Page last updated: 2024-09-02

valerates and biotin

valerates has been researched along with biotin in 47 studies

Compound Research Comparison

Studies
(valerates)
Trials
(valerates)
Recent Studies (post-2010)
(valerates)
Studies
(biotin)
Trials
(biotin)
Recent Studies (post-2010) (biotin)
2,25129445714,847953,882

Protein Interaction Comparison

ProteinTaxonomyvalerates (IC50)biotin (IC50)
nonstructural protein 1Influenza A virus (A/California/07/2009(H1N1))0.2

Research

Studies (47)

TimeframeStudies, this research(%)All Research%
pre-199017 (36.17)18.7374
1990's10 (21.28)18.2507
2000's15 (31.91)29.6817
2010's4 (8.51)24.3611
2020's1 (2.13)2.80

Authors

AuthorsStudies
Slyter, LL; Weaver, JM1
Fukuda, H; Izumi, Y; Ogata, K; Tani, Y1
Keeton, BR1
Mock, DM; Mock, NI1
Jackson, H; Lankford, GL; Mock, DM; Mock, NI; Weintraub, ST1
Holme, E; Jacobson, CE; Kristiansson, B1
Mock, DM; Mock, NI; Weintraub, S1
Baker, H; Baswell, DL; Holman, RT; Mock, DM; Sweetman, L1
Erasmus, C; Mienie, LJ; Reinecke, CJ; Wadman, SK1
Draffan, GH; Gompertz, D; Hull, D; Watts, JL1
Heiling, MS; Israsena, S; Perlman, D; Williams, C; Wormser, HC1
Gompertz, D1
Bartlett, K; Blair, D; Gompertz, D; Stern, CM1
Eldjarn, L; Jellum, E; Pande, H; Stokke, O; Waaler, PE1
Apitz-Castro, R; Lynen, F; Rehn, K1
Bartlett, K; Leonard, JV; Ng, H1
Sweetman, L1
Bergstrøm, T; Greter, J; Levin, AH; Steen, G; Tryding, N; Wass, U1
Berry, SA; Nyhan, WL; Thuy, LP; Tuchman, M1
Baumgartner, ER; Lehnert, W; Niederhoff, H; Suormala, T1
Bishop, WP; Malik, MI; Mock, DM; Mock, NI; Stumbo, PJ1
Mock, DM; Mock, NI; Stadler, DD; Stratton, SL1
Mock, DM; Stadler, DD1
Dyken, ME; Mock, DM1
Engelbrecht, V; Gärtner, J; Lenard, HG; Lohmeier, K; Schürmann, M; Wendel, U1
Lombard, KA; Mock, DM; Mock, NI; Nelson, RP1
Mock, DM1
Helm, RM; Mock, DM; Mock, NI; Simpson, P1
Mock, DM; Mock, NI; Quirk, JG1
Boylan, J; Cannon, MJ; Cederbaum, S; Cress, S; Jennings, ML; Mardach, R; Mock, DM; Roth, S; Wolf, B; Zempleni, J1
Carnell, N; Henrich, CL; Mock, DM; Mock, NI1
Aoki, Y; Baumgartner, ER; Duran, M; Muhle, H; Santer, R; Stephani, U; Suormala, T; Suzuki, Y; Yang, X1
Almashanu, S; Baumgartner, ER; Baumgartner, MR; Dantas, MF; Fowler, B; Friebel, D; Gebhardt, B; Giunta, C; Hoffmann, GF; Suormala, T; Valle, D1
Mock, DM; Sealey, WM; Stratton, SL; Teague, AM1
Fukui, T; Kumasaka, K1
Ebara, S; Fukui, T; Oguchi, K; Watanabe, T1
Abel, H; Flachowsky, G; Lebzien, P; Schröder, B1
Bogusiewicz, A; Mock, DM; Mock, MM; Mock, NI; Stratton, SL; Wells, AM1
Ferreira, G; Weiss, WP; Willett, LB1
López-Rosas, I; Rodríguez-Fuentes, N; Román-Cisneros, G; Velázquez-Arellano, A1
Ebara, S; Fukui, T; Kimura, S; Nagai, Y; Taniguchi, A; Watanabe, T1
Barshop, BA; Gangoiti, J; Nyhan, WL; Willis, M1
Boysen, G; Horvath, TD; Matthews, NI; Mock, DM; Stratton, SL1
Bogusiewicz, A; Boysen, G; Dawson, AM; Henrich, CL; Horvath, TD; Matthews, NI; Mock, DM; Moran, JH; Owen, SN; Spencer, HJ; Stratton, SL1
Caudill, MA; Gayle, A; Jiang, X; Lucas, LK; Malysheva, O; Perry, CA; West, AA; Yan, J1
Nakamura, T; Shibata, K; Tsuji, A1
Deng, Z; He, H; Hong, Q; Liu, S; Luo, X; Zhang, Y; Zheng, X1

Reviews

3 review(s) available for valerates and biotin

ArticleYear
Inborn errors of organic acid metabolism.
    Clinics in endocrinology and metabolism, 1974, Volume: 3, Issue:1

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Biotin; Carboxylic Acids; Chromatography, Gas; Coenzyme A; Crotonates; Female; Gestational Age; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Infant, Newborn; Isomerases; Leucine; Male; Malonates; Metabolism, Inborn Errors; Pedigree; Pregnancy; Prenatal Diagnosis; Propionates; Pyrrolidonecarboxylic Acid; Valerates; Vitamin B 12

1974
Biotin status: which are valid indicators and how do we know?
    The Journal of nutrition, 1999, Volume: 129, Issue:2S Suppl

    Topics: Animals; Biotin; Female; Humans; Nutritional Status; Pregnancy; Valerates

1999
[Biotin (vitamin H)].
    Nihon rinsho. Japanese journal of clinical medicine, 2004, Volume: 62 Suppl 12

    Topics: Biological Assay; Biomarkers; Biotin; Biotinidase; Biotinidase Deficiency; Dermatitis, Atopic; Epilepsies, Partial; Humans; Reference Values; Specimen Handling; Valerates

2004

Trials

3 trial(s) available for valerates and biotin

ArticleYear
Marginal biotin deficiency during normal pregnancy.
    The American journal of clinical nutrition, 2002, Volume: 75, Issue:2

    Topics: Adult; Biotin; Deficiency Diseases; Female; Humans; Pregnancy; Pregnancy Complications; Valerates

2002
Lymphocyte propionyl-CoA carboxylase and its activation by biotin are sensitive indicators of marginal biotin deficiency in humans.
    The American journal of clinical nutrition, 2006, Volume: 84, Issue:2

    Topics: Adult; Analysis of Variance; Biomarkers; Biotin; Cross-Over Studies; Deficiency Diseases; Female; Humans; Lymphocytes; Male; Methylmalonyl-CoA Decarboxylase; Nutrition Assessment; Nutritional Status; Sensitivity and Specificity; Valerates

2006
Pregnancy and lactation alter biomarkers of biotin metabolism in women consuming a controlled diet.
    The Journal of nutrition, 2014, Volume: 144, Issue:12

    Topics: Adult; Biomarkers; Biotin; Carbon-Carbon Ligases; Carnitine; Choline; Chromatography, Liquid; Diet; Dietary Supplements; Female; Humans; Lactation; Leucine; Milk, Human; New York; Patient Compliance; Pregnancy; Tandem Mass Spectrometry; Valerates; Young Adult

2014

Other Studies

41 other study(ies) available for valerates and biotin

ArticleYear
Tetrahydrofolate and other growth requirements of certain strains of Ruminococcus flavefaciens.
    Applied and environmental microbiology, 1977, Volume: 33, Issue:2

    Topics: Acetates; Amino Acids; Ammonia; Animals; Biotin; Butyrates; Carbon Dioxide; Cattle; Culture Media; Cysteine; Peptococcaceae; Rumen; Tetrahydrofolates; Thiamine; Valerates

1977
Action of 5-(2-thienyl)valeric acid as a biotin antagonist.
    Biochimica et biophysica acta, 1977, Sep-29, Volume: 499, Issue:2

    Topics: Biotin; Pentanoic Acids; Rhodotorula; Thiophenes; Valerates

1977
Organic aciduria. Treatable cause of floppy infant syndrome.
    Archives of disease in childhood, 1976, Volume: 51, Issue:8

    Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Crotonates; Female; Humans; Infant; Infant, Newborn; Ligases; Muscle Tonus; Muscular Diseases; Valerates

1976
Biotin deficiency in rats: disturbances of leucine metabolism are detectable early.
    The Journal of nutrition, 1992, Volume: 122, Issue:7

    Topics: Animals; Biotin; Gas Chromatography-Mass Spectrometry; Leucine; Male; Rats; Rats, Inbred Strains; Valerates

1992
Quantification of urinary 3-hydroxyisovaleric acid using deuterated 3-hydroxyisovaleric acid as internal standard.
    Biomedical & environmental mass spectrometry, 1989, Volume: 18, Issue:9

    Topics: Animals; Biotin; Deuterium; Gas Chromatography-Mass Spectrometry; Magnetic Resonance Spectroscopy; Rats; Reference Standards; Valerates

1989
Biotin-responsive multiple carboxylase deficiency in an 8-year-old boy with normal serum biotinidase and fibroblast holocarboxylase-synthetase activities.
    Journal of inherited metabolic disease, 1988, Volume: 11, Issue:3

    Topics: Amidohydrolases; Biotin; Biotinidase; Carbon-Nitrogen Ligases; Child; Fibroblasts; Glycine; Humans; Kinetics; Ligases; Male; Multiple Carboxylase Deficiency; Valerates

1988
Abnormal organic aciduria in biotin deficiency: the rat is similar to the human.
    The Journal of laboratory and clinical medicine, 1988, Volume: 112, Issue:2

    Topics: Animals; Biotin; Disease Models, Animal; Gas Chromatography-Mass Spectrometry; Glycine; Male; Random Allocation; Rats; Rats, Inbred Strains; Valerates

1988
Biotin deficiency complicating parenteral alimentation: diagnosis, metabolic repercussions, and treatment.
    The Journal of pediatrics, 1985, Volume: 106, Issue:5

    Topics: Alopecia; Biotin; Citrates; Diagnosis, Differential; Erythema; Fatty Acids, Essential; Female; Glycine; Humans; Infant; Isomerism; Lactates; Lactic Acid; Male; Nervous System Diseases; Parenteral Nutrition; Valerates; Zinc

1985
Organic aciduria in late-onset biotin-responsive multiple carboxylase deficiency.
    Journal of inherited metabolic disease, 1985, Volume: 8 Suppl 2

    Topics: Biotin; Carbon-Carbon Ligases; Carboxy-Lyases; Female; Humans; Infant; Lactates; Lactic Acid; Ligases; Methylmalonyl-CoA Decarboxylase; Pyruvate Carboxylase Deficiency Disease; Valerates

1985
Biotin-responsive beta-methylcrotonylglycinuria.
    Lancet (London, England), 1971, Jul-03, Volume: 2, Issue:7714

    Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Chromatography, Gas; Fatty Acids; Glycine; Humans; Infant; Leucine; Male; Partial Pressure; Valerates; Valine; Vomiting

1971
Synthesis and growth-promoting activity of dl-cis-hexahydro-4-(4-carboxybutyl)-2-cyclopentimidazolone: carbobiotin.
    Journal of pharmaceutical sciences, 1972, Volume: 61, Issue:7

    Topics: Biotin; Chromatography, Thin Layer; Cyclopentanes; Growth; Imidazoles; Infrared Rays; Ketones; Lactobacillus; Mitosporic Fungi; Saccharomyces cerevisiae; Spectrum Analysis; Ultraviolet Rays; Valerates

1972
Child with a defect in leucine metabolism associated with beta-hydroxyisovaleric aciduria and beta-methylcrotonylglycinuria.
    Archives of disease in childhood, 1973, Volume: 48, Issue:12

    Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Creatinine; Crotonates; Glycine; Humans; Infant; Leucine; Male; Pentanols; Pneumonia; Valerates

1973
Beta-methylcrotonyl-CoA carboxylase deficiency: a new metabolic error in leucine degradation.
    Pediatrics, 1972, Volume: 49, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Bronchopneumonia; Butyrates; Carbon Dioxide; Carbon-Carbon Ligases; Chromatography, Gas; Diet Therapy; Female; Glycine; Humans; Infant; Leucine; Ligases; Mass Spectrometry; Neurologic Manifestations; Odorants; Pentanols; Valerates

1972
[Beta methylcrotonyl-CoA-carboxylase. Crystallization and some physical properties].
    European journal of biochemistry, 1970, Volume: 16, Issue:1

    Topics: Alcaligenes; Aspartic Acid; Biotin; Butyrates; Calcium Phosphates; Chromatography, DEAE-Cellulose; Chromatography, Gel; Coenzyme A; Crystallization; Culture Media; Diffusion; Electrophoresis; Glutamates; Hydrogen-Ion Concentration; Ligases; Microscopy, Electron; Molecular Weight; Ultracentrifugation; Valerates

1970
A combined defect of three mitochondrial carboxylases presenting as biotin-responsive 3-methylcrotonyl glycinuria and 3-hydroxyisovaleric aciduria.
    Clinica chimica acta; international journal of clinical chemistry, 1980, Jan-15, Volume: 100, Issue:2

    Topics: Acidosis; Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Child, Preschool; Crotonates; Female; Fibroblasts; Glycine; Humans; Hydroxy Acids; Ligases; Mitochondria; Propionates; Pyruvate Carboxylase Deficiency Disease; Valerates

1980
Two forms of biotin-responsive multiple carboxylase deficiency.
    Journal of inherited metabolic disease, 1981, Volume: 4, Issue:2

    Topics: Acute Disease; Biotin; Carbon-Carbon Ligases; Chronic Disease; Fibroblasts; Humans; Hydroxy Acids; Infant; Lactates; Lactic Acid; Ligases; Lymphocytes; Pyruvate Carboxylase Deficiency Disease; Valerates

1981
Propionyl-CoA carboxylase deficiency: case report, effect of low-protein diet and identification of 3-oxo-2-methylvaleric acid 3-hydroxy-2-methylvaleric acid, and maleic acid in urine.
    Scandinavian journal of clinical and laboratory investigation, 1981, Volume: 41, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Caproates; Carboxy-Lyases; Dietary Proteins; Female; Humans; Hydroxy Acids; Infant; Infant, Newborn; Keto Acids; Leukocytes; Maleates; Methylmalonyl-CoA Decarboxylase; Pentanoic Acids; Propionates; Reye Syndrome; Valerates

1981
Partial methylcrotonyl-coenzyme A carboxylase deficiency in an infant with failure to thrive, gastrointestinal dysfunction, and hypertonia.
    Pediatrics, 1993, Volume: 91, Issue:3

    Topics: Biotin; Carbon-Carbon Ligases; Failure to Thrive; Gastrointestinal Diseases; Glycine; Humans; Infant; Ligases; Male; Metabolism, Inborn Errors; Muscle Hypertonia; Valerates

1993
Isolated biotin-resistant 3-methylcrotonyl-CoA carboxylase deficiency: long-term outcome in a case with neonatal onset.
    European journal of pediatrics, 1996, Volume: 155, Issue:7

    Topics: Age of Onset; Biotin; Carbon-Carbon Ligases; Developmental Disabilities; Diet, Protein-Restricted; Epilepsy, Generalized; Humans; Infant, Newborn; Ligases; Male; Metabolism, Inborn Errors; Patient Compliance; Valerates

1996
Increased urinary excretion of 3-hydroxyisovaleric acid and decreased urinary excretion of biotin are sensitive early indicators of decreased biotin status in experimental biotin deficiency.
    The American journal of clinical nutrition, 1997, Volume: 65, Issue:4

    Topics: Adult; Analysis of Variance; Avidin; Biotin; Chromatography, High Pressure Liquid; Egg White; Female; Gas Chromatography-Mass Spectrometry; Humans; Male; Reference Values; Reproducibility of Results; Sensitivity and Specificity; Valerates

1997
Biotin status assessed longitudinally in pregnant women.
    The Journal of nutrition, 1997, Volume: 127, Issue:5

    Topics: Adult; Analysis of Variance; Biotin; Biotransformation; Chromatography, High Pressure Liquid; Female; Gas Chromatography-Mass Spectrometry; Humans; Longitudinal Studies; Pregnancy; Retrospective Studies; Valerates

1997
Conflicting indicators of biotin status from a cross-sectional study of normal pregnancy.
    Journal of the American College of Nutrition, 1997, Volume: 16, Issue:3

    Topics: Adult; Biotin; Case-Control Studies; Chromatography, High Pressure Liquid; Cross-Sectional Studies; Female; Gas Chromatography-Mass Spectrometry; Humans; Nutritional Status; Pregnancy; Reference Values; Valerates

1997
Biotin catabolism is accelerated in adults receiving long-term therapy with anticonvulsants.
    Neurology, 1997, Volume: 49, Issue:5

    Topics: Adolescent; Adult; Anticonvulsants; Biotin; Epilepsy; Female; Humans; Male; Middle Aged; Time Factors; Valerates

1997
Cerebral metabolic changes in biotinidase deficiency.
    Journal of inherited metabolic disease, 1997, Volume: 20, Issue:6

    Topics: Amidohydrolases; Biotin; Biotinidase; Brain; Electroencephalography; Humans; Infant; Lactic Acid; Magnetic Resonance Imaging; Male; Pyruvic Acid; Seizures; Valerates

1997
Disturbances in biotin metabolism in children undergoing long-term anticonvulsant therapy.
    Journal of pediatric gastroenterology and nutrition, 1998, Volume: 26, Issue:3

    Topics: Anticonvulsants; Biotin; Carbamazepine; Child; Female; Humans; Male; Phenobarbital; Phenytoin; Valerates

1998
Certain immune markers are not good indicators of mild to moderate biotin deficiency in rats.
    The Journal of nutrition, 2001, Volume: 131, Issue:12

    Topics: Animals; Biomarkers; Biotin; Carbon-Carbon Ligases; Cell Division; Cells, Cultured; Cytokines; Haemophilus Vaccines; Immunoglobulin G; Interferon-gamma; Interleukin-4; Killer Cells, Natural; Leukocytes, Mononuclear; Liver; Lymphocyte Activation; Lymphocyte Subsets; Lymphocytes; Male; Rats; Rats, Sprague-Dawley; Spleen; Thymus Gland; Valerates

2001
Biotin dependency due to a defect in biotin transport.
    The Journal of clinical investigation, 2002, Volume: 109, Issue:12

    Topics: Amidohydrolases; Biological Transport; Biotin; Biotinidase; Carbon-Carbon Ligases; Carboxy-Lyases; Carrier Proteins; Cell Line, Transformed; Child, Preschool; Female; Humans; Lactic Acid; Leukocytes, Mononuclear; Male; Membrane Glycoproteins; Methylmalonyl-CoA Decarboxylase; Pyruvate Carboxylase; Substance Withdrawal Syndrome; Symporters; Valerates

2002
Indicators of marginal biotin deficiency and repletion in humans: validation of 3-hydroxyisovaleric acid excretion and a leucine challenge.
    The American journal of clinical nutrition, 2002, Volume: 76, Issue:5

    Topics: Adult; Biotin; Diet; Dose-Response Relationship, Drug; Egg White; Female; Humans; Leucine; Male; Time Factors; Valerates

2002
Partial response to biotin therapy in a patient with holocarboxylase synthetase deficiency: clinical, biochemical, and molecular genetic aspects.
    Molecular genetics and metabolism, 2003, Volume: 79, Issue:3

    Topics: Age of Onset; Biotin; Carbon-Carbon Ligases; Carbon-Nitrogen Ligases; Child; DNA Mutational Analysis; Female; Genes, Recessive; Holocarboxylase Synthetase Deficiency; Humans; Methylmalonyl-CoA Decarboxylase; Mutation; Phenotype; Pyruvate Carboxylase; Reverse Transcriptase Polymerase Chain Reaction; RNA Splicing; Valerates

2003
Isolated 3-methylcrotonyl-CoA carboxylase deficiency: evidence for an allele-specific dominant negative effect and responsiveness to biotin therapy.
    American journal of human genetics, 2004, Volume: 75, Issue:5

    Topics: Alleles; Base Sequence; Biotin; Carbon-Carbon Ligases; DNA Mutational Analysis; Dose-Response Relationship, Drug; Fibroblasts; Gene Expression; Genetic Vectors; Germany; Glycine; Greece; Humans; Infant, Newborn; Male; Mitochondrial Diseases; Molecular Sequence Data; Mutation; Reverse Transcriptase Polymerase Chain Reaction; Sequence Analysis, DNA; Transfection; Valerates

2004
Smoking accelerates biotin catabolism in women.
    The American journal of clinical nutrition, 2004, Volume: 80, Issue:4

    Topics: Adult; Avidin; Biomarkers; Biotin; Carbon-Carbon Ligases; Case-Control Studies; Chromatography, High Pressure Liquid; Cohort Studies; Creatinine; Female; Humans; Male; Middle Aged; Sex Factors; Smoking; Valerates

2004
Measurement of 3-hydroxyisovaleric acid in urine of biotin-deficient infants and mice by HPLC.
    The Journal of nutrition, 2005, Volume: 135, Issue:3

    Topics: Animals; Biomarkers; Biotin; Chromatography, High Pressure Liquid; Deficiency Diseases; Humans; Infant; Male; Mice; Mice, Inbred ICR; Regression Analysis; Valerates

2005
Effects of defaunation on fermentation characteristics and biotin balance in an artificial rumen-simulation system (RUSITEC) receiving diets with different amounts and types of cereal.
    The British journal of nutrition, 2006, Volume: 95, Issue:1

    Topics: Acetates; Animal Feed; Animals; Biotin; Butyrates; Edible Grain; Eukaryota; Fatty Acids, Volatile; Fermentation; Hydrogen-Ion Concentration; Methane; Models, Biological; Poaceae; Propionates; Quaternary Ammonium Compounds; Rumen; Valerates

2006
Changes in measures of biotin status do not reflect milk yield responses when dairy cows are fed supplemental biotin.
    Journal of dairy science, 2007, Volume: 90, Issue:3

    Topics: Animals; Biotin; Cattle; Dairying; Diet; Dietary Supplements; Fatty Acids, Volatile; Female; Lactation; Milk; Rumen; Time Factors; Valerates

2007
Biotin deficiency affects both synthesis and degradation of pyruvate carboxylase in rat primary hepatocyte cultures.
    Molecular genetics and metabolism, 2007, Volume: 92, Issue:3

    Topics: Animals; Biotin; Biotinylation; Hepatocytes; Lymphocytes; Male; Methylmalonyl-CoA Decarboxylase; Pyruvate Carboxylase; Rats; Rats, Wistar; Valerates

2007
Effects of biotin deficiency on embryonic development in mice.
    Nutrition (Burbank, Los Angeles County, Calif.), 2009, Volume: 25, Issue:1

    Topics: Animals; Biotin; Chromatography, High Pressure Liquid; Congenital Abnormalities; Embryonic Development; Energy Metabolism; Female; Fetus; Gestational Age; Male; Mice; Mice, Inbred ICR; Nutritional Requirements; Pregnancy; Pregnancy Outcome; Pregnancy, Animal; Random Allocation; Valerates

2009
Positive newborn screen in the biochemically normal infant of a mother with treated holocarboxylase synthetase deficiency.
    Journal of inherited metabolic disease, 2009, Volume: 32 Suppl 1

    Topics: Adult; Biotin; Carnitine; False Positive Reactions; Female; Holocarboxylase Synthetase Deficiency; Humans; Infant, Newborn; Male; Maternal-Fetal Exchange; Neonatal Screening; Pregnancy; Pregnancy Complications; Valerates

2009
Measurement of 3-hydroxyisovaleric acid in urine from marginally biotin-deficient humans by UPLC-MS/MS.
    Analytical and bioanalytical chemistry, 2011, Volume: 401, Issue:9

    Topics: Adult; Biomarkers; Biotin; Biotinidase Deficiency; Calibration; Chromatography, Liquid; Creatinine; Egg White; Female; Humans; Male; Reference Standards; Reproducibility of Results; Sensitivity and Specificity; Tandem Mass Spectrometry; Valerates

2011
Urinary excretion of 3-hydroxyisovaleric acid and 3-hydroxyisovaleryl carnitine increases in response to a leucine challenge in marginally biotin-deficient humans.
    The Journal of nutrition, 2011, Volume: 141, Issue:11

    Topics: Adult; Biotin; Carnitine; Cohort Studies; Female; Humans; Leucine; Male; Valerates

2011
Biotin-deficient diet induces chromosome misalignment and spindle defects in mouse oocytes.
    Bioscience, biotechnology, and biochemistry, 2015, Volume: 79, Issue:2

    Topics: Animals; Biotin; Body Weight; Cell Count; Chromosome Aberrations; Diet; Eating; Estradiol; Estrous Cycle; Female; Liver; Mice; Mice, Inbred ICR; Oocytes; Organ Size; Ovary; Spindle Apparatus; Uterus; Valerates

2015
Delayed Biotin Therapy in a Child with Atypical Profound Biotinidase Deficiency: Late Arrival of the Truth and a Lesson Worth Thinking.
    International journal of molecular sciences, 2023, Jun-16, Volume: 24, Issue:12

    Topics: Biotin; Biotinidase; Biotinidase Deficiency; Humans; Valerates

2023