume: 11, Issue:7

    Topics: Adenine; Animals; Animals, Newborn; Blood-Brain Barrier; Cerebrospinal Fluid; Creatinine; Crosses, Genetic; Female; Glutamine; Inositol; Leucine; Magnetic Resonance Spectroscopy; Metabolomics; Methylamines; Pentanoic Acids; Principal Component Analysis; Swine; Tyrosine; Valerates; Valine

2016
Effects of beta-hydroxy-beta-methylbutyrate (HMB) on the expression of ubiquitin ligases, protein synthesis pathways and contractile function in extensor digitorum longus (EDL) of fed and fasting rats.
    The journal of physiological sciences : JPS, 2018, Volume: 68, Issue:2

    Topics: Animals; Carrier Proteins; Fasting; Leucine; Ligases; Male; Muscle Contraction; Muscle, Skeletal; Phosphorylation; Rats; Rats, Wistar; Ubiquitin; Valerates

2018
Murine myoblast migration: influence of replicative ageing and nutrition.
    Biogerontology, 2017, Volume: 18, Issue:6

    Topics: Animals; Cell Movement; Cells, Cultured; Cellular Senescence; Leucine; Mice; Muscle, Skeletal; Myoblasts; Nutritional Status; Signal Transduction; Valerates

2017
β-Hydroxy-β-methyl Butyrate Is More Potent Than Leucine in Inhibiting Starvation-Induced Protein Degradation in C2C12 Myotubes.
    Journal of agricultural and food chemistry, 2018, Jan-10, Volume: 66, Issue:1

    Topics: Animals; Cell Line; Insulin; Keto Acids; Leucine; Mice; Muscle Fibers, Skeletal; Muscle Proteins; Phosphatidylinositol 3-Kinases; Proteolysis; Proto-Oncogene Proteins c-akt; SKP Cullin F-Box Protein Ligases; TOR Serine-Threonine Kinases; Tripartite Motif Proteins; Ubiquitin-Protein Ligases; Valerates

2018
Growth Responses of Preterm Pigs Fed Formulas with Different Protein Levels and Supplemented with Leucine or β-Hydroxyl β-Methylbutyrate.
    Nutrients, 2018, May-18, Volume: 10, Issue:5

    Topics: Animal Feed; Animal Nutritional Physiological Phenomena; Animals; Animals, Newborn; Birth Weight; Diet, High-Protein; Diet, Protein-Restricted; Dietary Proteins; Dietary Supplements; Female; Gestational Age; Leucine; Male; Nutritional Status; Parenteral Nutrition; Premature Birth; Sex Factors; Sus scrofa; Valerates; Weight Gain

2018
β-hydroxy-β-methyl butyrate promotes leucine metabolism and improves muscle fibre composition in growing pigs.
    Journal of animal physiology and animal nutrition, 2018, Volume: 102, Issue:5

    Topics: Amino Acids, Branched-Chain; Animals; Butyrates; Dietary Supplements; Leucine; Muscle Fibers, Skeletal; Muscle, Skeletal; Swine; Valerates

2018
β-hydroxy-β-methylbutyrate (HMB) improves mitochondrial function in myocytes through pathways involving PPARβ/δ and CDK4.
    Nutrition (Burbank, Los Angeles County, Calif.), 2019, Volume: 60

    Topics: Animals; Cell Culture Techniques; Cyclin-Dependent Kinase 4; Humans; Leucine; Mitochondria; Muscle Cells; PPAR gamma; PPAR-beta; Signal Transduction; Valerates

2019
Effects of beta-hydroxy-beta-methylbutyrate supplementation on skeletal muscle in healthy and cirrhotic rats.
    International journal of experimental pathology, 2019, Volume: 100, Issue:3

    Topics: Amino Acids, Branched-Chain; Animals; Carbon Tetrachloride; Dietary Supplements; Leucine; Liver; Liver Cirrhosis; Muscle, Skeletal; Rats, Wistar; Valerates

2019
Suppression of protein degradation by leucine requires its conversion to β-hydroxy-β-methyl butyrate in C2C12 myotubes.
    Aging, 2019, 12-24, Volume: 11, Issue:24

    Topics: Animals; Leucine; Mice; Muscle Fibers, Skeletal; Proteolysis; Valerates

2019
2,3-Dihydroxyisovalerate production by Klebsiella pneumoniae.
    Applied microbiology and biotechnology, 2020, Volume: 104, Issue:15

    Topics: Biosynthetic Pathways; Butylene Glycols; Culture Media; Fermentation; Hydrogen-Ion Concentration; Industrial Microbiology; Klebsiella pneumoniae; Lactic Acid; Leucine; Oxygen; Valerates; Valine

2020
Biosynthesis of 3-Hydroxy-3-Methylbutyrate from l-Leucine by Whole-Cell Catalysis.
    Journal of agricultural and food chemistry, 2021, Mar-31, Volume: 69, Issue:12

    Topics: Biocatalysis; Hemiterpenes; Leucine; Pentanoic Acids; Valerates

2021