valerates has been researched along with glycine in 100 studies
Studies (valerates) | Trials (valerates) | Recent Studies (post-2010) (valerates) | Studies (glycine) | Trials (glycine) | Recent Studies (post-2010) (glycine) |
---|---|---|---|---|---|
2,251 | 294 | 457 | 35,163 | 756 | 8,415 |
Protein | Taxonomy | valerates (IC50) | glycine (IC50) |
---|---|---|---|
Glutamate receptor ionotropic, NMDA 1 | Rattus norvegicus (Norway rat) | 1.4852 | |
Sodium- and chloride-dependent glycine transporter 1 | Homo sapiens (human) | 106 | |
Glutamate receptor ionotropic, NMDA 2A | Rattus norvegicus (Norway rat) | 0.3253 | |
Glutamate receptor ionotropic, NMDA 2B | Rattus norvegicus (Norway rat) | 0.3253 | |
Glutamate receptor ionotropic, NMDA 2C | Rattus norvegicus (Norway rat) | 0.3253 | |
Glutamate receptor ionotropic, NMDA 2D | Rattus norvegicus (Norway rat) | 0.3253 | |
Glutamate receptor ionotropic, NMDA 3B | Rattus norvegicus (Norway rat) | 0.3253 | |
Glutamate receptor ionotropic, NMDA 3A | Rattus norvegicus (Norway rat) | 0.3253 | |
Sodium- and chloride-dependent glycine transporter 2 | Homo sapiens (human) | 128 |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 85 (85.00) | 18.7374 |
1990's | 3 (3.00) | 18.2507 |
2000's | 10 (10.00) | 29.6817 |
2010's | 2 (2.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Horton, RW | 1 |
Tanaka, K | 2 |
Carchon, H; Casaer, P; Corbeel, L; Eeckels, R; Eggermont, E; Jaeken, J | 1 |
Bartlett, K | 1 |
Wolf, B | 1 |
Debray-Ritzen, P; Kamoun, P; Parvy, P | 1 |
Kølvraa, S | 1 |
Constanti, A | 1 |
Horton, RW; Meldrum, BS | 1 |
Cohn, RM; Puschak, R; Rothman, R; Segal, S; Yudkoff, M | 1 |
Cohn, RM; Rothman, R; Segal, S; Yudkoff, M | 1 |
O'Brien, WE | 1 |
Beccaria, L; Chiumello, G; Gianazza, E; Luppis, B; Righetti, PG | 1 |
Ehinger, B | 1 |
Mandell, R; Shih, VE; Tanaka, K | 1 |
Kelly, S; Leikhim, E | 1 |
Krieger, I; Tanaka, K | 1 |
Dembure, P; Elsas, L; Madsen, K; Naglak, M; Salvo, R | 1 |
Holme, E; Jacobson, CE; Kristiansson, B | 1 |
Bachmann, C; Dionisi-Vici, C; Graziani, MC; Sabetta, G | 1 |
Elsas, LJ; Naglak, M | 1 |
Mock, DM; Mock, NI; Weintraub, S | 1 |
Hagenfeldt, L; Naglo, AS | 1 |
Goodman, SI; Hack, AM; Hine, DG; Tanaka, K | 1 |
Bartlett, K; Cannon, RA; Conde, C; Gomez Vazquez, J; Lipson, M; Middleton, B; Nyhan, WL; Romanos, A; Sweetman, L | 1 |
Inoue, F; Maltby, DA; Millington, DS; Roe, CR | 1 |
Baker, H; Baswell, DL; Holman, RT; Mock, DM; Sweetman, L | 1 |
Bradley, D; Chalmers, RA; de Sousa, C; Stacey, TE; Tracey, BM; Weaver, C | 1 |
Bradley, D; Chalmers, RA; de Sousa, C; Stacey, TE; Tracey, BM; Weaver, CM | 1 |
Hynes, MJ; Pateman, JA | 1 |
Draffan, GH; Gompertz, D; Hull, D; Watts, JL | 1 |
Erickson, AM; Kurtz, DJ; Levy, HL; Lott, IT | 1 |
Biscoe, TJ; Duggan, AW; Lodge, D | 1 |
Bohunicky, L; Cerny, V; Halko, J; Koza, I; Krizan, Z; Petrek, C; Poliakova, L | 1 |
Johns, RB; Looney, FD; Whelan, DJ | 1 |
De Groat, WC; Lalley, PM; Saum, WR | 1 |
Kimura, K | 1 |
George, JM; Kier, LB | 1 |
Ikeda, K; Roberts, E; Swagel, MW | 1 |
Koda, A; Mori, H; Nagai, H; Watanabe, S | 1 |
Eldjarn, L; Jellum, E; Stokke, O | 1 |
Drobník, J; Spacek, P; Wichterle, O | 1 |
Kokkonen, H; Mäntsälä, P; Nurmikko, V | 1 |
Shigesada, K | 1 |
Capek, A; Cerný, A; Semonský, M | 1 |
Ando, T; Bachmann, C; Nyhan, WL; Rasmussen, K; Scott, R; Smith, EK | 1 |
Daum, RS; Delvin, E; Goldman, H; Lamm, P; Mamer, OA; Scriver, CR | 1 |
Beart, PM; Johnston, GA | 1 |
Kean, EA; Rainford, IJ | 1 |
Evered, DF; Hargreaves, BM | 1 |
Bartlett, K; Blair, D; Gompertz, D; Stern, CM | 1 |
Bartlett, K; Gompertz, D | 1 |
Ajl, SJ; Rabin, R; Reeves, HC; Wegener, WS | 1 |
Koga, T; Ressler, C | 1 |
Barker, HA; Winnacker, EL | 1 |
Folk, JE; Gross, M | 1 |
Isselbacher, KJ; Shih, V; Tanaka, K | 1 |
Prescott, JM; Wagner, FW; Wilkes, SH | 1 |
Draffan, GH; Gompertz, D | 1 |
Eldjarn, L; Jellum, E; Pande, H; Stokke, O; Waaler, PE | 1 |
Barrio, JR; Domínguez, JM; Gallina, DL; Hoschoian, JC | 1 |
Mády, G; Moravcsik, E; Otvös, L | 1 |
Cerný, V | 1 |
Reisener, HJ | 1 |
Cook, ES; Nutini, LG; Tanaka, K; Tsuchiya, Y | 1 |
Austic, RE; Nesheim, MC | 1 |
Boyarsky, LL; Wheeler, DD | 1 |
Engberg, I; Ten Bruggencate, G | 1 |
Behki, RM; Hochster, RM | 1 |
Ghadially, FN; Neame, KD | 1 |
Prieto, EC; Velazquez, A | 1 |
Audenaert, SM; Squillaro, EJ; Wilson, WG | 1 |
Hine, DG; Tanaka, K | 2 |
Bohan, TP; Kahler, SG; Maltby, DA; Millington, DS; Roe, CR | 1 |
Bartlett, K; Leonard, JV; Ng, H | 1 |
Batenburg-Plenter, AM; Bruinvis, L; Duran, M; Ketting, D; van Pelt, BC; Wadman, SK | 1 |
Burnham, BF; Kushner, JP; Morton, KA; Straka, JG | 1 |
Gregersen, N; Hobolth, N; Kølvraa, S; Lauritzen, R; Rasmussen, K; Rosleff, F | 1 |
Burnham, BF; Horton, WJ; Kushner, JP; Morton, KA | 1 |
Inoue, Y; Kameyama, J; Momoi, T; Shigematsu, Y; Sudo, M; Suzuki, Y | 1 |
Bakkeren, JA; Houben, ML; Ruitenbeek, W; Sengers, RC; Trijbels, JM; Van der Zeè, SP | 1 |
Al-Bassam, SS; Sherratt, HS | 1 |
Dahlberg, L; Schuberth, J | 1 |
Berry, SA; Nyhan, WL; Thuy, LP; Tuchman, M | 1 |
Berry, SA; Gage, DA; Huang, ZH; Iwamoto, T; Johnston, K; Millington, DS; Packman, S; Röschinger, W; Sweetman, L; Yano, S | 1 |
Bakkeren, J; Baumgartner, R; de Jong, J; Mourmans, J; Suormala, T; van Diggelen, OP; Wendel, U; Wevers, R | 1 |
Almashanu, S; Baumgartner, ER; Baumgartner, MR; Dantas, MF; Fowler, B; Friebel, D; Gebhardt, B; Giunta, C; Hoffmann, GF; Suormala, T; Valle, D | 1 |
Andresen, BS; Boneh, A; Gutman, A; Korman, SH; Pitt, JJ; Zeharia, A | 1 |
Baumgartner, MR; Baykal, T; Can, G; Dantas, MF; Demir, F; Demirkol, M; Fowler, B; Gokcay, GH; Ince, Z | 1 |
Barea, L; Baumgartner, MR; Dantas, MF; Fowler, B; Giugliani, R; Graziadio, C; Paskulin, G; Perla, A; Pinto, L; Rosa, R; Vargas, C; Wajner, M; Zen, P | 1 |
Yoon, HR | 1 |
Andresen, BS; Engel, K; Ensenauer, R; Häberle, J; Lehnert, W; Mégarbané, A; Reich, H; Röschinger, W; Sass, JO; Schirrmacher, O; Steuerwald, U; Zschocke, J | 1 |
Baldellou, A; Briones, P; Campistol, J; Cortés, N; Delpiccolo, C; Fernández, C; Fons, C; Fuentes-Castelló, MA; García-Villoria, J; González, I; Hernández-Gonzalez, A; Messeguer, A; Navarro-Sastre, A; Pérez-Cerdá, C; Ribes, A | 1 |
Calado, AR; Faustino, CM; Garcia-Rio, L | 1 |
Baumgartner, MR; Biberoglu, G; Demir, E; Eminoglu, FT; Hasanoglu, A; Okur, I; Ozcelik, AA; Tumer, L | 1 |
Amaral, AU; Beskow, AP; da Silva, Lde B; Fernandes, CG; Leipnitz, G; Ribeiro, CA; Seminotti, B; Vargas, CR; Wajner, M; Zanatta, A | 1 |
Choi, JH; Jung, CW; Kim, GH; Kim, JH; Lee, BH; Lee, J; Yoo, HW | 1 |
Afroze, B; Ali, ZZ; Fatimah, M; Jafri, L; Jamil, A; Khan, AH; Majid, H; Yusufzai, N | 1 |
1 review(s) available for valerates and glycine
Article | Year |
---|---|
Alternate pathways of metabolism of short-chain fatty acids.
Topics: Acetates; Acetoacetates; Carbon Dioxide; Escherichia coli; Fatty Acids; Glutarates; Glycine; Glyoxylates; Ketoglutaric Acids; Lyases; Malates; Mutation; Oxaloacetates; Propionates; Pyruvates; Valerates | 1968 |
99 other study(ies) available for valerates and glycine
Article | Year |
---|---|
The role of 2-keto-4-pentenoic acid in seizures induced by allylglycine.
Topics: Animals; Brain; Glutamate Decarboxylase; Glycine; Hydrogen-Ion Concentration; Keto Acids; Kinetics; Mice; Pentanoic Acids; Seizures; Time Factors; Valerates | 1978 |
Ackee poisoning.
Topics: Animals; Butyrates; Dicarboxylic Acids; Foodborne Diseases; Fruit; Glycine; Humans; Hypoglycins; Rats; Valerates | 1977 |
Dipropylacetate (valproate) and glycine metabolism.
Topics: Epilepsy; Glycine; Humans; Infant; Valerates; Valproic Acid | 1977 |
Sodium valproate and hyperglycinaemia.
Topics: Acetyltransferases; Glycine; Valerates; Valproic Acid | 1977 |
Dipropylacetate and propionyl CoA carboxylase.
Topics: Carboxy-Lyases; Glycine; Humans; Valerates; Valproic Acid | 1978 |
[Hyperglycinuria induced by n-dipropylacetate. Possible model of propionic acidemia].
Topics: Child; Child, Preschool; Glycine; Humans; Infant; Metabolic Diseases; Models, Biological; Propionates; Valerates; Valproic Acid | 1977 |
Inhibition of the glycine cleavage system by branched-chain amino acid metabolites.
Topics: Amino Acids, Branched-Chain; Animals; Butyrates; Coenzyme A; Glycine; Mitochondria, Liver; Rats; Valerates | 1979 |
The GABA dose/conductance relationship on lobster muscle.
Topics: Amino Acids; Amino Acids, Neutral; Animals; Bicuculline; Dose-Response Relationship, Drug; Electric Conductivity; GABA Antagonists; gamma-Aminobutyric Acid; Glycine; Guanidines; In Vitro Techniques; Muscles; Nephropidae; Picrotoxin; Piperazines; Propionates; Valerates | 1979 |
A comparison of the effects of allylglycine and 2-keto-4-pentenoic acid on cerebral glutamic acid decarboxylase activity and convulsions in mice [proceedings].
Topics: Animals; Brain; Carboxy-Lyases; Glutamate Decarboxylase; Glycine; Keto Acids; Mice; Pentanoic Acids; Seizures; Valerates | 1977 |
Glycine therapy in isovaleric acidemia.
Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Drug Administration Schedule; Female; Glycine; Humans; Keto Acids; Ketone Bodies; Lactates; Leucine; Pyruvates; Valerates | 1978 |
Isovaleric acidemia: use of glycine therapy in neonates.
Topics: Amino Acid Metabolism, Inborn Errors; Female; Glycine; Humans; Infant, Newborn; Male; Time Factors; Valerates | 1978 |
Inhibition of glycine synthase by branched-chain alpha-keto acids. A possible mechanism for abnormal glycine metabolism in ketotic hyperglycinemia.
Topics: Acidosis; Acyl Coenzyme A; Animals; Caproates; Glycine; Keto Acids; Ketosis; Liver; Male; Rats; Transferases; Valerates | 1978 |
Hemoglobin A1C separation by isoelectric focusing.
Topics: Alanine; Aminocaproic Acid; Diabetes Mellitus, Type 1; Glycine; Hemoglobin A; Histidine; Humans; Isoelectric Focusing; Proline; Threonine; Valerates | 1978 |
Swelling of rabbit retinal amacrines in response to omega-amino acids.
Topics: Alanine; Amino Acids; Animals; gamma-Aminobutyric Acid; Glutamates; Glycine; Rabbits; Retina; Taurine; Valerates; Valine | 1977 |
Metabolism of [1-(14)C] and [2-(14)C] leucine in cultured skin fibroblasts from patients with isovaleric acidemia. Characterization of metabolic defects.
Topics: 2-Methyl-4-chlorophenoxyacetic Acid; Amino Acid Metabolism, Inborn Errors; Carbon Dioxide; Cell Line; Cells, Cultured; Depression, Chemical; Fibroblasts; Flavin-Adenine Dinucleotide; Glycine; Humans; Leucine; Maple Syrup Urine Disease; Oxidation-Reduction; Skin; Succinates; Valerates; Valine | 1976 |
Isovalerylglycine detection by thin-layer chromatography: additional observations.
Topics: Child; Chromatography, Gas; Chromatography, Thin Layer; Evaluation Studies as Topic; Glycine; Humans; Hydroxybutyrates; Ketosis; Male; Methods; Valerates | 1975 |
Therapeutic effects of glycine in isovaleric acidemia.
Topics: Acidosis; Alkalies; Amino Acid Metabolism, Inborn Errors; Child; Female; Glycine; Humans; Inactivation, Metabolic; Ketosis; Oxidoreductases; Valerates | 1976 |
The treatment of isovaleric acidemia with glycine supplement.
Topics: Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1988 |
Biotin-responsive multiple carboxylase deficiency in an 8-year-old boy with normal serum biotinidase and fibroblast holocarboxylase-synthetase activities.
Topics: Amidohydrolases; Biotin; Biotinidase; Carbon-Nitrogen Ligases; Child; Fibroblasts; Glycine; Humans; Kinetics; Ligases; Male; Multiple Carboxylase Deficiency; Valerates | 1988 |
Laryngeal stridor as a leading symptom in a biotinidase-deficient patient.
Topics: Amidohydrolases; Biotinidase; Female; Glycine; Humans; Infant; Lactates; Larynx; Propionates; Valerates | 1988 |
Acute and chronic-intermittent isovaleric acidemia: diagnosis and glycine therapy.
Topics: Acute Disease; Child; Child, Preschool; Chronic Disease; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1988 |
Abnormal organic aciduria in biotin deficiency: the rat is similar to the human.
Topics: Animals; Biotin; Disease Models, Animal; Gas Chromatography-Mass Spectrometry; Glycine; Male; Random Allocation; Rats; Rats, Inbred Strains; Valerates | 1988 |
New conjugated urinary metabolites in intermediate type maple syrup urine disease.
Topics: Amino Acids; Amino Acids, Branched-Chain; Carboxylic Acids; Female; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant; Lactates; Lactic Acid; Maple Syrup Urine Disease; Valerates | 1987 |
Stable isotope dilution analysis of isovalerylglycine in amniotic fluid and urine and its application for the prenatal diagnosis of isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amniotic Fluid; Female; Gas Chromatography-Mass Spectrometry; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Risk; Valerates | 1986 |
3-Ketothiolase deficiency.
Topics: 3-Hydroxybutyric Acid; Acetyl Coenzyme A; Acetyl-CoA C-Acyltransferase; Acyl Coenzyme A; Acyltransferases; Child; Female; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Ketosis; Male; Valerates | 1986 |
Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Proteins; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates | 1987 |
Biotin deficiency complicating parenteral alimentation: diagnosis, metabolic repercussions, and treatment.
Topics: Alopecia; Biotin; Citrates; Diagnosis, Differential; Erythema; Fatty Acids, Essential; Female; Glycine; Humans; Infant; Isomerism; Lactates; Lactic Acid; Male; Nervous System Diseases; Parenteral Nutrition; Valerates; Zinc | 1985 |
L-carnitine and glycine therapy in isovaleric acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates | 1985 |
The response to L-carnitine and glycine therapy in isovaleric acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Carboxylic Acids; Carnitine; Child, Preschool; Combined Modality Therapy; Drug Therapy, Combination; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates | 1986 |
The use of amides as nitrogen sources by Aspergillus nidulans.
Topics: Acetamides; Acrylates; Amides; Amidohydrolases; Arylformamidase; Aspergillus; Barbiturates; Butyrates; Carbamates; Enzyme Induction; Formamides; Fumarates; Glycine; Glycolates; Lactates; Malonates; Niacinamide; Nitrogen; Phenylacetates; Propionates; Valerates | 1970 |
Biotin-responsive beta-methylcrotonylglycinuria.
Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Chromatography, Gas; Fatty Acids; Glycine; Humans; Infant; Leucine; Male; Partial Pressure; Valerates; Valine; Vomiting | 1971 |
Isovaleric acidemia: results of family study and dietary treatment.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Child; Child, Preschool; Developmental Disabilities; Diet Therapy; Fatty Acids; Female; Glycine; Humans; Infant, Newborn; Intellectual Disability; Intelligence Tests; Leucine; Male; Odorants; Pedigree; Valerates | 1973 |
Antagonism between bicuculline, strychnine, and picrotoxin and depressant amino-acids in the rat nervous system.
Topics: Alanine; Alkaloids; Amino Acids; Aminobutyrates; Animals; Central Nervous System; Central Nervous System Stimulants; Cerebral Cortex; Dioxoles; Drug Antagonism; Electric Stimulation; Glycine; In Vitro Techniques; Isoquinolines; Picrotoxin; Rats; Receptors, Drug; Sciatic Nerve; Spinal Cord; Strychnine; Valerates | 1972 |
Treatment of the blastic phase of chronic myeloid leukaemia. A question to solve.
Topics: Adult; Antineoplastic Agents; Child; Cytarabine; Glycine; Humans; Hydroxyurea; Leukemia, Myeloid; Purines; Remission, Spontaneous; Sulfides; Valerates; Vincristine | 1972 |
Photochemistry of biological molecules. I. Photolysis of amino acids in the solid state.
Topics: Alanine; Amino Acids; Aminobutyrates; Aminoisobutyric Acids; Crystallization; Deuterium; Electron Spin Resonance Spectroscopy; Free Radicals; Glycine; Isoleucine; Radiation; Radiation Effects; Ultraviolet Rays; Valerates; Valine | 1967 |
Depolarization of dorsal root ganglia in the cat by GABA and related amino acids: antagonism by picrotoxin and bicuculline.
Topics: Action Potentials; Alanine; Alkaloids; Aminobutyrates; Animals; Cats; Ganglia, Spinal; Glutamates; Glycine; Isoquinolines; Neural Inhibition; Picrotoxin; Spinal Nerve Roots; Strychnine; Sulfonic Acids; Synaptic Transmission; Valerates | 1972 |
[Electroencephalography studies on the actions of hypnotic agents. 2. effects of various hypnotic agents on electrical activity of the lower brain stem of rabbits].
Topics: Amides; Animals; Brain Stem; Bromine; Electric Stimulation; Electrodes, Implanted; Electroencephalography; Evoked Potentials; Eye Movements; Glycine; Hippocampus; Hypnotics and Sedatives; Male; Pentobarbital; Phthalic Acids; Rabbits; Reserpine; Sleep; Sleep Stages; Sleep, REM; Urea; Valerates | 1973 |
Molecular orbital studies of the conformation around the 5 position in angiotensin II.
Topics: Alanine; Aminobutyrates; Angiotensin II; Chemical Phenomena; Chemistry, Physical; Cyclohexanes; Cyclopentanes; Glycine; Isoleucine; Molecular Conformation; Norleucine; Valerates; Valine | 1974 |
Effects of GABA, imidazoleacetic acid, and related substances on conductance of crayfish abdominal stretch receptor.
Topics: Acetates; Alanine; Aminobutyrates; Aminocaproates; Animals; Astacoidea; Electric Conductivity; Glycine; Imidazoles; Mechanoreceptors; Valerates | 1973 |
Proceedings: Effect of drugs on antibody formation. VII. Tumor immunity.
Topics: Amino Acids, Sulfur; Animals; Antibody Formation; Glycine; Mice; Neoplasms, Experimental; Valerates | 1974 |
Combined use of gas chromatography, mass spectrometry, and computer in diagnosis and studies of metabolic disorders.
Topics: Adult; Biopsy; Blood Chemical Analysis; Butyrates; Carbon Dioxide; Chemistry, Clinical; Chromatography, Gas; Computers; Diagnosis, Computer-Assisted; Female; Glycine; Humans; Infant; Infant, Newborn; Ligases; Male; Malonates; Mass Spectrometry; Metabolic Diseases; Metabolism, Inborn Errors; Methods; Pentanols; Pyrrolidonecarboxylic Acid; Valerates | 1972 |
Diffusion of anti-tumor drugs through membranes from hydrophilic methacrylate gels.
Topics: Acrylates; Acrylic Resins; Antineoplastic Agents; Diffusion; Fluorouracil; Glycine; Membranes, Artificial; Mercaptopurine; Methacrylates; Polyhydroxyethyl Methacrylate; Purines; Sulfides; Tegafur; Valerates | 1974 |
On the regulation of the formation of the pantothenate transport system during the growth of Pseudomonas fluorescens P-2.
Topics: Biological Transport, Active; Carbon Isotopes; Citric Acid Cycle; Densitometry; Formates; Glycine; Glycolates; Glyoxylates; Malates; Pantothenic Acid; Pseudomonas; Pseudomonas fluorescens; Time Factors; Valerates | 1972 |
Possible occurrence of a succinate-glycine cycle in Rhodospirillum rubrum.
Topics: Amino Acids; Anaerobiosis; Carbon Isotopes; Cell-Free System; Chromatography; Esterases; Glutamates; Glutarates; Glycine; Levulinic Acids; Lyases; Oxidoreductases; Photosynthesis; Rhodospirillum; Rhodospirillum rubrum; Succinates; Valerates | 1972 |
[Antineoplastic agents. 48. Microbial catabolites of the ethyl esters of N-( -(6-purinylithio)-valeryl)-glycine, -diglycine and triglycine and their corresponding acids].
Topics: Amino Acids; Amino Alcohols; Antineoplastic Agents; Aspergillus nidulans; Bacillus cereus; Biotransformation; Chromatography, Paper; Chromatography, Thin Layer; Escherichia coli; Esters; Ethanol; Glycine; Purines; Sulfides; Valerates | 1972 |
On the mode of action of hypoglycin A. 3. Isolation and identification of cis-4-decene-1,10-dioic, cis, cis-4,7-decadiene-1,10-dioic, cis-4-octene-1,8-dioic, glutaric, and adipic acids, N-(methylenecyclopropyl)acetylglycine, and N-isovalerylglycine from u
Topics: Acetates; Adipates; Alanine; Animals; Carbon Isotopes; Chromatography, Gas; Chromatography, Thin Layer; Coenzyme A; Cyclopropanes; Dicarboxylic Acids; Dipeptides; Fatty Acids, Unsaturated; Glutarates; Glycine; Magnetic Resonance Spectroscopy; Male; Oxidoreductases; Rats; Valerates | 1972 |
Isovaleric acidemia: identification of isovalerate, isovalerylglycine, and 3-hydroxyisovalerate in urine of a patient previously reported as having butyric and hexanoic acidemia.
Topics: Butyrates; Caproates; Child; Chromatography, Gas; Chromatography, Thin Layer; Coenzyme A; Glycine; Humans; Mass Spectrometry; Metabolism, Inborn Errors; Valerates | 1973 |
An inherited disorder of isoleucine catabolism causing accumulation of alpha-methylacetoacetate and alpha-methyl-beta -hydroxybutyrate, and intermittent metabolic acidosis.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Butyrates; Cells, Cultured; Child; Child, Preschool; Chromatography, Gas; Chromatography, Paper; Chromatography, Thin Layer; Female; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Keto Acids; Ketones; Male; Mass Spectrometry; Mutation; Pedigree; Phenotype; Skin; Valerates | 1973 |
GABA uptake in rat brain slices: inhibition by GABA analogues and by various drugs.
Topics: Acetylation; Acylation; Aminobutyrates; Animals; Aspartic Acid; Betaine; Brain; Brain Chemistry; Chlorine; Choline; Esters; Fatty Acids; Fluorine; Glutamates; Glycine; Hydroxylation; Imidazoles; In Vitro Techniques; Methylation; Rats; Sulfur; Tritium; Valerates | 1973 |
Evidence of multiple and independent mechanisms for the action of hypoglycin in vivo.
Topics: Alanine; Animals; Blood Glucose; Body Weight; Carbon Isotopes; Chromatography, Thin Layer; Coenzyme A; Cyclopropanes; Esters; Fasting; Glycine; Male; Oxidation-Reduction; Oxidoreductases; Rats; Valerates | 1973 |
Metabolism of omega-amino acids by rat tissues in vitro.
Topics: Alanine; Amino Acids; Aminobutyrates; Aminocaproates; Aminoisobutyric Acids; Animals; Brain; Caprylates; Cyclohexanecarboxylic Acids; Glycine; Intestinal Mucosa; Kidney; Kinetics; Liver; Male; Methionine; Pyridoxal Phosphate; Rats; Schiff Bases; Spectrophotometry, Ultraviolet; Valerates; Valine | 1973 |
Child with a defect in leucine metabolism associated with beta-hydroxyisovaleric aciduria and beta-methylcrotonylglycinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Creatinine; Crotonates; Glycine; Humans; Infant; Leucine; Male; Pentanols; Pneumonia; Valerates | 1973 |
The specificity of glycine-N-acylase and acylglycine excretion in the organicacidaemias.
Topics: Acetyl Coenzyme A; Acyltransferases; Amino Acid Metabolism, Inborn Errors; Animals; Benzoates; Butyrates; Cattle; Chromatography, Gel; Chromatography, Ion Exchange; Computers; Crotonates; Glycine; Kinetics; Malonates; Mitochondria, Liver; Propionates; Regression Analysis; Spectrophotometry; Spectrophotometry, Ultraviolet; Valerates | 1974 |
-cyanoamino acids and related nitriles as inhibitors of glutamate decarboxylase.
Topics: Acetates; Amino Acids; Aminobutyrates; Animals; Carbon Isotopes; Carboxy-Lyases; Chickens; Cyanides; Depression; Escherichia coli; Glutamate Dehydrogenase; Glutarates; Glycine; Humans; Hypnotics and Sedatives; Infrared Rays; Kinetics; Nitriles; Propionates; Pyridoxal Phosphate; Seizures; Spectrophotometry; Structure-Activity Relationship; Succinates; Valerates | 1971 |
Aerobic metabolism of -amino-n-butyric acid by Pseudomonas putida.
Topics: Acetoacetates; Acyltransferases; Aerobiosis; Alanine; Amines; Aminobutyrates; Aminocaproates; Aminoisobutyric Acids; Cell-Free System; Chromatography, Paper; Coenzyme A; Deamination; Electrophoresis; Glycine; Glyoxylates; Isocitrate Dehydrogenase; Lyases; Lysine; Malates; Models, Biological; Paper; Pseudomonas; Pyruvates; Spectrophotometry; Stereoisomerism; Succinates; Transaminases; Valerates | 1971 |
Mechanism of action of guinea pig liver transglutaminase. 8. Active site studies with "reporter" group-labeled halomethyl ketones.
Topics: Acetophenones; Acyltransferases; Animals; Binding Sites; Bromine; Calcium Chloride; Carbon Isotopes; Catalysis; Chemical Phenomena; Chemistry; Chromatography, Thin Layer; Edetic Acid; Glutamine; Glycine; Guinea Pigs; Kinetics; Liver; Mathematics; Nitrophenols; Protein Binding; Spectrophotometry; Stereoisomerism; Sulfhydryl Compounds; Ultraviolet Rays; Valerates | 1971 |
Isovaleric and -methylbutyric acidemias induced by hypoglycin A: mechanism of Jamaican vomiting sickness.
Topics: Animals; Blood Glucose; Butyrates; Cyclopropanes; Fruit; Glutarates; Glycine; Leucine; Male; Plant Extracts; Rats; Valerates | 1972 |
Specificity of Aeromonas aminopeptidase toward amino acid amides and dipeptides.
Topics: Aeromonas; Alanine; Amides; Amino Acids; Aminocaproates; Aminopeptidases; Dipeptides; Glycine; Isoleucine; Kinetics; Leucine; Methionine; Phenylalanine; Structure-Activity Relationship; Tryptophan; Tyrosine; Valerates; Valine | 1972 |
The identification of tiglylglycine in the urine of a child with -methylcrotonylglycinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Butyrates; Child; Chromatography, Gas; Chromatography, Thin Layer; Coenzyme A; Diet Therapy; Dietary Proteins; Glycine; Humans; Hydro-Lyases; Male; Mass Spectrometry; Valerates | 1972 |
Beta-methylcrotonyl-CoA carboxylase deficiency: a new metabolic error in leucine degradation.
Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Bronchopneumonia; Butyrates; Carbon Dioxide; Carbon-Carbon Ligases; Chromatography, Gas; Diet Therapy; Female; Glycine; Humans; Infant; Leucine; Ligases; Mass Spectrometry; Neurologic Manifestations; Odorants; Pentanols; Valerates | 1972 |
Maintenance of nitrogen balance in a young woman by substitution of -ketoisovaleric acid for valine.
Topics: Adolescent; Amino Acids; Body Weight; Citrates; Diet; Dietary Proteins; Eggs; Feces; Female; Glycine; Humans; Keto Acids; Metabolism; Nitrogen; Quaternary Ammonium Compounds; Stimulation, Chemical; Valerates; Valine | 1971 |
Investigation on the mechanism of acylase-I-catalyzed acylamino acid hydrolysis.
Topics: Acetates; Amidohydrolases; Amino Acids; Benzoates; Bromine; Catalysis; Chlorine; Ethers; Glycine; Kinetics; Mathematics; Nitrobenzenes; Phenylacetates; Propionates; Structure-Activity Relationship; Valerates | 1971 |
Preliminary clinical trial with a purine analogue butocine.
Topics: Antineoplastic Agents; Bronchial Neoplasms; Carcinoma, Bronchogenic; Drug Tolerance; Glycine; Humans; Leukemia; Leukemia, Myeloid; Leukemia, Myeloid, Acute; Mercaptopurine; Purines; Sulfides; Valerates | 1971 |
[The metabolism of alanin, glycine and arginine in uredospores of Puccinia graminis var. tritici during germination].
Topics: Alanine; Amino Acids; Arginine; Basidiomycota; Carbon Dioxide; Carbon Isotopes; Chromatography, Paper; Glucose; Glycine; Guanidines; Spores; Valerates | 1969 |
Effects of omega-amino acids and related compounds on staphylococcal infections in mice: a combined prophylactic-therapeutic procedure.
Topics: Alanine; Amino Acids; Aminobutyrates; Aminocaproates; Animals; Culture Media; Cyclohexanecarboxylic Acids; Cysteine; Dipeptides; Female; Glycine; Histidine; Hydroxybutyrates; Injections, Subcutaneous; Mice; Staphylococcal Infections; Staphylococcus; Sulfinic Acids; Taurine; Valerates | 1970 |
Role of kidney arginase in variations of the arginine requirement of chicks.
Topics: Aminoisobutyric Acids; Animals; Arginase; Arginine; Chickens; Feeding Behavior; Glycine; Kidney; Nutritional Requirements; Threonine; Time Factors; Urea; Valerates | 1970 |
Influx of glutamic acid in peripheral nerve--characteristics in influx.
Topics: Aminobutyrates; Animals; Anura; Aspartic Acid; Carbon Dioxide; Carbon Isotopes; Chromatography; Extracellular Space; Glutamates; Glutamine; Glycine; In Vitro Techniques; Ketoglutaric Acids; Lysine; Metabolic Clearance Rate; Radiochemistry; Sciatic Nerve; Valerates | 1968 |
Analysis of glycine actions on spinal interneurones by intracellular recording.
Topics: Aminocaproates; Animals; Cats; Electrophysiology; Glycine; Interneurons; Membrane Potentials; Spinal Cord; Synapses; Valerates | 1968 |
Metabolism of amino acids in Agrobacterium tumefaciens. II. Uptake of L-valine by growing cells.
Topics: Amino Acids; Carbon Isotopes; Chloramphenicol; Glutamates; Glycine; Hydroxylamines; Puromycin; Rhizobium; Valerates; Valine | 1967 |
Uptake of L-histidine alone and in the presence of other amino acids by carcinogen-induced sarcomas of the rat in vitro.
Topics: Alanine; Amino Acids; Aminobutyrates; Aminocaproates; Animals; Benz(a)Anthracenes; Brain; Carcinogens; Glycine; Histidine; In Vitro Techniques; Intestinal Mucosa; Kidney; Male; Neoplasm Transplantation; Rats; Sarcoma, Experimental; Spleen; Testis; Valerates | 1967 |
Glycine in acute management of isovalericacidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Female; Glycine; Humans; Infant; Leucine; Oxidoreductases; Valerates | 1980 |
Hyperammonaemia in a preterm infant with isovaleric acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Female; Glycine; Hemiterpenes; Humans; Infant, Newborn; Infant, Premature; Pentanoic Acids; Valerates | 1984 |
Capillary gas chromatographic/mass spectrometric analysis of abnormal metabolites in hypoglycin-treated rat urine.
Topics: Adipates; Animals; Cyclopropanes; Dicarboxylic Acids; Gas Chromatography-Mass Spectrometry; Glucuronates; Glucuronic Acid; Glucuronidase; Glycine; Hydroxy Acids; Hypoglycins; Isoleucine; Male; Rats; Rats, Inbred Strains; Valerates; Valine | 1984 |
The identification and the excretion pattern of isovaleryl glucuronide in the urine of patients with isovaleric acidemia.
Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Glucuronates; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates | 1984 |
L-carnitine therapy in isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromatography, Ion Exchange; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Male; Mass Spectrometry; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1984 |
A combined defect of three mitochondrial carboxylases presenting as biotin-responsive 3-methylcrotonyl glycinuria and 3-hydroxyisovaleric aciduria.
Topics: Acidosis; Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Child, Preschool; Crotonates; Female; Fibroblasts; Glycine; Humans; Hydroxy Acids; Ligases; Mitochondria; Propionates; Pyruvate Carboxylase Deficiency Disease; Valerates | 1980 |
Isovaleric acidaemia presenting with dwarfism, cataract and congenital abnormalities.
Topics: Abnormalities, Multiple; Amino Acid Metabolism, Inborn Errors; Cataract; Child; Dwarfism; Female; Glycine; Hemiterpenes; Humans; Intellectual Disability; Pentanoic Acids; Valerates | 1982 |
Biosynthesis of 5-aminolevulinic acid and heme from 4,5-dioxovalerate in the rat.
Topics: Aminolevulinic Acid; Anemia, Hemolytic; Animals; Glycine; Heme; Levulinic Acids; Liver; Male; Phenylhydrazines; Rats; Rats, Inbred Strains; Valerates | 1983 |
Non-ketotic C6-C10-dicarboxylic aciduria: biochemical investigations of two cases.
Topics: Adipates; Caproates; Caprylates; Child, Preschool; Chromatography, Gas; Decanoic Acids; Dicarboxylic Acids; Fatty Acid Desaturases; Fatty Acids; Glycine; Humans; Hydroxy Acids; Hydroxybutyrates; Hypoglycemia; Infant; Lipid Metabolism, Inborn Errors; Male; Mass Spectrometry; Valerates | 1980 |
Biosynthesis of porphyrins and heme from gamma, delta-dioxovalerate by intact hepatocytes.
Topics: Alanine; Aminolevulinic Acid; Animals; Cells, Cultured; Glycine; Heme; Keto Acids; Levulinic Acids; Liver; Male; Porphyrins; Rats; Succinates; Succinic Acid; Valerates | 1981 |
Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Hydroxybutyrates; Leucine; Pentanoic Acids; Valerates | 1982 |
[Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidation-Reduction; Pentanoic Acids; Valerates | 1982 |
The antagonism of the toxicity of hypoglycin by glycine.
Topics: Animals; Blood Glucose; Body Temperature; Cyclopropanes; Fatty Acids, Volatile; Gluconeogenesis; Glycine; Hemiterpenes; Hypoglycins; Kinetics; Liver; Male; Pentanoic Acids; Rats; Rats, Inbred Strains; Valerates | 1981 |
Antagonistic effects of isovalerate and glycine on plasma choline levels in rabbits.
Topics: Animals; Choline; Glycine; Male; Rabbits; Serine; Valerates | 1980 |
Partial methylcrotonyl-coenzyme A carboxylase deficiency in an infant with failure to thrive, gastrointestinal dysfunction, and hypertonia.
Topics: Biotin; Carbon-Carbon Ligases; Failure to Thrive; Gastrointestinal Diseases; Glycine; Humans; Infant; Ligases; Male; Metabolism, Inborn Errors; Muscle Hypertonia; Valerates | 1993 |
3-Hydroxyisovalerylcarnitine in patients with deficiency of 3-methylcrotonyl CoA carboxylase.
Topics: Carbon-Carbon Ligases; Carnitine; Child, Preschool; Female; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Ligases; Male; Valerates | 1995 |
Isolated (biotin-resistant) 3-methylcrotonyl-CoA carboxylase deficiency: four sibs devoid of pathology.
Topics: Carbon-Carbon Ligases; Carnitine; Child; Child, Preschool; Dietary Proteins; Female; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant; Ligases; Male; Valerates | 1995 |
Isolated 3-methylcrotonyl-CoA carboxylase deficiency: evidence for an allele-specific dominant negative effect and responsiveness to biotin therapy.
Topics: Alleles; Base Sequence; Biotin; Carbon-Carbon Ligases; DNA Mutational Analysis; Dose-Response Relationship, Drug; Fibroblasts; Gene Expression; Genetic Vectors; Germany; Glycine; Greece; Humans; Infant, Newborn; Male; Mitochondrial Diseases; Molecular Sequence Data; Mutation; Reverse Transcriptase Polymerase Chain Reaction; Sequence Analysis, DNA; Transfection; Valerates | 2004 |
2-ethylhydracrylic aciduria in short/branched-chain acyl-CoA dehydrogenase deficiency: application to diagnosis and implications for the R-pathway of isoleucine oxidation.
Topics: Biomarkers; Butyrates; Butyryl-CoA Dehydrogenase; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant, Newborn; Isoleucine; Mutation; Oxidation-Reduction; Stereoisomerism; Valerates | 2005 |
Consanguineous 3-methylcrotonyl-CoA carboxylase deficiency: early-onset necrotizing encephalopathy with lethal outcome.
Topics: Carbon-Carbon Ligases; Consanguinity; Diagnosis, Differential; Fatal Outcome; Glycine; Humans; Infant; Infant, Newborn; Leukoencephalitis, Acute Hemorrhagic; Male; Metabolism, Inborn Errors; Mutation; RNA Splice Sites; Valerates | 2005 |
Isolated 3-methylcrotonyl-coenzyme A carboxylase deficiency in a child with metabolic stroke.
Topics: Amino Acid Metabolism, Inborn Errors; Carbon-Carbon Ligases; Child, Preschool; Glycine; Humans; Male; Phenotype; Stroke; Valerates | 2006 |
Two step derivatization for the analyses of organic, amino acids and glycines on filter paper plasma by GC-MS/SIM.
Topics: Amino Acids; Blood Specimen Collection; Filtration; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant; Infant, Newborn; Lactic Acid; Orotic Acid; Valerates | 2007 |
2-Methylbutyryl-coenzyme A dehydrogenase deficiency: functional and molecular studies on a defect in isoleucine catabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Butyryl-CoA Dehydrogenase; Cells, Cultured; Child; Child, Preschool; Female; Genotype; Glycine; Humans; Infant; Isoleucine; Male; Metabolism; Valerates | 2008 |
Study of patients and carriers with 2-methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency: difficulties in the diagnosis.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Alcohol Oxidoreductases; Amino Acid Metabolism, Inborn Errors; Female; Glycine; Heredodegenerative Disorders, Nervous System; Humans; Hydroxybutyrates; Infant; Infant, Newborn; Male; Valerates | 2009 |
New urea-based surfactants derived from alpha,omega-amino acids.
Topics: Alanine; Amino Acids; Calorimetry; Electric Conductivity; Ethanolamines; Glycine; Organophosphates; Spectroscopy, Fourier Transform Infrared; Structure-Activity Relationship; Surface Properties; Surface-Active Agents; Urea; Valerates | 2009 |
3-Methylcrotonyl-CoA carboxylase deficiency: phenotypic variability in a family.
Topics: Adult; Brain; Carbon-Carbon Ligases; Carnitine; Cells, Cultured; Child, Preschool; DNA Mutational Analysis; Epilepsy; Fibroblasts; Gene Deletion; Genetic Predisposition to Disease; Genetic Testing; Genotype; Glycine; Humans; Infant; Language Development Disorders; Male; Mutation; Phenotype; Valerates | 2009 |
Striatum is more vulnerable to oxidative damage induced by the metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency as compared to liver.
Topics: Animals; Corpus Striatum; Glutarates; Glutathione; Glycine; Humans; Liver; Male; Meglutol; Oxidative Stress; Oxo-Acid-Lyases; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances; Valerates | 2009 |
Uneventful clinical courses of Korean patients with methylcrotonylglycinuria and their common mutations.
Topics: Asian People; Carbon-Carbon Ligases; Child; Child, Preschool; Disease Progression; Female; Glycine; Humans; Infant; Infant, Newborn; Male; Mutation; Republic of Korea; Urea Cycle Disorders, Inborn; Valerates | 2012 |
Diagnostic dilemma of patients with methylmalonic aciduria: Experience from a tertiary care centre in Pakistan.
Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Citrates; Cross-Sectional Studies; Female; Glycine; Humans; Infant; Lactic Acid; Male; Methionine; Mitochondrial Diseases; Pakistan; Tertiary Care Centers; Urinalysis; Valerates; Vitamin B 12 Deficiency | 2018 |